Skip to main content

Wetin na di sik we dɛn kɔl Lennox-Gastaut Syndrome (LGS)? Lɛ wi tɔk bɔt am!

Wetin na di sik we dɛn kɔl Lennox-Gastaut Syndrome (LGS)? Lɛ wi tɔk bɔt am!

Yu smɔl pikin kin gɛt sik we de mek i sik ɔltɛm? I gɛt big chenj dɛn pan aw i de lan ɛn aw i de biev? If na so, wetin a go tɔk kin rili impɔtant to yu. Tide wi go tɔk bɔt Lennox-Gastaut Syndrome , ɔ (LGS) fɔ shɔt, wan bad bad ɛn at fɔ trit epilepsy kɔndishɔn. Dis kin bigin we i yɔŋ. Bɔt nɔ wɔri, nyu mɛrɛsin ɛn tritmɛnt dɛn de naw.

Wetin rili na Lennox-Gastaut syndrome (LGS)? Udat kin gɛt am?

Fɔ tɔk am simpul wan, LGS na wan bad bad sik we kin bigin we dɛn smɔl, bɔku tɛm bifo i ol 10 ia, ɛn mɔ bitwin 3 ɛn 5 ia. I kin bɔku smɔl pan bɔy pikin dɛn. Bɔt, i nɔ kin rili kɔmɔn. I kin afɛkt lɛk wan to tu pipul dɛn pan wan milyɔn. Na lɛk 1% to 2% pan ɔl di wan dɛn we gɛt ɛpilepshi gɛt LGS.

Aw dis kin afɛkt wi bɔdi?

Epilepsy na wan sik wae de mek di bren in ilɛktrik signal ɔr infɔmeshɔn de pas bitwin di sɛl dɛm. (LGS) na wan kayn we we kin mek pɔsin gɛt ɛpilepshɔn we kin rili bad . Bɔku tin dɛn de we kin mek i apin:

  • Insay LGS, pas wan kayn sik kin apin. Sɔm pan dɛn kayn sik ya kin mek di pikin gɛt siriɔs injury.
  • Dɛn sik ya kin pwɛl di bren insɛf. Pikin dεm we gεt LGS kin gεt bad bad bren dεm, dεn kin tranga fכ lan, εn dεn kin delay fכ divεlכpmεnt. Dis min se di pikin kin lɔs ɔ fɔgɛt tin dɛn we i dɔn ɔlrɛdi lan, lɛk fɔ waka ɛn tɔk. Dis na tin we rili sɔri.
  • (LGS) kin rili rεsistεnt to tritmεnt. Dis min se i nɔ kin izi fɔ kɔntrol am wit mɛrɛsin. Mɛrɛsin na di fɔs tritmɛnt, bɔt bɔku tɛm dɛn kin gi bɔku kayn mɛrɛsin di sem tɛm. Ivin if dɛn gi dɛn, mɛrɛsin nɔmɔ nɔ kin ebul fɔ stɔp di sik dɛn we de mek pɔsin sik kpatakpata.

Wetin na di sayn dɛm fɔ (LGS)?

Pikin we gɛt LGS kin sho difrɛn kayn sayn dɛn. Sɔm pan dɛn kin notis na ɛvride layf ɛn tin dɛn we pɔsin kin du, ɛn ɔda wan dɛn kin jɔs notis we pɔsin de sik.

Prɔblɛm dɛn we pɔsin kin gɛt we i de lan ɛn di we aw i de biev

I kɔmɔn fɔ mek pikin dɛn we gɛt LGS gɛt prɔblɛm fɔ lan ɛn gɛt prɔblɛm wit aw dɛn de biev . Dɛn tin ya kin apin jɔs afta di sik bigin, ɛn dɛn kin wɔs as di sik kin kɔntinyu. Bɔrku tɛm, dɛn prɔblɛm ya wae de kam pan pɔrsin wae de lan ɛn in maynd kin de fɔ ɔltɛm, dat min se dɛn kin kɔntinyu fɔ de te dɛn big.

Pikin dɛn we gɛt LGS kin gɛt prɔblɛm fɔ lan, fɔ mek padi, ɛn fɔ tɔk to ɔda pipul dɛn. I nɔ kin izi bak fɔ dɛn fɔ kɔntrol di we aw dɛn de fil. Sɔm pikin dɛn kin sho bak di sayn dɛm we fiba di wan dɛm wae gɛt dis sik wae gɛt Autism Spectrum Disorder .

Stej we pɔsin kin gɛt we i sik

Wan sik kin apin insay tri stej dɛm:

1. Prodrome ɔ aura: Dis na sɔntin we sɔm pipul dɛn kin gɛt bifo dɛn gɛt sik, pan ɔl we nɔto ɔltɛm. Dis kin bi filin wae nɔr kin fayn fɔ yu. Chenj na di vishɔn, chenj na ɔda sɛns, ɔr chenj na di mud ɔr bihayvya kin apin dis tɛm.

2. Seizure: Dis na we di sik de kam. Dis kin difrɛn difrɛn wan bay di kayn sik wae de kam (wi go tɔk bɔt di difrɛn kayn sik wae de kam dɔŋ ya).

3. Pɔst-seizure recovery: Dis na di tɛm afta di seizure dɔn dɔn. Dis na we pɔsin kin gɛt ful kɔnshɛns bak.

Di kayn sik dɛn we dɛn kin si na LGS

Bɔku men kayn sik dɛn de we dɛn kin si na LGS. Di kayn sik wae kin kam pan pɔrsin wae gɛt dis sik ɛn di tin dɛm wae kin apin to pɔrsin na dɛn wan ya:

  • Atonik sik dɛn we kin mek pɔsin sik:
  • we yu lכs di mכsul kכntrכl/fεn: dεn kכl dis bak "drכp atak" biכs i involv fכ lכs kכntrol wan wan εn fכ fכl na grכn, lεk pכpεt we in strכng dεm dכn brok. Dis kin rili denja bikɔs di pikin nɔ kin ebul fɔ kɔntrol am we dɛn fɔdɔm ɛn i kin gɛt siriɔs injury na in ed, in nɛk, in chɛst, ɛn bak we kin mek i day.
  • Sɔm pat pan yu nɔr de no natin: Dis sik wae de mɛk yu nɔr de mɛmba ɔltɛm.
  • Fɔ shɔt tɛm: Dɛn sik ya kin las fɔ shɔt tɛm, lɛk fɔ sɔm sɛkɔn.
  • Tonik kɔnvulshɔn dɛn:
  • di ol bכdi stiff/friz: Dis na we כl di mכsul dεm na di bכdi de kכntrakt wan wan, we de mek di bכdi stif kכmplit lεk se i tכn to ston.
  • Wan spɛshal pozishɔn: We dɛn de na grɔn, dɛn leg ɛn sholda dɛn de na grɔn, dɛn bak kin arch. di an dεm kin es oba dεn ed, כ dεn kin kכl di an dεm εn di εlbo dεm kin pכynt to di sayd dεm, εn di fist dεm kin de nia di hip dεm.
  • Bɔrku tɛm kin apun wae yu de slip: Dɛn kin apun bɔrku tɛm wae yu de slip. Bɔt dɛn kin apin bak insay di de. If dis kin apin we di pikin wek, i kin izi fɔ mek i wund bikɔs di pikin kin fɔdɔm.
  • Fɔ shɔt tɛm: Dis kin te bak frɔm sɔm sɛkɔn to lɛk wan minit.
  • Atypical absɛns sik dɛn: .
  • Yay dεm opin εn de luk blank: Insay dis sik, dεn kin lכs kכnsεns, bכt di yay dεm kin stil opin. So, bɔku tɛm dɛn kin mistek kɔl dis fɔ drim de, nɔ de pe atɛnshɔn, ɛn fɔ fil se i nɔ de na di say we i de.
  • Muvmɛnt dɛn we de ripit: We yu de du dis sik, yu kin si we yu de muv yu yay ɛn yu mɔt. I kin bi bak se di an dɛn kin muv.
  • Fɔ shɔt tɛm: Dis bak nɔ kin te pas sɔm sɛkɔn.

