Ua lohe paha ʻoe i ka maʻi `(Sweet Syndrome)`? Malia paha ke lohe ʻoe i kēia inoa, manaʻo ʻoe he maʻi kō ia, akā ʻaʻole. He mea kākaʻikahi loa kēia, ʻo ia hoʻi, ʻaʻole ia he maʻi i loaʻa i nā kānaka he nui. Akā, he ʻehaʻeha ia e ʻike koke ʻia ma ke kino, nā lima, nā wāwae, a me ka ʻāʻī, me ke kuni. E kamaʻilio hou anei kākou e pili ana i kēia? No ka mea, ʻoiai he mea kākaʻikahi ia, he mea pono ke ʻike ʻia.
He aha maoli ka `(Sweet Syndrome)`?
I ka ʻōlelo maʻalahi, ʻo Sweet Syndrome kahi maʻi mumū o ka ʻili. Hoʻomaka koke ia. ʻO nā hōʻailona nui he kuni nui, ʻulaʻula, ʻeha nā ʻeha ʻili, a i kekahi manawa he mau pehu liʻiliʻi. ʻIke pinepine ʻia kēia mau ʻeha ma nā lima, nā wāwae, ke kino o luna, a i kekahi manawa ma ka maka a me ka ʻāʻī. Ua kapa pū nā kauka iā ia he Acute Febrile Neutrophilic Dermatosis. ʻAʻole anei he inoa lōʻihi kēlā? ʻO ia hoʻi "he maʻi ʻili e pili ana i ke kuni koke e pili ana i kahi ʻano cell i kapa ʻia ʻo neutrophil." ʻO Neutrophils kahi ʻano cell koko keʻokeʻo i loko o kā mākou ʻōnaehana pale.
I kekahi manawa hiki ke loaʻa kēia `(Sweet Syndrome)` me nā maʻi ʻē aʻe. No ka laʻana, hiki ke ʻike ʻia i nā maʻi kanesa `(Cancer)`, nā maʻi ʻōpū `(Gastrointestinal Infections)`, a i ʻole i ka wā hāpai. Ua ʻike ʻia hoʻi hiki ke hana ʻia kēia maʻi e kekahi mau lāʻau lapaʻau a mākou e lawe ai. No ka laʻana, hiki i kekahi mau ʻano `(Antibiotics)`, ʻo ia hoʻi, nā lāʻau pepehi bacteria, (e.g. `(Co-trimoxazole (Bactrim™))`) a me `(NSAIDs)` (Nonsteroidal Anti-inflammatory Drugs) nā mea hoʻomaha ʻeha (e.g. `(Advil®)`) ke hana i kēia.
ʻO ka mea maikaʻi loa, aia kahi lāʻau lapaʻau no kēia. ʻO ka hapa pinepine, ua kuhikuhi ʻia ke ʻano lāʻau lapaʻau `(Corticosteroid)` (e.g. `(Prednisone)`). Hoʻemi kēia mau lāʻau lapaʻau i ka mumū a kāohi i nā hōʻailona. Inā hana ʻia kēia e kahi maʻi kumu, a laila e hoʻomaikaʻi pū ka `(Sweet Syndrome)` ke mālama ʻia kēlā maʻi.
Pehea ka maʻamau o kēia ʻano?
He maʻi laha ʻole ka Sweet Syndrome. He kakaikahi wale nō nā hihia i hōʻike ʻia ma ka honua holoʻokoʻa. No laila, ʻaʻole ia he mea maʻamau ka lohe ʻana e pili ana i ia mea.
ʻO wai ka mea kūpono loa e hoʻomohala i kēia?
Hiki i kēia "Sweet Syndrome" ke hiki i kekahi. Eia nō naʻe, e like me nā hōʻike , ʻoi aku ka maʻamau o kēia ʻano maʻi i nā wahine ma waena o 30 a me 50 mau makahiki. Eia naʻe, ʻaʻole ia manaʻo ʻaʻole hiki i nā kāne a i ʻole nā kānaka o nā hui makahiki ʻē aʻe ke loaʻa iā ia.
He aha nā pilikia ʻē aʻe e hiki ke kū mai ma muli o ka `(Sweet Syndrome)`?
I kekahi mau hihia, hiki i ka Sweet Syndrome ke hoʻopilikia i nā mea ʻē aʻe ma mua o ka ʻili wale nō, akā hiki ke hoʻopilikia i nā ʻōnaehana kino ʻē aʻe o ke kino. No ka laʻana, hiki ke hoʻopilikia ʻia ka ʻōnaehana nerve a me ka ʻōnaehana gastrointestinal.
Eia nō naʻe, ʻo ka pilikia maʻamau ka pilikia o nā maka.Hiki i kēia ke komo pū me ka mumū o nā maka (ʻulaʻula, ʻeha), ka piʻi ʻana o ke kaomi o ka maka (glaucoma), a me ka ʻeha o ka cornea. No laila, he mea nui loa i kekahi me Sweet Syndrome ke mālama i ko lākou mau maka.
He aha nā kumu o ka `(Sweet Syndrome)`?
ʻO kaʻoiaʻiʻo, ʻaʻole i ʻike ʻia ke kumu kikoʻī o ka Sweet Syndrome. Eia nō naʻe, ua hoʻokaʻawale nā kauka iā ia i ʻekolu mau ʻāpana nui e pili ana i ke ʻano o kona hanana ʻana:
1. Kaila kuʻuna
ʻO ka mea e hana ʻia ma kēia hihia, ʻo ia ka ʻike ʻia ʻana o ka "Sweet Syndrome" i ka manawa like me kekahi maʻi ʻē aʻe.
- Eia kekahi laʻana, hiki ke hele mai me nā maʻi hanu o luna e like me nā maʻi ʻāʻī a me nā maʻi māmā. E noʻonoʻo he anu nui kou, he kuni, a laila loaʻa koke iā ʻoe kēlā mau ʻulaʻula ʻili. Hiki paha ke like me ia.
- Hiki i kēia ke hana i ka wā hāpai no kekahi poʻe.
- Hiki ke pili pū me nā maʻi gastrointestinal (e.g., ʻeha ʻōpū, diarrhea).
2. Pili i ka maʻi ʻino
I kekahi manawa, pili ka Sweet Syndrome me kekahi mau ʻano maʻi kanesa . He ʻoiaʻiʻo loa kēia me nā maʻi kanesa e pili ana i ke koko e like me ka Acute Myeloid Leukemia. Hana ʻia kēia maʻi ʻili ma muli o nā loli i ke kino i hoʻokumu ʻia e ka maʻi kanesa.
3. `(Hoʻoulu ʻia e ka lāʻau lapaʻau)` ma muli o kekahi mau lāʻau lapaʻau
He mea nui nō hoʻi kēia. Hiki i kekahi mau lāʻau lapaʻau a mākou e lawe ai ke hana i ka "Sweet Syndrome".
- Kekahi mau ʻano `(Antibiotics)`, no ka laʻana `(Bactrim™)` (nona ka `(Co-trimoxazole)`).
- Nā lāʻau hoʻopau ʻeha a me nā lāʻau anti-inflammatory i kapa ʻia ʻo "NSAIDs".
- He lāʻau lapaʻau i kapa ʻia ʻo `Granulocyte Colony-Stimulating Factor (G-CSF). Hāʻawi ʻia kēia e hoʻoulu i ke kino e hana i kahi ʻano keʻokeʻo koko i kapa ʻia ʻo `Neutrophil`. ʻO kēia mau keena nā mea e hakakā ai i nā maʻi.
E noʻonoʻo, ma hope o kou hoʻomaka ʻana e lawe i ka lāʻau lapaʻau no kahi maʻi, inā loaʻa koke iā ʻoe ke kuni a me nā ʻulaʻula ma kou ʻili i loko o kekahi mau lā a i ʻole hoʻokahi a ʻelua paha pule, pono ʻoe e kānalua he hiki ke kumu o kēlā lāʻau lapaʻau.
He aha nā hōʻailona o ka `(Sweet Syndrome)`?
Hoʻomaka koke nā hōʻailona o ka "Sweet Syndrome". ʻO nā hōʻailona nui e ʻike ʻia:
- ʻIke ʻia nā puʻupuʻu ʻulaʻula ʻeha a i ʻole nā pehu liʻiliʻi i piha i ka nahu ma ka maka, ka ʻāʻī, nā lima, a me nā wāwae. Aia paha kekahi a ʻoi aku paha o kēia mau ʻeha, a i kekahi manawa hiki iā lākou ke ulu pū.
- Nā ʻeha a i ʻole nā pūpū ma ka ʻili a i kekahi manawa i loko o ka waha.
- ʻOle ke kala o ka ʻili: Hiki ke loli ke kala o nā wahi i hoʻopilikia ʻia i ka hala ʻana o ka manawa.
- Wela loa.Ke lawe nei. Aia paha ke kuni he 38 kekelē Celsius (100.4 Fahrenheit) a ʻoi aku paha.
- ʻEha ʻiʻo a me nā hono, ʻeha poʻo, a me ka luhi.
- He manaʻo maʻi maʻamau.
Inā ʻike koke ʻia kekahi a ʻoi aku paha o kēia mau hōʻailona, ʻoiai inā hele pū lākou me ke kuni a me nā ʻeha ʻili ʻeha, ʻoi aku ka maikaʻi o ka ʻimi ʻana i ke kōkua lapaʻau.
Pehea ʻoe e ʻike ai inā loaʻa iā ʻoe ka `(Sweet Syndrome)`?
Inā loaʻa iā ʻoe kēia mau hōʻailona, e hana ke kauka i kahi hoʻokolokolo kino piha. E nīnau lākou iā ʻoe i nā nīnau he nui e pili ana i kāu mau hōʻailona, e like me ka wā i hoʻomaka ai, inā he mau maʻi olakino ʻē aʻe kāu, a inā paha ʻoe e lawe nei i kekahi mau lāʻau lapaʻau.
I kekahi manawa, inā ʻaʻole lawa ka hoʻokolohua kino wale nō e hana i kahi hōʻailona, hiki i kāu kauka ke ʻōlelo aku i kahi biopsy ʻili, ʻo ia hoʻi ka lawe ʻana i kahi ʻāpana liʻiliʻi o ka ʻili a hoʻouna iā ia i kahi lab e hoʻāʻo ʻia . Hiki i kēia ke kōkua i ka hoʻoholo ʻana inā loaʻa iā ʻoe ʻo Sweet Syndrome a i ʻole kekahi maʻi ʻē aʻe ma ka nānā ʻana i nā loli i loko o kou mau ʻili ʻili.
Eia kekahi, aia kekahi mau kumu ʻē aʻe e kōkua i ka hōʻoia ʻana:
- Loaʻa ke kuni ma luna o 38 kekelē Celsius (100.4 Fahrenheit).
- Hoʻomaikaʻi maikaʻi i nā lāʻau corticosteroid.
- I ka manawa like, loaʻa i ka maʻi ʻaʻai, kahi maʻi ʻē aʻe, a hāpai paha.
- Nā pae kiʻekiʻe ma ke ʻano ʻē o nā hōʻailona koko mumū.
Ma hope o ka noʻonoʻo ʻana i kēia mau mea a pau, ua hoʻoholo ke kauka ʻo ia ka "Sweet Syndrome".
He aha nā lāʻau lapaʻau no ka `(Sweet Syndrome)`?
ʻO ka nūhou maikaʻi, i kekahi manawa e nalowale ana ka Sweet Syndrome iā ia iho me ka ʻole o ka lāʻau lapaʻau. Eia nō naʻe, pono ka nui o ka poʻe i ka lāʻau lapaʻau.
ʻO ka lāʻau lapaʻau nui ka lāʻau corticosteroid systemic (e.g., prednisone). Hana kēia mau lāʻau lapaʻau ma ka hōʻemi ʻana i ka mumū i loko o ke kino a me ke kāohi ʻana i ka ʻōnaehana pale. Hoʻemi nā Corticosteroids i ka helu o nā hunaola koko keʻokeʻo a me nā ʻāpana ʻē aʻe o ka ʻōnaehana pale, e pale ana i ka hōʻino ʻana o nā ʻiʻo.
ʻO ka mea nui loa, ʻo ia ka lawe ʻana i kēia lāʻau lapaʻau e like me ke kuhikuhi a kāu kauka, ma ka nui i kuhikuhi ʻia, a no ka manawa i kuhikuhi ʻia. ʻAʻole ia he manaʻo maikaʻi e hoʻōki koke i ka lawe ʻana.
- Inā he kumu ʻē aʻe o ka Sweet Syndrome (e like me ka maʻi, ka maʻi kanesa), ʻo ka mālama ʻana i kēlā kūlana e hoʻoponopono paha i kēia mau pilikia ʻili.
- Inā ua hoʻoholo ʻia ua hoʻokumu ʻia kēia e kahi lāʻau lapaʻau (Drug-induced Sweet Syndrome), e hoʻomaka nā hōʻailona e hoʻopau ke hoʻōki ʻia ka lāʻau lapaʻau .
