Wetin na di Epithelioid Hemangioendothelioma (EHE)? Lɛ wi lan bɔt dis kansa we nɔ kin bɔku insay simpul wɔd dɛn

Sɔntɛm yu nɔ bin dɔn yɛri dis nem bifo. Epithelioid Hemangioendothelioma (EHE) na wan kansa we rili, rili rare, we kin apin pan lɛk wan pan ɛvri milyɔn pipul dɛn. Di nem kɔmplikt smɔl, so i kin mek pɔsin fred. Bɔt nɔ wɔri. E fayn fɔ ɔndastand dis rare kɔndishɔn simpul ɛn klia wan. So tide, mek wi tok abaut exactly wetin EHE bi.

Fɔ tɔk am simpul wan, us kayn kansa na EHE?

Imajin se di blɔd vesel ( arteries , veins, and capillaries) we de ɔlsay na wi bɔdi tan lɛk wan netwɔk we gɛt rod dɛn we de go ɔlsay na wan kɔntri. Insay dɛn rod ya, dɛn gɛt wan layt we rili tan lɛk sɛl dɛn. dεn kכl dεn sεl dεm ya εndoteyl sεl dεm na mεdikal sayns.

di εndoteyl kεnsar de stat na di sεl dεm we de layn di bכdi vεsul dεm. Bikɔs blɔd vesel dɛn de ɔlsay na wi bɔdi, EHE kansa kin kam ɛnisay na di bɔdi. Bɔt bɔku tɛm, dɛn tumbu ya kin bigin na di liva, di lɔng, ɔ di bon dɛn . Bɔt dɛn kin divɛlɔp bak na ɔda say dɛn lɛk di ed, nɛk, tayroyd, bɛlɛ, ovaria, prɔstat, bren, ɛn spɛnal kɔd.

Sɔntɛnde EHE kin apia lɛk wan lump. כda tεm dεm, i kin apia lεk bכku bכku bכku dεm na di sem כgan כ insay bכku כgan dεm. Bɔku tɛm, we dɛn no se di kansa gɛt EHE, di kansa dɔn ɔlrɛdi skata to pas wan ɔgan.

EHE na wan kayn sarkoma?

Yɛs, na so i bi. Sarkoma na wan kayn kansa we kin kam na di sɔft tisu dɛm na wi bɔdi, lɛk di blɔd vesel dɛm. biכs EHE kεnsar de bigin na di εndoteyl sεl dεm na di bכdi vεsul dεm, dεn kin klas am as wan kayn sarkoma.

Dis kansa na bad bad tin?

Yes, EHE na malignant , we min se na malignant ɔ kansa kɔndishɔn. difrεnt frכm benign tכmכro dεm, dεn kεnsar sεl dεm ya kin gro we dεn nכ kin kכntro, spre (mεtastasize) to כda pat dεm na di bכdi, εn pwεl di hεlty tisu dεm.

Wetin na di sayn dɛm fɔ EHE?

Bɔku pasɛnt dɛn we gɛt EHE nɔ kin gɛt ɛni sayn fɔs. Dis na di rizin we mek dɛn kin no bɔt am bay we dɛn de du tɛst fɔ ɔda sik. Bɔt if di sayn dɛn we de apin, dɛn kin dipen pan usay di kansa gɛt.

Sɔm kɔmɔn sayn dɛm wae yu kin si na:

• Lump we yu kin fil ɔnda di skin (dis kin mek yu fil pen ɔ i nɔ kin fil pen) .
• We yu de lɔs yu wet we yu nɔ gɛt rizin
• Fiva ɛn taya pasmak

Lɛ wi tek wan luk aw di sik kin difrɛn difrɛn wan fɔ di say we di kansa de.

Wetin kin mek pɔsin gɛt EHE kansa?

kansa lεk EHE de divεlכp we wan hεlty sεl de tכn to kεnsar sεl εn bigin fכ sheb we i nכ de kכntro.

We dɛn bin de tray fɔ no wetin kin mek dis apin, sɔm pipul dɛn we de stɔdi bɔt dis dɔn kam fɔ no se na wan patikyula jɛnɛtik chenj kin mek i apin . Fɔ tɔk am simpul wan, tu kromozom dɛn na wi sɛl dɛn nɔ gɛt wanwɔd togɛda di rɔŋ we, ɛn dis kin mek tu jin dɛn jɔyn togɛda. dεn kכl dεn jin dεm ya (WWTR1) (dεn kכl dεm bak (TAZ) ) εn (CAMTA1) . we dεn tu jin dεm ya kam togeda, i de mek di EHE kεnsar sεl dεm bigin fכ fכm.

So, yu dɔktɔ kin tɛst bak fɔ dis abnɔmal kromozom asosieshɔn we i de mek diagnosis.

Aw dɛn kin du di diagnosis?

As wi bin dɔn tɔk, bɔku tɛm dɛn kin fɛn EHE bay chans. Dɔktɔ dɛn kin jɔs notis di lump we dɛn de du imej tɛst, lɛk CT skan ɔ MRI skan, fɔ ɔda rizin. Dɔn dɛn kin luk fɔ di say we i de, di sayz, ɛn if i dɔn skata to ɔda say dɛn.

Dis na di tɛst dɛm we dɛn kin yuz mɔ fɔ no EHE.

Apat frɔm dat, fɔ no di lumps ɛn si if dɛn dɔn spre (ultrasound) ɔYu dɔktɔ kin tɛl yu bak fɔ du ɔda tɛst dɛn lɛk fɔ du PET skan .

Wetin na di tritmɛnt dɛm fɔ EHE?

Bikɔs EHE na so wan rare kɔndishɔn, no standad tritmɛnt gaydlayn nɔ de fɔ am yet. So, na wan tim we gɛt bɔku bɔku dɔktɔ dɛn we gɛt ɛkspiriɛns fɔ trit sarkoma go trit yu. Dis tim kin gɛt ɔspitul ɔnkɔlɔjis , raydiɔlɔjis , ɛn, dipen pan di ɔgan we di kansa de (fɔ ɛgzampul, bon), ɔtpidik ɔspitul ɔspitul , ɔ spɛshal liva transplant.

De tritmɛnt wae yu kin gɛt kin dipen pan sɔm tin dɛm, lɛk di sayz fɔ di lump, usay i de, ɔmɔs lumps de, ɛn if di kansa dɔn skata.

Na sɔm tritmɛnt dɛn ya:

Wachful Waitin

If yu nɔ gɛt ɛni sayn ɛn yu nɔto gud pɔsin fɔ ɔpreshɔn, yu dɔktɔ go disayd nɔ fɔ trit yu fɔs ɛn jɔs wach yu sik gud gud wan. Dis na bikɔs sɔntɛnde, di bad tin dɛn we kin apin we pɔsin de trit pɔsin kin pas di bɛnifit dɛn we i kin gɛt. As wi bin dɔn tɔk, sɔm EHE tumor dɛn kin shrink if dɛn nɔ trit dɛn ɔ dɛn kin gro sloslo. Bɔt if di sik wɔs, yu dɔktɔ kin tɛl yu fɔ yuz ɔda tritmɛnt.

Ɔpreshɔn

Di tritmɛnt we dɛn kin yuz mɔ fɔ wan tumbu na ɔpreshɔn. Insay dis we aw dɛn de du dis, di dɔktɔ we de du di ɔpreshɔn kin pul di kansa tɔŋ ɛn smɔl wɛlbɔdi tisu we de rawnd am fɔ mek shɔ se nɔ kansa sɛl nɔ lɛf.

Vaskulεr εmbolizεshכn

Dis min se dɛn fɔ blok di blɔd vesel dɛn we de gi di tumbu blɔd. Jɔs lɛk aw plant kin day we yu stɔp fɔ wata am, we dɛn kɔt di blɔd, di tumbu nɔ kin ebul fɔ gro ɔ smɔl. Dɛn kin du dis fɔ mek di tumbu smɔl bifo dɛn du di ɔpreshɔn ɔ as di men tritmɛnt. Transartrial kemoembolizεshכn (TACE) εn redio εmbolizεshכn na tu dεn kayn tritmεnt dεm ya.

Tɛrapi we dɛn de tɔk bɔt

Dis na di tritmɛnt we dɛn kin yuz mɔ fɔ advans EHE. Dis tritmɛnt de yuz drɔgs we de blok di nyutriɛnt ɛn ɔksijɛn we di kansa sɛl dɛn nid fɔ gro.

Rɛdieshɔn Tɛrapi

Dɛn kin yuz dis tritmɛnt fɔ pwɛl ɛni kansa sɛl we kin lɛf afta dɛn dɔn du di ɔpreshɔn. Dɛn kin gi redyushɔn tɛrapi bak as di men tritmɛnt fɔ pɔsin we nɔ ebul fɔ du ɔpreshɔn. Insay dis tritmɛnt, dɛn kin yuz di raytin we gɛt ay ɛnaji we dɛn dɔn tayt fɔ pwɛl di kansa sɛl dɛn.

Kimotɛrapi

Fɔ EHE (Kɛmotɛrapi) .Dɛn nɔ kin yuz am bɔku tɛm, bɔt if di kansa dɔn go bifo, dɛn kin se dɛn fɔ yuz am wit ɔda tritmɛnt dɛn.

Ɔgan we dɛn kin transplant

If bɔku bɔku tumbu dɛn dɔn afɛkt wan big ɔgan (bɔku tɛm na di liva), di dɔktɔ kin se dɛn fɔ transplant wan ɔgan.

Aw lɔŋ yu kin liv wit EHE?

We yu yɛri dis, yu go de wɔnda, ‘Aw lɔng a go liv da tɛm de?’ Fɔ tɔk tru, i at fɔ gi stret ansa to da kwɛstyɔn de. Bikɔs EHE na wan sik we nɔ kin apin so ɔltɛm, dɛn stil de gɛda infɔmeshɔn bɔt am.

Dɔn bak, lɛk aw wi bin dɔn tɔk, dis kansa nɔ de biev di sem we pan ɔlman. Fɔ sɔm pipul dɛn, di kansa kin skata kwik kwik wan ivin if dɛn gɛt tritmɛnt. Fɔ ɔda pipul dɛm, di kansa kin liv fɔ lɔng tɛm ɛn nɔr gɛt ɛni big sayn ɔr di tumbu kin skata. Sɔm tumbu dɛn kin shrin if dɛn nɔ gɛt tritmɛnt.

So, na frɔm yu dɔktɔ we de trit yu nɔmɔ yu go gɛt di bɛst infɔmeshɔn bɔt yu sik ɛn tumara bambay. I go tink bɔt ɔl yu tɛst ripɔt ɛn kɔndishɔn ɛn gi yu di infɔmeshɔn we kɔrɛkt pas ɔl.

Kwɛstyɔn dɛn we yu fɔ aks yu dɔktɔ

Na nɔmal tin fɔ gɛt bɔrku kwɛstyɔn wae yu lan bɔt dis kayn sik wae nɔr kin bɔrku. We yu go si yu dɔktɔ, nɔ fɔgɛt fɔ aks dɛn kwɛstyɔn ya.

I impɔtant ɔltɛm fɔ go to tritmɛnt frɔm dɔktɔ dɛn we yu trɔst. I impɔtant pasmak we i kam pan wan rare kɔndishɔn lɛk EHE. Bikɔs bɔku tin stil de wae wi nɔr no bɔt dis, fɔ fɛn tritmɛnt frɔm dɔktɔ dɛm wae gɛt ɛkspiriɛns fɔ trit sarkoma ɛn kɔmpleks kansa kin mek big difrɛns pan yu wɛl bɔdi joyn.