Koj puas tau pom tias qee zaum peb cov neeg hlub pib luag yam tsis muaj laj thawj, lossis pib quaj yam tsis tu siab? Los yog lawv puas hais lus tsis meej thaum tham lus, lossis nyuaj nqos zaub mov? Yog tias koj muaj ib lossis ntau yam ntawm cov no ua ke, nws yuav yog vim muaj tus mob hu ua 'Pseudobulbar Palsy' uas peb yuav tham txog hnub no. Qhov no tsis yog ib yam kab mob sib cais, tab sis yog cov tsos mob uas tshwm sim los ntawm qee yam kab mob ntawm lub paj hlwb. Yog li, cia peb tham txog qhov no kom ntxaws ntxiv?
Pseudobulbar Palsy yog dab tsi?
Hais yooj yim xwb, Pseudobulbar Palsy yog ib pawg ntawm cov tsos mob ntawm lub paj hlwb uas tshwm sim los ntawm kev puas tsuaj rau ib feem ntawm peb lub hlwb hu ua corticobulbar tract. Qhov corticobulbar tract no pab tswj cov leeg nqaij hauv peb lub taub hau thiab lub ntsej muag. Thaum qhov no puas tsuaj, peb qhov teeb meem tseem ceeb tshwm sim:
- Hais lus nyuaj, peb kho mob hu qhov no tias 'dysarthria' .
- Qhov nyuaj nqos zaub mov lossis kua dej hu ua dysphagia .
- Qhov uas ib tug neeg tsis muaj peev xwm tswj tau nws txoj kev xav, xws li luag lossis quaj tam sim ntawd, hu ua "pseudobulbar affect."
Qhov tseem ceeb yog tias qhov no tsis yog ib yam kab mob xwb, tab sis yog ib qho teeb meem uas tshwm sim los ntawm lwm yam kab mob ntawm lub paj hlwb lossis cov mob ntawm lub hlwb. Qee zaum cov kws kho mob kuj hu nws tias 'supranuclear bulbar palsy'.
Cov tsos mob ntawm tus mob no yog dab tsi?
Raws li tau hais ua ntej lawm, peb yam tsos mob tseem ceeb yog hais lus tsis tau zoo, nqos tsis tau zoo, thiab tswj tsis tau kev xav. Txawm li cas los xij, kuj tseem yuav pom lwm yam tsos mob, xws li:
- Qaug dej los yog qaub ncaug ntau dhau: Qee zaum cov qaub ncaug tuaj yeem tawm ntawm lub qhov ncauj yam tsis koj paub txog.
- Kev hloov pauv ntawm tus cwj pwm thiab lub suab hais lus: Tej zaum yuav hais lus tsis meej. Tej zaum yuav zoo li koj hais lus los ntawm koj lub qhov ntswg (lub suab ntswg dhau lawm).
- Tus nplaig tsis muaj zog lossis tuag tes tuag taw: Qhov no hu ua 'glossoplegia'. Qhov no tuaj yeem ua rau nws nyuaj rau hais lus thiab zom zaub mov.
- Cov leeg nqaij ntawm lub ntsej muag tsis muaj zog: Ib sab lossis ob sab ntawm lub ntsej muag yuav tsis muaj sia.
- Nyuaj zom zaub mov: Vim tias koj tsis tuaj yeem zom zaub mov kom zoo, nws yuav nyuaj rau nqos.
- Luag lossis quaj uas tsis tswj tau lossis tsis tsim nyog: Xav txog kev quaj tam sim ntawd yam tsis muaj laj thawj, lossis luag nrov nrov rau qee yam me me, thiab tsis tuaj yeem tswj tau nws. Qhov no hu ua "pseudobulbar affect."
- Kev nruj ntawm cov leeg nqaij ntawm lub puab tsaig: Qhov no kuj hu ua 'trismus'. Nws tuaj yeem nyuaj rau qhib thiab kaw koj lub qhov ncauj.
- Kev ua kom lub ntsej muag rov qab zoo dua: Piv txwv li, tej zaum yuav muaj kev co ntawm lub puab tsaig.
Kuj tseem muaj kev tshaj tawm tias kwv yees li 85% ntawm cov menyuam yaus uas muaj Pseudobulbar Palsy yuav muaj cov mob xws li kev tsis taus ntawm lub hlwb thiab qaug dab peg .
Nrog rau cov tsos mob no, lwm cov tsos mob kuj tseem yuav tshwm sim nyob ntawm seb tus kab mob twg ua rau muaj tus kab mob pseudobulbar palsy.
Vim li cas qhov no thiaj tshwm sim? Yog vim li cas?
Qhov ua rau muaj Pseudobulbar Palsy yog kev puas tsuaj rau ob sab ntawm lub corticobulbar tract hauv peb lub hlwb. Lub luag haujlwm ntawm txoj hlab ntsha no yog tswj cov leeg nqaij hauv lub taub hau thiab lub ntsej muag. Qhov no kuj muab cov tswv yim rau cov hlab ntsha cranial uas muab cov lus tsim nyog rau cov leeg no.
Yog li, muaj ntau yam mob uas tuaj yeem ua rau puas tsuaj rau "corticobulbar tract" no. Lawv yog:
- Kev raug mob taub hau loj heev (kev raug mob hlwb).
- Cov qog nqaij hlav ntawm lub hlwb .
- Kev o thiab kev kis kab mob cuam tshuam rau lub hlwb.
- Cov mob hlwb ntev .
- Cov kab mob ntsig txog cov hlab ntsha ntawm lub hlwb, piv txwv li "mob stroke" thiab "mob vascular malformations".
Qee cov mob neurological uas feem ntau tshwm sim ntev thiab ua rau muaj pseudobulbar palsy muaj xws li:
- Kab mob Amyotrophic lateral sclerosis (ALS).
- Kab mob Parkinson .
- Mob caj dab supranuclear palsy nce qib.
- Kab mob ntau yam sclerosis ('Multiple sclerosis - MS').
Koj paub qhov no li cas?
Feem ntau cov kws kho mob kuaj mob Pseudobulbar Palsy raws li koj cov tsos mob. Qhov tseem ceeb ntawm no yog nrhiav seb qhov mob hauv qab no yog dab tsi ua rau muaj mob. Tej zaum koj twb paub txog nws lawm, lossis koj yuav tsum nrhiav ib yam dab tsi tshiab.
Tus kws kho mob yuav nug koj txog koj cov tsos mob, thaum twg lawv pib, thiab koj keeb kwm kev kho mob tag nrho, xws li seb koj puas tau muaj mob yav dhau los xws li mob stroke. Tom qab ntawd lawv yuav kuaj lub cev thiab kuaj lub paj hlwb .
Vim muaj ntau yam mob uas ua rau mob pseudobulbar palsy, koj tus kws kho mob kuj tseem yuav pom zoo kom kuaj ntau yam. Qee qhov ntawm cov no suav nrog:
- Kev kuaj ntshav .
- Kev ntsuas cov kua dej hauv lub hlwb txha caj qaum (CSF analysis).
- Kev kuaj duab, zoo li kev luam theej duab MRI ntawm lub hlwb .
- Kev kuaj 'EEG' ('EEG - electroencephalogram'), uas ntsuas qhov ua haujlwm hluav taws xob ntawm lub hlwb.
- Kev ntsuam xyuas 'Evoked Potential'(`Ua rau muaj kev sim ua ntej`).
- Kev ntsuam xyuas kev hais lus thiab kev paub .
Cov kev ntsuam xyuas no yuav pab peb nrhiav seb qhov ua rau yog dab tsi.
Yuav kho li cas?
Tsis muaj kev kho mob ncaj qha rau tus kab mob Pseudobulbar Palsy. Hloov chaw, koj pab neeg kho mob yuav pom zoo ntau yam kev kho mob los tswj cov tsos mob ntawm tus mob. Tsis tas li ntawd, tej zaum yuav tsum tau kho tus mob tseem ceeb.
Rau qhov no, koj yuav xav tau kev pab los ntawm ib pab kws kho mob uas muaj ntau tus kws tshwj xeeb. Ntawm lawv yog:
- Koj tus kws kho mob hauv tsev neeg ('Tus kws kho mob thawj zaug').
- Cov kws kho mob hlwb.
- Cov kws kho mob hais lus.
- Cov kws kho mob ua pa.
- Cov kws kho mob hlwb lossis cov kws kho mob hlwb.
- Cov neeg ua haujlwm pabcuam zej zog.
- Cov kws muag tshuaj.
Kev kho mob rau qhov nyuaj nqos (Dysphagia)
Muaj ntau txoj kev kho mob sib txawv nyob ntawm seb qhov teeb meem nqos hnyav npaum li cas. Qee qhov ntawm lawv suav nrog:
- Hloov qhov chaw noj mov, hloov cov khoom siv noj mov, thiab hloov qhov sib xws ntawm cov khoom noj. Piv txwv li, koj tuaj yeem zom cov khoom noj kom zoo thiab ua kom nws ua kua ntau dua kom yooj yim dua rau nqos.
- Kev tawm dag zog kom cov leeg nqaij muaj zog uas pab nqos ('Kev cob qhia cov leeg nqaij nqos').
- Kev kho mob lub cev, xws li kev siv hluav taws xob, sib nqus lossis thermal stimulation.
- Cov tshuaj, piv txwv li, cov tshuaj xws li 'nifedipine' thiab 'metoclopramide'.
Nco ntsoov tias, yog tias koj noj tsis tau lossis haus tsis tau zoo, lossis yog tias koj muaj feem yuav ua rau koj txhaws, koj tus kws kho mob yuav pom zoo kom koj pub koj noj los ntawm ib lub raj ('feeding tube') uas muab ntxig ncaj qha rau hauv koj lub qhov ntswg lossis lub plab .
Kev kho mob rau kev hais lus tsis meej
Yog koj muaj teeb meem hais lus, kev kho mob hais lus yuav pab tau heev. Tus kws kho mob hais lus tsis yog qhia koj xwb, tab sis kuj qhia koj tsev neeg txog kev sib txuas lus zoo dua nrog koj.
Thaum lub sijhawm kawm txog kev hais lus, koj tuaj yeem kawm tej yam xws li:
- Cov kev tawm dag zog uas ua rau tus nplaig, daim di ncauj, thiab cov leeg ntawm lub puab tsaig muaj zog (yog tias ua tau).
- Cov tswv yim rau kev hais lus kom meej dua, xws li qeeb koj qhov kev hais lus thiab siv cov leeg nqaij tshwj xeeb los hais cov suab thiab cov lus.
- Cov kev qhia tawm cov tswv yim yam tsis siv cov lus, xws li kev siv lus piav tes lossis kev sau ntawv.
Kev kho mob rau kev qhia tawm kev xav uas tsis tswj tau (`Pseudobulbar Affect - PBA`)
Cov tshuaj siv los tswj "Pseudobulbar Affect (PBA), ib yam mob uas koj luag thiab quaj tsis tu ncuaNws yuav pab tau. Koj tus kws kho mob yuav sau ntawv kom koj noj cov tshuaj xws li:
- Dextromethorphan/quinidine sulfate (Nuedexta®): Lub Koom Haum Saib Xyuas Khoom Noj thiab Tshuaj ntawm Teb Chaws Asmeskas (FDA) tau pom zoo cov tshuaj no ua thawj cov tshuaj uas tsim tshwj xeeb los kho PBA. Nws muaj cov tshuaj hnoos thiab cov tshuaj tsawg uas tau siv los kho cov teeb meem plawv dhia tsis zoo.
- Cov Tshuaj Tiv Thaiv Kev Nyuaj Siab : Cov tshuaj xws li tricyclic antidepressants, SSRIs (Selective serotonin reuptake inhibitors), thiab SNRIs (Serotonin thiab norepinephrine reuptake inhibitors) kuj tuaj yeem pab tswj cov tsos mob ntawm PBA.
Qhov teeb meem no yuav zoo li cas? Puas kho tau?
Qhov kev kwv yees ntawm ib tus neeg uas muaj tus kab mob pseudobulbar palsy feem ntau yog txiav txim siab los ntawm tus kab mob hauv qab.
Xav txog seb, yog tias koj muaj tus mob no vim yog "mob stroke" lossis "raug mob hlwb, " muaj peev xwm ua rau cov hlab ntsha ua haujlwm qeeb qeeb rov qab mus rau qhov qub. Yog li ntawd, cov tsos mob ntawm pseudobulbar palsy yuav maj mam txo qis.
Txawm li cas los xij, yog tias tus mob no yog tshwm sim los ntawm cov mob hnyav xws li ntau yam sclerosis (MS), Parkinson's disease, thiab ALS, feem ntau nws nyuaj rau xav tias yuav kho tau.
Koj pab neeg kho mob yuav muaj peev xwm muab lub tswv yim meej rau koj txog yav tom ntej rau koj qhov xwm txheej tshwj xeeb.
Qhov no ua rau muaj teeb meem dab tsi ntxiv?
Kab mob Pseudobulbar palsy tuaj yeem ua rau muaj teeb meem xws li:
- Mob ntsws los ntawm kev nqus pa: Vim tias cov leeg ntawm tus nplaig thiab qhov ncauj nyuaj rau tswj, me ntsis khoom noj lossis dej haus tuaj yeem nkag mus rau hauv lub ntsws, ua rau muaj mob hu ua mob ntsws los ntawm kev nqus pa. Qhov no tuaj yeem txaus ntshai.
