Dɛn dɔn chenj di blɔd we de kɔmɔt na yu at? Lɛ wi lan bɔt PAPVR (Partial Anomalous Pulmonary Venous Return)!

Sɔntɛnde, yu kin fil taya? Yu kin si se i nɔ kin izi fɔ yu fɔ blo we yu de klaym wan stej? Ɔ yu de dawt smɔl bɔt aw yu smɔl pikin de gro? Bɔku rizin dɛn kin de we kin mek dɛn tin ya apin. Bɔt sɔntɛnde, di tin we kin mek wi du dis kin bi smɔl chenj na di at we dɛn bɔn wi wit. Tide wi go tɔk bɔt dis kayn tin, we gɛt fɔ du wit di blɔd we de go na di at, bɔt i nɔ kin rili kɔmɔn. Dɛn kɔl dis PAPVR, we tinap fɔ (Partial Anomalous Pulmonary Venous Return).

Yu no wetin na PAPVR (Partial Anomalous Pulmonary Venous Return)?

Fɔ tɔk am simpul wan, PAPVR na wan sik we dɛn kin bɔn wit at sik . Wetin kin apin pan dis na dat smɔl prɔblɛm de wit di we aw di blɔd we dɛn dɔn klin ɛn we gɛt ɔksijɛn frɔm wi lɔng dɛn kin kam bak na di at. Nɔmal wan, ɔl dis blɔd we gɛt ɔksijɛn kin go na di lɛft say na di at. Dɔn, di lɛft say na di at kin pɔmp da blɔd de go na di wan ol bɔdi.

Bɔt pan pɔsin we gɛt PAPVR, na smɔl pan dis blɔd we gɛt ɔksijɛn we de kɔmɔt na di lɔng dɛn kin go na di rayt say na di at . Yu no, nɔmal wan, di rayt say na di at kin gɛt blɔd we di bɔdi dɔn yuz, we nɔ gɛt bɔku ɔksijɛn. So we sɔm pan di blɔd we gɛt ɔksijɛn go rɔng we, di blɔd we de kam na di rayt say na di at kin jɔs bɔku. Wetin kin apin da tɛm de? Di rayt say na di at gɛt fɔ wok wit dis ɛkstra blɔd, we min se i fɔ wok tranga wan . Dis ekstra lod kin bil pan di at as tɛm de go, ɛn i kin ivin afɛkt wi ɔl wɛlbɔdi.

Bɔt PAPVR nɔ de afɛkt ɔlman di sem we. I dipen pan di blɔd we dɛn kin chenj. Sɔm pipul kin gɛt wan sik wae nɔr kin pasmak, ɛn nɔr kin gɛt ɛni sayn fɔ di res ɔf dɛn layf. Bɔt if di sayn dɛn kin apin ɔ ɔda prɔblɛm dɛn kin apin, wi dɔktɔ dɛn kin ebul fɔ kɔntrol di sik fayn fayn wan. Bɔrku tɛm, ɔpreshɔn kin trit PAPVR fayn fayn wan ɛn ɛp yu fɔ liv lɔng, wɛl bɔdi layf.

Dis na di nɔmal we aw blɔd de flɔ na wi at, ɛn aw i kin chenj we wi gɛt PAPVR.

Fɔ ɔndastand di impak we PAPVR gɛt pan blɔd flɔ, lɛ wi fɔs luk aw blɔd kin flɔ nɔmal wan bitwin wi at ɛn wi lɔng. Tink bɔt am lɛk smɔl waka.

1. fכs, di bכdi in bכdi we dεn yuz, we nכ gεt כksijεn, de fכlכ tru tu big vein dεm (di supεriכr vena cava εn di infεriכr vena cava) εn go insay di כp chεmba (di rayt atrium) na di rayt say na di at.

2. afta dat, dis bכdi we nכ gεt כksijεn de muv frכm di כp rayt chεmba to di lכw rayt chεmba (`(rayt vεntrikl)`).

3. dis b כdi de pכmp frכm di lכw rayt chεmba to di lכng , we di pulmonari at dεm de εp. Insay di lɔng dɛn, dis blɔd kin gɛt ɔksijɛn bak, lɛk se dɛn dɔn gi am nyu layf.

4. di nyu bכdi we gεt כksijεn naw de kam bak na di at tru sεvεra vein dεm (pulmonary veins) frכm di lכng dεm, dεn de go insay di כp lεft chεmba na di at.(`(lɛft atria)`).

5. dis bכdi we gεt כksijεn frכm di כp chεmba na di lεft de go na di lכw chεmba na di lεft (`(lεft vεntrikl)`).

