Sɔm sik dɛn de, we dɛn fɔ yuz rili patikyula kayn mɛrɛsin fɔ. So if dɛn dɔn gi yu dis kayn mɛrɛsin, i rili impɔtant fɔ mek yu no bɔt am gud gud wan. Mitapivat na wan pan dɛn spɛshal mɛrɛsin dɛn de. Insay dis atikul tide, wi go tɔk bɔt dis mɛrɛsin we dɛn kɔl Mitapivat, lɛk se wi de tɔk to wi padi.
Us kayn mɛrɛsin na Mitapivat?
Fɔ tɔk am simpul wan, wi blɔd gɛt rɛd blɔd sɛl dɛn. Dis na di sɛl dɛn we de kɛr ɔksijɛn go ɔlsay na di bɔdi. sכm pipul dεn bכn wit wan jεnεtik kכndishכn we de mek dεn nכ gεt wan εnzym we dεn kכl ‘Pyruvate Kinase’. We dis ɛnzaym nɔ bɔku, di rɛd blɔd sɛl dɛn kin brok bifo tɛm ɛn dɛn kin pwɛl. dis kכndyushכn dεn kכl am ‘hεmolytic anemia’ , we min se anemia we de kכz we di rεd bכdi sεl dεm de brok.
So, wetin dis mɛrɛsin we dɛn kɔl Mitapivat de du na fɔ stɔp dɛn rɛd blɔd sɛl dɛn de fɔ brok tu kwik. I de kam bak ɔnda di brand nem `PYRUKYND`. Dis mɛrɛsin de mek da ɛnzaym de wok ɛn i de mek di rɛd blɔd sɛl dɛn liv lɔng. So, dɛn kin kɔntrol di anemia.
Tin dɛn we yu fɔ tɛl yu dɔktɔ bifo yu tek mɛrɛsin
Bifo yu bigin dis mɛrɛsin, i impɔtant fɔ tɛl yu dɔktɔ bɔt sɔm tin dɛn bɔt yu wɛlbɔdi prɔblɛm. Na da tɛm de nɔmɔ yu go disayd if i fayn fɔ yu ɛn aw fɔ gi am.
| Situeshɔn we yu nid fɔ ripɔt | Wetin mek na so i bi? (I impɔtant) |
|---|---|
| Liva sik | Dis mɛrɛsin de klin frɔm di bɔdi tru di liva, so if yu gɛt ɛni liva sik, yu kin nid fɔ ajɔst di doz we yu de tek. |
| Alɛji dɛn we pɔsin kin gɛt | If yu gɛt alɛji nɔto jɔs to dis Mitapivat mɛrɛsin, bɔt yu gɛt ɛni ɔda mɛrɛsin, it, ɔ day, mek shɔ se yu tɛl wi bɔt am. |
| Fɔ gɛt bɛlɛ ɔ fɔ plan fɔ gɛt bɛlɛ | If yu gɛt bɛlɛ ɔ yu de plan fɔ bɔn pikin, yu fɔ tɔk to yu dɔktɔ bɔt aw dis mɛrɛsin kin afɛkt di pikin. |
| If yu na mama we de gi pikin in bɛlɛ | Fɛn ɔut if di mɛrɛsin kin pas to di pikin tru in mama in milk, ɛn tɛl yu dɔktɔ if yu na mama we de gi pikin in bɛlɛ. |
Aw a fɔ yuz di mɛrɛsin?
Dis na pil fɔ tek yu mɔt. I rili impɔtant fɔ tek di rayt doz lɛk aw yu dɔktɔ tɛl yu.
- Tek am di rayt tɛm: Ɛnitɛm we i pɔsibul, tray fɔ tek yu mɛrɛsin di sem tɛm ɛvride . Dis go ɛp fɔ mek di lɛvɛl dɛn we di mɛrɛsin de na yu bɔdi nɔ chenj.
- Fɔ swɛla: Dis na di tin we impɔtant pas ɔl. Nɔ brok, krɔs, ɔ chew di tablɛt. Swɛla di tablɛt ɔl wit wan glas wata.
- Nɔ stɔp: Nɔ stɔp fɔ tek yu mɛrɛsin te yu dɔktɔ tɛl yu fɔ tek am. I impɔtant fɔ kɔntinyu fɔ tek yu mɛrɛsin, ilɛksɛf yu fil fayn.
- If dɛn gi am to pikin dɛn: If dɛn gi dis mɛrɛsin to pikin dɛn, dɛn kin nid spɛshal kia. Fɔ fala di dɔktɔ in instrɔkshɔn dɛn di rayt we.
Atɛnshɔn: Ɔvados
If yu tink se yu go dɔn tek ɔvados, nɔ panik ɛn kɔl di Nashɔnal Pɔyzin Infɔmeshɔn Sɛnta na di Kɔlɔmbɔ Nashɔnal Ospital wantɛm wantɛm. Ɔ go na di Imejɛnsi Tritmɛnt Yunit (ETU) na di ɔspitul we de nia yu. Dis rili impɔtant.
Ɛn mɛmba se na fɔ yu nɔmɔ dɛn gi dis mɛrɛsin. Nɔ ɛva sheb am wit ɛni ɔda pɔsin.
Wetin fɔ du if yu mis wan doz fɔ mɛrɛsin?