- Kev tsis noj zaub mov zoo thiab lub cev qhuav dej: Yog tias dysphagia hnyav heev, kev tsis noj zaub mov zoo thiab lub cev qhuav dej tuaj yeem tshwm sim vim tsis muaj peev xwm noj thiab haus dej kom zoo. Hauv cov xwm txheej hnyav, tej zaum yuav xav tau ib lub raj pub mis.
- Tej yam kev mob hlwb: Kab mob Pseudobulbar palsy muaj peev xwm cuam tshuam loj rau koj lub neej txhua hnub. Tej zaum koj yuav tsis koom nrog lwm tus vim yog tej yam xws li nyuaj hais lus thiab tsis tswj tau kev xav. Qhov no tuaj yeem ua rau muaj teeb meem kev noj qab haus huv xws li kev nyuaj siab thiab kev ntxhov siab .
Puas yog Pseudobulbar Palsy ua rau tuag taus?
Kab mob Pseudobulbar palsy tsis yog qhov ua rau neeg tuag taus. Txawm li cas los xij, tus kab mob hauv qab uas ua rau nws (piv txwv li, tuag tes tuag taw )`, `ALS`) tuaj yeem ua rau tuag taus. Tsis tas li ntawd, cov teeb meem xws li 'mob ntsws los ntawm kev nqus pa' tuaj yeem ua rau tuag taus yog tias tsis kho kom zoo.
Puas muaj ib txoj kev los tiv thaiv qhov no?
Vim muaj ntau yam ua rau mob pseudobulbar palsy, tsis muaj txoj hauv kev los tiv thaiv nws. Txawm li cas los xij, kev ua raws li kev noj qab haus huv uas tuaj yeem tiv thaiv cov yam txaus ntshai xws li "kev tuag tes tuag taw" tuaj yeem pab tau tsis ncaj qha.
Kuv yuav tsum mus ntsib kws kho mob thaum twg?
Yog koj muaj mob Pseudobulbar Palsy, koj yuav tsum ntsib koj pab neeg kho mob tsis tu ncua kom paub tseeb tias koj txoj kev npaj kho mob ua haujlwm tau zoo.
Qhov mob no tuaj yeem muaj kev cuam tshuam loj rau koj lub neej txhua hnub, thiab koj yuav xav tias koj ntxhov siab heev. Thaum lub sijhawm zoo li no , tsis txhob yig nrhiav kev pab los ntawm koj cov neeg hlub, nrog rau tus kws pab tswv yim kev noj qab haus huv ntawm lub hlwb . Nco ntsoov, koj pab neeg kho mob yeej ib txwm nrog koj los nrhiav txoj kev npaj kho mob uas zoo tshaj plaws rau koj.
Cov Lus Qhia Txog Kev Coj Mus Tsev
Zoo, yog li cia peb nco ntsoov qhov no ua ib qho kev qhia luv luv ntawm tus kab mob Pseudobulbar Palsy uas peb tau tham txog hnub no:
- Qhov no tsis yog ib yam kab mob sib cais, tab sis yog cov tsos mob uas tshwm sim los ntawm kev puas tsuaj rau ib feem ntawm lub hlwb.
- Cov tsos mob tseem ceeb yog nyuaj hais lus, nyuaj nqos, thiab luag lossis quaj tsis tuaj yeem tswj tau.
- Cov ua rau muaj xws li cov kab mob ntawm lub paj hlwb xws li tuag tes tuag taw, kab mob Parkinson, MS, lossis raug mob taub hau .
- Kev kho mob yog tsom mus rau kev kho qhov mob tseem ceeb thiab tswj cov tsos mob. Kev kho kev hais lus, kev cob qhia nqos, thiab cov tshuaj tuaj yeem pab tau qhov no.
- Nws yog ib qho tseem ceeb heev uas yuav tsum paub txog cov tsos mob sai sai thiab nrhiav kev pab kho mob.
- Koj txoj kev hlub, kev txhawb nqa, thiab kev nkag siab muaj nqis heev rau ib tus neeg uas muaj tus mob no.
Yog koj lossis ib tug neeg ze koj muaj cov tsos mob no, thov mus ntsib kws kho mob kom tau lus qhia. Qhov ntawd yog qhov zoo tshaj plaws uas koj ua tau.
` Kab mob Pseudobulbar palsy, teeb meem ntawm lub hlwb, teeb meem hais lus, teeb meem nqos, kab mob ntawm lub paj hlwb, kev tswj hwm kev xav, PBA











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus