Yu tink se di rayt say na yu at wik? Lɛ wi lan bɔt dis denja ARVD (Arrhythmogenic Right Ventricular Dysplasia)?

Oh, sɔntɛnde yu kin fil lɛk se yu chɛst de bit wantɛm wantɛm, yu kin fil lɛk se yu gɛt prɔblɛm fɔ blo, ɔ yu jɔs fil lɛk se yu gɛt at atak? Yu go dɔn yɛri se sɔntɛnde ivin yɔŋ atlet we gɛt wɛlbɔdi kin gɛt at atak wantɛm wantɛm. Na dat wi go tɔk bɔt tide, bɔt na smɔl tin we pipul dɛn nɔ no bɔt, na smɔl at sik we nɔ kin apin so ɔltɛm. dis dεn kכl am ``Arhythmogenic Right Ventricular Dysplasia``, כ ARVD fכ sכt.

Wetin na ARVD (Aritmojɛnik Rayt Vɛntrikular Displasia)? Lɛ wi ɔndastand am rili simpul wan!

Fɔ tɔk am simpul wan, ARVD na sik we de afɛkt di at mɔsul, we na wan kayn `cardiomyopathy`. Wi at gɛt 4 rum dɛn. wetin de apin insay dis na di mכsul we de na di lכw chεmba na di rayt say na yu at, di `rayt vεntrikl`, de gro insted fכ fεt εn fayv tisu. Tink bɔt am lɛk se dɛn dɔn rɔtin di mɔsul we gɛt wɛlbɔdi ɛn put sɔntin lɛk fat in ples.

Wetin kin apin we dis kin apin? Da rayt vεntrikl de de strεch sכmtεm, i de tכn, εn i nכ de ebul fכ kכntrak fayn fayn wan. Dat min se di ebul we i ebul fɔ pɔmp blɔd to di at kin wik.

di tin we imכtant pas ɔl na dat di nyu fεt כ fayv tisu we dεn fכm de ambɔg di at in ilektrikal signal dεm. Na dat mek bɔku pipul dɛm wae gɛt ARVD kin gɛt at bit we nɔr de ɔltɛm (arrhythmias). Dis kin rili denja, bikɔs i kin mek yu at at pwɛl wantɛm wantɛm ɔ day.

dis ARVD dεn kכl am bak `Aritmojεnik Rayt Vεntrikulכr Kadiomyopathy` (ARVC). sכmtεm i kin afekt di lεft sayd bak, so dεn kin kכl am bak `Arrhythmogenic Cardiomyopathy` (ACM).

Wetin na di stej dɛm fɔ ARVD?

If yu gɛt ARVD, i kin go tru sɔm stej dɛn as tɛm de go.

1. Stej we yu ayd: Insay dis stej, yu nɔ kin gɛt ɛni sayn. Bɔt yu kin gɛt at bit we nɔ de bit ɔltɛm we yu de du ɛksɛsayz. I sɔprayz fɔ no se sɔm tɛst dɛn we dɛn kin du insay dis stej kin sho se natin nɔ bad.

2. Ilektrikal stej: insay dis stej, yu kin gεt vεntrikulכr aritmia. Yu kin gɛt ay risk bak fɔ mek yu at day wantɛm wantɛm. ECG kin no dɛn at ritm prɔblɛm ya.

3. Structural stej: Insay dis stej, di risk fכ abnכmal hat ritm (ventricular rhythms) εn di kadyak day wan wan de ivin hכy. Test we dɛn kin yuz fɔ tek pikchɔ, lɛk fɔ skan, kin sho klia wan se di we aw yu at de chenj.

Udat dɛn kin afɛkt mɔ pan dis ARVD?

Dɔktɔ dɛn kin si dis sik bɔku tɛm pan yɔŋ pipul dɛn.Dat min se, bitwin yɔŋ pipul dɛn ɔ yɔŋ pipul dɛn. Dɛn dɔn no bak se ARVD na wan tin we kin mek sɔm yɔŋ atlet dɛn day wantɛm wantɛm. Sɔm stɔdi dɛn dɔn sho se dis sik kin mɔna man dɛn smɔl .

We yu tink bɔt aw i kɔmɔn, ARVD na sik we nɔ kin bɔku. Bɔrku tɛm, dɛn kin ripɔt se i kin afɛkt wan pan ɛvri 1,000 ɔ wan pan ɛvri 5,000 pipul dɛm. E kin apun wae nobodi na di famili nɔr gɛt am, bɔt bɔrku tɛm e kin rɔn na famili.

Wetin na di sayn dɛm fɔ ARVC? Mek wi no se!

Yu nɔ go gɛt ɛni sayn fɔ ARVD di fɔs tɛm, bɔt risk de fɔ mek yu at day wantɛm wantɛm.

De men sayn wae yu kin si na:

• Ventricular arrhythmias: Dɛn tin ya kin rili denja. Na lɛk af pan pipul dɛm wae gɛt dis arrhythmia, de autkam kin kil ɔr kin nia fɔ kil. di ritm we kכmכn pas כl na vεntrikul takikardia, we de apin pan 77% pan di pipul dεm we gεt dis kכndyushכn.
• Supraventricular arrhythmias: Di wan we kin kכmכn pas כl na wan kכndyushכn we dεn kכl atrial fibrillation.
• At de bit: Dis kin fil lɛk se sɔntin de bit insay yu chɛst. Dis kin kam bikɔs di at nɔ de bit fayn.
• Diziz, layt ed ɔr fɔdɔm: Dis kin kam bak bikɔs yu at nɔ de bit ɔltɛm.
• Chɛst de pen.
• Di at kin day wantɛm wantɛm: Sɔntɛnde dis kin bi di fɔs sayn fɔ ARVD.
• Shot we yu de blo.
• Di leg, anklɛ, fut, ɔ bɛlɛ kin swel.
• At we nɔ de wok fayn.

Dɛn sayn ya kin bigin bitwin 20 ɛn 50 ia.Dɔkta dɛn kin no se i gɛt ARVD we dɛn yɔŋ (bɔku tɛm bifo dɛn ol 40 ia).

Wetin na di tin dɛn we kin mek pɔsin gɛt ARVD?

Na lɛk 60% pan di pipul dɛm wae gɛt ARVD gɛt jɛnɛtik muteshon. Risach pipul dɛn dɔn no at le 13 jin dɛn we kin mek pɔsin gɛt dis sik.

dis abnכmal jin dεm de pwεl di protin dεm we de εp di at mכsul sεl dεm fכ kכnekt εn kכmכnik wit dεn wan dεm. dis kin mek di at mכsul sεl dεm na di rayt vεntrikl separet εn day. Dis kin apin mɔ we yu strɛs ɔ yu de tray tranga wan.

At ɔl 30% to 50% pan di wan dɛn we gɛt ARVD gɛt famili histri.So, i rili impɔtant fɔ mek dɔktɔ chɛk pɔsin we gɛt ARVD in fɔs ɛn sɛkɔn digri fambul (mama ɛn papa, brɔda ɛn sista, pikin, granpikin, ɔnkul, anti, neba, nius) in. Ivin if no sayn nɔ de, yɔŋ fambul dɛn fɔ go to dɔktɔ.

Risach pipul dεn dכn fכn tu patεn fכ inhεrit insay ARVD dεm:

1. `Autosomal dominant`: wan mama εn papa gεt di jin mכtεshכn. Insay dɛn kayn famili ya, pikin dɛn kin gɛt 50% chans fɔ gɛt di sik. Bɔt di sayn dɛm ɛn di ej we di sik bigin kin difrɛn bitwin di famili mɛmba dɛm. ARVD kin bɔku na sɔm say dɛn we pipul dɛn kin de, lɛk Itali.

2. `Autosomal recessive` (no bכku kכmכn): dεn tu mama εn papa gεt di jin mכtεshכn, bכt dεn nכ de sho di simptom dεm. `Naxos disease` na ɛgzampul fɔ dis. i de mek di כta layεr na di skin tik (`hyperkeratosis`) εn tik, "wul-lεk hair`) na di palm εn di sכl dεm.

ARVD kin kam bak bikɔs ɔf ɔda rizin dɛn:

• di abnכmaliti dεm we dεn bכn wit di rayt vεntrikl.
• Vayral ɔ inflammatory `myocarditis` (inflameshɔn na di at mɔsul).
• Rizin dɛn we dɛn nɔ dɔn fɛn yet.

Aw dɛn kin no se dɛn gɛt ARVD (Arrhythmogenic Right Ventricular Dysplasia)?

Yu dɔktɔ kin no se yu gɛt ARVD bay yu mɛdikal istri, yu bɔdi ɛgzam, ɛn difrɛn tɛst dɛn.

Yu dɔktɔ kin no se yu gɛt ARVD if yu gɛt kɔmbayn sɔm pan dɛn prɔblɛm ya:

• di rayt vεntrikl de wok abnכmal.
• di prεsεns fכ fεt כ fibro-fεt tisu na di at mכsul (`myocardium`) na di rayt vεntrikl.
• Wan abnɔmal `ECG/EKG` (Ilektrokardiogram) ripɔt.
• di at ritm we nɔ de ritm (arithmias): Fɔ ɛgzampul, supraventricular tachycardia, ventricular tachycardia, ɔ ventricular fibrillation, mɔ we yu de du ɛksɛsayz.
• Wan famili istri bɔt ARVD.

Dipen pan ɔmɔs pan dɛn tin ya yu gɛt, yu dɔktɔ kin gi yu diagnosis fɔ "definite," "borderline," ɔ "possible." Sɔntɛnde, bɔt nɔto ɔltɛm, yu dɔktɔ kin sɛn yu bak fɔ mek dɛn chɛk yu jɛnɛtiks .

Wetin na di tɛst dɛn we dɛn kin yuz fɔ no if pɔsin gɛt ARVD?

• Ilɛktrokardiogram (ECG/EKG): Na tɛst we de luk di ilɛktrik wok we di at de du.
• Transthoracic echocardiogram: Semweso lɛk ɔltra saund fɔ di at, i kin luk di at in chɛmba dɛn, valv dɛn, ɛn di we aw i kin pɔmp.
• `Holter monitor`: Dis na lɛk smɔl `ECG` mashin we yu de wɛr fɔ 24 to 48 awa. I de rayt aw yu at de bit ɔl di de.
• Rayt ventricular angiogram: Dɛn nɔ kin yuz dis.
• `Ilektrofisioloji tɛst`: .Wan spɛshal tɛst fɔ chɛk if prɔblɛm de wit di at in ilɛktrik sistɛm.
• Cardiac magnetic resonance imaging (MRI): Dis kin mek yu gɛt ditayla pikchɔ dɛn bɔt di at. dis rili imכtant fכ no tin dεm lεk fεt dεposit dεm na di rayt vεntrikl na ARVD.
• `Cardiac computed tomography (CT)`: Dis na ɔda we fɔ gɛt imej dɛn fɔ di at.
• `Biopsy` (we yu tek tisu sεmpl): dis dεn kin du dis bak bכku bכku wan. Dɛn kin pul wan smɔl tisu na di at ɛn chɛk am.

Wetin na di tritmɛnt dɛm fɔ ARVD?

Naw, no mɛrɛsin nɔ de fɔ ARVD. Bɔt yu dɔktɔ go tray fɔ du dɛn tin ya:

• kכntrol yu at ritm irεgulεriti dεm (`ventricular arrhythmias`).
• Nɔ mek blɔd nɔ klɔt.
• Manej yu at we nɔ de wok fayn.

Di tritmɛnt dɛn fɔ ARVD na:

• Antiarrhythmic drugs: Fɔ mek yu nɔ bit di at ɔltɛm fɔ lɔng tɛm ɛn/ɔ mek yu day wantɛm wantɛm. Dis na di tritmɛnt we dɔktɔ dɛn kin yuz mɔ. Dɛn kin gi yu mɛrɛsin lɛk sotalol ɔ amiodarone.
• Blɔd prɛshɔn mɛrɛsin: Mɛrɛsin lɛk diuretics (we de pul di wata we pasmak na di bɔdi) ɔ beta-blocker (we de ridyus di wok we di at de du).
• Anticoagulant (blood thinner): Dɛn kin gi mɛrɛsin lɛk warfarin fɔ mek blɔd nɔ klɔt.
• Radiofrequency catheter ablation: Na tritmɛnt fɔ di at ritm we kin apin ɔltɛm we dɛn nɔ kin kɔntrol wit mɛrɛsin. Dis kin min fɔ pwɛl wan smɔl pat na di at we de mek di at nɔ de bit ɔltɛm.
• Implantable cardioverter-defibrillator (ICD): Na smɔl tin we dɛn kin put insay pipul dɛn at we de pan denja fɔ day wantɛm wantɛm. If i si wan denja at ritm, i go no am ɛn gi ilɛktrik shɔk to di at fɔ kɔrɛkt am.
• At transplant: Dɛn kin du dis we ɔl di ɔda tritmɛnt dɛn nɔ wok. Na smɔl pasɛnt pan pipul dɛm wae gɛt dis sik, lɛk 2% to 4%, nid nyu at.

Mɛmba se yu kin nid pas wan tritmɛnt fɔ dis sik ɔlsay na yu layf.

Ɛni kɔmplikeshɔn ɔ sayd ɛfɛkt de fɔ di tritmɛnt?

Yɛs, sɔm tin dɛn de we yu fɔ tek tɛm wit wit sɔm tritmɛnt dɛn.

• If yu de tek warfarin, yu go nid fɔ du yu blɔd tɛst ɔltɛm . Yu dɔktɔ go nid fɔ mek shɔ se yu de gɛt di rayt doz. Dɛn kin ajɔst yu doz bay di tɛst rizɔlt.
• Pan ɔl we di tritmɛnt we dɛn kin yuz fɔ pul di kateshɔn kin wok fayn fɔ bɔku pipul dɛn fɔs, as di sik kin wɔs as tɛm de go, lɛk 60% pan pipul dɛn kin gɛt prɔblɛm wit dɛn at ritm bak.
• Di waya dɛn we de na di ICD divays kin muv rawnd ɔ nɔ kin wok fayn, so yu nid fɔ kɔntinyu fɔ chɛk dɛn.

Aw a kin kia fɔ misɛf? Us chenj dɛn we wi nid fɔ chenj di we aw wi de liv in layf?

I rili impɔtant fɔ mek sɔm chenj dɛn na yu layf fɔ mek yu at izi.

• Limit fɔ drink rɔm.
• Stɔp fɔ yuz tin dɛn we dɛn kin mek wit tabak ɔltogɛda.
• It fayn it (we nɔ gɛt bɔku fat, bɔku frut ɛn vɛjitebul) .
• Limit it ɛn drink dɛn we gɛt kafin (lɛk kɔfi, ti, chɔklɛt).
• Mek yu bɔdi gɛt di rayt wet.
• Limit fɔ du bɔku bɔku tin dɛn fɔ du wit yu bɔdi.

Di tin we impɔtant pas ɔl: Chek wit yu dɔktɔ ɔltɛm bifo yu bigin fɔ du ɛksɛsayz. Dɛn nɔ kin advays fɔ ple spɔt dɛn we gɛt kɔmpitishɔn. Spɔt dɛn we nɔ gɛt bɔku pawa kin fayn.

Tɔk to yu dɔktɔ ɔltɛm ɔl di tɛm we yu de trit yu. Dɛn go mek shɔ se yu de gɛt di rayt doz fɔ mɛrɛsin. Dɔn bak, bay we yu go na di say dɛn we dɛn kin go fɔ fala yu ɔltɛm, yu kin kech ɛni chenj na yu kɔndishɔn kwik kwik wan.

Yu tink se dɛn kin ridyus di prɔblɛm?

Yɛs, te to sɔm mak. If pɔsin na yu famili gɛt ARVD, fɔ mek dɛn chɛk yu kwik kwik wan na di bɛst we fɔ ridyus di prɔblɛm we yu gɛt. Simpul tɛst dɛn we nɔ de mek yu fil pen kin no if yu de pan denja fɔ gɛt abnɔmal at ritm. If na so, yu dɔktɔ kin ɛp yu fɔ mek wan tritmɛnt plan we go fayn fɔ yu.

Wetin na di layf we pɔsin kin liv wit ARVD?

Di layf we pɔsin kin liv fɔ ARVD kin difrɛn difrɛn wan bay we dɛn no se i gɛt am. Di bɛst tin fɔ du na fɔ no di sik kwik kwik wan ɛn gɛt tritmɛnt fɔ mek di at nɔ bit ɔltɛm. Dis sik kin wɔs as tɛm de go.

If dɛn nɔ trit ARVD, yu rayt ventricle kin fel. Dɔn yu lɛft ventricle kin fel bak. dis kin mek yu gεt kכndyushכn lεk `at fεil` εn `atrial fibrillation`. Risach pipul dεm biliv se di tin kin bכku if ARVD afekt כl tu di vεntrikl dεm.

Bɔt, wit tritmɛnt, yu kin gɛt di ɛp we yu nid fɔ ridyus di strɛs pan yu at ɛn fɔ mek yu nɔ gɛt at atak we de mek yu gɛt prɔblɛm. Sɔm stɔdi dɔn sho se sɔm pipul dɛn kin gɛt dis sik afta dɛn dɔn ol 65. Dɛn kin tɔk bak se lɛk wan pan ɛvri fayv pipul dɛn we gɛt ARVC kin bigin fɔ gɛt dis sik afta dɛn dɔn ol 50. So, i pɔsibul fɔ liv lɔng layf wit ARVC.

Naw, di advans imej teknɔlɔji dɛm lɛk CT ɛn MRI de alaw fɔ no di sik kwik kwik wan ɛn trit am, so di lɔng tɛm lukin-grɔn fɔ pipul dɛm we gɛt ARVD fayn.

Bɔt, di wan dɛn we nɔ gɛt di sik ɔ we nɔ gɛt di tritmɛnt we dɛn nid, kin day wantɛm wantɛm. Dɛn se na ARVD na in de mek 11% pan di wan dɛn we nɔ rich 35 ia yet we dɛn at kin day wantɛm wantɛm ɛn 22% pan di atlet dɛn we kin day wantɛm wantɛm bikɔs dɛn at kin day.

Ustɛm a fɔ go to dɔktɔ? Ustɛm a fɔ go na di imejensi rum?

If yu gɛt ARVD, yu go nid fɔ kɔntinyu fɔ gɛt mɛdikal chɛk-ap ɔlsay na yu layf.Yu dɔktɔ go nid fɔ chɛk ɔltɛm fɔ mek shɔ se yu de gɛt di rayt tritmɛnt. If yu gɛt ICD, yu go nid fɔ de chɛk am ɔltɛm .

Wetin fɔ du we ɛnitin apin we nɔ izi fɔ du?

If pɔsin fɔdɔm wantɛm wantɛm ɛn nɔ ansa yu kɔl, kɔl 1990 (Sri Lanka in imejensi ambulans savis) wantɛm wantɛm. Dɔn, if i pɔsibul, bigin fɔ du CPR (cardiopulmonary resuscitation), ɔ at ɔl CPR we yu de yuz yu an nɔmɔ.

If yu de pan denja fɔ mek yu at stɔp wantɛm wantɛm, i fayn fɔ mek di wan dɛn we de na os wit yu gɛt CPR trenin.

Us kwɛstyɔn dɛn a fɔ aks mi dɔktɔ?

• A kin du ɛksɛsayz ɔ tek pat pan spɔt? If na so i bi, us kayn spɔt?
• Us tritmɛnt we bɛtɛ fɔ mi?
• A nid ICD dis tɛm?

Bikɔs i kin at fɔ no bɔt ARVD bifo di sayn dɛn we yu gɛt, i impɔtant fɔ no yu famili histri. If yu de pan denja bikɔs yu gɛt dis sik na yu famili, yu dɔktɔ kin tɛst yu.

Mɛsej we dɛn kin kɛr go na os

Okay, so naw yu don andastan beta wetin wi tok abaut tide, ARVD. Pan ɔl we i nɔ kin apin so ɔltɛm, i kin bi siriɔs at sik. Bɔku tɛm na di tin dɛn we de mek pɔsin in jɛnɛtiks kin mek i apin . So, if sɔmbɔdi na yu famili gɛt dis sik, i rili impɔtant fɔ mek dɛn tɛst ɔda pipul dɛn.

If yu no di sik kwik kwik wan, gɛt di rayt tritmɛnt, ɛn chenj di we aw yu de liv yu layf, yu go ebul fɔ liv fayn wit dis sik. Stay in kɔntakt wit yu dɔktɔ ɛn fala dɛn advays. Dɔn bak, fɔ mek shɔ se yu pipul dɛn we yu lɛk no bɔt `CPR` kin ɛp fɔ sev yu layf pan imejensi. Nɔ fred, awareness na di big big trɛnk!

` ARVD, Arrhythmogenic Right Ventricular Dysplasia, hat sik, hat atak, kadiomayopathy, kadyak day wantɛm wantɛm, jenɛtik sik, at atak