Yu at de bit wantɛm wantɛm strenj wan? Yu tink se na Brugada Sindrom?

Yu dɔn ɛva lɔs kɔnshɛns wantɛm wantɛm, fil se yu ed de tɔn? Ɔ yu bin fil se yu at de bit kwik kwik wan, ɔ i nɔ bin izi fɔ yu fɔ blo? Sɔntɛnde, dɛn tin ya kin apin bikɔs ɔf sɔntin we nɔ rili siriɔs. Bɔt nɔr kin bɔrku, dɛn kin bi sayn fɔ wan hat sik wae dɛn kɔl Brugada Syndrome. Lɛ wi tɔk bɔt dis smɔl tide, bikɔs i impɔtant fɔ no bɔt am.

Wetin na Brugada Sindrom?

Fɔ tɔk am simpul wan, Brugada Syndrome na wan sik we de mek ilɛktrik wok we nɔr de wok fayn na di lכw chεmba dεm na yu at, we dεn kכl di vεntrikl dεm. Dis kin mek yu at nɔ gɛt ritm wantɛm wantɛm . Dɛn kɔl dis ventricular fibrillation ɔ v-fib . Imajin se yu at de flɔt instead fɔ pɔmp blɔd fayn fayn wan. Dis kin mek yu bren nɔ gɛt bɛtɛ blɔd. Na da tɛm de yu kin lɔs kɔnshɛns (syncope) .

Dis kin bi wan denja kכndyushכn, biכs dis `v-fib` kin ivin mek di kadyak day wan wan . Bɔrku tɛm, dis kin apun wae yu de rɛst ɔr de slip. Risach pipul dɛm se Brugada Syndrome na in de mek lɛk 4% pan di wan dɛm wae kin day kwik kwik wan bikɔs dɛn gɛt at na di wɔl.

Bɔt dis nɔto sik we bɔku pipul dɛn kin gɛt. Na lɛk tri to 4 pipul dɛn pan tɛn tawzin pipul dɛn gɛt dis sik.

Us sayn dɛn kin sho?

Brugada Syndrome simptom kin apia pan ɛni ej. Bɔt dɛn kin bigin arawnd di ej we dɛn ol 40. Sɔm pipul dɛn nɔ kin sho ɛni sayn atɔl. Dɛn se pas 70% pan pipul dɛm nɔr gɛt ɛni sayn. Bɔt if di sayn dɛn we de sho se yu gɛt dis sik, dɛn kin gɛt:

• abnכmal hat bit (`ventricular arrhythmia`) : Dis min se di hat in ritm de disturb.
• Sinkope: Wae yu nɔr de no natin wantɛm wantɛm ɛn fɔdɔm.
• Diziz : Na filin fɔ spin.
• I nɔ kin izi fɔ yu fɔ blo .
• At palpitations : Na filin fɔ flɔt ɔ spin na yu chɛst.
• Cardiac arrest : Sɔntɛnde dis na di fɔs sayn we de sho. Sɔm pipul dɛn kin day we dɛn de slip bikɔs ɔf dis.

Impɔtant: If yu kin gɛt wan ɔ mɔ pan dɛn sik ya ɔltɛm, i go fayn fɔ mek yu go to dɔktɔ fɔ advays.

Wetin na di tin dɛm wae kin mek yu gɛt Brugada syndrome?

Sɔm tin kin mek di Brugada syndrome simptom dɛn apia wantɛm wantɛm ɔr kin wɔs. Wi kin kɔl dɛn tin ya `trig`.

• Fiva : Dɛn sayn ya kin apin wae pɔrsin wae gɛt Brugada sindrom gɛt fiva.I rili impɔtant fɔ mek di fiva kam dɔŋ kwik kwik wan . Ivin if yu gɛt implantable cardioverter defibrillator (ICD), yu stil nid fɔ briŋ di fiva dɔŋ. Dɛn kin du dis wit mɛrɛsin dɛn we dɛn kin bay fɔ ridyus fiva we dɛn kin bay na di famasi.
• Ɔt taya / Dehydration : Wata de kip na di bɔdi, taya bikɔs ɔf ɔt pasmak.
• Sɔm mɛrɛsin dɛn : .
• Sɔdiɔm chanɛl blɔk dɛn.
• Litiɔm we dɛn kɔl.
• Trisayklik antidipreshan.
• Alcohol : Fɔ drink pasmak.
• Drugs : Yuz drɔgs lɛk kɔkɛyn ɛn marijuana.

I rili impɔtant fɔ no bɔt dɛn tin ya ɛn avɔyd dɛn as yu ebul.

Wetin na di rizin dɛn we mek dɛn de du dis?

Sɔntɛnde dɛn nɔ kin no di rayt tin we kin mek pɔsin gɛt Brugada Syndrome . Ɔ i kin bi se na jɛnɛtiks . Dɛn nɔ stil no ustɛm us jɛnɛtik muteshon de mek dis sik na lɛk 70% pan pipul dɛm.

Bɔt sɔm pipul dɛn kin gɛt 18 ɔ mɔ tin dɛn we kin chenj dɛn jɛnɛtiks. di mכst kכmכn pan dεm na di vεryushכn insay wan jin we dεn kכl SCN5A . dis vεryushכn dεm de ambɔg di we aw ilektrikal signal dεm na di at de travul.

Dis na sik we pɔsin kin gɛt frɔm wan mama ɔ papa nɔmɔ . dat min se, pikin fכ pכsin we gεt jin mכtεshכn we de asai wit Brugada sεndrכm gεt 50% chans fכ divεlכp am.

Udat dɛn kin gɛt dis sik mɔ? (Di tin dɛn we kin mek pɔsin gɛt prɔblɛm)

Dis sik kin mɔna man dɛn . I kin apin lɛk 8 to 10 tɛm pas man dɛn pas uman dɛn.

Dɔn bak, if pɔsin na yu famili dɔn day bikɔs in at dɔn stɔp wantɛm wantɛm, ɔ dɛn dɔn no se i gɛt Brugada sindrom , i go fayn fɔ mek dɛn du tɛst fɔ dis bak.

Wan ɔda tin na dat dɛn se dis sik kin bɔku smɔl pan pipul dɛn we kɔmɔt na Eshia .

Aw dɔktɔ kin no bɔt dis? (Diagnosis) .

Fɔ no if yu gɛt Brugada Syndrome, dɔktɔ go du dɛn tin ya:

• Dɛn go gi yu ɛgzam fɔ yu bɔdi .
• Dɛn go rivyu yu mɛdikal istri .
• Dɛn go aks bɔt yu famili in wɛl bɔdi istri (biological family history) , mɔ fɔ si if ɛnibɔdi na yu famili dɔn day wantɛm wantɛm.
• Dɛn go aks yu fɔ du sɔm spɛshal tɛst dɛn .

Us tɛst dɛn dɛn kin du?

Bɔku men tɛst dɛn de we dɛn kin yuz fɔ no dis sik:

• Test fɔ di jenɛtiks: Dis tɛst kin no if yu gɛt wan patikyula jin muteshon we gɛt fɔ du wit Brugada sindrom bay we yu tek wan sɛmpul pan yu saliva ɔ blɔd. I fayn bak fɔ mek dɛn du dis tɛst fɔ si if ɔda pipul dɛn na yu famili sɛf gɛt dis jin muteshon. Ɛspɛshali if yu gɛt yu fambul we de nia yu (`fɔs-digri fambul`) we gɛt Brugada sindrom, lɛk yu mama ɛn papa, brɔda ɛn sista, ɔ pikin dɛm, yu fɔ rili gɛt skrinin fɔ dis .
• Ilɛktrokardiogram (EKG ɔ ECG) : Dɛn kin yuz dis fɔ rayt di ilɛktrik wok we yu at de du we i de bit. Dɔktɔ dɛn kin luk fɔ wan patikyula patɛn (di Brugada sindrom tayp 1 EKG patɛn) pan di EKG. Sɔmtɛm dɛn kin si wan wik pat we dɛn kɔl tayp 2 ɔ tayp 3, bɔt dat nɔmɔ nɔ kin ebul fɔ kɔnfirm di sik. כltu, biכs fכ di trigεr dεm we wi bin dכn tכk bכt (e.g. fiva), dis tayp 2 כ tayp 3 patεn kin chenj to tayp 1 patεn. Sɔntɛnde dis patɛn nɔ kin si wantɛm wantɛm na di EKG, so di dɔktɔ kin ripit di EKG tu ɔ tri tɛm, ɛn chenj di lid dɛn. Sɔntɛnde, dɛn kin du EKG bak afta dɛn dɔn it ful-ɔp.
• EKG wit mɛrɛsin (drug challenge test) : Bifo di EKG, yu dɔktɔ kin gi yu mɛrɛsin we go ɛp yu EKG fɔ sho klia wan if yu gɛt Brugada sindrom. Dɛn kin yuz dis tɛst fɔ si if yu EKG gɛt tayp 2 ɔ tayp 3 patɛn, we kin chenj to tayp 1 patɛn.

Dipen pan yu EKG rizɔlt, dɛn kin du ɔda tɛst dɛn:

• εlektrofisioloji (EP) tεst : Dis involv fכ pas wan tin tכb (kateta) tru wan big vein na yu leg (femoral vein) insay yu at fכ mכsu di ilektrikal aktiviti insay yu at. Dis kin bi if di diagnosis nɔr klia afta ɔda tɛst.
• Lab test: Dɛn kin du blɔd tɛst fɔ chɛk di lɛvɛl dɛn we di ilɛktrɔlayt dɛn lɛk potashɔm, kalsiɔm, ɛn magnɛsiɔm de na di blɔd, ɛn fɔ chɛk fɔ ɔda tin dɛn we kin mek di at nɔ de rit ɔltɛm.

Aw fɔ trit am? (Tritmɛnt)

Di men gol fɔ trit Brugada Syndrome na fɔ mek di ventricular arrhythmias nɔ apin ɛn fɔ kɔntrol am kwik kwik wan if i apin.

Yu kin gi yusɛf tritmɛnt dɛn lɛk dis:

• Mɛrɛsin dɛn lɛk Isoproterenol .
• Mɛrɛsin dɛn lɛk kinidin .
• Wan smɔl tin we dɛn kin put insay di at (Implantable Cardioverter Defibrillator - ICD) .: If yu dɔn gɛt at atak (ventricular tachycardia), yu fɔdɔm, ɔ yu at nɔ de wok, dɛn kin fit yu ICD. Dis divays de no wan denja at ritm ɛn gi smɔl ilɛktrik shɔk to di at fɔ mek i kam bak to nɔmal.
• Ablashɔn ( insay sɔm kes dɛm): Dis kin min fɔ no ɛn pwɛl di say dɛm na di at we de kɔz abnɔmal ilɛktrik signal dɛm.

Ivin if yu nɔ gɛt di sik, yu dɔktɔ kin disayd fɔ put ICD bay yu famili histri ɛn di tɛst rizɔlt. Sɔm dɔktɔ dɛn kin disayd fɔ chɛk yu ɔltɛm ɛn jɔs trit yu if yu gɛt sɔm sayn dɛn. Bɔt ɔda dɔktɔ dɛn nɔ go gri wit dis we fɔ du dis, bikɔs di fɔs sayn we yu go gɛt na we yu at day wantɛm wantɛm.

Ɛni kɔmplikeshɔn de pan di tritmɛnt?

ICD nɔto 100% fulpruf divays. Sɔntɛnde, tin dɛn lɛk dis kin apin:

• Yu kin gi wan shɔk di rɔng tɛm .
• Sɔntɛm fɔlt de na wan pan di lid dɛn na di mashin.
• Infεkshכn kin apin rawnd di mashin.

So, afta dɛn dɔn put ICD insay, i rili impɔtant fɔ go fɔ tɛst jɔs lɛk aw di dɔktɔ se.

Aw lɔng i kin tek fɔ mek i wɛl?

Afta dɛn dɔn put ICD, yu kin du bɔku pan yu nɔmal tin dɛn insay sɔm dez. Bɔt yu go nid fɔ stɔp fɔ drayv fɔ lɛk wan wik so. Yu kin du sɔm wok dɛn we de mek yu tranga ɛvride, bɔt nɔ du am te yu taya. Nɔ es wet ɔ du ɛksɛsayz we yu de du tranga wan te yu dɔktɔ tɛl yu fɔ du dat.

Yu tink se dɛn go ebul fɔ stɔp dis? (Prɛvenshɔn) .

If yu gɛt Brugada Syndrome frɔm yu mama ɛn papa, yu nɔ go ebul fɔ chenj am. Bɔt if yu no se sɔmbɔdi na yu famili gɛt Brugada Syndrome, yu ɛn yu fambul dɛn kin du wan jenɛtik tɛst fɔ si if yu gɛt am.

Dɔn bak, if yu de op fɔ bɔn pikin, yu kin mit wit pɔsin we de advays yu bɔt yu jɛnɛtiks ɛn tɔk to dɛn bɔt di prɔblɛm we kin apin we yu pas dis to yu pikin dɛn.

Wetin yu kin ɛkspɛkt we yu de liv wit Brugada sindrom?

Nɔr mɛrɛsin nɔr de fɔ Brugada Syndrome. Bɔt tritmɛnt kin rili ridyus di risk fɔ mek pɔsin day wantɛm wantɛm na in at.

Pipul wae gɛt Brugada sindrom wae gɛt sɔm kayn sik bɔt nɔr de gɛt tritmɛnt kin gɛt bɔrku risk fɔ day kwik kwik wan. Dis risk kin smɔl pasmak pan pipul dɛm wae nɔr gɛt ɛni sayn ɛn gɛt nɔrmal EKG.

Aw a kin kia fɔ misɛf? (Fɔ kia fɔ yusɛf) .

If dɔktɔ tɛl yu se yu gɛt Brugada Syndrome, di tin we impɔtant pas ɔl na fɔ avɔyd bɔku pan di tin dɛn we kin mek yu nɔ gɛt da ritm de.

• Fɔ mek yu nɔ gɛt fiva. If yu gɛt fiva, briŋ am kam dɔŋ kwik kwik wan.
• Stay away frɔm sɔm mɛrɛsin ɛn tin dɛn . Aks yu dɔktɔ fɔ wan list fɔ di mɛrɛsin dɛn we yu gɛt alɛji to.
• Nɔ drink pasmak ɛn tek drɔgs kpatakpata .
• Drink bɔku wata fɔ mek yu nɔ gɛt wata na yu bɔdi .
• Tek tɛm we yu de du tin dɛn we go mek yu strɛs .

Ustɛm yu nid fɔ go to dɔktɔ? / Yu nid fɔ go na di imejensi rum?

If yu gɛt Brugada sindrom, yu fɔ go to yu dɔktɔ wan tɛm insay di ia fɔ mek dɛn chɛk yu . If yu gɛt ICD, yu fɔ mek dɛn chɛk am tu tɛm insay di ia . If yu fil ɛnitin we nɔ kɔmɔn, tɛl yu dɔktɔ .

Sɔntin yu nɔ plan! If yu at pwɛl, yu nɔ go ebul fɔ ɛp yusɛf. So, yu go nid pɔsin fɔ ɛp yu. If yu de pan denja fɔ mek yu at pwɛl, tɛl yu famili fɔ lan CPR (Cardiopulmonary Resuscitation) , ɛn kɔl 1990 (Sri Lanka in imejensi ambulans savis) ɔ di imejensi nɔmba we de nia yu. Tɛl bak yu wokples bɔt dis risk.

Impɔtant kwɛstyɔn dɛn fɔ aks yu dɔktɔ

We yu go si dɔktɔ, nɔ fɔgɛt fɔ aks kwɛstyɔn dɛn lɛk dis:

• A nid fɔ gɛt ICD?
• Aw dɛn fɔ kip ICD?
• Yu kin tɛl mi bɔt sɔpɔt grup usay ɔda pipul dɛn we gɛt dis kɔndishɔn kin jɔyn?
• Us mɛrɛsin dɛn a fɔ avɔyd? Yu kin gi mi wan list?
• Yu tink se dɛn fɔ tɛst di ɔda pipul dɛn na mi famili fɔ si dis?

Mɛsej we dɛn kin kɛr go na os

Na nɔmal tin fɔ fil bad we yu kam fɔ no se yu gɛt wan sik we go mek yu gɛt at atak wantɛm wantɛm. Bɔt we yu no se yu de pan denja, dat de gi yu di chans fɔ du tin dɛn fɔ ridyus da prɔblɛm de . Yu dɔktɔ go fɛn di bɛst tritmɛnt fɔ yu.

If i pɔsibul, i go rili fayn if yu os ɛn yu pikin in skul gɛt wan Automatic External Defibrillator (AED) . Dɔn bak, aks yu neba ɛn yu kɔmpin wokman dɛn fɔ lan CPR. Dɛn tin ya kin ɛp fɔ sev pipul dɛn layf. Ɔltɛm fala yu dɔktɔ in instrɔkshɔn, go de chɛk yu ɔltɛm, ɛn avɔyd tin dɛn we go mek yu day .

` Brugada sindrom, kadyak aritmia, kadyak arɛst wantɛm wantɛm, jɛnɛtik sik, EKG, ICD, at sik