Ua lohe mākou a pau mai ko mākou wā kamaliʻi mai i ka maikaʻi o ka hao no ke kino, a inā nele ka hao, e loaʻa iā mākou nā maʻi. Kamaʻilio mau mākou e pili ana i ka "hemahema hao", ʻo ia hoʻi, ka anemia. Akā, ua manaʻo anei ʻoe he pilikia koʻikoʻi ka nui o ka hao i loko o ke kino? ʻAe, he ʻoiaʻiʻo. ʻO kēia kūlana ka mea a mākou e kapa nei he "hemochromatosis" a i ʻole "iron overload" wale nō i ka lāʻau lapaʻau. I kēia lā, ke kamaʻilio nei mākou e pili ana i kēia kūlana i ʻike ʻole ʻia e ka poʻe he nui, akā pono e makaʻala nā mea a pau.
He aha maoli ka Hemochromatosis?
I ka ʻōlelo maʻalahi, ʻo ia ka manawa e omo ai kou kino i ka hao mai ka meaʻai āu e ʻai ai ma mua o ka mea e pono ai. ʻO ka maʻamau, maikaʻi loa ko mākou kino i ka lawe ʻana i ka nui o ka hao e pono ai a hōʻole i ke koena. Akā i loko o kekahi me ka hemochromatosis, aia kekahi mea hewa me kēia ʻōnaehana kaohi.
No laila, ʻoiai ʻaʻohe ala e wehe ai i kēia hao keu mai ke kino, hoʻomaka ke kino e mālama iā ia i loko o nā ʻano kino like ʻole. E like me kā mākou e mālama ai i nā mea makemake ʻole ʻia ma kahi kihi o ko mākou hale. I ka hala ʻana o ka manawa, hōʻiliʻili kēia hao i loko o nā ʻano kino nui e like me ka puʻuwai, ke akepaʻa, a me ka pancreas, e hōʻino ana i kēlā mau ʻano kino. Inā ʻaʻole mālama ʻia, hiki i kēia ke hoʻoweliweli i ke ola. Akā ʻo ka mea maikaʻi loa, he kūlana hiki ke mālama ʻia a kāohi ʻia kēia.
He aha nā hōʻailona o kēia maʻi? Pehea e ʻike ʻia ai?
ʻO ka pilikia nui me kēia, ʻo ia ka lōʻihi o ka manawa e ʻike ʻia ai nā hōʻailona. ʻOiai he maʻamau kēia ʻano hānau ʻia, he mau makahiki ka lōʻihi no ke kino e hōʻiliʻili i nā pae hao ʻino. No laila, hoʻomaka ka nui o ka poʻe e ʻike i nā hōʻailona ma hope o 40 a 50 paha mau makahiki . I kekahi manawa hoʻowahāwahā ʻia kēia mau hōʻailona, me ka manaʻo he mau kūlana maʻamau ia e kū mai ana me ka ʻelemakule.
E nānā kākou i nā hōʻailona nui o kēia maʻi ma ka papa ma lalo nei.
| Hōʻailona | He wehewehe maʻalahi |
|---|---|
| Luhi mau loa | Manaʻo mau i ka luhi a me ka luhi ʻole me ke kumu ʻole. |
| ʻEha hui | ʻEha, ʻoi aku hoʻi ma nā puʻupuʻu o nā manamana lima kuhikuhi a me waena. Ua kapa ʻia hoʻi kēia he "lima hao". |
| ʻOle ke kala ʻili | Ua lilo ka ʻili i hina a keleawe paha. Me he mea lā ua puhi ʻia i ka lā. |
| ʻEha ʻōpū o luna | ʻEha ka manaʻo ma kahi o ke akepaʻa, ʻo ia hoʻi, ma ka ʻaoʻao ʻākau o luna o ka ʻōpū. |
| Nā ʻano kūlike ʻole o ka puʻuwai | Hiki ke ʻike ʻia nā loli i ka helu o ka puʻuwai a me ka ʻeha o ka umauma (arrhythmias). |
| Ua emi ka makemake moekolohe | Hiki i nā kāne a me nā wahine ke loaʻa i ka libido haʻahaʻa a i ʻole ka erectile dysfunction. |
| ʻO ka pohō kaumaha me ke kumu ʻole | Ka pohō kaumaha me ka ʻole o ka ʻai ʻana a i ʻole ka hoʻoikaika kino. |
No ke aha lā kēia e hana nei? He aha nā kumu?
