He urethra a he vagina anei ko kāu pēpē? (Urogenital Sinus) E kamaʻilio kākou e pili ana i kēia!

Pehea ka nui o ka hopohopo o ka makuahine a i ʻole ka makuakāne ke nānā lākou i kahi pēpē hānau hou a ʻike i kahi loli liʻiliʻi i ko lākou kino? I kekahi manawa, ʻoiai kahi mea kakaikahi loa, hiki ke hoʻopilikia i kā mākou pēpē a hoʻoluhi iā mākou. I kēia lā, e kamaʻilio mākou e pili ana i kahi maʻi i lohe pinepine ʻole ʻia, akā he mea nui loa ia e ʻike. Kāhea mākou i kēia (Urogenital Sinus).

He aha kēia (Urogenital Sinus)? E hoʻomaopopo maʻalahi kākou?

I ka ʻōlelo maʻalahi, ʻo ka Urogenital Sinus kahi kīnā hānau i loko o ka ʻōnaehana mimi a me ka ʻōnaehana hānau o kahi wahine. I kēia manawa, e nānā, ʻo ka maʻamau he ʻekolu mau puka no ka ʻōpala e puka i waho o ke kino o kahi pēpē wahine: ʻo kekahi ka rectum, kahi e puka mai ai ka ʻōpala, ʻo kekahi ka puka urethral, ​​kahi e puka mai ai ka mimi, a ʻo ke kolu ka vagina . Eia nō naʻe, ʻelua mau puka o kahi pēpē me Urogenital Sinus. ʻO kekahi ka rectum, kahi e puka mai ai ka ʻōpala, a ʻo kekahi he puka maʻamau no ka urethra a me ka vagina. ʻO ke ʻano kēia e puka mai ai ka mimi a pili i ka vagina mai kahi hoʻokahi.

ʻO kēia kūlana (Urogenital Sinus) e kū mai ana i nā wā mua o ka ulu ʻana o ka fetal. E noʻonoʻo, no kahi manawa pōkole loa i ka wā fetal, ʻo nā ʻōnaehana ʻekolu - ke ala ʻōpū (rectum), ke ala genital (vagina), a me ke ala mimi (urinary bladder) - ua pili pū ʻia i hoʻokahi lua a me ka puka. Kāhea mākou i kēia ( Cloaca ). I ka ulu ʻana o ka fetus , hoʻokaʻawale kēia mau ʻōnaehana ʻekolu a hana i ʻekolu mau puka kaʻawale (vagina, urethra , a me anus). Akā i kekahi manawa, no kekahi kumu, ʻaʻole hoʻokaʻawale pono ke ala mimi a me ka ʻōnaehana hānau hou - ʻo ia hoʻi ka urethra a me ka vagina, akā hoʻomau i ka mālama ʻana i hoʻokahi puka. Ua kapa ʻia kēlā puka maʻamau (Urogenital Sinus). Kāhea pū kekahi poʻe i kēia (Persistent Urogenital Sinus - PUGS).

He aha nā kumu pinepine o ka sinus urogenital?

I ka wā o ka ulu ʻana maʻamau, e lilo kēia wahi (i kapa ʻia ʻo Urogenital Sinus) i ka urethra a me ka ʻili a puni ka puka o ka vagina (vulvar vestibule). ʻO ka urethra ka ʻōmole e puka ai ka mimi i kou kino. ʻO ka ʻili a puni ka puka o ka vagina (vulvar vestibule) ʻo ia ka ʻili ma loko o ka labia, ma waena o ka urethra a me ka puka o ka vagina.

Aia ma hea ka Urogenital Sinus i loko o ke kino?

Ua pili kēia (Urogenital Sinus) i ka urethra a me ka vagina.

Aia kekahi mau ʻano o ka sinus urogenital?

ʻAe, ʻelua ʻano nui o ka Urogenital Sinus. He mea nui loa ka ʻike ʻana i kēia no ka hoʻolālā ʻana i ka mālama ʻana.

1. Hoʻohui haʻahaʻa / hui haʻahaʻa: Ma kēia ʻano, hui ka urethra a me ka vagina kokoke loa i ka puka waho o ke kino, ʻo ia hoʻi, ma lalo. No laila, he pōkole loa kēia alahele maʻamau. I kēia hihia, ua like loa ka nui a me ke kūlana o ka urethra a me ka vagina me ka maʻamau. He ʻano maʻi ʻoi aku ka liʻiliʻi o ke koʻikoʻi o kēia.

2. Hui kiʻekiʻe / Hui kiʻekiʻe: I kēia hihia, hui ka urethra a me ka vagina ma kahi mamao mai ka puka waho o ke kino, ʻo ia hoʻi, ma luna. A laila lōʻihi loa kēia ala maʻamau. ʻO kēia ʻano hui kiʻekiʻe ka mea koʻikoʻi loa. No ka mea, hiki ke loaʻa nā pilikia ʻē aʻe me kēia. No ka laʻana, hiki ke loaʻa ka anus ma mua loa ma mua o ka maʻamau i loko o ke kino.

Pehea ka laha ʻole o kēia maʻi (Urogenital Sinus)?

He maʻi laha ʻole ka Sinus Urogenital. Ma ke ʻano maʻamau, hoʻopilikia ia ma kahi o 0.6 o 10,000 mau pēpē hānau hou.

He aha nā hōʻailona o ka sinus urogenital?

Hiki ke ʻokoʻa nā hōʻailona o ka Urogenital Sinusitis ma muli o ke koʻikoʻi o ke kūlana. ʻO kekahi o nā hōʻailona ʻike nui ʻia:

• Hoʻokahi wale nō puka no ka feces a hoʻokahi puka ʻē aʻe e like me ka mea i loaʻa i ka vagina a me ka urethra.
• Ka pehu ʻana o ka ʻōpū ma muli o ka hōʻiliʻili ʻana o ka mimi. Ua kapa ʻia hoʻi kēia ʻo (Hydrocolpos).
• Hiki ke pani ʻia ka vagina ma ke ʻano ʻē.
• I kekahi manawa ʻaʻohe paha he vagina.
• ʻAʻole i hoʻomohala pono ʻia ka ʻōpū, nā ovaries, a i ʻole nā ​​​​tubes fallopian .

He aha nā kumu o ka maʻi ʻōpū o ka sinus urogenital?

ʻO kaʻoiaʻiʻo, ʻoiai nā loea lapaʻau e paʻakikī ke kuhikuhi i kahi kumu kūpono no ka Urogenital Sinus.

I kekahi mau hihia, hiki ke pili kēia i kahi kūlana i kapa ʻia ʻo Congenital Adrenal Hyperplasia (CAH). He hui o nā maʻi genetic ʻo CAH. Inā loaʻa iā ʻoe ʻo CAH, ʻaʻole hana kekahi a i ʻole ʻelua o kāu mau kelepa adrenal i kahi enzyme e pono ai e hana i nā hormones. Hiki i kēia ke kumu i ka ulu ʻana o nā ʻōpū moekolohe i kahi ʻano ʻē. Hiki i ka CAH ke hoʻopilikia i kekahi, akā ʻoi aku ka nui o nā kaikamahine i loaʻa nā ʻōpū moekolohe ʻē.

Hiki i kahi kūlana i kapa ʻia ʻo virilization ke hana i ka sinusitis urogenital. ʻO ka Virilization ka wā i loaʻa ai i ke keikikāne ka nui o nā hormones kāne (androgens) i loko o kona kino. ʻO Androgens nā mea e kōkua ai i ke kino e oʻo, a hoʻopilikia pū lākou i nā mea e like me ka hohonu o ka leo, ka lauoho o ke kino, a me ka ulu ʻana o nā ʻiʻo.

Pehea e ʻike ʻia ai ka maʻi sinus Urogenital?

He mea nui loa ka (Urogenital Sinus) i ka hoʻoholo ʻana pehea e mālama ai i ke kūlana. Hiki i kēia ke hoʻopilikia ʻaʻole wale i nā ʻōpū o kāu keiki, akā, i ko lākou ulu a me ka ulu ʻana.

