Puas muaj tej lub sij hawm koj cia li pib khaus, koj daim tawv nqaij liab thiab tawm pob liab? Los yog koj cia li mob plab thiab xav ntuav? Tej lub sij hawm tej yam no tshwm sim tom qab siv tshuaj tsw qab, los yog tom qab noj ib yam khoom noj, thiab tej lub sij hawm lawv tuaj yeem tshwm sim yam tsis muaj laj thawj li. Yog tias koj nrhiav tsis tau ib qho laj thawj rau qhov no, thiab koj muaj cov tsos mob sib txawv ntawm lub sij hawm sib txawv, tej zaum nws yog ib yam dab tsi ntau tshaj li kev ua xua xwb. Hnub no peb tab tom tham txog ib qho mob zoo li no, Mast Cell Activation Syndrome (MCAS).
Kab mob Mast Cell Activation Syndrome (MCAS) yog dab tsi?
Hais yooj yim xwb, MCAS yog ib qho mob uas ib hom cell hauv peb lub cev hu ua 'mast cells' ua haujlwm ntau dhau thiab tsis tsim nyog, tso tawm ntau cov tshuaj lom neeg uas lawv muaj rau hauv lub cev.
Tam sim no cia peb saib seb cov mast cell no yog dab tsi. Xav txog cov cell no ua lub cev tiv thaiv kev nyab xeeb. Lawv yog ib feem ntawm peb lub cev tiv thaiv kab mob. Lawv txoj haujlwm tseem ceeb yog tawm tsam kev kis kab mob. Tab sis kev ua xua kuj yog los ntawm cov cell no. Feem ntau, thaum muaj qee yam tsis zoo rau peb, piv txwv li, ib qho allergen nkag mus rau hauv lub cev, cov mast cell no ua haujlwm thiab tso cov tshuaj hu ua 'mediators'. Cov tshuaj no yog qhov ua rau muaj kev ua xua hauv peb lub cev. Hauv ib tus neeg noj qab haus huv, cov txheej txheem no yog los tiv thaiv peb.
Tiam sis, rau ib tug neeg uas muaj MCAS, cov mast cell no rhiab heev heev . Lawv zoo siab dhau txog txawm tias yog yam me tshaj plaws thiab tso tawm ntau yam tshuaj lom neeg ib zaug. Zoo li coj ib pab tub rog tag nrho mus ntes ib tug tub sab me me. Cov tshuaj lom neeg tsis xav tau no yog qhov ua rau muaj ntau yam tsos mob txawv txawv, uas peb tau tham txog ua ntej.
Muaj ntau yam uas feem ntau tuaj yeem ua rau cov hlwb mast no ua haujlwm:
- Kev kis kab mob
- Qee cov tshuaj
- Tshuaj lom los ntawm kab tom
- Cov tshuaj tsw qab
- Kev ntxhov siab
- Kev tawm dag zog
- Qee cov khoom noj
- Kev hloov pauv sai sai ntawm qhov kub thiab txias
MCAS thiab Mastocytosis puas yog ob yam sib txawv?
Yog, tsis txhob xav tsis thoob ob qho no. Txawm hais tias ob qho mob no cuam tshuam nrog cov hlwb mast, lawv txawv.
| Mob nkeeg | Hais yooj yim xwb, ua li cas lawm? |
|---|---|
| Mastocytosis | Qhov tshwm sim hauv qhov no yog tias lub cev tsim cov mast cell ntau dhau. Nws zoo li nrhiav neeg ua haujlwm ntau dhau rau cov neeg saib xyuas kev ruaj ntseg. Cov cell ntau dhau no sib sau ua ke hauv cov kabmob xws li daim tawv nqaij, siab, thiab txoj hnyuv. Qhov no yog ib qho mob tsis tshua muaj. |
| MCAS (Mast Cell Activation Syndrome) | Qhov uas tshwm sim hauv qhov no yog tias cov mast cell hauv lub cev yog qhov ib txwm muaj, tab sis cov cell uas nyob ntawd dhau los ua hyperactive. Cov neeg zov uas nyob ntawd zoo siab txog qhov me me thiab tso cov tshuaj lom neeg tawm. |
Cov ua rau muaj MCAS yog dab tsi?
MCAS muaj peb pawg tseem ceeb raws li qhov ua rau.