Aia ʻelua mau ʻano nui o nā kumu o ka hemochromatosis.
1. Nā kumu hoʻoilina (Hereditary Hemochromatosis)
ʻO kēia ke ʻano maʻamau. I ka ʻōlelo maʻalahi, he ʻano hoʻoilina ia āu e hoʻoilina ai mai kou mau mākua mai . Aia kahi gene e kāohi ana i ka hao i loko o ko mākou kino. Ua kapa ʻia ʻo ia ʻo `(HFE gene)`. Inā he mutation (hoʻololi) i loko o kēia gene, ʻaʻole hiki i ke kino ke kāohi i ka hao.
E noʻonoʻo, i mea e ulu ai kēia maʻi, pono ʻoe e hoʻoilina i ʻelua kope o kēia gene kīnā mai kou makuahine a me kou makuakāne. Inā hoʻoilina ʻoe i hoʻokahi kope wale nō mai nā mea ʻelua, he mea lawe wale ʻoe a ʻaʻole pinepine ʻoe e loaʻa i ka maʻi. No laila, inā loaʻa i kou mau mākua kēia gene, ʻaʻole paha lākou e loaʻa i ka maʻi. ʻO nā hoʻololi genetic maʻamau ʻo `(C282Y)` a me `(H63D)`.
Eia kekahi, aia kekahi ʻano kakaikahi i kapa ʻia ʻo "Juvenile Hemochromatosis" e ʻike ʻia i ka wā ʻōpiopio, ʻo ia hoʻi, ma waena o nā makahiki 15-30. Hoʻokumu ʻia ia e nā mutations i loko o nā genes `(HJV)` a i ʻole `(HAMP)`. I loko o kēia, hikiwawe loa ka hōʻiliʻili ʻana o ka hao.
2. Hoʻokumu ʻia e nā maʻi a i ʻole nā lāʻau lapaʻau ʻē aʻe (Secondary Hemochromatosis)
Hana ʻia kēia ke piʻi aʻe ka nui o ka hao i loko o ke kino ma muli o kekahi maʻi ʻē aʻe a i ʻole kekahi lāʻau lapaʻau ʻē aʻe.
- Ka Hoʻoili Koko Pinepine: Pono nā maʻi me ka anemia e like me ka thalassemia i ka hoʻoili koko mau. Hiki ke hana ʻia kēia ʻano i ka wā e hōʻiliʻili ai ka hao i loko o ke koko i loko o ke kino.
- Maʻi Akepaʻa Mau Loa: Inā ua hōʻino nui ʻia ke akepaʻa, ʻaʻole hiki iā ia ke hoʻopili pono i ka hao.
- Ka inu nui ʻana i ka waiʻona: ʻAʻole wale ka waiʻona e hōʻino i ke akepaʻa, akā hoʻonui pū i ka omo ʻana o ke kino i ka hao.
He aha nā pilikia o ka hoʻonui nui ʻana o ka hao?
E like me kā mākou i ʻōlelo ai ma mua, he mea ʻawahia ka hao i ke kino inā ʻoi aku ia ma mua o ka nui e pono ai. ʻOiai ʻaʻohe ala e wehe ai i kēia hao keu, mālama ke kino iā ia i loko o nā ʻiʻo. ʻAʻole liʻiliʻi ka pōʻino e hiki ai i kēia ke hana.