I kekahi manawa, hiki i nā kauka ke ʻike i kēia kūlana (Urogenital Sinus) i ka wā o ka ultrasound ʻoiai ke pēpē i loko o ka ʻōpū. Eia nō naʻe, ʻo ka hapa nui, ʻike nā kauka iā ia i ka wā o ka hoʻokolokolo kino mua ma hope o ka hānau ʻana o ke pēpē. A laila hiki iā lākou ke hana i nā hoʻokolohua koko e aʻo hou e pili ana i ke olakino holoʻokoʻa o ka pēpē a me nā pilikia genetic.

Hiki i ke kauka ke kauoha i nā hoʻokolohua hou aʻe e hōʻoia i ka hōʻailona a i ʻole e aʻo hou e pili ana i ka nui o ka Urogenital Sinus. Hiki i kēia mau mea ke komo pū me:

• Ultrasound: Hoʻohana kēia i nā nalu kani alapine kiʻekiʻe e lawe i kahi wikiō a i ʻole nā ​​kiʻi o nā ʻōpū i loko o ke kino. Hiki i kēia ke hōʻike i nā pilikia me nā puʻupaʻa o kāu pēpē, ka ʻōpū mimi, ka vagina, a me ka rectum. Hiki iā ia ke ʻike inā he hōʻiliʻili mimi kāu pēpē i loko o ka vagina (hydrocolpos).
• Retrograde genitogram: He ʻano hoʻāʻo kiʻi kēia. Ma kēia hoʻāʻo, hoʻokomo ke kauka i kahi kala kūikawā i loko o ka urethra/vagina a lawe i nā kukuna X. Hiki i kēia kala ke ʻike maopopo i ka nui, ke ʻano, a me kahi o nā ʻiʻo a me nā ʻōpū.
• Hoʻāʻo Magnetic Resonance Imaging (MRI): Hoʻohana kahi MRI i kahi magnet, nā nalu lekiō, a me kahi kamepiula e kiʻi i nā kiʻi maopopo o ke kino. Hiki i kēia ke hāʻawi i nā kiʻi kikoʻī loa o ka Urogenital Sinus. Hiki ke hoʻohana ʻia ka MRI e nānā i nā pilikia me ka pelvis a me ka iwi kuamoʻo o ke keiki.
• Endoscopy: Hoʻohana ka endoscopy i kahi ʻōmole lahilahi a lōʻihi (endoscope) me ke kukui a me ke kāmela ma kekahi ʻaoʻao. Hoʻokomo ʻia kēia endoscope i loko o ka urethra/vagina maʻamau e nānā i ke kino o loko.

Pehea e mālama ai i ka sinus urogenital?

ʻO ke ala wale nō e mālama ai i kahi maʻi Urogenital Sinus, ʻo ia ke hana ʻoki kino e hoʻokaʻawale i ka vagina a me ka urethra o kāu pēpē. I kekahi manawa, ʻoi aku hoʻi i nā keiki i virilized (ma muli o ka Congenital Adrenal Hyperplasia (CAH)) a ua ʻike ʻia me ka Disordered Sexual Development (DSD), hiki ke hui pū ʻia nā manaʻo e pili ana i ka hana ʻoki kino. No laila, ma mua o ke ʻoki kino ʻana, pono ʻoe e kamaʻilio kikoʻī me ka hui lapaʻau e mālama ana i kāu keiki. ʻO ka maʻamau, aia kēia hui:

• He kauka loea i nā maʻi o ka ʻōnaehana mimi a me ka ʻōnaehana hānau keiki ((Urologist)).
• He kauka endocrinologist kahi loea i nā maʻi e pili ana i ka ʻōnaehana endocrine. ʻO kāu ʻōnaehana endocrine ka mea e hana a hoʻokuʻu i nā hormones.

Hana pinepine ʻia ke ʻoki ʻana i loko o ka makahiki mua o ka pēpē . Hana ʻia kēia ʻoki e ke kauka urologist.

No ke kūlana haʻahaʻa (Urogenital Sinus), e hana pinepine kekahi (Urologist) i kahi ʻoki kino i kapa ʻia ʻo (Flap vaginoplasty). Ma kēia, hana lākou i ʻelua mau puka kaʻawale i waho o ke kino - hoʻokahi no ka vagina, a ʻo kekahi no ka urethra.

No ke kūlana i hui pū ʻia me ke kiʻekiʻe (Urogenital Sinus), hana pinepine kekahi (Urologist) i kahi ʻoki kino i kapa ʻia ʻo (Pull-through vaginoplasty). He ʻoki kino paʻakikī iki kēia. Ma kēia, hoʻokaʻawale ka (Urologist) i ka vagina mai ka puka maʻamau, hana i kahi ʻokoʻa, a pani i kēlā puka maʻamau. A laila, hoʻomau ka mimi i ke kahe ʻana mai kahi i kū ai ka puka maʻamau.

I kekahi mau hihia o ka hui kiʻekiʻe (Urogenital Sinus), hiki i kahi (Urologist) ke hana i kahi kaʻina hana i kapa ʻia ʻo (Urogenital mobilization) me (Flap vaginoplasty). I ka wā (Urogenital mobilization), e hana lākou:

• Ua hoʻokaʻawale ʻia ka rectum.
• Hoʻokaʻawale ʻia ka urethra a me ka vagina a hoʻoneʻe pū ʻia a lawe ʻia i ka perineum.
• Ua pili ka rectum i ka anal sphincter.
• A laila (flap vaginoplasty) e hana ʻia.

Pono paha kekahi mau keiki e hana i kahi ʻoki kino i kapa ʻia ʻo Clitoroplasty a/a i ʻole Labiaplasty. Pili ka Clitoroplasty i ke ʻano hou ʻana o ke kino e hana i kahi clitoris maʻamau. Hoʻāʻo ke kauka lapaʻau e mālama i nā aʻalolo he nui i hiki i ke keiki ke loaʻa kahi ola moekolohe olakino ke ulu lākou. Pili ka Labiaplasty i ke ʻano hou ʻana o ka labia, ʻo ia hoʻi nā lehelehe a puni ka vagina.

ʻEhia ka manawa e ola ai ke keiki ma hope o ka mālama ʻana no ka sinus urogenital?

Pono kāu keiki e noho ma ka haukapila no kekahi mau lā ma hope o ke ʻoki kino (Urogenital Sinus). Pono e hoʻomaka ka ʻeha e emi i loko o hoʻokahi pule, a pono e ho'ōla loa ʻia ke keiki i loko o hoʻokahi mahina. Eia nō naʻe, ma muli o ke koʻikoʻi o kāu keiki (Urogenital Sinus), e hāʻawi ke kauka o kāu keiki iā ʻoe i kahi manaʻo maopopo aʻe no kēia.

Hiki ke pale ʻia ka maʻi ʻana o ka sinus Urogenital?

Inā loaʻa i kekahi o kou ʻohana kahi maʻi i kapa ʻia ʻo Congenital Adrenal Hyperplasia (CAH), a ke hāpai nei ʻoe a i ʻole e hoʻāʻo nei e hāpai, he mea nui e kamaʻilio me kāu kauka. No ka pale ʻana i ka Urogenital Sinus, hiki ke hāʻawi ʻia nā hormones i ka wā ma mua o ka hānau ʻana.

He aha kaʻu e manaʻo ai inā loaʻa i kaʻu keiki ka sinus urogenital?

Aia ka hopena o kāu keiki i ka nui o kona sinus urogenital. ʻO ka pahuhopu o ke ʻoki ʻana, ʻo ia ke hāʻawi i kāu keiki i ka hana maʻamau a me ke ʻano o nā ʻāpana genital. Hiki i ka hapa nui o nā keiki i hana ʻia ke ʻoki ʻana ke mimi maʻamau ma hope o ka hoʻōla ʻana.

I ka ulu ʻana o ke pēpē, e lilo paha ka ʻōpū i mea haiki (stenosis ʻōpū) a pōkole. Hiki i kēia ke hana i nā pilikia i ka wā o ka moekolohe ʻana.

ʻAʻole pale ke keiki me ka maʻi Urogenital Sinus iā lākou mai ka hāpai ʻana. Eia nō naʻe, inā nui loa ke ʻoki ʻana, ʻoi aku ka maikaʻi o ka hana ʻana i ka ʻoki cesarean (C-section) i ka wā hānau. E kūkākūkā kāu kauka i kēia me kāu keiki i kahi manawa kūpono.

Pehea lā wau e mālama ai i kaʻu keiki?