6. fכ finish, dis bכdi we gεt כksijεn we de kכmכt na di lכw chεmba na di lεft say de sheb כlsay na di b כdi tru di big bכdi vεsεl (di aorta).

Yu si, nɔmal wan di blɔd we nɔ gɛt bɔku ɔksijɛn de na di chɛmba dɛn we de na di rayt say, ɛn di blɔd we gɛt mɔ ɔksijɛn de na di chɛmba dɛn na di lɛft say. Dem no get mix up.

Bɔt wit PAPVR, dis we fɔ du tin nɔ de wok fayn. PAPVR de mek wan abnכmal bכdi fכ fכlכ insay di at, we dεn kכl lεft-to-rayt kadyak shunt. "Patially anomalous" min se na wan pat pan di bכdi we gεt כksijεn fr כ m di lכng dεm nכ de rich di at nכmal wan.

dis na biכs wan כ mכr pan yu pulmonari vein dεm de pכmp blכd we gεt כksijεn insay di כp chεmba na di rayt say, insted fכ go insay di כp chεmba na di lεft say. Wetin kin apin da tɛm de? Di blɔd we nɔ gɛt ɔksijɛn na yu ɔpa chɛmba na di rayt say, de miks wit di blɔd we gɛt ɔksijɛn. So, dis miks bכdi de pכmp insay di lכw chεmba na di rayt say, insay di lכng dεm.

Dis gɛt tu sayd ɛfɛkt dɛn:

• Di fɔs wan na dat sɔm pan di blɔd we gɛt bɔku ɔksijɛn kin kam bak di sem we aw i kam, dat na, to di lɔng dɛn we nɔ nid .
• Sɛkɔn, di blɔd we yu rayt dɔŋ chɛmba gɛt fɔ pɔmp to yu lɔng dɛn kin bɔku . Dis ekstra wok kin mek yu at pwɛl as tɛm de go.

Ɔda at sik kin apin wit PAPVR?

Sɔm pipul dɛn kin gɛt PAPVR nɔmɔ, we nɔ gɛt ɛni ɔda at sik. Dɛn kɔl dis "isolated PAPVR". Bɔt bɔku pipul dɛn we gɛt PAPVR kin gɛt ɔda tin dɛn bak we nɔ kin apin, lɛk wan ol bitwin di tu ɔpa chɛmba dɛn na di at . Dɛn kɔl dis Atrial Sɛptal Difɛkt (ASD).

rεli rεli, PAPVR kin kכnεkt wit maldivεlכpmεnt fכ di rayt lכng εn di vein we de kכri bכdi to di lכng (`(Scimitar syndrome)`).

Aw PAPVR nɔ kin bɔku?

Risach pipul dεm se na lɛk 4 to 7 pan ɛvri 1,000 pipul dɛm gɛt PAPVR. Bɔt di nɔmba kin pas dat pasmak, bikɔs sɔm pipul dɛn nɔ kin ɛva gɛt ɛni sayn ɛn dɛn nɔ kin ɛva no se dɛn gɛt dis sik.

Wetin na di sayn dɛm fɔ PAPVR?

If di blɔd we de go na di rɔng say (dɛn kɔl am `shunting`) smɔl, PAPVR nɔ kin mek pɔsin gɛt di sik ɔltɛm. Bɔt we dis `shunting` de bɔku, yu kin notis di sayn dɛm. Yɔŋ pikin dɛn kin gɛt di sik if dɛn gɛt dis sik wit ɔda at sik. Bɔt bɔrku pipul dɛm wae gɛt PAPVR kin bigin fɔ gɛt dis sik wae dɛn dɔn pas 20 ɔr 30 ia .

Di sayn dɛm we kin apin to yɔŋ pikin dɛm:

• Divɛlɔpmɛnt dilɛys.
• Fɔ taya kwik kwik wan we yu de du ɛksɛsayz ɔ ple.
• Infεkshכn dεm we de apin na di rεspiretכri fכs tεm (e.g., chεst kכnjεshכn).
• Shot we yu de blo.
• I nɔ izi fɔ mek yu gɛt mɔ wet.

Di sayn dɛm wae kin kam pan big pipul dɛm:

• I nɔ kin izi fɔ yu fɔ blo.
• Fɔ fil taya ɔltɛm (`(Fatigue)`).
• Fכ fil wan abnכmal hat rεt (`(Hat palpitations)`).
• Chɛst pen (`(Chɛst pen)`).
• Di at rit de go ɔp.
• Infεkshכn dεm we de apin na di rεspiretכri bכku tεm.

Wetin mek dis PAPVR kin apin?

lεk כda at sik dεm we dεn kin bכn wit, PAPVR kin apin we di at nכ de fכm fayn fayn wan we di pikin de divεlכp . nכmal wan, insay di fכs wik dεm we di bεlε de, fכ pulmonari vein dεm de fכm frכm wan kכmכn pulmonari vein. dis vein dεm de kכnekt to di lεft כp chεmba na di fetal at. כltu, if εni chenj de na dis prכsεs, di pulmonari vein kin kכnekt to di rayt כp chεmba insted fכ di lεft כp chεmba, כ to כda vein dεm we de nia (lεk di supεriכr vena cava כ di lεft brachiocephalic vein). Dis na we PAPVR kin apin.

Wetin na di pɔsibul kɔmplikeshɔn dɛm fɔ PAPVR?

Di shunt dɛn we de kɔmɔt na di lɛft to rayt we dɛn nɔ bin dɔn trit fɔ lɔng tɛm kin tɔn bak ɛn mek dɛn gɛt wan siriɔs sik we dɛn kɔl Eisenmenger syndrome. So, i impɔtant fɔ go to dɔktɔ wantɛm wantɛm if yu gɛt sɔm sayn dɛn.

Aw yu go no if yu gɛt PAPVR?

Dɔktɔ dɛn kin no PAPVR wit fizik ɛgzam ɛn ɔda spɛshal tɛst dɛn . We yu dɔktɔ de chɛk yu, i go lisin to yu at wit stetɔskɔp. Sɔm pipul dɛm wae gɛt PAPVR kin yɛri abnɔmal at sawnd (at kin grɔmbul). If dɛn tink se dis, yu dɔktɔ go ɔda fɔ mek dɛn du ɔda tɛst dɛn.

Di ej wae dɛn kin no PAPVR kin difrɛn frɔm pɔrsin to ɔda pɔrsin. Dɛn kin no am we i smɔl, ɔ dɛn kin no am we i dɔn big. Yu kin gɛt PAPVR, bɔt nɔr gɛt ɛni sayn, so yu nɔr kin no am fɔ yu layf. Sɔntɛnde, dɛn kin no di sik bay we dɛn de du tɛst fɔ ɔda tin.

Us tɛst dɛn dɛn kin du?

Test dɛm wae de ɛp fɔ no PAPVR na:

• Echocardiogram (Echocardiogram) - spεshal wan na transεsophageal echocardiogram (TEE). Dis kin tek wan ɔltra saund pikchɔ fɔ di at.
• MRI fɔ di at (MRI fɔ di at).
• Kadyak kɔmpyuta tomografi (CT) skan.

Yu tink se PAPVR nid fɔ gɛt ɔpreshɔn?

Sɔm pikin ɛn big pipul dɛn nid fɔ gɛt PAPVR ripa ɔpreshɔn fɔ kɔrɛkt di rod we blɔd de flɔ tru di at. Pikin dɛm we dɛn no se gɛt PAPVR kin nid ɔpreshɔn pas big pipul dɛm. Dis na bikɔs bɔku tɛm dɛn kin gɛt PAPVR wit ɔda at kɔndishɔn dɛn we kin nid ɔpreshɔn.

Dɔktɔ dɛn kin se dɛn fɔ du ɔpreshɔn.Na if i rili nid fɔ mek dɛn nɔ gɛt di sik ɔ fɔ mek dɛn nɔ gɛt prɔblɛm dɛn tumara bambay. Yu ɔ yu pikin kin nid ɔpreshɔn if PAPVR mek big big shunt frɔm lɛft to rayt. Dis min se wan big bכdi we fכ de go na di bכdi de go bak na di rayt say na di at εn di lכng. Dis kin mek yu gɛt sɔm kayn sik ɛn kɔmplikeshɔn wae nɔr kin fayn lɛk pulmonary hypertension (PAH) ɔr at pwɛl. Yu dɔktɔ go yuz imej tɛst fɔ no aw dis shunt de fa.

Bɔku tɛm, ɔpreshɔn kin ebul fɔ trit PAPVR fayn fayn wan. I impɔtant fɔ tɔk to yu dɔktɔ bɔt di ditil dɛm bɔt yu ɔpreshɔn ɛn wetin fɔ ɛkspɛkt.

Di we aw dɛn kin du ɔpreshɔn kin difrɛn difrɛn wan bay aw yu at ɛn yu pulmonari vein dɛn shep. Jɛnɛral wan, di dɔktɔ dɛn we de du ɔpreshɔn kin want fɔ chenj di we aw di blɔd de flɔ so dat blɔd we gɛt ɔksijɛn go flɔ insay di lɛft say dɛn na di at.

Bɔt bɔku pipul dɛn nɔ go nid ɔpreshɔn . If yu PAPVR nɔ at, yu dɔktɔ go wach yu kɔndishɔn. If yu gɛt sɔm sayn dɛn ɔ yu sho sayn dɛn fɔ se yu gɛt prɔblɛm, yu dɔktɔ kin tɛl yu fɔ du ɔpreshɔn da tɛm de.

Yu tink se dɛn kin ebul fɔ stɔp PAPVR?

Na ɔnfɔni, no we nɔ de fɔ mek dɛn nɔ gɛt PAPVR. Na sɔntin we dɛn bɔn wi wit. Bɔt if yu de plan fɔ gɛt bɛlɛ, tɔk to yu dɔktɔ bɔt aw fɔ ridyus di risk fɔ bɔn pikin we gɛt at prɔblɛm we dɛn bɔn wit. Na sɔm advays dɛn ya:

• Nɔ drink rɔm, drɔgs, tin dɛn we dɛn kin yuz fɔ smok, ɛn smok we dɛn dɔn yuz fɔ smok, kpatakpata.
• Atɛnd ɔl di apɔntinmɛnt dɛn we yu kin gɛt bifo yu bɔn wit yu dɔktɔ.
• Wok wit yu dɔktɔ fɔ manej ɛni ɔda ɔndalayn wɛlbɔdi prɔblɛm we yu go gɛt (e.g., dayabitis, ay blɔd prɛshɔn).

Pɔsin we gɛt PAPVR kin liv nɔmal layf?

I rili pɔsibul fɔ liv lɔng, wɛlbɔdi layf wit PAPVR. Bɔrku pipul dɛn kin liv fɔ lɔng lɔng tɛm ɛn nɔr kin gɛt ɛni sayn ɔr prɔblɛm. Ivin di wan dɛn we nid ɔpreshɔn kin gɛt gud rizulyt. Bɔt di rizɔlt kin difrɛn difrɛn wan bay ɔda at sik ɔr ɔndalayn kɔndishɔn dɛn we pɔsin gɛt. So i bɛtɛ fɔ tɔk to yu dɔktɔ bɔt wetin fɔ ɛkspɛkt bay yu wan wan sityueshɔn.

If yu gɛt PAPVR, aw yu kin tek kia ɔf yusɛf? / Aw yu de tek kia ɔf yu pikin?

Fɔ liv wit wan at sik we dɛn bɔn wit kin mek yu strɛs sɔntɛnde. I impɔtant fɔ mɛmba fɔ tek tin wan de wan tɛm. Na sɔm jenɛral advays dɛn we yu kin fala:

• Fɛn tritmɛnt frɔm dɔktɔ we de mɛn yu at we spɛshal pan big pipul dɛn we dɛn bɔn wit at sik. I go wach yu kɔndishɔn tru di chɛk-ap ɛn tɛst ɔltɛm.
• Aks yu dɔktɔ us kayn ɛksesaiz we fayn fɔ yu. Tugeda, una kin mek wan eksasaiz plan.
• Fɔ fala di it we go ɛp yu at (e.g., di Mɛditarenian Dayt).
• Tek ɔl di mɛrɛsin dɛn jɔs lɛk aw yu dɔktɔ tɛl yu fɔ tek.
• Nɔ smok ɛn ɔl di tin dɛn we dɛn kin yuz fɔ smok. Aks yu dɔktɔ if yu nid ɛp fɔ lɛf fɔ smok.

If yu pikin gɛt PAPVR, aks in dɔktɔ aw fɔ kia fɔ am di bɛst we. Yu pikin kin nid fɔ fala spɛshal gaydlain fɔ ɛksesaiz ɔ ɔda tin dɛn fɔ du, mɔ if i gɛt ɔda at prɔblɛm dɛn bak we i bɔn wit.

Ustɛm yu nid fɔ go to dɔktɔ?

Si yu dɔktɔ lɛk aw dɛn dɔn plan fɔ du am. Fɔ fala-ap apɔntinmɛnt ɔltɛm ɛn imej tɛst impɔtant fɔ monitar di stetɔs fɔ yu PAPVR ɛn manej kɔmplikeshɔn dɛn.

Kɔl yu dɔktɔ wantɛm wantɛm if yu ɔ yu pikin gɛt ɛni wan pan dɛn tin ya:

• If nyu sayn dɛm de sho ɔr di sayn dɛm wae dɔn de chenj.
• If sayd ɛfɛkt dɛn de frɔm di mɛrɛsin.
• If yu gɛt ɛni kwɛstyɔn ɔ tin we de mɔna yu.

Insay us sityueshɔn yu nid fɔ go na di Imejɛnsi Tritmɛnt Yunit (ETU) ?

If yu ɔ yu pikin sho ɛni wan pan dɛn sik ya, kɔl 911 ɔ yu lokal imejensi nɔmba wantɛm wantɛm:

• di at rεt we tu fast (100-150 bit pan minit) εn nכ de slo.
• I nɔ kin no natin ɛn i kin fɔdɔm.
• Difεlεns fכ brith we pasmak we i kam pan εksεsayz εn/כ nכ de go ivin afta yu rεst.
• Chest pen we kin kam wantɛm wantɛm ɛn we kin rili bad.
• Wan ed we kin at wantɛm wantɛm ɛn we kin at bad bad wan.
• Di an ɔ leg kin wik ɔ swɛ wantɛm wantɛm.

Impɔtant kwɛstyɔn dɛn fɔ aks yu dɔktɔ

Tɔk to yu dɔktɔ bɔt yu sik ɛn wetin fɔ ɛkspɛkt tumara bambay. Na sɔm kwɛstyɔn dɛn we yu kin aks:

If yu gɛt PAPVR:

• Aw siriɔs mi sik de?
• Us chenj dɛn we a nid fɔ chenj mi layf?
• Yu tink se a go nid ɔpreshɔn?
• Wetin na di bɛnifit ɛn prɔblɛm dɛn we pɔsin kin gɛt we i du ɔpreshɔn?
• Aw mi tumara bambay go tan lɛk?

If yu pikin gɛt PAPVR, aks dɛn dɔktɔ:

• Aw siriɔs di sik we mi pikin gɛt?
• Mi pikin gɛt ɛni ɔda at sik we dɛn bɔn wit?
• Yu tink se mi pikin go nid ɔpreshɔn ɔ ɔda tritmɛnt?
• Aw a go kia fɔ mi pikin na os?
• I gɛt ɛnitin we de stɔp am fɔ du sɔntin?
• Us tin dɛn de fɔ ɛp mi pikin fɔ ɔndastand dis di we aw i ol?

Wetin na di difrɛns bitwin PAPVR ɛn TAPVR?

PAPVR difrεn frכm wan kכndyushכn we dεn kכl ``Tכtal Anomalous Pulmonary Venous Return (TAPVR)``. pan pכsin we gεt TAPVR, כl di vein dεm na di lכng dεm de kכnekt to di at insay wan abnכmal we. TAPVR na wan sik we siriɔs pas bɔku pan di kayn PAPVR, ɛn i kin nid fɔ gɛt imejensi tritmɛnt jɔs afta dɛn bɔn am. Bɔt di PAPVR ɛn TAPVR ɔl tu fiba bikɔs dɛn de ambɔg di nɔmal we aw blɔd de flɔ tru di at.

Fɔ dɔn, mɛmba dɛn tin ya:

PAPVR nɔ kin afɛkt yu layf atɔl. Ɔ, e kin mek yu gɛt sɔm kayn sik ɔr prɔblɛm wae nid fɔ gɛt tritmɛnt. Bɔt i nɔmal fɔ mek yu fil strɛs ɔ wɔri bɔt PAPVR. If yu pikin gɛt PAPVR, i nɔmal bak fɔ mek yu wɔri bɔt dɛn wɛlbɔdi. Dɛn filin ya kin rili nɔrmal, ɛn nɔr kin fil bad bɔt dɛn.

Tɔk bɔt di tin dɛn we de mɔna yu wit yu dɔktɔ. Aks bɔt tin dɛn we go ɛp yu ɛn yu famili. We yu lan mɔ bɔt at sik we yu bɔn wit – ilɛksɛf i de afɛkt yu, yu pikin, ɔ pɔsin we yu lɛk – kin ɛp yu fɔ kɔntrol yu kɔndishɔn bɛtɛ bɛtɛ wan. We yu tɔk to pɔsin we de gi yu advays, dat kin ɛp yu bak fɔ mek yu maynd fil fayn. We yu de travul, nɔ ɛva shem fɔ aks yu dɔktɔ bɔt ɛni kwɛstyɔn ɔ tin we de mɔna yu. Nɔto yu wan de.

` PAPVR, at sik, sik dɛm we dɛn bɔn wit, lɔng, blɔd sirkuleshɔn, at ɔpreshɔn, at sik we dɛn bɔn wit, pulmonari vein, at ɔpreshɔn