Oh, sohmtem wi kin yeri tin lek, ‘bren tumor’, ‘A geht ed pen en a go chek am out’. I kin rili mek mi at flay we a yɛri sɔntin lɛk dat. Bɔt yu no se nɔto ɔl di tumbu dɛn we kin mek na di bren na di sem kayn kansa we denja. Sɔm tumbu dɛn de we de gro sloslo, we nɔ gɛt wan sik, dat min se nɔ gɛt kansa. Tide wi go tɔk bɔt tu kayn bren tumbu dɛn lɛk dis, we nɔ kin bɔku, bɔt we fayn fɔ no. dis na gangliocytoma εn pineocytoma.
Wetin na Gangliocytoma ɛn Pineocytoma?
fכ simpul wan, dεn tu na rili rεs, nכ denja (i.e. nכn kεnsar - `benign`) tכp dεm na di bren tכmכro.
gangliocytoma na wan kayn tכmכro we de afekt pat dεm na yu sεntri nεv sεstem (dεn kכl am bak di CNS).
di ɔda kayn we na pineocytoma de divɛlɔp na di pineal gland, we na wan smɔl gland we de dip insay yu bren. Di pineal gland na di gland we de ɛp fɔ kɔntrol wi slip. Imajin, dis smɔl gland rili impɔtant fɔ tin dɛn lɛk fɔ slip na nɛt ɛn wek na mɔnin.
Dɛn tu kayn tɔŋ ya kin gro sloslo . Na dat mek sɔmtɛm i kin tek sɔm tɛm fɔ mek di sayn dɛm fɔ sho. Bɔku tɛm, dɔktɔ dɛn kin trit dɛn wit ɔpreshɔn ɛn sɔntɛnde dɛn kin trit dɛn wit raytin.
Udat kin gɛt dɛn kayn tumbu ya na in bren?
Infakt, wan kayn tumbu we dɛn kɔl gangliocytoma kin kam pan pipul dɛn we ol ɛni ej. Dis min se ivin smɔl pikin ɔ ol pɔsin kin de pan denja. Bɔt dɛn kin si am mɔ pan yɔŋ pipul dɛn we ol bitwin 10 ɛn 30 ia .
Pineocytoma tumor kin afekt big pipul, we min se pipul dεm we ol bitwin 20 εn 64. Di avrej ej fכ no di sik na bכt 38 ia.
na us pat dεm na wi sεntri nεv sεstem (CNS) we di gangliocytoma tכmכro dεm de divεlכp?
di gangliocytomas kin divεlכp bכku tεm na di pat dεm na yu bren we dεn kכl di tεmporal lכb dεm . Dɛn tin ya de biɛn yu yes. Dɛn tɛmporal lɔb ya de ɛp fɔ kɔntrol tin dɛn lɛk aw yu de mɛmba, aw yu de yɛri, ɛn aw yu de fil. Imajin, yu mɛmba wan ol ivent, lisin to wan siŋ ɛn ɛnjɔy am, ɛn fil gladi ɔ sɔri bikɔs ɔf di aktiviti we dɛn pat ya de du.
nכto dat nכmכ, dis tכmכro kin divεlכp bak na dεn ples dεm ya na yu bכdi:
- Bren stεm: Dis na di pat pan yu bren we lεk brij we de kכnekt di tכp pat pan yu bren (sεribram), spεnal kכd, εn sεribεl. I de sɛn signal dɛn we de kɔntrol impɔtant wok dɛn lɛk aw yu de blo ɛn aw yu at de bit.
- Sɛribɛlɔm: .Dis pat na yu bren, we de biɛn yu ed, de kɔntrol yu balans, muvmɛnt, ɛn si. Tink bɔt am, dis pat na yu bren na in de mek yu tinap stret we yu de waka, mek yu nɔ fɔdɔm, ɛn ɛp yu fɔ es yu an fɔ kech bɔl.
- di fכlכ fכ di tכd vεntrikl: Dis na wan sכmכl kכva we de bifo di bren. I de protɛkt di bren frɔm injuri ɛn ɛp fɔ muv di nyutriɛnt ɛn west prɔdak dɛm rawnd.
- di spεnal kכd: Dis na di men rod we de kכri di nεv signal dεm frכm yu bren to yu bכdi εn frכm yu bכdi to yu bren. dis nεv signal dεm na dεn de mek yu fil tin dεm (hεt, kol, pen) εn muv yu bכdi.
Wetin na di difrɛns bitwin pineal sist ɛn pineocytoma?
Dis na sɔntin bak we kin mek bɔku pipul dɛn kɔnfyus. Tink bɔt am, pineal cyst na sak we ful-ɔp wit wata ɔ briz . I tan lɛk wata blista. Bɔku tɛm, dɛn kin fɛn dɛn tin ya bay we dɛn de skan. Bɔt pineocytoma na wan tumbu we bɔku bɔku sɛl dɛn we nɔ nɔmal de mek .
di pineal sist dεm nכ kin big, we min se dεn nכ kin chenj in saiz nכ kin chenj. Bɔt di pineocytomas kin gro smɔl smɔl. Bɔt dɛn ɔl tu na benign (nɔto kansa) kɔndishɔn. Dis min se dɛn nɔ gɛt kansa.
Wetin na de sayn wae de kam wit dis sik?
Bɔrku tɛm, yu nɔr kin gɛt ɛni sayn ivin if yu gɛt gangliocytoma. Sɔntɛnde, dɔktɔ dɛn kin fɛn dɛn tumbu ya bay we dɛn de du imej tɛst (lɛk MRI ɔ CT skan) fɔ ɔda prɔblɛm.
Bɔt ɔl tu di kayn tumbu dɛn we dɛn kɔl gangliocytoma ɛn pineocytoma kin mek sɔm kayn tin dɛn we gɛt difrɛn sayn dɛn.
Di kɔmɔn simptom dɛm fɔ Gangliocytoma
Dis tumbu kin mek yu gɛt sɔm kayn sik lɛk:
- Di chenj dɛn we de apin na di muvmɛnt: I tan lɛk we pɔsin nɔ ebul fɔ kɔntrol di mɔsul dɛn. Fɔ ɛgzampul, pɔsin we de shek shek, we pɔsin paralayz, we i wik. Imajin se, i nɔ kin izi fɔ yu fɔ ol kɔp wantɛm wantɛm, ɔ yu leg dɛn kin fil lɛk se dɛn de trip we yu de waka.
- Chenj na di sens: Na filin wae yu de fil fɔ swɛt na sɔm say dɛm, lɛk wae yu de fil tingling na yu leg.
- Difikulti fɔ tɔk: Tɔk we nɔ de tɔk fayn, i kin tan lɛk se yu nɔ ebul fɔ tɔk. Yu nɔ go ebul fɔ tɔk wetin yu want fɔ tɔk klia wan.
- Vishɔn kin chenj: Yu kin si blɔk, i kin tan lɛk se yu de si na tu pat, ɛn sɔntɛnde i kin tan lɛk se yu de lɔs pat pan yu vishɔn.
Gangliocytoma kin mek yu gɛt siriɔs mɛrɛsin?
Yɛs, dis tumbu kin mek sɔm siriɔs sik dɛn we pɔsin kin gɛt. Fɔ ɛgzampul:
- Di prɔblɛm dɛn we kin apin na di ɛndokrin sistɛm:Dis na tin dεm we kin apin we di כmon dεm we di gland dεm na yu bכdi de mek de bכku כ dכn. Dis kin ambɔg bɔku pan yu bɔdi in wok.
- Seizure: Yu go dɔn yɛri bɔt dis, we yu nɔ no natin wantɛm wantɛm ɛn yu kin kɔnvulshɔn. dis tכmכro dεm kin mek dis kכndyushכn bay we dεn de mek di bren wok.
- Prɛshɔn we de insay di bren we de go ɔp: Dis kin mek yu ed at, yu nɔs, yu de vɔmit, ɛn yu kɔnfyus. I kin fil lɛk se dɛn de swɛt yu ed frɔm insay.
- Lhermitte-Duclos disease (LDD): Dis na wan tumbu we nɔ kin bɔku ɛn we nɔ kin du bad. I de divεlכp na yu sεribεl. sכmtεm dεn kin kכl am dysplastic gangliocytoma fכ di sεribεl. Pɔsin we gɛt LDD kin gɛt ed pen, nɔs, wata na in bren (hydrocephalus), i nɔ kin izi fɔ waka ɛn nɔ balans (ataxia), ɛn i kin gɛt prɔblɛm wit di we aw i de si. Pipul wae gɛt LDD kin gɛt wan sik bak we dɛn kɔl Cowden syndrome, we kin mek dɛn gɛt tumbu na dɛn skin ɛn dɛn kin gɛt kansa mɔ ɛn mɔ.
Di kɔmɔn simptom dɛm fɔ Pineocytoma
Pineocytoma kin mek wata kam insay yu bren, we kin mek yu prɛshɔn go ɔp. Dɛn kɔl dis haydrosɛfalɔs . If yu gɛt haydrosɛfalɔs, yu kin gɛt sɔm kayn sik lɛk:
- Prɔblɛm fɔ balans: Fɔ lɔs balans we yu de waka, fil lɛk se yu go fɔdɔm.
- Prɔblɛm fɔ muv di yay (`Parinaud syndrome`): I nɔ kin izi fɔ luk ɔp, mɔ we yu de luk stret bifo. Sɔntɛm yu nɔ go ebul fɔ muv yu tu yay dɛn di sem tɛm.
- Ɛd we de at: Yu kin gɛt siriɔs ed we nɔ de at we nɔ de chenj. Sɔmtɛm dis pen kin wɔs we yu wek na mɔnin.
- Prɔblɛm fɔ mɛmba tin: Fɔgɛt tin, i nɔ kin izi fɔ mɛmba nyu tin.
- Nɔs ɛn vɔmit: Dis kin wɔs, mɔ na mɔnin.
- Slip disorder: Nɔr kin ebul fɔ slip, ɔr kin slip pasmak. dis na biכs di pineal gland de involv fכ slip.
- I nɔ izi fɔ waka: I kin tan lɛk se yu nɔ ebul fɔ waka, yu leg dɛn de shek shek.
Wetin na di rial tin we kin mek dɛn gɛt dɛn bren tumbu ya?
lεk mכst כda tכmכro dεm, gangliocytomas εn pineocytomas de divεlכp we chenj de na di jεnεtik instrכkshכn dεm fכ wi sεl dεm. Tink bɔt dis we: di sɛl dɛn na wi bɔdi tan lɛk smɔl smɔl faktri dɛn. Dɛn kin gɛt instrɔkshɔn fɔ wok. We dɛn instrɔkshɔn ya chenj, di sɛl dɛn kin bigin fɔ sheb we dɛn nɔ ebul fɔ kɔntrol. Na da tɛm de dɛn kin mek wan tumbu.
כltu, di wan dεm we de du risach stil nכ no εksεkεkt wetin na di εksakεt ``trig'' we de mek dεn chenj ya. Dat min se, no klia ansa nɔ de fɔ wetin mek dɛn sɛl ya kin bigin fɔ biev dis kayn we wantɛm wantɛm.
Bɔt dɛn dɔn kam fɔ no se di sik we dɛn kɔl Cowden syndrome, we gɛt fɔ du wit Lhermitte-Duklos sik, na bikɔs wan jin we dɛn kɔl PTEN chenj. dis PTEN jin de mek wan protin we de εp fכ kכntrכl aw di sεl dεm de gro εn divayd. So, we di PTEN jin chenj, di prodakshכn fכ da protin de stכp, εn di sεl dεm bigin fכ gro we dεn nכ ebul fכ kכntrol.
Aw dɔktɔ dɛn kin no se dɛn gɛt dɛn tumbu ya? (Diagnosis) .
If yu gɛt dɛn sik ya, dɔktɔ go aks yu fɔs bɔt yu sik ɛn if ɛnibɔdi na yu famili dɔn gɛt dɛn sik ya (`family health history`). Dɔn, dɛn go chɛk yu. Dɛn go du wan `nyurolɔjik ɛgzam`, spɛshal wan tɛst fɔ yu nervɔs sistɛm . Dis go luk fɔ dɛn tin ya:
- Di we aw yu yay ɛn yu mɔt de muv.
- Di trɛnk we di mɔsul dɛn gɛt.
- Rifleks (lɛk if di leg go jomp we dɛn hit am na di ni wit smɔl hama) .
Apat frɔm dat, di dɔktɔ kin du dɛn tɛst ya bak:
- Magnetic Resonance Imaging (MRI): Dis na tɛst we nɔ de mek pɔsin fil pen. I de yuz big magnet, redio wev, ɛn kɔmpyuta fɔ mek pikchɔ dɛn we rili klia bɔt di ɔgan dɛn ɛn di tin dɛn we de insay yu bɔdi. Dɛn kin yuz am fɔ si if ɛni tumbu de, aw dɛn big, ɛn usay dɛn de.