Na nā kauka o kāu keiki e haʻi iā ʻoe pehea e mālama pono ai iā ia. ʻO ke koʻikoʻi o ka (Urogenital Sinus) a me nā hopena o ke ʻoki ʻana e hoʻoholo ai pehea ʻoe e hoʻomau ai i ka mālama ʻana iā ia.

Āhea wau e ʻike ai i ke kauka?

Ma hope o ke ʻoki ʻana, pono kāu keiki e loaʻa i nā manawa hoʻokolokolo maʻamau e hōʻoia i ka ho'ōla pono ʻana o kona kino a me ka hana ʻana e like me ka mea i manaʻo ʻia. E hōʻoia e hele i kēia mau manawa a pau.

Inā ʻike ʻoe i kekahi mau hōʻailona hou, e like me ka incontinence urinary, e kamaʻilio me ke kauka pediatric a urologist paha o kāu keiki.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka o kaʻu keiki?

Eia kekahi mau nīnau hiki iā ʻoe ke nīnau i kāu kauka:

• He aha ke ʻano o ka Sinus Urogenital a kaʻu keiki?
• He aha ke ʻano hana āu e paipai nei?
• I ka makahiki hea e ʻōlelo ʻia ai ke ʻoki kino?
• E ʻeha ana anei kaʻu keiki, a i ʻole ua ʻeha mua ʻo ia?
• E pono anei ke keiki i nā ʻoki kino hou aku i kona wā e ulu ana?
• Ke manaʻo nei ʻoe e loaʻa i kāu keiki nā pilikia me ko lākou urethra a i ʻole ka vagina i ko lākou ulu ʻana?
• E hoʻopilikia anei kēia i ke kaʻina hana menstrual o kaʻu keiki?
• E pili anei kēia i koʻu hiki ke hāpai i kahi keiki?
• E hiki anei i kaʻu keiki ke hānau me ka palekana?

Mea nui: Mai makaʻu e nīnau i kāu kauka i nā nīnau āu e loaʻa ai, ʻaʻohe mea liʻiliʻi. Loaʻa iā ʻoe ke kuleana e ʻike maopopo i nā mea āpau.

He aha ka maʻi Urogenital ma ke ʻano laulā?

ʻO ka maʻi Urogenital kekahi ʻano e hoʻopilikia ai i kāu ʻōnaehana urinary a me ka ʻōnaehana hānau keiki. ʻO nā hiʻohiʻona ʻē aʻe:

• Nā puʻupuʻu maikaʻi.
• ʻUlūlū.
• Nā Maʻi Lapaʻau i Hoʻoili ʻia e ke Kaulike (STI).
• Nā maʻi ʻaʻai e like me ke kanesa ʻōpū, ke kanesa ovarian, a i ʻole ke kanesa uterine.
• ʻO ka maʻi ʻeha cystitis interstitial/ʻōpū mimi (IC/BPS).

ʻO ka mea hope loa, nā mea e hoʻomanaʻo ai (Leka Lawe-Home)

He mea maʻamau ke hopohopo a me ka makaʻu ke ʻike ʻoe he Urogenital Sinus ko kāu keiki. Akā e hoʻomanaʻo, hiki ke mālama ʻia kēia ʻano me ke ʻoki ʻana e hoʻokaʻawale i ka urethra a me ka vagina o kāu keiki. ʻO ke ʻano kēia e hiki i kāu keiki ke mimi me ka ʻoluʻolu.I kona wā ʻelemakule, pono nō hoʻi e loaʻa iā ia kona wā ʻōpiopio. Eia nō naʻe, i kekahi manawa, i kona wā ʻelemakule, hiki iā ia ke loaʻa i kekahi ʻehaʻeha i ka wā o ka moekolohe ʻana me ka wahine.

ʻO ka mea nui, ʻaʻole pono ʻoe e lawelawe wale i kēia mau mea. E kamaʻilio me ke kauka o kāu keiki. Hiki iā lākou ke pane i kāu mau nīnau a pau, e hōʻoluʻolu i kou mau makaʻu, a kōkua iā ʻoe e loaʻa ka lāʻau lapaʻau a me ka mālama maikaʻi loa no kāu keiki.

ʻO ka sinus urogenital, PUGS, nā kīnā hānau, ʻōnaehana mimi, ʻōnaehana hānau hou, ʻoki kino, olakino keiki