Fɔ fɔgɛt fɔ tek wan doz fɔ mɛrɛsin na sɔntin we kin apin to ɛnibɔdi. If yu du dat, tek am jɔs afta yu mɛmba. Bɔt if i pas 4 awa afta di tɛm we yu kin tek am, skip di doz we yu mis. Tek di nɛks doz na di tɛm we dɛn dɔn sɛtul. Nɔ ɛva tek tu doz wan tɛm fɔ mek di doz we yu dɔn fɔgɛt.
Ɔda mɛrɛsin dɛm wae kin miks wit dis mɛrɛsin
Mitapivat kin intarakt wit ɔda mɛrɛsin dɛm we yu de tek, we kin ridyus di ɛfɛktiv fɔ dis mɛrɛsin ɔr kin mek di sayd ɛfɛkt dɛn bɔku.
| Tayp fɔ mɛrɛsin | Ɛgzampul dɛn |
|---|---|
| Pils dɛn we dɛn kin yuz fɔ kɔntrol pikin | Pils dɛn we dɛn kin yuz fɔ kɔntrol pikin |
| Sɔm tin dɛn we dɛn kin yuz fɔ kil fɛns | Flukonazɔl, Itrakonazɔl, Kɛtokonazɔl |
| Mɛrɛsin fɔ HIV | Efavirenz bin de du dat |
| Mɛrɛsin we de mek pɔsin fil fayn/we de mek pɔsin slip | Midazolam we dɛn kɔl midazolam |
| Sɔm mɛrɛsin fɔ TB | Rifampin bin de du am |
Dis nɔto wan kɔmplit list. So, tɛl yu dɔktɔ bɔt ɔl di mɛrɛsin dɛn, srɔp dɛn, ɔyl dɛn, vaytamɛn dɛn, ɛn sɔpɔtmɛnt dɛn we yu de tek. I impɔtant bak fɔ tɛl yu dɔktɔ if yu de smok ɔ drink rɔm.
Wetin na di bad tin dɛn we kin apin to pɔsin?
Lɛk ɛni mɛrɛsin, dis wan kin gɛt sɔm bad bad tin dɛn. Sɔm siriɔs, sɔm kɔmɔn.
| 🚨 Sayd ifekt dɛm we dɛn fɔ ripɔt to di dɔktɔ wantɛm wantɛm | |
|---|---|
| Alɛji we pɔsin kin gɛt | Skin rash, it, swel na yu fes, yay, lip, tong ɔ trot, i nɔ izi fɔ blo. |
| ✅ Tɛl yu dɔktɔ if i kɔntinyu ɔ i de mɔna yu | |
| Bak pen | Bak pen |
| Pen na di jɔyn dɛn | Pen na di jɔyn dɛn |
If yu gɛt ɛni ɔda kayn sik we dɛn nɔ tɔk bɔt na dis list, duya kɔl yu dɔktɔ fɔ advays.
Aw yu fɔ kip di mɛrɛsin?
- Kip am fa frɔm pikin dɛn: Ɔltɛm kip mɛrɛsin usay pikin ɛn animal dɛn we yu de mɛn nɔ go ebul fɔ rich.
- Tɛmpratura: Stɔr am na rum tɛmpracha (bitwin 20-25 digri sɛlshiɔs). Protɛkt frɔm ɔt ɔ mɔs we pasmak.
- Di ɔrijinal kɔntena: I bɛtɛ fɔ kip di mɛrɛsin insay di ɔrijinal bɔtul we dɛn bin gɛt am insay.
- Di mɛrɛsin dɛn we dɔn dɔn: Nɔ yuz di mɛrɛsin afta di de we dɛn dɔn dɔn. Trowe di mɛrɛsin dɛn we dɔn pas ɔ we yu nɔ want fayn fayn wan. Sɔm ɔspitul famasi dɛn kin gɛt program fɔ tek ol mɛrɛsin dɛn. Ɔda we de fɔ pul di pils dɛn na di bɔtul, miks dɛn wit sɔntin lɛk kɔfi grɔn ɔ dɔti we dɛn dɔn yuz, put dɛn insay bag we dɛn tayt tayt, ɛn trowe dɛn na dɔti. Nɔ ɛva flush mɛrɛsin dɛn dɔŋ di tɔylɛt fɔ ɛni rizin.
Mɛsej we dɛn kin kɛr go na os
- Mitapivat na spɛshal mɛrɛsin fɔ anemia we pɔsin kin gɛt we i nɔ gɛt Pyruvate Kinase. Tek di doz we dɛn tɛl yu fɔ tek lɛk aw yu dɔktɔ tɛl yu.
- Nɔ ɛva brok, krɔs, ɔ chew di tablɛt. Swɛla am ɔl.
- Mek shɔ se yu tɛl yu dɔktɔ bɔt ɔl di ɔda mɛrɛsin dɛn, vaytamɛn dɛn, ɛn wɛlbɔdi prɔblɛm dɛn we yu de tek.
- If yu mis wan doz fɔ pas 4 awa, skip da doz de ɛn tek di nɛks doz di tɛm we dɛn dɔn sɛtul. Nɔ ɛva dubl di doz.
- If yu tink se yu dɔn tek am pasmak, go wantɛm wantɛm na di Nashɔnal Pɔyzin Infɔmeshɔn Sɛnta ɔ di ɔspitul ETU we de nia yu.
- If yu gɛt alɛji wantɛm wantɛm (yu fes de swel, i nɔ izi fɔ blo), go to dɔktɔ wantɛm wantɛm.











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