ʻOiai he mea nui ka hao no ko kākou kino, inā nui loa ia, hana ia e like me ka mea make. No laila, he mea nui loa ka makaʻala i kēia.
Ua hoʻopilikia nui ʻia ke akepaʻa, ka puʻuwai, a me ka pancreas . Inā ʻaʻole mālama ʻia, hiki ke loaʻa nā pilikia koʻikoʻi penei:
- ʻO ka hemahema o ke akepaʻa mau loa: Hoʻokumu ʻia ka Cirrhosis e ka hōʻiliʻili hao i loko o ke akepaʻa, a hiki i ka hopena ke alakaʻi i ka hemahema piha o ke akepaʻa.
- ʻO ka hāʻule ʻana o ka puʻuwai paʻa: ʻO nā waihona hao i loko o ka ʻiʻo o ka puʻuwai e hiki ai ke hoʻonāwaliwali i ka puʻuwai a lilo i mea hiki ʻole ke pamu i ke koko kūpono i ke kino.
- Maʻi diabetes: ʻO nā waihona hao i loko o ka pancreas e hōʻino i nā hunaola e hana ana i ka insulin, hiki ke alakaʻi i ka maʻi diabetes (ʻAno 3c).
Eia kekahi, hiki ke hoʻopilikia i ka hana o ka thyroid gland, ka pituitary gland, nā adrenals, a me ka ʻōnaehana hānau.
Pehea e ʻike ai ke kauka i kēia?
Inā loaʻa iā ʻoe kekahi o nā hōʻailona i luna a i ʻole inā loaʻa i kekahi o kou ʻohana kēia maʻi, he mea nui e ʻike i kāu kauka. E nīnau mua ke kauka iā ʻoe i kekahi mau nīnau.
- Ua loaʻa anei i kou mau mākua a i ʻole kekahi o kou ʻohana ka maʻi akepaʻa a i ʻole ka hao nui?
- Ke lawe nei ʻoe i nā mea hoʻohui hao a i ʻole ka wikamina C (kahi e hoʻonui ai i ka omo ʻana o ka hao)?
- ʻEhia ka nui o ka waiʻona āu e inu ai?
A laila, hana ʻia kahi hoʻokolohua kino a, inā pono, hana ʻia nā hoʻokolohua aʻe.
| Hoʻāʻo | He aha kāu e ʻike ai ma kēia? |
|---|---|
| Nā hoʻāʻo koko | Ana ʻia nā mea e like me ka nui o ka hao i loko o ke koko, ka nui o ka hao i mālama ʻia (Serum Ferritin), a me ka Transferrin Saturation. |
| Hoʻāʻo ʻana i ka genetics | I mea e hōʻoia ai inā he kūlana hoʻoilina kēia, ua hoʻāʻo ʻia ka gene HFE no nā mutations. |
| Biopsy akepaʻa | I kekahi mau hihia, lawe ʻia kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ke akepaʻa me ka hoʻohana ʻana i kahi nila liʻiliʻi a nānā ʻia ma lalo o kahi microscope e loiloi i ka nui o ka hao i waiho ʻia i loko o ke akepaʻa a me ka nui o ka hōʻino ʻia i ke akepaʻa. |
| Nānā MRI | Hiki ke hoʻohana ʻia kahi scan MRI ma ke ʻano he ala ʻeha ʻole e ana i ka nui o ka hao i waiho ʻia i loko o nā ʻōpū e like me ke akepaʻa. |
He aha nā lāʻau lapaʻau maikaʻi loa?
ʻO ka pahuhopu nui o ka mālama ʻana i ka hemochromatosis, ʻo ia ka hoʻēmi ʻana i ka nui o ka hao keu i loko o ke kino a mālama iā ia ma kahi pae maʻamau. Hiki i kēia ke pale aku i ka hōʻino hou ʻana i nā ʻōpū.
| ʻAno Lapaʻau | He aha ka mea e hana ʻia me kēia? |
|---|---|
| Phlebotomy Lapaʻau | ʻO kēia ka lāʻau lapaʻau koʻikoʻi a maikaʻi loa. E like me ka hāʻawi ʻana i ke koko, wehe kahi nila i kahi koko liʻiliʻi mai kou kino. ʻOiai ʻo ka hapa nui o ka hao i loko o ko kākou kino aia i loko o nā hunaola koko ʻulaʻula, ke wehe ʻia ke koko, wehe ʻia nō hoʻi ka hao. Pono paha e hana ʻia kēia ma kahi o hoʻokahi manawa i ka pule i ka wā mua. Ke kāohi ʻia kou pae hao, pono paha e hana ʻia kēia i kēlā me kēia mau mahina. |
| Lapaʻau Chelation Hao | Hāʻawi ʻia kēia lāʻau lapaʻau i nā poʻe hiki ʻole ke wehe ʻia ke koko no kekahi kumu (e.g., maʻi puʻuwai, anemia). Pili ia i ka hāʻawi ʻana i kahi lāʻau (kahi pila a i ʻole injection) e hoʻopaʻa ai i ka hao i loko o ke kino a hoʻokuʻu ʻia i loko o ka mimi a i ʻole ka ʻōpala. |
| Nā loli i ka ʻai | Hiki i kāu kauka ke ʻōlelo aku iā ʻoe e kaupalena i kāu ʻai ʻana i nā meaʻai waiwai i ka hao (e like me ka ʻiʻo ʻulaʻula, nā legume) a me nā meaʻai waiwai i ka wikamina C, kahi e hoʻonui ai i ka omo ʻana o ka hao. Hiki iā ia ke aʻo aku iā ʻoe e hoʻōki i ka lawe ʻana i nā pila wikamina i loaʻa ka hao a pale i ka inu ʻana i ka waiʻona. |
Pehea ke ola me kēia kūlana?
He mea weliweli paha kēia iā ʻoe. Akā ʻo ka ʻoiaʻiʻo, inā ʻike mua ʻia a mālama pono ʻia, he kūlana hiki ke hoʻokele ʻia ka hemochromatosis . Hiki iā ʻoe ke ola i kahi ola maʻamau a olakino. I kekahi mau hihia, hiki ke hoʻohuli ʻia kekahi o nā hōʻino o ke kino ke hoʻomaka ka mālama ʻana.
ʻO ka pilikia, inā ʻaʻole ʻoe e mālama ʻia no ka manawa lōʻihi, ʻaʻole paha e hoʻihoʻi ʻia ka pōʻino i kou mau kino. No laila he mea nui e ʻike koke i ke kauka inā he mau hopohopo kāu.
Leka Lawe-Home
- ʻAʻole ka hemochromatosis kahi nele o ka hao i loko o ke kino, akā, he keu o ia mea .
- ʻO ka hapa nui o kēia ma muli o nā kumu genetic, akā hiki ke hana ʻia e nā pilikia olakino ʻē aʻe.
- ʻOiai ke ʻike ʻia nā hōʻailona ma hope o ka manawa lōʻihi, mai hoʻowahāwahā i nā mea e like me ka luhi mau a me ka ʻeha o nā hono.
- Inā ʻaʻole mālama ʻia, hiki iā ia ke hōʻeha nui i nā ʻōpū koʻikoʻi e like me ke akepaʻa, ka puʻuwai, a me ka pancreas.
- ʻAʻohe mea e makaʻu ai kēia. Inā ʻike mua ʻia, hiki ke kāohi piha ʻia me nā lāʻau lapaʻau maʻalahi a hiki iā ʻoe ke ola i kahi ola olakino.
- Inā he kānalua kou no kēia, e ʻoluʻolu e kamaʻilio me kāu kauka ʻohana.
💬 Comments (0)
ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.
Hoʻohui i kāu manaʻo