I kekahi manawa, loaʻa iā mākou kekahi mau maʻi ma muli o nā kumu hoʻoilina. ʻO 'Cystinuria' kekahi o ia ʻano maʻi. Ma muli o kēia, e ʻeha pinepine ana paha ʻoe i nā pōhaku puʻupaʻa. No laila, ʻo kahi lāʻau lapaʻau kūikawā a nā kauka e kuhikuhi ai e hoʻōki i ka hoʻokumu ʻia ʻana o ia mau pōhaku puʻupaʻa ʻo 'Tiopronin'. E kamaʻilio kākou e pili ana i kēia lāʻau lapaʻau i kēia lā.
He aha ka Tiopronin?
I ka ʻōlelo maʻalahi, ʻo ka tiopronin kahi lāʻau lapaʻau e hoʻopaʻa i kahi kemika i loko o kou kino i kapa ʻia ʻo cystine. Hoʻokumu ʻia nā pōhaku puʻupaʻa ke kūkulu ʻia kēia cystine i loko o ke kino o kekahi me cystinuria. No laila, hana kēia lāʻau lapaʻau ma ka hoʻōki ʻana i ka kūkulu ʻia ʻana o ka cystine a me ka hoʻēmi ʻana i ka pilikia o nā pōhaku puʻupaʻa. ʻŌlelo pinepine ʻia kēia e nā kauka ke ʻaʻole i holo pono nā lāʻau ʻē aʻe.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau
Ma mua o ke kau ʻana o kāu kauka i kēia lāʻau lapaʻau, he mea nui loa ia e hāʻawi iā ʻoe i kahi wehewehe piha o kou kūlana olakino. ʻO ka mea nui, pono ʻoe e haʻi iā lākou e pili ana i kēia mau mea:
- Inā he pilikia ʻē aʻe kou e pili ana i ka puʻupaʻa.
- Inā ua loaʻa iā ʻoe kahi hopena maʻi ma mua iā Tiopronin a i ʻole kekahi lāʻau lapaʻau ʻē aʻe, meaʻai, a mea hoʻoluʻu paha.
- Inā ʻoe e hoʻāʻo nei e hāpai a ua hāpai mua paha.
- Inā he makuahine hānai waiū ʻoe.
Ma muli o kēia ʻike, e hoʻoholo ke kauka inā kūpono kēia lāʻau lapaʻau iā ʻoe a ʻaʻole paha.
Pehea e pono ai iaʻu ke hoʻohana i ka lāʻau lapaʻau?
Hiki ke hoʻokō ʻia nā hopena maikaʻi loa ma ka hoʻohana pono ʻana i kēia lāʻau.
Pono e lawe ʻia kēia lāʻau me ka wai. ʻOi aku ka maikaʻi o ka lawe ʻana i ka manawa like i kēlā me kēia lā, e like me ke kauoha a kāu kauka. E hoʻomau i ka lawe ʻana a hiki i ka wā e ʻōlelo ai kāu kauka e hoʻōki.
ʻO ka mea nui e pili ana i kēia, ʻo ia ka lawe ʻana i kēia pila ma ka ʻōpū ʻole. ʻO ia hoʻi, pono ʻoe e lawe iā ia ma ka liʻiliʻi he hola ma mua o ka ʻai ʻana, a i ʻole ʻelua hola ma hope o ka ʻai ʻana. ʻO ia ka manawa e komo pono ai ka lāʻau i loko o ke kino.
Pono anei e hāʻawi ʻia kēia lāʻau lapaʻau i nā keiki?
Inā ʻoe e hāʻawi ana i kēia lāʻau lapaʻau i nā keiki, e kamaʻilio me kāu kauka e pili ana i ia mea. I kekahi manawa, ʻoiai ke kuhikuhi ʻia i nā keiki, aia kekahi mau mea kūikawā e pono e noʻonoʻo ʻia.
He aha kāu e hana ai inā lawe nui ʻoe i ka lāʻau lapaʻau?
Inā manaʻo ʻoe ua lawe hewa ʻoe i kēia lāʻau lapaʻau ma mua o ka mea i kuhikuhi ʻia, mai hoʻokaʻulua . E hele koke i ka haukapila kokoke loa i ka Emergency Department (ETU). A i ʻole e kelepona i ke National Poisons Information Centre ma ka Colombo National Hospital no ka ʻōlelo aʻoaʻo.
He aha inā e hala iaʻu kahi mahele o ka lāʻau lapaʻau?
Inā poina iā ʻoe ke lawe i kahi lāʻau, e lawe koke i ka wā e hoʻomanaʻo ai ʻoe. Eia nō naʻe, inā kokoke ka manawa no kāu lāʻau aʻe, e kāpae i ka lāʻau i hala ʻole a lawe i kāu lāʻau aʻe i ka manawa i hoʻonohonoho ʻia. Mai lawe pālua i ka lāʻau.
He aha nā mea e makaʻala ai i ka wā e lawe ai i kēia lāʻau?
ʻOiai e lawe ana i kēia lāʻau lapaʻau, pono ʻoe e ʻike pinepine i kāu kauka e nānā i kou kūlana. Pono paha ʻoe e hana i nā hoʻāʻo koko a me ka mimi e ʻike ai inā e hana ana ka lāʻau lapaʻau a inā he mau hopena ʻaoʻao.
Eia kekahi, e noi ʻia paha ʻoe e hahai i kahi papaʻai kūikawā. No laila e kamaʻilio me kāu kauka e pili ana i nā meaʻai a me nā wikamina āu e lawe ai. ʻO ka mea nui e pale aku ai i nā pōhaku puʻupaʻa, ʻo ia ka inu ʻana i ka wai he nui. E nīnau i kāu kauka i ka nui o ka wai āu e inu ai i kēlā lā, a e hōʻoia e inu i kēlā nui.
ʻO ka mea nui loa: Inā he makuahine hānai ʻoe, e pale i ka hānai ʻana i kāu pēpē i ka waiū piha ʻana i ka wā e lawe ana i kēia lāʻau. E kamaʻilio me kāu kauka e pili ana i kēia.
He aha nā hopena ʻaoʻao e hiki mai ana?
E like me nā lāʻau lapaʻau āpau, hiki i ka Tiopronin ke hana i kekahi mau hopena ʻaoʻao. Eia naʻe, ʻaʻole loaʻa i nā kānaka a pau. He koʻikoʻi loa kekahi, no laila he mea nui e makaʻala iā lākou.
| Nā hopena ʻaoʻao o Tiopronin | |
|---|---|
| Nā hopena ʻaoʻao e pono ʻoe e hōʻike koke i kāu kauka | |
| Nā hopena alerika | ʻŌhūhū ʻili, maneʻo, pehu o ka maka, nā lehelehe a i ʻole ke alelo. |
| Nā loli i ka mimi | ʻO ka mimi ʻeleʻele, ka paʻakikī o ka mimi ʻana, a i ʻole kahi loli i ka nui o ka mimi āu e hana ai. |
| Nā hōʻailona ʻē aʻe i ke kino | Kuni, ʻeha hui, ʻeha waha, pehu o nā kuʻekuʻe wāwae, nā wāwae a i ʻole nā lima, nā ʻōpū pehu a me ka ʻeha. |
| Nā hopena ʻili koʻikoʻi | ʻUlaʻula ka ʻili, ka pehu, ka ʻili ʻana (a hiki i loko o ka waha). |
| Nā hōʻailona o nā hunaola koko ʻulaʻula haʻahaʻa (Anemia) | Manaʻo i ka luhi a luhi paha i ʻike ʻole ʻia, maule, pilikia ka hanu ʻana. |
| Ke kahe koko ʻano ʻē | ʻO ka palapū ma ke kino holoʻokoʻa a i ʻole ke kahe ʻana o ke koko mai kahi ʻeha liʻiliʻi. |
| Nā hopena ʻaoʻao e pono e hōʻike ʻia i ke kauka inā hoʻomau lākou a hoʻopilikia paha | |
| Nā pilikia o ka ʻōnaehana hoʻoheheʻe | Ka maʻi pākī, ka nausea, ka luaʻi ʻana, ka ʻeha ʻōpū. |
| Nā hiʻohiʻona liʻiliʻi ʻē aʻe | Nā loli i ka ʻono o ka meaʻai, ka luhi, ka ʻāʻī ʻana a i ʻole ka lahilahi ʻana o ka ʻili. |
Pehea ʻoe e mālama ai i kāu lāʻau lapaʻau?
- E mālama pono i kēia lāʻau lapaʻau mai ka hiki ʻana aku o nā keiki .
- ʻOi aku ka maikaʻi o ka mālama ʻana i ka mahana o ka lumi (ma waena o 15 a me 30 kekelē Celsius).
- E mālama i ka lāʻau lapaʻau i loko o ka ʻōmole kumu i hoʻokomo ʻia ai.
- E hoʻolei i ka lāʻau lapaʻau i pau me ka hoʻohana ʻole ʻana.
Leka Lawe-Home
- E lawe mau i nā papa Tiopronin ma ka ʻōpū ʻole. ʻO ia hoʻi, hoʻokahi hola ma mua a ʻelua paha hola ma hope o ka ʻai ʻana.
- E inu i ka wai he nui i kēlā me kēia lā, e like me ka ʻōlelo a kāu kauka. He mea nui kēia no ka pale ʻana i nā pōhaku puʻupaʻa.
- Mai poina i nā manawa i hoʻonohonoho ʻia e kāu kauka a me nā hoʻokolohua i hoʻonohonoho ʻia.
- Inā loaʻa iā ʻoe kahi hopena koʻikoʻi a lawe paha i ka nui o ka lāʻau lapaʻau, e ʻimi koke i ke kōkua lapaʻau .
- Inā he mau nīnau a hopohopo paha kāu e pili ana i kēia lāʻau lapaʻau, e kamaʻilio ākea me kāu kauka e pili ana.











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