1. MCAS Thawj Zaug: Qhov no yog tshwm sim los ntawm teeb meem nrog cov hlwb mast lawv tus kheej. Feem ntau, kev hloov pauv hauv cov noob caj noob ces "(KIT)" ua rau cov hlwb no ua haujlwm tsis zoo. Mastocytosis yog qhov mob tseem ceeb hauv hom no.
2. MCAS Thib Ob: Qhov no tshwm sim thaum cov hlwb mast raug txhawb los ntawm lwm yam ua rau sab nraud. Piv txwv li, qhov no tuaj yeem tshwm sim los ntawm kev ua xua hnyav, kev kis kab mob ntev, lossis lwm yam mob.
3. Idiopathic MCAS: "Idiopathic" txhais tau tias "tsis muaj laj thawj twg nrhiav tau." Feem ntau ntawm cov neeg mob MCAS muaj hom no. Qhov no txhais tau tias tsis muaj laj thawj tshwj xeeb vim li cas cov mast cell no thiaj ua tsis zoo. Cov tsos mob yuav tshwm sim rau tej yam tshiab txhua lub sijhawm.
Cov tsos mob ntawm MCAS yog dab tsi?
Ib qho ntawm cov teeb meem loj tshaj plaws nrog MCAS yog tias cov tsos mob muaj ntau yam thiab tuaj yeem cuam tshuam rau ntau lub cev tib lub sijhawm.
| Pawg tsos mob | Cov tsos mob uas pom ntau zaus |
|---|---|
| Daim tawv nqaij thiab cov yam ntxwv dav dav | Ntshav ntws, khaus, ua pob khaus/mob pob khaus, o, tawm hws ntau dhau, qaug zog tas li, mob lub cev. |
| Kev zom zaub mov | Mob plab, xeev siab, ntuav, raws plab, cem quav. |
| Lub paj hlwb (Neurological) | Mob taub hau, nco qab thiab tsom ntsoov (Lub hlwb tsis meej), kiv taub hau, tsaus muag, ntxhov siab, nyuaj siab, pw tsis tsaug zog. |
| Lub plawv thiab lub cev ua pa | Lub plawv dhia ceev los yog tsis xwm yeem (palpitations), ua pa nyuaj, hauv siab nruj. |
Kev Ceeb Toom Tshwj Xeeb: Kev Poob Siab Anaphylactic
Anaphylaxis yog qhov mob txaus ntshai tshaj plaws thiab ua rau tuag taus uas tuaj yeem tshwm sim rau cov neeg uas muaj MCAS. Qhov no yog ib qho mob uas xav tau kev kho mob thaum muaj xwm txheej ceev.
Cov tsos mob ntawm anaphylaxis:
- Ua pa nyuaj, xav tias koj lub caj pas raug nqaim
- Qhov o ntawm daim di ncauj, tus nplaig, lossis lub ntsej muag
- Lub plawv dhia ceev heev.
- Ntshav siab poob qis tam sim ntawd
- Mob taub hau hnyav thiab tsaus muag
- Ntuav thiab raws plab
- Muaj pob liab thiab pob khaus thoob plaws lub cev tam sim ntawd
Yog tias koj muaj ib lossis ntau yam ntawm cov tsos mob no, tsis txhob ncua sijhawm. Hu rau lub tsheb thauj neeg mob tam sim ntawd lossis mus rau Chav Kho Mob Thaum Muaj Xwm Ceev (ETU) ntawm lub tsev kho mob ze tshaj plaws.
Kuv yuav ua li cas thiaj paub tias kuv muaj MCAS?
Kev kuaj mob MCAS yuav nyuaj me ntsis vim tias cov tsos mob sib txawv heev. Koj tus kws kho mob feem ntau yuav saib peb yam tshwj xeeb.
1. Cov tsos mob: Muaj cov tsos mob zoo li ua xua rov tshwm sim tas li hauv ob lossis ntau lub cev (piv txwv li, daim tawv nqaij thiab txoj hnyuv).
2. Kev Kuaj: Cov ntshav lossis zis uas tau coj thaum cov tsos mob tshwm sim qhia tau tias muaj cov tshuaj lom neeg xws li "tryptase" thiab "histamine" ntau heev, uas cov hlwb mast tso tawm.
3. Kev teb rau kev kho mob: Cov tsos mob yuav txo qis thaum muab cov tshuaj uas thaiv cov mast cell ua haujlwm, xws li cov tshuaj antihistamines.
Yog tias ua tau raws li peb yam no, tus kws kho mob yuav xav tias muaj MCAS. Qee zaum MCAS muaj ib yam mob hu ua "(POTS)" - Postural Orthostatic Tachycardia Syndrome. Qhov no yog thaum lub plawv dhia nce ntxiv tsis zoo thaum sawv ntsug.
Yuav kho li cas?
Tseem tsis tau muaj tshuaj kho mob MCAS. Txawm li cas los xij, cov tsos mob tuaj yeem tswj tau zoo thiab ua tau lub neej zoo li qub. Kev kho mob muaj ob lub hom phiaj tseem ceeb.
1. Tsis txhob ua rau muaj mob: Qhov tseem ceeb tshaj plaws yog nrhiav seb yam dab tsi ua rau koj muaj mob thiab zam kom tsis txhob muaj mob.
2. Tswj cov tsos mob nrog tshuaj: Tus kws kho mob yuav sau ntau yam tshuaj rau koj.
- Cov tshuaj antihistamines H1 thiab H2: Cov tshuaj zoo li Cetirizine, Loratadine, Famotidine.
- Cov Tshuaj Tiv Thaiv Mast Cell: Cov tshuaj uas tiv thaiv kev tso tawm cov tshuaj lom neeg los ntawm cov hlwb mast.
- Cov tshuaj Leukotriene Inhibitors: Cov tshuaj zoo li Montelukast.
- Rau tej xwm txheej ceev: Yog tias muaj kev pheej hmoo ntawm kev ua xua anaphylaxis, cov kws kho mob qhia kom ib txwm muaj lub tshuab txhaj tshuaj (xws li EpiPen) uas muaj '(epinephrine)' nyob ze.
Tej yam yuav tsum xav txog thaum nyob nrog MCAS
Kev nyob nrog MCAS tuaj yeem nyuaj, tab sis nrog kev tswj hwm kom zoo , koj tuaj yeem nyob tau zoo nrog tus mob no.
- Kev Noj Haus: Tej yam khoom noj muaj peev xwm ua rau MCAS ua rau muaj. Ceev faj tshwj xeeb nrog cov khoom noj uas muaj histamine ntau (cheese fermented, ntses kaus poom, txiv lws suav, spinach, chocolate). Nws yog qhov zoo tshaj plaws los sab laj nrog koj tus kws kho mob thiab mus ntsib tus kws noj zaub mov kom tsim ib txoj kev npaj noj haus uas haum rau koj.
- Kev tswj kev ntxhov siab: Kev ntxhov siab yog ib qho tseem ceeb uas ua rau muaj MCAS. Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum ua kom koj lub siab so. Tej yam xws li kev xav, kev yoga, thiab kev ua si nyiam yuav pab tau.
- Nrhiav kev pab: Tham nrog tsev neeg thiab cov phooj ywg txog koj tus mob. Nws kuj tseem yuav pab tau yog tias koj koom nrog cov pab pawg txhawb nqa nrog cov neeg uas tab tom ntsib cov xwm txheej zoo sib xws.
- Kev sib txuas lus tsis tu ncua nrog koj tus kws kho mob: Tham nrog koj tus kws kho mob tsis tu ncua thiab hloov kho koj txoj kev npaj kho mob raws li qhov xav tau.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Kab mob Mast Cell Activation Syndrome (MCAS) tsis yog ib qho kev xav xwb, tab sis yog ib qho mob tiag tiag uas cuam tshuam nrog lub cev tiv thaiv kab mob.
- Cov tsos mob yuav txawv ntawm ib tus neeg mus rau ib tus neeg. Yog tias koj muaj ntau yam tsos mob uas koj nrhiav tsis tau qhov ua rau, mus ntsib kws kho mob.
- Kev txheeb xyuas thiab zam cov teeb meem uas ua rau koj cov tsos mob yog ib feem tseem ceeb ntawm kev kho mob.
- Anaphylaxis yog ib qho xwm txheej ceev uas ua rau tuag taus thiab yuav tsum tau kho tam sim ntawd. Yuav tsum paub txog nws cov tsos mob.
- Yog tias koj kho tau zoo thiab hloov koj txoj kev ua neej, MCAS yuav tswj tau zoo thiab koj yuav ua tau lub neej zoo li qub. Ua haujlwm nrog koj tus kws kho mob kom ua tau li no.











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus