Koj puas tau hnov txog lo lus G6PD? Tej zaum ib tug kws kho mob tau qhia koj txog nws, lossis tej zaum ib tug neeg hauv koj tsev neeg tau qhia. Los yog tej zaum nws yog ib yam dab tsi tshiab rau koj. Txawm li cas los xij, tsis txhob ntshai thaum koj hnov lub npe. G6PD deficiency yog ib qho mob caj ces uas cuam tshuam rau kwv yees li 400 lab tus tib neeg thoob ntiaj teb. Nws zoo li kev hloov pauv me me hauv peb lub cev dua li kab mob. Yog li cia peb tham txog nws yooj yim heev thiab hauv txoj kev phooj ywg hnub no.
Qhov tsis muaj G6PD yog dab tsi tiag?
Zoo, cia peb hais yooj yim xwb. Peb cov ntshav muaj ib hom qe ntshav hu ua qe ntshav liab . Cov qe ntshav no nqa oxygen thoob plaws peb lub cev. Nws zoo li lub tsheb uas nqa khoom mus rau lub tsev.
Tam sim no, muaj ib qho enzyme tshwj xeeb uas pab cov qe ntshav liab no kom noj qab nyob zoo thiab muaj zog. Peb hu nws tias 'Glucose-6-Phosphate Dehydrogenase', lossis G6PD luv luv. Xav txog qhov enzyme no ua tus tiv thaiv cov qe ntshav liab, lossis 'lub zog' uas muab zog rau lawv. Qhov enzyme G6PD no tiv thaiv cov qe ntshav liab ntawm qee cov tshuaj lom hauv cov ntshav.
Qhov uas tshwm sim hauv lub cev ntawm ib tus neeg uas muaj G6PD deficiency yog tias cov G6PD enzyme tsis tau tsim tawm ntau txaus. Los yog cov enzyme uas tsim tawm tsis ua haujlwm zoo. Qhov no yog los ntawm noob caj noob ces . Qhov ntawd txhais tau tias koj tau txais qhov no los ntawm koj niam lossis koj txiv, thiab nws tsis yog ib yam kab mob sib kis.
Feem ntau, qhov muaj G6PD deficiency tsis yog teeb meem loj. Txawm li cas los xij, yog tias koj noj qee yam tshuaj, tshuaj lom neeg, lossis qee yam khoom noj (tshwj xeeb tshaj yog qee hom taum), cov qe ntshav liab pib puas tsuaj vim tias tus tiv thaiv ntawd ploj lawm. Qhov no yog qhov peb hu ua 'hemolytic anemia.' Cia peb saib nws ntxiv me ntsis.
Cov tsos mob yog dab tsi? Peb yuav paub qhov no li cas?
Qhov xav tsis thoob ntawm no yog tias ntau tus neeg uas muaj G6PD deficiency tsis qhia cov tsos mob . Lawv ua neej nyob li qub. Qhov teeb meem tsuas yog tshwm sim thaum lawv raug ib qho ntawm cov 'ua rau' uas peb tau hais ua ntej, uas yog, tshuaj lossis zaub mov tsis zoo.
Txawm li cas los xij, qee zaum tus menyuam mos tuaj yeem muaj mob daj ntseg (tawv nqaij daj) tom qab yug los, uas feem ntau yooj yim kho.
Yog tias ib tug neeg uas muaj G6PD deficiency raug rau ib yam dab tsi uas ua rau mob, lawv tuaj yeem tsim ib qho mob hu ua 'hemolytic anemia.' Hais yooj yim xwb, qhov no yog thaum cov qe ntshav liab tawg thiab raug rhuav tshem sai dua li lawv tuaj yeem tsim tau. Cov qe ntshav liab yog cov uas nqa oxygen mus thoob plaws lub cev. Yog li thaum lawv raug rhuav tshem, lub cev cov kabmob tsis tau txais oxygen uas lawv xav tau.
Yog tias qhov mob "hemolytic anemia" no tshwm sim, nws yuav loj heev. Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum paub txog cov tsos mob no.
Cov lus hauv qab no teev cov tsos mob ntawm cov ntshav tsis txaus (hemolytic anemia).
| Cov tsos mob | Kev piav qhia |
|---|---|
| Daim tawv nqaij daj ntseg | Daim tawv nqaij yuav hloov xim thiab dawb, zoo li lub cev tsis muaj ntshav. |
| Tawv nqaij thiab qhov muag daj (Jaundice) | Bilirubin, ib yam khoom tsim tawm thaum cov qe ntshav liab tawg, ua rau daim tawv nqaij thiab dawb ntawm lub qhov muag tig daj. |
| Cov zis tsaus nti | Cov zis hloov ua xim av tsaus lossis xim cola. |
| Ua npaws | Tej zaum koj yuav kub taub hau tsis muaj laj thawj. |
| Qaug zog thiab tsis muaj zog | Xav tias tsis muaj sia nyob, ua tsis taus pa, thiab qaug zog heev. |
| Kev tsis meej pem | Thaum lub hlwb tsis tau txais oxygen txaus, koj yuav xav tias tsis meej pem thiab tsis paub dab tsi. |
| Lub plawv dhia ceev | Lub plawv dhia nce ntxiv. |
Yog tias cov tsos mob no hnyav thiab kav ntev, koj yuav tsum mus ntsib kws kho mob tam sim ntawd . Qee zaum koj yuav tsum mus rau chav kho mob ceev (ETU) ntawm tsev kho mob.Nws kuj tseem yuav tsum tau muab tshem tawm. Tab sis feem ntau, thaum qhov ua rau muaj tus mob no raug tshem tawm, nws yuav kho nws tus kheej li ntawm ob lub lis piam.
Vim li cas ho muaj li no? Leej twg yuav muaj feem ntau dua?
Raws li peb tau hais ua ntej lawm, G6PD deficiency yog ib yam mob uas los ntawm noob caj noob ces . Qhov no txhais tau tias koj tau txais nws los ntawm koj niam koj txiv. Tsis muaj ib txoj kev los tiv thaiv nws.
Txawm li cas los xij, qee pawg neeg muaj feem yuav mob no ntau dua.
- Rau cov txiv neej (ntau dua li cov poj niam).
- Rau cov neeg nyob hauv cov tebchaws hauv Africa, Asia, Middle East, thiab thaj tsam Mediterranean.
Yog koj paub tias muaj ib tug neeg hauv koj tsev neeg muaj tus kab mob G6PD deficiency, ces tej zaum koj kuj yuav muaj tus kab mob no thiab. Yog li ntawd, nws yog ib lub tswv yim zoo uas koj nrog koj tus kws kho mob tham txog qhov no.
Yuav ua li cas koj thiaj paub tias koj muaj G6PD deficiency?
Muaj ib txoj kev yooj yim heev los nrhiav. Qhov ntawd yog los ntawm kev kuaj ntshav . Koj tus kws kho mob yuav pom zoo kom ua qhov kev kuaj no raws li koj keeb kwm tsev neeg thiab yog tias koj muaj cov tsos mob.
Feem ntau, yuav tsum kuaj ua ntej kom paub seb puas muaj G6PD deficiency. Yog tias qhia tau tias muaj deficiency, yuav tsum kuaj ntxiv kom paub seb nws hnyav npaum li cas. Ib qho kev kuaj hu ua 'Beutler' yog ib qho kev kuaj zoo li no.
Los ntawm cov kev kuaj no, koj tuaj yeem paub tseeb tias koj puas muaj G6PD deficiency thiab, yog tias muaj, qib twg yog.
Yuav ua li cas thiaj nyob tau nrog tus neeg uas muaj G6PD deficiency? Yuav tsum zam tej yam dab tsi?
Qhov no yog qhov tseem ceeb tshaj plaws. Yog tias koj raug kuaj pom tias muaj G6PD deficiency, tsis tas yuav kho mob tshwj xeeb . Txhua yam koj yuav tsum ua yog zam cov 'triggers' uas ua rau koj cov qe ntshav liab puas tsuaj thiab ua rau muaj mob hu ua hemolytic anemia.
Qhov ntawd txhais tau tias koj yuav tsum tsis txhob noj tshuaj, tshuaj lom neeg, thiab zaub mov kiag li. Cov no hu ua tej yam uas ua rau 'oxidative stress'.
Nco ntsoov lub rooj hauv qab no. Nws yog ib qho tseem ceeb heev uas yuav tsum tsis txhob muab tej no tso rau hauv koj lub neej.
| Tej yam uas cov neeg uas muaj G6PD deficiency yuav tsum tsis txhob ua | |
|---|---|
| Hom | Piv txwv |
| Khoom noj | Taum Fava - Qhov no yog cov khoom noj tseem ceeb thiab txaus ntshai tshaj plaws. Hauv qee lub tebchaws, cov no kuj hu ua taum dav. |
| Cov tshuaj kho mob | Qee cov tshuaj tua kab mob (piv txwv li, tshuaj aspirin ntau) |
| Cov tshuaj tua kab mob uas muaj "Sulf" (piv txwv li Sulfonamides) | |
| Cov tshuaj tiv thaiv kab mob malaria uas muaj "quine" | |
| Cov tshuaj lom neeg | Naphthalene - Cov no pom muaj nyob rau hauv cov npauj npaim uas muab tso rau hauv cov khaub ncaws. Txawm tias nqus lawv cov ntxhiab tsw kuj yog qhov txaus ntshai. |
Tseem Ceeb: Yog tias koj muaj G6PD deficiency, koj yuav tsum qhia rau koj tus kws kho mob txhua zaus koj mus ntsib nws. Tom qab ntawd, thaum nws sau ntawv kom koj noj tshuaj, nws yuav xaiv cov tshuaj uas muaj kev nyab xeeb rau koj. Tsis txhob noj tshuaj yam tsis tau sab laj nrog kws kho mob ua ntej.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Tsis yog ib yam kab mob uas yuav tsum ntshai. Nws yog ib yam kab mob uas ntau tus neeg hauv ntiaj teb muaj, thiab nws yog ib yam kab mob uas tau kis los ntawm ib tiam dhau ib tiam.
- Muaj coob tus neeg tsis muaj tsos mob thiab tsuas yog mob yog tias lawv raug tshuaj, khoom noj (tshwj xeeb tshaj yog taum fava), lossis tshuaj lom neeg.
- Yuav kom koj tswj tau koj lub neej kom zoo, koj yuav tsum paub meej tias yam twg tsis zoo rau koj thiab nyob deb ntawm tej yam ntawd.
- Yog koj muaj cov tsos mob xws li kub taub hau, qaug zog heev, tawv nqaij daj, thiab zis dub, mus ntsib kws kho mob tam sim ntawd.
- Nco ntsoov qhia koj tus kws kho mob txhua zaus koj mus ntsib nws tias koj muaj G6PD deficiency. Nws yog ib qho tseem ceeb heev rau koj txoj kev nyab xeeb.











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus