Yu dɔn ɛva yɛri bɔt Behçet in Sik? Di nem kin tan lɛk se i strenj smɔl. Bɔt na tru tru wan kɔmpleks, bɔt we pɔsin kin ebul fɔ kɔntrol we kin afɛkt bɔku difrɛn pat dɛn na wi bɔdi. So, lɛ wi tɔk bɔt am ditayli tide, rili simpul, lɛk fɔ tɔk to yu padi.
Wetin na Behçet in Sik?
Fɔ tɔk am simpul wan, di sik we dɛn kɔl Behçet na
wan sik we de mek di blɔd vesel dɛn na wi bɔdi wam ɔltɛm. dכkta dεn kin kכl am bak ``vasculitis.'' Dis na kכndyushכn we di bכdi kin swεla, rεd, εn i kin fil pen. I kin afɛkt ɔl tu di big blɔd vesel dɛm (arteries) ɛn di smɔl blɔd vesel dɛm (veins). Sɔmtɛm dɛn kin kɔl dis sik "Silk Road disease" bikɔs i kɔmɔn na di eria dɛn we de nia di Silk Road insay istri.
Udat dɛn kin gɛt dis sik mɔ?
Behçet in sik kin afɛkt ɛnibɔdi na di wɔl. Bɔt i kin apin mɔ na sɔm kɔntri dɛn. Fɔ ɛgzampul, i kin bɔku na di nɔt pat na Tɛki, kɔntri dɛn we de rawnd di Mɛditarenian Si, di Midul Is ɛn Is Eshia. I nɔ kin bɔku na kɔntri dɛn lɛk Amɛrika. Bɔrku tɛm, di sayn dɛm kin bigin fɔ sho
bitwin 20 ɛn 30 ia. Bɔt i kin apin pan ɛni ej. Pan ɔl we dɛn bin tink fɔs se i kin afɛkt man ɛn uman ikwal, sɔm stɔdi dɛn dɔn sho se
man dɛn kin gɛt dis sik smɔl .
Wetin na di sayn dɛm fɔ dis sik? Aw wi de fil?
Dis na di tin we impɔtant pas ɔl. De sayn dɛm fɔ Behçet in sik kin difrɛn frɔm wan pɔrsin to ɔda pɔrsin. Dis min se di sayn dɛm wae yu gɛt nɔr kin bi di sem wit ɔda pɔrsin. Bɔt sɔm impɔtant sayn dɛn de we kin apin.
Sɔl dɛn na yu mɔt
Dis na
di fɔs sayn we bɔku pipul dɛn kin notis . I tan lɛk di kansa sos we wi kin gɛt na wi mɔt, bɔt i kin
big, i kin gɛt mɔ ɛn mɔ, ɛn i kin mek wi fil pen . Sɔm pipul dɛn kin gɛt dɛn mɔt sos ya bifo ɛni ɔda sayn fɔ sho. Dɛn kin apia na di lip, di tɔŋ, ɛn insay di chɛst.
Imajin, yu kin gɛt ɔlsa na yu mɔt ɔltɛm , i kin at so dat yu nɔ kin ivin ebul fɔ it ɔ drink, ɛn ivin afta yu dɔn tek mɛrɛsin, i kin kam bak afta sɔm dez. Dat na situeshɔn lɛk dat.
Sɔl dɛn we de na di bɔdi
Lεk mכt sכm, jεnital sכr kin apin bak. Dɛn tin ya kin mek pɔsin fil pen bak. dεn kin apin bak na di skrotum pan man dεm εn di vulva na uman dεm. Bɔt dɛn nɔ kin bɔku lɛk aw pɔsin kin gɛt mɔt.
Ay inflamɛns
Inflameshɔn na di yay na siriɔs sayn bak fɔ dis sik. Dis kin mek yu
gɛt rɛd rɛd, pen, yu nɔ kin si fayn, yu nɔ kin si layt, ɛn yu yay kin gɛt wata . If dɛn nɔ trit am fayn,
i kin mek i nɔ ebul fɔ si fayn igen.Chans de fɔ du dat. Ripɔt dɔn se dis kayn we aw pɔsin in yay kin pwɛl kin bɔku mɔ na kɔntri dɛn lɛk di Midul Is ɛn Jepan.
Prɔblɛm dɛn we de na di skin
Prɔblɛm dɛn bak na di skin kin bɔku. sכmtεm, blista dεm we lεk pimple εn rεd nodul dεm (erythema nodosum) kin apia. Dɛn bɔmp dɛn ya kin mek pɔsin fil pen fɔ tɔch. Ɔda tɛm dɛn, ɔlsa kin kam na di skin. Sɔm pan dɛn tin ya kin de ɔp ɔp, ɛn ɔda wan dɛn kin dip. Wan ɔda tin we nɔ kɔmɔn na dat
if dɛn skrach ɔ chuk di skin, di say go tɔn rɛd ɛn smɔl blista go kɔmɔt insay sɔm dez . Dɔktɔ dɛn kɔl dis "positiv pathergy test."
Pen na di jɔyn dɛn
Jɔyn pen kin kɔmɔn bak pan dɛn sik pipul ya. I kin afɛkt
di anklɛ, ni, ɛlb, ɛn hip mɔ . Di jɔyn dɛn kin swel, dɛn kin rɛd, ɛn dɛn kin fil pen we dɛn tɔch dɛn. Bɔt bɔku tɛm, i nɔ kin pwɛl di jɔyn dɛn sote go.
Inflameshɔn na di vein
If yu inflamɛns insay di blɔd vesel dɛn, i kin mek
di blɔd klɔt, blok , ɔ ivin blok ɔl di blɔd vesel dɛn. dis kin afekt כl tu di supεrfishal vein dεm, we de nia di skin, εn di dip vein dεm, we de dip insay di bכdi. Sɔntɛnde, di big vein na wi bɔdi, we na di vena cava, kin afɛkt, we kin mek wi gɛt siriɔs wɛlbɔdi prɔblɛm. Dɛn blɔd vesel prɔblɛm ya kin kam bikɔs ɔf inflamɛns, nɔto bikɔs ɔf di bad tin we de na di blɔd we de mek di blɔd klɔt.
Di we aw di bren de involv
Sɔmtɛm dis sik kin afɛkt di bren bak. spεshal wan, di mεmbran dεm we de kכba di bren (meninges). Dɔn yu kin si sɔm sayn dɛm
lɛk fiva, bad bad ed pen, nɛk stif, i nɔ kin izi fɔ kɔdinɛt muvmɛnt we yu de waka . Sɔntɛnde
, strok kin apin bak. Dis na we wan blɔd vesel na di bren de blok ɔ bɔs.
di gεstrointestinal (GI) trakt fכm dεm
Prɔblɛm kin apin bak na di dijestiv sistɛm, dat na di intestinal. Yu kin si tin dɛn lɛk
bɛlɛ kramp ɛn blɔd na di stɔl . dis na biכs wund dεm na di mכt εn di jεnital εria, εn wund dεm insay di intestines. Dɛn wund ya na di intestinal kin denja smɔl, bikɔs dɛn kin mek blɔd kɔmɔt na di intestin ɔ i kin brok.
Efεkt pan כda כgan dεm
Pan ɔl we i nɔ kin apin so ɔltɛm, dis sik kin afɛkt ɔda pat dɛn bak lɛk di lɔng, kidni, ɛn big blɔd vesel (aorta).
Wetin mek di sik we dɛn kɔl Behçet kin apin? Wetin na di kɔz?
Dɛn nɔ no yet di rayt tin we kin mek pɔsin gɛt dis sik . Sayɛnsman dɛn stil de du risach bɔt am. wan tiori na se i kin bi ``autoimmune disorder.`` Fɔ tɔk am simpul wan, i min se
wi yon imyun sistεm, di sistεm we de protεkt wi frכm sik, de mistek atak wi כwn hεlty sεl dεm.. Dis atak na in de mek di inflammatory kondishכn dεm we wi bin dכn tכk bכt. sכm jin mak dεm, lεk `(HLA-B5)` εn `(HLA-B51), dεn kin si pan sכm pipul dεm we gεt dis sik. Bɔt nɔto ɔlman we gɛt dɛn jin mak ya kin gɛt di sik we dɛn kɔl Behçet. So, wi nɔ go ebul fɔ se na di jin dɛn nɔmɔ na in de mek i gɛt dis sik. Risach pipul dɛm biliv bak se
pan pipul dɛm wae gɛt dis sik na dɛn jɛnɛtiks, pipul dɛn kin tink se dis sik kin kam bikɔs ɔf infekshɔn (baktri ɔ vayral) . Dis min se ɔl tu di tin dɛn we de apin na di bɔdi ɛn di tin dɛn we de apin na di say we i de, kin afɛkt am.
Udat dɛn kin gɛt dis sik?
Sɔm pipul dɛn kin gɛt dis sik pas ɔda pipul dɛn:
- Pipul wae de liv na say wae dis sik kin kam (e.g. Turkey, Middle East).
- Pipul dɛn we ol bitwin 20 ɛn 40 ia .
- Pipul dεm we gεt sכm spεshal jin dεm (HLA-B5 כ HLA-B51) .
- Man dɛm (man dɛn kin gɛt dis sik pas uman dɛm).
Aw dɛn kin no dis sik kɔrɛkt wan? (Diagnosis) .
Nɔr wan tɛst nɔr de na di lɛbɔraytri fɔ no if yu gɛt Behçet in sik. Dɔktɔ dɛn kin no di sik bay di sayn dɛn we yu gɛt. Dɛn kin luk mɔ fɔ:
- Bɔku tɛm (bɔku tɛm pas tri tɛm insay di ia) we yu gɛt ɔlsa na yu mɔt bak .
- Apat frɔm dat, at le tu pan dɛn kwaliti dɛn ya fɔ de de :
- Injury to di genital eria.
- Inflameshɔn na di yay.
- Prɔblɛm dɛn we de na di skin.
- Pɔsitiv patɛji tɛst - Dis min se wan rɛd, we tan lɛk blista de apia insay sɔm dez afta yu dɔn prik ɔ prik yu skin. Dis kin gi yu aidia bɔt aw di imyun sistɛm de wok fayn fayn wan.
Fɔ no dis sik kɔrɛkt wan, i nid fɔ pul ɔda sik dɛn we kin mek pɔsin gɛt mɔt we fiba
di sik we dɛn kɔl Behçet . fכ egzampl, `(systemic lupus)`, `(Crohn's disease)` (wan inflammatory kכndishכn na di intestines), εn כda kayn `(vasculitis)`. Yu dɔktɔ kin tɛl yu fɔ du blɔd tɛst fɔ ɛp fɔ mek dɛn nɔ gɛt dɛn ɔda sik ya.
Dis na sik we pɔsin kin gɛt frɔm in mama ɛn papa?
No klia pruf nɔ de fɔ se di sik we Behçet gɛt frɔm in mama ɛn papa . Bɔrku pan di kes dɛm kin apin randomly, wae nɔr kin gɛt ɛni famili histri. Pan ɔl we dɛn dɔn ripɔt wan rili smɔl pasɛnt pan di kes dɛm pan sɔm pipul dɛm na di sem famili, no klia patɛn nɔ de we dɛn kin gɛt frɔm dɛn mama ɛn papa.
Wetin na di tritmɛnt dɛm fɔ dis? (Tritmɛnt)
No mɛrɛsin nɔ de fɔ dis sik yet . Bɔt sɔm mɛrɛsin dɛn de we kin ɛp fɔ kɔntrol di sayn dɛm:
- Kɔtikosterɔyd (e.g., prɛdnisɔn): Dɛn wan ya na di men tritmɛnt. Dɛn mɛrɛsin ya de ridyus di inflamɛns ɛn di ɔva aktiviti fɔ di imyun sistɛm.
- Colchicine (Colcrys®): Dis kin ɛp fɔ mek yu gɛt mɔt sɔri, yu bɔdi we gɛt bɔdi, ɛn sɔntɛnde yu gɛt pen na yu jɔyn.
- Ɔda mɛrɛsin dɛn we de mek pɔsin nɔ ebul fɔ fɛt di sik : Sɔm ɛgzampul dɛn na mɛtɔtreksɛt (Trexall®, Rasuvo®), azathioprine (Imuran®, Azasan®), sayklofosfamid (Cytoxan®, Neosar®), ɛn sayklosporin (Gengraf®, Neoral®, Sandimmune®). Insay di kes dɛm we rili siriɔs, dɛn kin yuz anti-TNF (Tumor Necrosis Factor) bayolojikal dɛm lɛk infliximab (Remicade®), etanercept (Enbrel®), ɛn tocilizumab (Actemra®) bak.
Impɔtant: Dɛn mɛrɛsin ya we de mek yu bɔdi nɔ gɛt bɛtɛ wɛlbɔdi kin mek yu bɔdi nɔ ebul fɔ fɛt sik, ɛn dis kin mek yu gɛt ɔda sik dɛn.
- Apremilast (Otezla®) : Dis na tablɛt we dɛn kin tek bay mɔt. Dɛn dɔn gri fɔ trit di mɔt sos pan pipul dɛn we gɛt di sik we dɛn kɔl Behçet.
Dipen pan aw yu sik bad, yu dɔktɔ kin tray fɔ kɔntrol di sayn dɛm wit tin dɛm lɛk ay drɔp, fɔ was yu mɔt, ɛn ɔnt fɔ yu skin bifo yu yuz dɛn mɛrɛsin ya.
Us kayn op yu kin gɛt we yu de liv wit dis sik?
Behçet in sik na
wan sik we nɔ de mɛn . Dis min se, pan ɔl we dɛn dɔn trit am, sɔntɛnde i kin dɔnawe ɛn i kin kam bak. Dis kin mek i nɔ izi fɔ tɔk klia wan aw di tritmɛnt kin wok fayn. Bɔrku pasɛnt go gɛt fɔ dil wit dɛn sik ya sɔmtɛm ɔlsay na dɛn layf. Bɔt
bɔku pipul dɛn kin liv nɔmal layf ɛn ful layf .
Aw fɔ bia wit dis sik fayn fayn wan?
Bɔrku we de fɔ ɛp wae yu de liv wit dis sik:
- Balans bitwin rɛst ɛn aktiviti : If yu de du ɛksɛsayz ɔltɛm, dat go mek yu bɔdi fil fayn, ridyus di pen na yu jɔyn ɛn ɔda say dɛn we yu gɛt prɔblɛm. Dɔn bak, fɔ tek sɔm tɛm fɔ rɛst we di sayn dɛn kin tranga, kin fayn fɔ yu maynd ɛn i kin ridyus di impak we di sayn dɛn kin gɛt.
- Shared experience and community : Dis min fɔ fɛn ɛn tɔk to ɔda pipul dɛm wae gɛt di sem kayn sik. Dis kin tranga bikɔs de sik nɔ kin bɔku. Bɔt yu dɔktɔ kin ɛp yu fɔ fɛn pipul dɛn we dɔn gɛt di sem tin.
Yu tink se dis sik kin kil pɔsin?
Di rεt wae de mכtalman frכm dis sik
na lεk 5%.Di men tin dɛn we kin mek pɔsin day na we di intestinal pɔrfyushɔn, strok, ɛn we di anɛrizm kin brok. Pan ɔl we di sik we dɛn kɔl Behçet nɔ kin kil pɔsin dairekt wan, i kin mek pɔsin gɛt difrɛn kayn wɛlbɔdi prɔblɛm ɛn sik dɛn we pɔsin kin gɛt na in bɔdi, ɛn bɔku pan dɛn kin mek pɔsin fil pen. Bɔt i
pɔsibul fɔ mek dɛn ebul fɔ kɔntrol di sik fayn fayn wan ɛn liv nɔmal layf . Ɛspɛshali if yu de ɛksesaiz ɔltɛm, rɛst, ɛn tɔk to ɔda pipul dɛn we de go tru di sem tin.
Fɔ dɔn, mɛmba dɛn tin ya!
Behçet in sik kin bi wan kɔmplikɛt ɛn nɔr kin fil fayn. Bɔt mɛmba se:
- Dis na sik we pɔsin kin ebul fɔ kɔntrol .
- If yu gɛt dɛn sik ya, go to dɔktɔ wantɛm wantɛm .
- Yu kin tray fɔ liv nɔrmal layf wit di rayt tritmɛnt ɛn chenj yu layf.
- Nɔ sɔfa yu wan, kɔnɛkt wit sɔpɔt grup ɔ ɔda pasɛnt dɛn .
A op se dis infɔmeshɔn go yusful to yu. Stay wit wɛlbɔdi!
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