Impɔtant: Pikin dɛn we gɛt LGS kin gɛt sik na "klɔsta," we min se sɔm sik kin apin insay shɔt tɛm. I pas tu-tɛd pan di pikin dɛnWan kכndyushכn we dεn kכl "Status Epilepticus" kin apin. Dis na sik we nid fɔ gɛt mɛrɛsin kwik kwik wan!

Wetin na Status Epilepticus?

Dis min wan pan tu tin dɛn:

  • Wan wan sik we kin tek lɔng tɛm we kin tek bitwin 5 ɛn 30 minit.
  • Mɔ pas wan sik kin apin insay 30 minit, ɛn di pɔsin nɔ kin gɛt ful kɔnshɛns bak di tɛm we i kin gɛt dɛn sik dɛn de.

Status epilepticus na wan mɛdikal imejensi. I rili denja bikɔs i kin mek yu bren pwɛl sote go ɛn ivin day.

Ɔda sayn dɛm ɛn di kayn sik dɛm wae gɛt fɔ du wit am

  • Tonic-clonic seizures: Tonic-clonic seizures (we dɛn bin de kɔl "grand mal") kin bigin di sem we lɛk tonic seizures, bɔt dɛn kin gɛt ɔda pat. di klonik faz na we di bכdi de jכk, di mכst kכmכn fכm fכ di sik, de apin. Tonic ɛn tonic-clonic seizures kin las fɔ lɛk tu minit.
  • Kwik, shɔt, jεk muvmεnt: Mayoklɔnik sik na we yu de muv wantɛm wantɛm, we de jεk. Dɛn kin las fɔ sɔm sɛkɔn dɛn nɔmɔ, bɔt sɔntɛnde dɛn kin las fɔ lɔng tɛm. Pipul wae nɔr gɛt sik kin gɛt dis kayn "myoclonic jerks" bak. Fɔ ɛgzampul, dɛn kin mek pɔsin hiccups ɔ wek wantɛm wantɛm we i dɔn slip.
  • Sεns, mental, ɔr ɔda sayn dɛm: Sɔm pat ɔ fכs sik kin afɛkt wan smɔl pat pan di bɔdi nɔmɔ.

Wetin na di tin dɛn we kin mek pɔsin gɛt LGS?

Bɔku tin dɛn de we kin mek pɔsin gɛt di sik we dɛn kɔl Lennox-Gastaut syndrome. Sɔm pan di tin dɛn we kin mek i apin kin de bifo dɛn bɔn pikin. Ɔda wan dɛn kin apin bikɔs ɔf tin dɛn we kin apin we dɛn smɔl. Insay lɛk wan kwata pan di kes dɛm we ``(LGS)``, dɛn nɔ kin no klia kɔz.

Na sɔm pan di rizin dɛn we dɛn dɔn no:

  • Prɔblɛm dɛn we de wit di bren we de gro bifo dɛn bɔn am.
  • Sivɛri ed injuri (traumatik bren injuri ɔ kɔnkyushɔn).
  • Infεkshכn dεm we de pwεl di bren, lεk mεningayt כ εnεfalaytis.
  • di mεtabolik sik dεm we dεn kin gεt inhεrit, fכ egzampl `(Mitochondrial diseases)`.
  • di bren dεm we de pwεl we dεn nכ gεt כksijεn bifo כ we dεn bכn (sεribral haypoksia).
  • Tuberous sclerosis we gɛt di sik.
  • Tumɔs dɛn na di bren.
  • Wεst sεndrכm (dis na כda kayn εpilepshכn, we leta kin divεlכp to LGS).

Risach pipul dεn fכnshכn se "de novo mutations" na kכmכn pan pipul dεm we gεt LGS.De novo min "frɔm di biginin." dis na difεkt dεm na pכsin in `(DNA)` we de apin wan wan, randomly. dat min se di mכtayshכn de kכz fכ difεkt na di `(DNA)` na di sεl כ eg we prodyuz di pכsin, bכt i nכ de fכ di `(DNA)` fכ εni wan pan di mama εn papa.

Bɔt, i kin bi se sɔntin de we kin mek pɔsin gɛt sɔntin fɔ du wit di sik. Na lɛk 30% pan di pipul dɛm wae gɛt LGS gɛt famili histri fɔ gɛt ɛpilepsi. Bɔt dɛn nid fɔ du mɔ risach fɔ no ustɛm dis na sɔntin we de mek pɔsin gɛt jɛnɛtiks.

Yu tink se dis kin pas?

Nɔ, di sik we dɛn kɔl Lennox-Gastaut syndrome nɔ kin gɛt di sik. I nɔ de skata frɔm wan pɔsin to ɔda pɔsin. Bɔt sɔm sik dɛn we kin kam pan pɔsin kin mek di bren pwɛl ɛn mek i gɛt ``LGS''. Bɔt nɔto ɔlman we gɛt dɛn infɛkshɔn ya go gɛt ``LGS''.

Aw dɛn kin no se pɔsin gɛt di sik we dɛn kɔl Lennox-Gastaut syndrome (LGS)?

Bɔku tɛm dɛn kin du bɔku tɛst fɔ no if pɔsin gɛt LGS, ɛn dɔktɔ go du nyurolɔjik ɛgzam. Wan dɔktɔ we de mɛn pikin dɛn kin sɔprayz se i gɛt dis sik bay wetin di mama ɛn papa tɔk bɔt dɛn pikin in sik, mɔ if di pikin nɔ ebul fɔ lan ɔ i gɛt prɔblɛm wit aw i de biev.

Us tɛst dɛn kin du fɔ no dis?

Di tɛst dɛm we dɛn kin yuz mɔ na:

  • ilektroεnsεfalogram (EEG): dis involv fכ put sεvεra εlektrod dεm na di sכl wit kכnduktiv jel fכ mכsu di ilektrikal aktiviti na di bren. EEG imכtant fכ no LGS biכs i de sho wan difrεnt ilektrikal patεn na di bren wev dεm.
  • Magnetic Resonance Imaging (MRI): Dis kin yuz pawaful magnet ɛn kɔmpyuta fɔ tek ay rɛsɔlɔshɔn pikchɔ dɛn fɔ di insay pat na di bɔdi, mɔ di bren. Dis kin rili ɛp fɔ no di prɔblɛm dɛn we de wit di bren divɛlɔpmɛnt.
  • Lab testing: Dɛn tɛst ya kin chɛk blɔd ɛn urine fɔ si if ɔda tin dɛn de we kin mek pɔsin gɛt di sik. Dɛn kin luk tin dɛn lɛk di blɔd kemistri, di liva ɛnzaym dɛn, ɛn di we aw di kidni de wok. Pan ɔl we dɛn tɛst ya nɔ kin ebul fɔ no LGS fayn fayn wan, dɛn kin ɛp fɔ pul ɔda kɔndishɔn dɛn we kin falamakata LGS.
  • jεnεtik tεst: Dis kin εp fכ no if kכndishכn dεm de we dεn kin gεt we kin mek LGS, כ if spontan mכtεshכn dεm de.

Apat frɔm dat, dɛn kin du ɔda tɛst dɛn fɔ mek dɛn nɔ no di sem kayn tin. Yu dɔktɔ go tɛl yu mɔ bɔt dis.

Aw dɛn go trit dis? Yu tink se dɛn kin mɛn am?

Bɔku tritmɛnt opshɔn dɛn de fɔ LGS. Bɔt, dɛn no se i nɔ izi fɔ trit dis sik. Bɔrku tɛm, dɛn kin yuz wan ɔr kɔmbayn pan dɛn tritmɛnt ya:

  • Di mɛrɛsin dɛn we dɛn kin yuz
  • Di tritmɛnt dɛn we dɛn kin yuz fɔ it
  • Ɔpreshɔn fɔ di bren ɔ tin dɛn we dɛn kin put insay pɔsin in bren

Di mɛrɛsin dɛn we dɛn kin yuz

Bɔku tɛm, di sik we dɛn kɔl Lennox-Gastaut syndrome kin rili bia wit mɛrɛsin. Na dat mek i rili at fɔ manej. Bɔku tɛm, dɛn kin nid fɔ tek bɔku mɛrɛsin dɛn. Wan ɔda tin we kin mek i nɔ izi na dat sɔm mɛrɛsin dɛn we kin mek pɔsin nɔ gɛt sik, we kin kɔntrol sɔm kayn sik dɛn, kin mek ɔda kayn sik dɛn we pɔsin kin gɛt mɔ ɛn mɔ.

We di sik nɔ kin ebul fɔ gɛt tritmɛnt, dɔktɔ dɛn kin tray fɔ mek sɔm kayn sik nɔ kam ɔ fɔ mek i nɔ gɛt bɔku sik. Fɔ ɛgzampul, atonic seizures impɔtant mɔ fɔ mek yu nɔ gɛt am, bikɔs i gɛt fɔ du wit big risk fɔ injuri we yu fɔdɔm.

Di tritmɛnt dɛn we dɛn kin yuz fɔ it

Fɔ bɔrku pipul dɛm wae gɛt siriɔs epilepsy, wae dɛn chenj dɛn it kin ɛp fɔ ridyus di sik wae dɛn kin gɛt ɔr stɔp dɛm ɔltogɛda. di ketogenic diet fכ epilepsy – di it we gεt hכy protin εn fεt εn we nכ gεt kכbכhaydrεt – na in dכkta dεn kin rεkomεnd bכku tεm. I kin bi gud opshɔn we di mɛrɛsin nɔ dɔn wok.

Pan ɔl we di ketogenic diet na pɔpul tritmɛnt fɔ siriɔs ɛpilepsi, i gɛt sɔm bad bad tin dɛn. Dis it kin wok if yu fala am di rayt we. Dis na bikɔs if yu it bɔku tin dɛn we gɛt kabɔhaydrɛt lɛk shuga ɛn it dɛn we gɛt stach, dat kin mek yu gɛt sik. Bɔt ɔda it dɛn we dɛn dɔn chenj kin ɛp bak. If yu want fɔ no mɔ, yu dɔktɔ kin ɛp yu fɔ tray wan pan dɛn it ya.

Ɔpreshɔn fɔ di bren ɛn tin dɛn we dɛn kin put insay pɔsin in bren

Sɔntɛnde, mɔ we ɔda tritmɛnt dɛn nɔ wok, ɔpreshɔn na di bɛst tin fɔ du. Na sɔm kayn ɔpreshɔn dɛn ya:

  • Vagus Nerve Stimulation (VNS): dis involv fכ implant wan divays insay di bכdi we de gi mild ilektrikal kכrant to di 10th kraynia nεv, di vagus nεv – we kכnekt dairekt to di bren. Dis kɔrɛnt kin ridyus di frɛkuɛns ɛn di kayn we aw pɔsin kin sik. As tɛm de go, di tin dɛn we i kin du kin bɔku. Dis min se yu nɔ go gɛt bɔku sik ɛn yu nɔ go gɛt siriɔs sik. Fɔ put dis divays insay pɔsin in bɔdi na tin we pɔsin kin chenj, i nɔ kin gɛt bɔku prɔblɛm dɛn ɛn i kin tek shɔt tɛm fɔ mek i wɛl, so bɔku tɛm dɛn kin tink bɔt am bifo dɛn du big ɔpreshɔn.
  • di kכpas kכlכsכtכmi: di kכpas kכlכsכm na pat pan di bren we de wok lεk brij bitwin di lεft εn rayt εmisfya. we dεn kכl di kכpas kכlכs, di abnכmal signal dεm we de mek di sik de stכp fכ go bak εn bak. Dis kin ridyus di frɛkuɛns fɔ di sik, ɔ ivin stɔp di siriɔs, disable di sik ɔltogɛda.
  • Hεmisfεrεktכmi `(Hεmisfεrεktכmi)`: .Dis min se dɛn fɔ ɔpreshɔn wan say na di bren. Pan ɔl we dis kin tan lɛk se i rili bad, spɛshal pipul dɛn kin yuz am fɔ stɔp di sik dɛn we pɔsin kin gɛt we i nɔ ebul fɔ kɔntrol. Leta, bɔku tɛm, fizik tritmɛnt kin ɛp di bren fɔ ajɔst to di chenj. Di bren de rimap insɛf, ɛn di pat we lɛf de tek di wok we di pat we dɛn pul de du.
  • rεsεkshכn: strכkchכral anomaly dεm na di bren kin mek sכmtεm LGS. If dɔktɔ dɛn kin si dis kayn abnɔmal tin, dɛn kin ebul fɔ pul di bren tisu we dɔn pwɛl ɔ we gɛt sik ɛn stɔp di sik dɛn we de mek pɔsin sik. כltu, biכs insay LGS, di sik we de kכmכt na di bכdi de na mכr dan wan εria na di bren, dis nכ kin bi wan opshכn we rili saksesful fכ LGS.

Kɔmplikɛshɔn/sayd ifɛkt dɛm fɔ tritmɛnt

Di kɔmplikɛshɔn dɛn we kin kam pan di tritmɛnt kin spɛshal fɔ ɛni tritmɛnt. So, i go fayn fɔ mek yu tɔk to yu dɔktɔ bɔt di prɔblɛm dɛn ɛn di sayd ɛfɛkt dɛn we di tritmɛnt we yu ɔ yu pikin de gɛt kin gɛt. Dɔn di dɔktɔ kin gi yu infɔmeshɔn we fit yu sik, di tin dɛn we de apin to yu, ɛn ɔda tin dɛn we yu de du.

Aw kwik a go fil fayn afta dɛn dɔn trit mi? Aw lɔng i go tek fɔ mek i wɛl?

Di tɛm fɔ wɛl afta tritmɛnt kin difrɛn bad bad wan dipen pan di tritmɛnt we dɛn yuz ɛn yu ɔl di kɔndishɔn. Yu dɔktɔ na di bɛst pɔsin fɔ tɛl yu di rayt tin fɔ ɛkspɛkt ɛn aw lɔng i go tek fɔ mek yu wɛl.

Dɛn kin ebul fɔ protɛkt di sik we dɛn kɔl Lennox-Gastaut syndrome (LGS)?

Bɔku tɛm, LGS nɔto kɔndishɔn we pɔsin kin ebul fɔ avɔyd. Ɛn dɛn nɔ go ebul fɔ ridyus di risk fɔ gɛt am. di onli eksepshכn na fכ mek dεn nכ gεt ed εn bren injuri we kin kכmכt frכm LGS. Di wangren we fɔ mek dis sik nɔ apin na fɔ mek yu pikin dɛn wɛr ɛlmɛt we dɛn dɔn gri fɔ ɛn we gɛt sɛtifiket.

Wetin a fɔ ɛkspɛkt if mi ɔ mi pikin gɛt dis sik?

Lennox-Gastaut syndrome na wan sik wae kin gɛt siriɔs prɔblɛm. Bɔrku pikin dɛm wae gɛt dis sik kin gɛt disabled fɔ lan ɛn de pwɛl dɛn bren fɔ ɔltɛm we kin mek dɛn nɔ ebul fɔ tink gud wan. Dɔn bak, bikɔs atonic seizures (drop attack) kin kɔmɔn, ɛn bɔku tɛm i kin mek pɔsin fɔdɔm, pikin dɛn we gɛt dis sik kin gɛt mɔ risk fɔ injuri.

Dis sik kin tranga bak fɔ trit. Bɔrku pikin dɛm wae gɛt am kin nid spɛshal kia fɔ ɔl dɛn layf bikɔs dɛn nɔr kin ebul fɔ kia fɔ dɛnsɛf. Bɔt sɔm pipul dɛm wae gɛt dis sik kin jɔs gɛt smɔl smɔl bren damej, dat min se dɛn kin liv fɔ dɛnsɛf.

Aw lɔŋ (LGS) kin las?

If dɛn nɔ gi tritmɛnt fɔ stɔp di sik dɛn we de mek pɔsin sik kpatakpata (we nɔ kin apin so ɔltɛm), LGS na sik we pɔsin kin gɛt fɔ ɔl in layf.

Wetin na di lukin-grɔn fɔ dis sityueshɔn?

Di big big risk fɔ gɛt Lennox-Gastaut syndrome na di bren we de pwɛl we pɔsin nɔ ebul fɔ kɔntrol am, ɔ we i fɔdɔm bikɔs i gɛt sik. Bikɔs ɔf dɛn risk dɛm de, di rεt fɔ pipul dɛm wae gɛt ``LGS'' insay 10 ia afta dɛn dɔn no di sik na bitwin 3% ɛn 7%.

Sɔntɛnde, di mɛrɛsin we dɛn kin du kin stɔp di sik we LGS kin kam wit. Dis kin stɔp di sik, bɔt i nɔ kin ebul fɔ mek di bren we dɔn pwɛl bikɔs ɔf di sik dɛn we i bin dɔn gɛt trade.

Aw a kin kia fɔ misɛf? / Aw a go tek kia ɔf mi pikin?

If yu ɔ pɔsin we yu lɛk gɛt LGS, i rili impɔtant fɔ fala yu dɔktɔ in instrɔkshɔn dɛn kɔrɛkt wan. Dis inklud:

  • Fɔ tek mɛrɛsin lɛk aw dɛn tɛl yu fɔ tek am.
  • Go to di dɔktɔ lɛk aw dɛn se.
  • Fɔ wach aw yu de sik ɛn fɔ avɔyd tin dɛn we de mek yu sik ɔ tin dɛn we kin mek yu gɛt sik.

Ustɛm a fɔ go to di dɔktɔ?

Yu ɔ yu pikin in dɔktɔ go tɛl yu fɔ kam insay fɔ fala-ɔp visit as nid de. Yu fɔ go to yu dɔktɔ bak if yu sik dɛn we de sho se yu gɛt sik chenj bad bad wan ɔ if dɛn afɛkt yu nɔmal tin dɛn we yu de du ɛvride ɛn di tin dɛn we yu de du.

Ustɛm a fɔ go na di Imejɛnsi Tritmɛnt Yunit (ETU) ?

If yu ɔ yu pikin gɛt sik ɔr bɔku bɔku sik dɛn we mit di krayteria fɔ wan mɛdikal imejensi we dɛn kɔl status epilepticus , yu fɔ go na di imejensi rum na di ɔspitul we de nia yu. Dis min se insay dɛn tin ya:

  • If wan sik we de mek yu sik de te bitwin 5 ɛn 30 minit.
  • If tu ɔ mɔ sik dɛn apin insay 30 minit ɛn di pɔsin nɔ gɛt ful kɔnshɛns bak di tɛm we di sik de kam.

Mɛsej we dɛn kin kɛr go na os

Lennox-Gastaut syndrome (LGS) na wan kayn sik wae kin kam pan pɔrsin wae gɛt epilepsy wae kin bigin kwik kwik wan. Bɔku tɛm, i kin afɛkt di pikin in layf bad bad wan, sɔntɛnde i kin afɛkt in layf. Pan ɔl we i nɔ kin izi fɔ trit am, nyu mɛrɛsin, ɔpreshɔn, ɛn tritmɛnt kin ɛp fɔ ridyus di kayn sik ɛn fɔ mek di sik nɔ bɔku. Na smɔl tɛm nɔmɔ, tritmɛnt kin mɛn di sik kpatakpata. Bɔt dɛn nid fɔ du mɔ risach fɔ no if dɛn kin trit dis sik ɔ nɔ kin mɛn am. If yu pikin gɛt ɛni wan pan dɛn sik ya, i go fayn fɔ mek yu go to dɔktɔ kwik kwik wan.


` Lennox-Gastaut syndrome, LGS, epilepsy, seizure, pikin dεm, bren dizayd, nyurolכjik sik dεm

Frequently Asked Questions (FAQ)

Wetin na Status Epilepticus?

Dis min wan pan tu tin dɛn:

Us tɛst dɛn kin du fɔ no dis?

Di tɛst dɛm we dɛn kin yuz mɔ na:

Wetin na di lukin-grɔn fɔ dis sityueshɔn?

Di big big risk fɔ gɛt Lennox-Gastaut syndrome na di bren we de pwɛl we pɔsin nɔ ebul fɔ kɔntrol am, ɔ we i fɔdɔm bikɔs i gɛt sik. Bikɔs ɔf dɛn risk dɛm de, di rεt fɔ pipul dɛm wae gɛt ``LGS'' insay 10 ia afta dɛn dɔn no di sik na bitwin 3% ɛn 7%.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

No kɔmɛnt nɔ de yet. Ad yu kɔmɛnt ya fɔ di fɔs tɛm.