He aha ka mea e hana ʻia ma hope o ka lāʻau lapaʻau?
No nā kānaka he nui, ho'ōla nā ʻeha a me nā ʻeha o ka ʻili i hoʻokumu ʻia e ka Sweet Syndrome me ka ʻole o ka ʻōpala. He mea maikaʻi kēia. Eia nō naʻe, ma hope o ka nalowale loa ʻana o nā hōʻailona, hiki ke hoʻomau ka hoʻololi ʻana o ka ʻili no kekahi mau mahina.Ke lilo mālie nei ia i mea maʻamau.
Hiki ke pale ʻia ka Sweet Syndrome?
ʻO ka mea pōʻino, ʻoiai ʻaʻole ʻike ʻia ke kumu kikoʻī o ka Sweet Syndrome, ʻaʻohe ala e pale aku ai. Ua ʻike mākou aia kekahi mau mea pilikia (e.g., kekahi mau lāʻau lapaʻau, kekahi mau maʻi), akā ʻaʻole i loaʻa i nā kānaka a pau.
He aha ka manaʻo no kekahi me kēia maʻi? (Manaʻo)
No ka hapa nui o nā kānaka, e pau koke nā hōʻailona o ka Sweet Syndrome a i ʻole me ka mālama ʻana i ke olakino. Hiki i nā hōʻailona ke mau no kekahi mau pule a i ʻole nā mahina.
Eia nō naʻe, inā ua hoʻokumu ʻia ka Sweet Syndrome e kahi maʻi lapaʻau a i ʻole ka lāʻau lapaʻau, hiki ke hoʻomau nā hōʻailona no kekahi manawa. Hiki ke hoʻomau nā hōʻailona a hiki i ka mālama ʻia ʻana o ke kumu kumu a i ʻole ka hoʻōki ʻana i ka lāʻau lapaʻau.
Āhea ʻoe e ʻike ai i ke kauka?
Inā loaʻa iā ʻoe nā hōʻailona e like me nā mea i wehewehe ʻia ma kēia ʻatikala, ʻo ia hoʻi ka hoʻomaka koke ʻana o ke kuni a me nā kiko ʻulaʻula ʻeha, nā puʻupuʻu, a i ʻole nā pehu ma kou ʻili, pono ʻoe e ʻike i ke kauka. Eia kekahi, inā ua ʻike mua ʻoe he Sweet Syndrome kou a me he mea lā e ʻoi aku ka ʻino o kāu mau hōʻailona, a i ʻole inā loaʻa iā ʻoe nā hōʻailona hou, e haʻi koke i kāu kauka. ʻO ka loaʻa ʻana o ka lāʻau lapaʻau i ka wā mua e hiki ke kōkua i ka hōʻemi ʻana i ka pilikia o nā pilikia.
Leka Lawe-Home
- ʻO ka Sweet Syndrome kahi maʻi mumū laha ʻole e hoʻoulu ai i nā ʻeha ʻulaʻula ʻeha i ka ʻili me ke kuni koke.
- ʻOiai ʻaʻole ʻike ʻia ke kumu kikoʻī o kēia, hiki ke hana ʻia e kekahi mau maʻi, ka hāpai ʻana, a me kekahi mau lāʻau lapaʻau.
- ʻO nā hōʻailona nui ka wela, nā ʻulaʻula o ka ʻili, a me nā ʻehaʻeha o ke kino.
- Hiki ke loaʻa nā pilikia maka.
- Hiki ke mālama pono ʻia me nā corticosteroids. He mea nui hoʻi e mālama i ke kumu kumu.
- I ka hapanui o ka manawa, ho'ōla ia me ka ʻole o ka ʻeha, akā aia paha kahi loli i ke kala o ka ʻili no kekahi manawa.
- Inā loaʻa iā ʻoe kēia mau hōʻailona, e ʻimi koke i ke kōkua lapaʻau.
Manaʻolana wau he mea pono kēia ʻike iā ʻoe. ʻOiai ke ʻano o kou kūlana olakino, he mea nui loa ka hoʻomaopopo pono ʻia e pili ana i ia mea.
ʻO ka Sweet Syndrome, ke kuni, nā ʻeha ʻili, nā maʻi dermatological, ka mumū, nā corticosteroids, nā maʻi laha ʻole











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