Ad yu kɔmɛnt

Duya kɔlkul: 9 + 9 =
Wetin na di sik we dɛn kɔl Lennox-Gastaut Syndrome (LGS)? Lɛ wi tɔk bɔt am!

Wetin na di sik we dɛn kɔl Lennox-Gastaut Syndrome (LGS)? Lɛ wi tɔk bɔt am!

Yu smɔl pikin kin gɛt sik we de mek i sik ɔltɛm? I gɛt big chenj dɛn pan aw i de lan ɛn aw i de biev? If na so, wetin a go tɔk kin rili impɔtant to yu. Tide wi go tɔk bɔt Lennox-Gastaut Syndrome , ɔ (LGS) fɔ shɔt, wan bad bad ɛn at fɔ trit epilepsy kɔndishɔn. Dis kin bigin we i yɔŋ. Bɔt nɔ wɔri, nyu mɛrɛsin ɛn tritmɛnt dɛn de naw.

Wetin rili na Lennox-Gastaut syndrome (LGS)? Udat kin gɛt am?

Fɔ tɔk am simpul wan, LGS na wan bad bad sik we kin bigin we dɛn smɔl, bɔku tɛm bifo i ol 10 ia, ɛn mɔ bitwin 3 ɛn 5 ia. I kin bɔku smɔl pan bɔy pikin dɛn. Bɔt, i nɔ kin rili kɔmɔn. I kin afɛkt lɛk wan to tu pipul dɛn pan wan milyɔn. Na lɛk 1% to 2% pan ɔl di wan dɛn we gɛt ɛpilepshi gɛt LGS.

Aw dis kin afɛkt wi bɔdi?

Epilepsy na wan sik wae de mek di bren in ilɛktrik signal ɔr infɔmeshɔn de pas bitwin di sɛl dɛm. (LGS) na wan kayn we we kin mek pɔsin gɛt ɛpilepshɔn we kin rili bad . Bɔku tin dɛn de we kin mek i apin:

  • Insay LGS, pas wan kayn sik kin apin. Sɔm pan dɛn kayn sik ya kin mek di pikin gɛt siriɔs injury.
  • Dɛn sik ya kin pwɛl di bren insɛf. Pikin dεm we gεt LGS kin gεt bad bad bren dεm, dεn kin tranga fכ lan, εn dεn kin delay fכ divεlכpmεnt. Dis min se di pikin kin lɔs ɔ fɔgɛt tin dɛn we i dɔn ɔlrɛdi lan, lɛk fɔ waka ɛn tɔk. Dis na tin we rili sɔri.
  • (LGS) kin rili rεsistεnt to tritmεnt. Dis min se i nɔ kin izi fɔ kɔntrol am wit mɛrɛsin. Mɛrɛsin na di fɔs tritmɛnt, bɔt bɔku tɛm dɛn kin gi bɔku kayn mɛrɛsin di sem tɛm. Ivin if dɛn gi dɛn, mɛrɛsin nɔmɔ nɔ kin ebul fɔ stɔp di sik dɛn we de mek pɔsin sik kpatakpata.

Wetin na di sayn dɛm fɔ (LGS)?

Pikin we gɛt LGS kin sho difrɛn kayn sayn dɛn. Sɔm pan dɛn kin notis na ɛvride layf ɛn tin dɛn we pɔsin kin du, ɛn ɔda wan dɛn kin jɔs notis we pɔsin de sik.

Prɔblɛm dɛn we pɔsin kin gɛt we i de lan ɛn di we aw i de biev

I kɔmɔn fɔ mek pikin dɛn we gɛt LGS gɛt prɔblɛm fɔ lan ɛn gɛt prɔblɛm wit aw dɛn de biev . Dɛn tin ya kin apin jɔs afta di sik bigin, ɛn dɛn kin wɔs as di sik kin kɔntinyu. Bɔrku tɛm, dɛn prɔblɛm ya wae de kam pan pɔrsin wae de lan ɛn in maynd kin de fɔ ɔltɛm, dat min se dɛn kin kɔntinyu fɔ de te dɛn big.

Pikin dɛn we gɛt LGS kin gɛt prɔblɛm fɔ lan, fɔ mek padi, ɛn fɔ tɔk to ɔda pipul dɛn. I nɔ kin izi bak fɔ dɛn fɔ kɔntrol di we aw dɛn de fil. Sɔm pikin dɛn kin sho bak di sayn dɛm we fiba di wan dɛm wae gɛt dis sik wae gɛt Autism Spectrum Disorder .

Stej we pɔsin kin gɛt we i sik

Wan sik kin apin insay tri stej dɛm:

1. Prodrome ɔ aura: Dis na sɔntin we sɔm pipul dɛn kin gɛt bifo dɛn gɛt sik, pan ɔl we nɔto ɔltɛm. Dis kin bi filin wae nɔr kin fayn fɔ yu. Chenj na di vishɔn, chenj na ɔda sɛns, ɔr chenj na di mud ɔr bihayvya kin apin dis tɛm.

2. Seizure: Dis na we di sik de kam. Dis kin difrɛn difrɛn wan bay di kayn sik wae de kam (wi go tɔk bɔt di difrɛn kayn sik wae de kam dɔŋ ya).

3. Pɔst-seizure recovery: Dis na di tɛm afta di seizure dɔn dɔn. Dis na we pɔsin kin gɛt ful kɔnshɛns bak.

Di kayn sik dɛn we dɛn kin si na LGS

Bɔku men kayn sik dɛn de we dɛn kin si na LGS. Di kayn sik wae kin kam pan pɔrsin wae gɛt dis sik ɛn di tin dɛm wae kin apin to pɔrsin na dɛn wan ya:

  • Atonik sik dɛn we kin mek pɔsin sik:
  • we yu lכs di mכsul kכntrכl/fεn: dεn kכl dis bak "drכp atak" biכs i involv fכ lכs kכntrol wan wan εn fכ fכl na grכn, lεk pכpεt we in strכng dεm dכn brok. Dis kin rili denja bikɔs di pikin nɔ kin ebul fɔ kɔntrol am we dɛn fɔdɔm ɛn i kin gɛt siriɔs injury na in ed, in nɛk, in chɛst, ɛn bak we kin mek i day.
  • Sɔm pat pan yu nɔr de no natin: Dis sik wae de mɛk yu nɔr de mɛmba ɔltɛm.
  • Fɔ shɔt tɛm: Dɛn sik ya kin las fɔ shɔt tɛm, lɛk fɔ sɔm sɛkɔn.
  • Tonik kɔnvulshɔn dɛn:
  • di ol bכdi stiff/friz: Dis na we כl di mכsul dεm na di bכdi de kכntrakt wan wan, we de mek di bכdi stif kכmplit lεk se i tכn to ston.
  • Wan spɛshal pozishɔn: We dɛn de na grɔn, dɛn leg ɛn sholda dɛn de na grɔn, dɛn bak kin arch. di an dεm kin es oba dεn ed, כ dεn kin kכl di an dεm εn di εlbo dεm kin pכynt to di sayd dεm, εn di fist dεm kin de nia di hip dεm.
  • Bɔrku tɛm kin apun wae yu de slip: Dɛn kin apun bɔrku tɛm wae yu de slip. Bɔt dɛn kin apin bak insay di de. If dis kin apin we di pikin wek, i kin izi fɔ mek i wund bikɔs di pikin kin fɔdɔm.
  • Fɔ shɔt tɛm: Dis kin te bak frɔm sɔm sɛkɔn to lɛk wan minit.
  • Atypical absɛns sik dɛn: .
  • Yay dεm opin εn de luk blank: Insay dis sik, dεn kin lכs kכnsεns, bכt di yay dεm kin stil opin. So, bɔku tɛm dɛn kin mistek kɔl dis fɔ drim de, nɔ de pe atɛnshɔn, ɛn fɔ fil se i nɔ de na di say we i de.
  • Muvmɛnt dɛn we de ripit: We yu de du dis sik, yu kin si we yu de muv yu yay ɛn yu mɔt. I kin bi bak se di an dɛn kin muv.
  • Fɔ shɔt tɛm: Dis bak nɔ kin te pas sɔm sɛkɔn.

Impɔtant: Pikin dɛn we gɛt LGS kin gɛt sik na "klɔsta," we min se sɔm sik kin apin insay shɔt tɛm. I pas tu-tɛd pan di pikin dɛnWan kכndyushכn we dεn kכl "Status Epilepticus" kin apin. Dis na sik we nid fɔ gɛt mɛrɛsin kwik kwik wan!

Wetin na Status Epilepticus?

Dis min wan pan tu tin dɛn:

  • Wan wan sik we kin tek lɔng tɛm we kin tek bitwin 5 ɛn 30 minit.
  • Mɔ pas wan sik kin apin insay 30 minit, ɛn di pɔsin nɔ kin gɛt ful kɔnshɛns bak di tɛm we i kin gɛt dɛn sik dɛn de.

Status epilepticus na wan mɛdikal imejensi. I rili denja bikɔs i kin mek yu bren pwɛl sote go ɛn ivin day.

Ɔda sayn dɛm ɛn di kayn sik dɛm wae gɛt fɔ du wit am

  • Tonic-clonic seizures: Tonic-clonic seizures (we dɛn bin de kɔl "grand mal") kin bigin di sem we lɛk tonic seizures, bɔt dɛn kin gɛt ɔda pat. di klonik faz na we di bכdi de jכk, di mכst kכmכn fכm fכ di sik, de apin. Tonic ɛn tonic-clonic seizures kin las fɔ lɛk tu minit.
  • Kwik, shɔt, jεk muvmεnt: Mayoklɔnik sik na we yu de muv wantɛm wantɛm, we de jεk. Dɛn kin las fɔ sɔm sɛkɔn dɛn nɔmɔ, bɔt sɔntɛnde dɛn kin las fɔ lɔng tɛm. Pipul wae nɔr gɛt sik kin gɛt dis kayn "myoclonic jerks" bak. Fɔ ɛgzampul, dɛn kin mek pɔsin hiccups ɔ wek wantɛm wantɛm we i dɔn slip.
  • Sεns, mental, ɔr ɔda sayn dɛm: Sɔm pat ɔ fכs sik kin afɛkt wan smɔl pat pan di bɔdi nɔmɔ.

Wetin na di tin dɛn we kin mek pɔsin gɛt LGS?

Bɔku tin dɛn de we kin mek pɔsin gɛt di sik we dɛn kɔl Lennox-Gastaut syndrome. Sɔm pan di tin dɛn we kin mek i apin kin de bifo dɛn bɔn pikin. Ɔda wan dɛn kin apin bikɔs ɔf tin dɛn we kin apin we dɛn smɔl. Insay lɛk wan kwata pan di kes dɛm we ``(LGS)``, dɛn nɔ kin no klia kɔz.

Na sɔm pan di rizin dɛn we dɛn dɔn no:

  • Prɔblɛm dɛn we de wit di bren we de gro bifo dɛn bɔn am.
  • Sivɛri ed injuri (traumatik bren injuri ɔ kɔnkyushɔn).
  • Infεkshכn dεm we de pwεl di bren, lεk mεningayt כ εnεfalaytis.
  • di mεtabolik sik dεm we dεn kin gεt inhεrit, fכ egzampl `(Mitochondrial diseases)`.
  • di bren dεm we de pwεl we dεn nכ gεt כksijεn bifo כ we dεn bכn (sεribral haypoksia).
  • Tuberous sclerosis we gɛt di sik.
  • Tumɔs dɛn na di bren.
  • Wεst sεndrכm (dis na כda kayn εpilepshכn, we leta kin divεlכp to LGS).

Risach pipul dεn fכnshכn se "de novo mutations" na kכmכn pan pipul dεm we gεt LGS.De novo min "frɔm di biginin." dis na difεkt dεm na pכsin in `(DNA)` we de apin wan wan, randomly. dat min se di mכtayshכn de kכz fכ difεkt na di `(DNA)` na di sεl כ eg we prodyuz di pכsin, bכt i nכ de fכ di `(DNA)` fכ εni wan pan di mama εn papa.

Bɔt, i kin bi se sɔntin de we kin mek pɔsin gɛt sɔntin fɔ du wit di sik. Na lɛk 30% pan di pipul dɛm wae gɛt LGS gɛt famili histri fɔ gɛt ɛpilepsi. Bɔt dɛn nid fɔ du mɔ risach fɔ no ustɛm dis na sɔntin we de mek pɔsin gɛt jɛnɛtiks.

Yu tink se dis kin pas?

Nɔ, di sik we dɛn kɔl Lennox-Gastaut syndrome nɔ kin gɛt di sik. I nɔ de skata frɔm wan pɔsin to ɔda pɔsin. Bɔt sɔm sik dɛn we kin kam pan pɔsin kin mek di bren pwɛl ɛn mek i gɛt ``LGS''. Bɔt nɔto ɔlman we gɛt dɛn infɛkshɔn ya go gɛt ``LGS''.

Aw dɛn kin no se pɔsin gɛt di sik we dɛn kɔl Lennox-Gastaut syndrome (LGS)?

Bɔku tɛm dɛn kin du bɔku tɛst fɔ no if pɔsin gɛt LGS, ɛn dɔktɔ go du nyurolɔjik ɛgzam. Wan dɔktɔ we de mɛn pikin dɛn kin sɔprayz se i gɛt dis sik bay wetin di mama ɛn papa tɔk bɔt dɛn pikin in sik, mɔ if di pikin nɔ ebul fɔ lan ɔ i gɛt prɔblɛm wit aw i de biev.

Us tɛst dɛn kin du fɔ no dis?

Di tɛst dɛm we dɛn kin yuz mɔ na:

  • ilektroεnsεfalogram (EEG): dis involv fכ put sεvεra εlektrod dεm na di sכl wit kכnduktiv jel fכ mכsu di ilektrikal aktiviti na di bren. EEG imכtant fכ no LGS biכs i de sho wan difrεnt ilektrikal patεn na di bren wev dεm.
  • Magnetic Resonance Imaging (MRI): Dis kin yuz pawaful magnet ɛn kɔmpyuta fɔ tek ay rɛsɔlɔshɔn pikchɔ dɛn fɔ di insay pat na di bɔdi, mɔ di bren. Dis kin rili ɛp fɔ no di prɔblɛm dɛn we de wit di bren divɛlɔpmɛnt.
  • Lab testing: Dɛn tɛst ya kin chɛk blɔd ɛn urine fɔ si if ɔda tin dɛn de we kin mek pɔsin gɛt di sik. Dɛn kin luk tin dɛn lɛk di blɔd kemistri, di liva ɛnzaym dɛn, ɛn di we aw di kidni de wok. Pan ɔl we dɛn tɛst ya nɔ kin ebul fɔ no LGS fayn fayn wan, dɛn kin ɛp fɔ pul ɔda kɔndishɔn dɛn we kin falamakata LGS.
  • jεnεtik tεst: Dis kin εp fכ no if kכndishכn dεm de we dεn kin gεt we kin mek LGS, כ if spontan mכtεshכn dεm de.

Apat frɔm dat, dɛn kin du ɔda tɛst dɛn fɔ mek dɛn nɔ no di sem kayn tin. Yu dɔktɔ go tɛl yu mɔ bɔt dis.

Aw dɛn go trit dis? Yu tink se dɛn kin mɛn am?

Bɔku tritmɛnt opshɔn dɛn de fɔ LGS. Bɔt, dɛn no se i nɔ izi fɔ trit dis sik. Bɔrku tɛm, dɛn kin yuz wan ɔr kɔmbayn pan dɛn tritmɛnt ya:

  • Di mɛrɛsin dɛn we dɛn kin yuz
  • Di tritmɛnt dɛn we dɛn kin yuz fɔ it
  • Ɔpreshɔn fɔ di bren ɔ tin dɛn we dɛn kin put insay pɔsin in bren

Di mɛrɛsin dɛn we dɛn kin yuz

Bɔku tɛm, di sik we dɛn kɔl Lennox-Gastaut syndrome kin rili bia wit mɛrɛsin. Na dat mek i rili at fɔ manej. Bɔku tɛm, dɛn kin nid fɔ tek bɔku mɛrɛsin dɛn. Wan ɔda tin we kin mek i nɔ izi na dat sɔm mɛrɛsin dɛn we kin mek pɔsin nɔ gɛt sik, we kin kɔntrol sɔm kayn sik dɛn, kin mek ɔda kayn sik dɛn we pɔsin kin gɛt mɔ ɛn mɔ.

We di sik nɔ kin ebul fɔ gɛt tritmɛnt, dɔktɔ dɛn kin tray fɔ mek sɔm kayn sik nɔ kam ɔ fɔ mek i nɔ gɛt bɔku sik. Fɔ ɛgzampul, atonic seizures impɔtant mɔ fɔ mek yu nɔ gɛt am, bikɔs i gɛt fɔ du wit big risk fɔ injuri we yu fɔdɔm.

Di tritmɛnt dɛn we dɛn kin yuz fɔ it

Fɔ bɔrku pipul dɛm wae gɛt siriɔs epilepsy, wae dɛn chenj dɛn it kin ɛp fɔ ridyus di sik wae dɛn kin gɛt ɔr stɔp dɛm ɔltogɛda. di ketogenic diet fכ epilepsy – di it we gεt hכy protin εn fεt εn we nכ gεt kכbכhaydrεt – na in dכkta dεn kin rεkomεnd bכku tεm. I kin bi gud opshɔn we di mɛrɛsin nɔ dɔn wok.

Pan ɔl we di ketogenic diet na pɔpul tritmɛnt fɔ siriɔs ɛpilepsi, i gɛt sɔm bad bad tin dɛn. Dis it kin wok if yu fala am di rayt we. Dis na bikɔs if yu it bɔku tin dɛn we gɛt kabɔhaydrɛt lɛk shuga ɛn it dɛn we gɛt stach, dat kin mek yu gɛt sik. Bɔt ɔda it dɛn we dɛn dɔn chenj kin ɛp bak. If yu want fɔ no mɔ, yu dɔktɔ kin ɛp yu fɔ tray wan pan dɛn it ya.

Ɔpreshɔn fɔ di bren ɛn tin dɛn we dɛn kin put insay pɔsin in bren

Sɔntɛnde, mɔ we ɔda tritmɛnt dɛn nɔ wok, ɔpreshɔn na di bɛst tin fɔ du. Na sɔm kayn ɔpreshɔn dɛn ya:

  • Vagus Nerve Stimulation (VNS): dis involv fכ implant wan divays insay di bכdi we de gi mild ilektrikal kכrant to di 10th kraynia nεv, di vagus nεv – we kכnekt dairekt to di bren. Dis kɔrɛnt kin ridyus di frɛkuɛns ɛn di kayn we aw pɔsin kin sik. As tɛm de go, di tin dɛn we i kin du kin bɔku. Dis min se yu nɔ go gɛt bɔku sik ɛn yu nɔ go gɛt siriɔs sik. Fɔ put dis divays insay pɔsin in bɔdi na tin we pɔsin kin chenj, i nɔ kin gɛt bɔku prɔblɛm dɛn ɛn i kin tek shɔt tɛm fɔ mek i wɛl, so bɔku tɛm dɛn kin tink bɔt am bifo dɛn du big ɔpreshɔn.
  • di kכpas kכlכsכtכmi: di kכpas kכlכsכm na pat pan di bren we de wok lεk brij bitwin di lεft εn rayt εmisfya. we dεn kכl di kכpas kכlכs, di abnכmal signal dεm we de mek di sik de stכp fכ go bak εn bak. Dis kin ridyus di frɛkuɛns fɔ di sik, ɔ ivin stɔp di siriɔs, disable di sik ɔltogɛda.
  • Hεmisfεrεktכmi `(Hεmisfεrεktכmi)`: .Dis min se dɛn fɔ ɔpreshɔn wan say na di bren. Pan ɔl we dis kin tan lɛk se i rili bad, spɛshal pipul dɛn kin yuz am fɔ stɔp di sik dɛn we pɔsin kin gɛt we i nɔ ebul fɔ kɔntrol. Leta, bɔku tɛm, fizik tritmɛnt kin ɛp di bren fɔ ajɔst to di chenj. Di bren de rimap insɛf, ɛn di pat we lɛf de tek di wok we di pat we dɛn pul de du.
  • rεsεkshכn: strכkchכral anomaly dεm na di bren kin mek sכmtεm LGS. If dɔktɔ dɛn kin si dis kayn abnɔmal tin, dɛn kin ebul fɔ pul di bren tisu we dɔn pwɛl ɔ we gɛt sik ɛn stɔp di sik dɛn we de mek pɔsin sik. כltu, biכs insay LGS, di sik we de kכmכt na di bכdi de na mכr dan wan εria na di bren, dis nכ kin bi wan opshכn we rili saksesful fכ LGS.

Kɔmplikɛshɔn/sayd ifɛkt dɛm fɔ tritmɛnt

Di kɔmplikɛshɔn dɛn we kin kam pan di tritmɛnt kin spɛshal fɔ ɛni tritmɛnt. So, i go fayn fɔ mek yu tɔk to yu dɔktɔ bɔt di prɔblɛm dɛn ɛn di sayd ɛfɛkt dɛn we di tritmɛnt we yu ɔ yu pikin de gɛt kin gɛt. Dɔn di dɔktɔ kin gi yu infɔmeshɔn we fit yu sik, di tin dɛn we de apin to yu, ɛn ɔda tin dɛn we yu de du.

Aw kwik a go fil fayn afta dɛn dɔn trit mi? Aw lɔng i go tek fɔ mek i wɛl?

Di tɛm fɔ wɛl afta tritmɛnt kin difrɛn bad bad wan dipen pan di tritmɛnt we dɛn yuz ɛn yu ɔl di kɔndishɔn. Yu dɔktɔ na di bɛst pɔsin fɔ tɛl yu di rayt tin fɔ ɛkspɛkt ɛn aw lɔng i go tek fɔ mek yu wɛl.

Dɛn kin ebul fɔ protɛkt di sik we dɛn kɔl Lennox-Gastaut syndrome (LGS)?

Bɔku tɛm, LGS nɔto kɔndishɔn we pɔsin kin ebul fɔ avɔyd. Ɛn dɛn nɔ go ebul fɔ ridyus di risk fɔ gɛt am. di onli eksepshכn na fכ mek dεn nכ gεt ed εn bren injuri we kin kכmכt frכm LGS. Di wangren we fɔ mek dis sik nɔ apin na fɔ mek yu pikin dɛn wɛr ɛlmɛt we dɛn dɔn gri fɔ ɛn we gɛt sɛtifiket.

Wetin a fɔ ɛkspɛkt if mi ɔ mi pikin gɛt dis sik?

Lennox-Gastaut syndrome na wan sik wae kin gɛt siriɔs prɔblɛm. Bɔrku pikin dɛm wae gɛt dis sik kin gɛt disabled fɔ lan ɛn de pwɛl dɛn bren fɔ ɔltɛm we kin mek dɛn nɔ ebul fɔ tink gud wan. Dɔn bak, bikɔs atonic seizures (drop attack) kin kɔmɔn, ɛn bɔku tɛm i kin mek pɔsin fɔdɔm, pikin dɛn we gɛt dis sik kin gɛt mɔ risk fɔ injuri.

Dis sik kin tranga bak fɔ trit. Bɔrku pikin dɛm wae gɛt am kin nid spɛshal kia fɔ ɔl dɛn layf bikɔs dɛn nɔr kin ebul fɔ kia fɔ dɛnsɛf. Bɔt sɔm pipul dɛm wae gɛt dis sik kin jɔs gɛt smɔl smɔl bren damej, dat min se dɛn kin liv fɔ dɛnsɛf.

Aw lɔŋ (LGS) kin las?

If dɛn nɔ gi tritmɛnt fɔ stɔp di sik dɛn we de mek pɔsin sik kpatakpata (we nɔ kin apin so ɔltɛm), LGS na sik we pɔsin kin gɛt fɔ ɔl in layf.

Wetin na di lukin-grɔn fɔ dis sityueshɔn?

Di big big risk fɔ gɛt Lennox-Gastaut syndrome na di bren we de pwɛl we pɔsin nɔ ebul fɔ kɔntrol am, ɔ we i fɔdɔm bikɔs i gɛt sik. Bikɔs ɔf dɛn risk dɛm de, di rεt fɔ pipul dɛm wae gɛt ``LGS'' insay 10 ia afta dɛn dɔn no di sik na bitwin 3% ɛn 7%.

Sɔntɛnde, di mɛrɛsin we dɛn kin du kin stɔp di sik we LGS kin kam wit. Dis kin stɔp di sik, bɔt i nɔ kin ebul fɔ mek di bren we dɔn pwɛl bikɔs ɔf di sik dɛn we i bin dɔn gɛt trade.

Aw a kin kia fɔ misɛf? / Aw a go tek kia ɔf mi pikin?

If yu ɔ pɔsin we yu lɛk gɛt LGS, i rili impɔtant fɔ fala yu dɔktɔ in instrɔkshɔn dɛn kɔrɛkt wan. Dis inklud:

  • Fɔ tek mɛrɛsin lɛk aw dɛn tɛl yu fɔ tek am.
  • Go to di dɔktɔ lɛk aw dɛn se.
  • Fɔ wach aw yu de sik ɛn fɔ avɔyd tin dɛn we de mek yu sik ɔ tin dɛn we kin mek yu gɛt sik.

Ustɛm a fɔ go to di dɔktɔ?

Yu ɔ yu pikin in dɔktɔ go tɛl yu fɔ kam insay fɔ fala-ɔp visit as nid de. Yu fɔ go to yu dɔktɔ bak if yu sik dɛn we de sho se yu gɛt sik chenj bad bad wan ɔ if dɛn afɛkt yu nɔmal tin dɛn we yu de du ɛvride ɛn di tin dɛn we yu de du.

Ustɛm a fɔ go na di Imejɛnsi Tritmɛnt Yunit (ETU) ?

If yu ɔ yu pikin gɛt sik ɔr bɔku bɔku sik dɛn we mit di krayteria fɔ wan mɛdikal imejensi we dɛn kɔl status epilepticus , yu fɔ go na di imejensi rum na di ɔspitul we de nia yu. Dis min se insay dɛn tin ya:

  • If wan sik we de mek yu sik de te bitwin 5 ɛn 30 minit.
  • If tu ɔ mɔ sik dɛn apin insay 30 minit ɛn di pɔsin nɔ gɛt ful kɔnshɛns bak di tɛm we di sik de kam.

Mɛsej we dɛn kin kɛr go na os

Lennox-Gastaut syndrome (LGS) na wan kayn sik wae kin kam pan pɔrsin wae gɛt epilepsy wae kin bigin kwik kwik wan. Bɔku tɛm, i kin afɛkt di pikin in layf bad bad wan, sɔntɛnde i kin afɛkt in layf. Pan ɔl we i nɔ kin izi fɔ trit am, nyu mɛrɛsin, ɔpreshɔn, ɛn tritmɛnt kin ɛp fɔ ridyus di kayn sik ɛn fɔ mek di sik nɔ bɔku. Na smɔl tɛm nɔmɔ, tritmɛnt kin mɛn di sik kpatakpata. Bɔt dɛn nid fɔ du mɔ risach fɔ no if dɛn kin trit dis sik ɔ nɔ kin mɛn am. If yu pikin gɛt ɛni wan pan dɛn sik ya, i go fayn fɔ mek yu go to dɔktɔ kwik kwik wan.


` Lennox-Gastaut syndrome, LGS, epilepsy, seizure, pikin dεm, bren dizayd, nyurolכjik sik dεm

Frequently Asked Questions (FAQ)

Wetin na Status Epilepticus?

Dis min wan pan tu tin dɛn:

Us tɛst dɛn kin du fɔ no dis?

Di tɛst dɛm we dɛn kin yuz mɔ na:

Wetin na di lukin-grɔn fɔ dis sityueshɔn?

Di big big risk fɔ gɛt Lennox-Gastaut syndrome na di bren we de pwɛl we pɔsin nɔ ebul fɔ kɔntrol am, ɔ we i fɔdɔm bikɔs i gɛt sik. Bikɔs ɔf dɛn risk dɛm de, di rεt fɔ pipul dɛm wae gɛt ``LGS'' insay 10 ia afta dɛn dɔn no di sik na bitwin 3% ɛn 7%.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

No kɔmɛnt nɔ de yet. Ad yu kɔmɛnt ya fɔ di fɔs tɛm.

Ad yu kɔmɛnt

Duya kɔlkul: 9 + 9 =