- CT (computed tomography) scan: Dis kin yuz sɔm X-ray ɛn kɔmpyuta fɔ mek tri-dimɛnshɔnal pikchɔ dɛn fɔ yu sɔft tisu ɛn bon dɛn. Lɛk MRI, dɛn kin yuz am fɔ fɛn ɛn chɛk di tɔŋ dɛn.
- Blɔd tɛst: Dɛn kin du dis fɔ si if yu gɛt abnɔmal lɛvɛl dɛn na yu blɔd (espɛshali we yu gɛt pineocytoma, bikɔs i gɛt fɔ du wit di pineal gland).
- spεnal tap (lumbar pancture): Dis min se yu tek wan sεmpl fכ di sεribrospεnal fכluid (CSF) we de rawnd yu bren εn spεnal kכd εn chεk am fכ tכmכro sεl dεm.
- Bayopsi: Dis na fɔ tek smɔl sampul pan di sɛl dɛn frɔm di tɔŋ ɛn tɛst dɛn na lab fɔ no ustɛm di tɔŋ i bi. Bɔku tɛm, dɔktɔ dɛn kin yuz tin dɛn we nɔ kin tek bɔku tin lɛk ɛndoskopi ɔ stiriɔtaktik nidul bayɔpsi.
Aw dɛn kin trit Gangliocytoma?
Imajin se yu gɛt gangliocytoma, bɔt yu nɔ gɛt ɛni sayn. Na da tɛm de, yu dɔktɔ go tɛl yu se, "Lɛ wi wach am." Dat min se, i go tɛl yu fɔ kam insay fɔ chɛk-ap ɔltɛm fɔ si if yu gɛt ɛni nyu sayn, ɔ if di tumbu dɔn chenj ɔ big. I kin du tin dɛn bak lɛk fɔ tek pikchɔ ɛn fɔ tɛst blɔd.
Bɔt,If yu nid tritmɛnt, dɔktɔ dɛn kin du ɔpreshɔn pan yu bren fɔ pul di tumbu. bכtεm, di gangliocytomas nכ kin kam bak afta dis kayn we dεn pul dεm.
Aw dɛn kin trit Pineocytoma?
Sɔntɛnde we pɔsin gɛt pineocytoma, dɔktɔ dɛn kin du ɔpreshɔn pan in bren fɔ pul ɔl ɔ pat pan di tumbu. Dɛn kin yuz wan tritmɛnt bak we dɛn kɔl redyushɔn tɛrapi .
We dɛn de du ɔpreshɔn, if yu gɛt haydrosɛfalɔs (na wan sik we de mek yu bren ful-ɔp wit wata ɛn yu gɛt prɛshɔn we de go ɔp), dɔktɔ dɛn kin put wan smɔl plastic tiub we dɛn kɔl shunt insay yu bren. dis shunt de pul di ekstra sεribrospεnal fכluid we de kכmכt na yu bren, we de ridyus di prεshכn we de insay yu ed. Dis kin ridyus yu sayn dɛm bad bad wan.
Wan we de we wi go mek dɛn bren tumbu ya nɔ fɔm?
Wɛl, natin nɔ de we yu go rili du fɔ mek dɛn tumbu ya nɔ fɔm . As wi bin dɔn tɔk, dɛn kin mek we di sɛl dɛn chenj ɛn bigin fɔ sheb we dɛn nɔ ebul fɔ kɔntrol. If i nɔ gɛt ɛnitin fɔ du wit di sik we dɛn kɔl Cowden syndrome, di wan dɛn we de stɔdi bɔt dis stil nɔ no bɛtɛ bɛtɛ wan wetin de mek dis muteshon. di Cowden syndrome de kכz fכ wan chenj na wan jin we de kכntro di sεl dεm we de gro. So, dis nɔto sɔntin we wi go ebul fɔ kɔntrol.
Wetin kin apin if yu gɛt tumbu lɛk dis? Wetin yu go ɛkspɛkt?
Bɔku tɛm, afta dɛn dɔn du ɔpreshɔn fɔ pul dis tumbu, di chans fɔ mek i kam bak kin rili smɔl . Dat kin rili kɔrej wi, nɔto so? Dat min se yu kin rili liv nɔmal layf afta yu dɔn gɛt tritmɛnt. Bɔt, as di dɔktɔ se, na fɔ go fɔ `fɔl-ap` chɛk-ap.
Ustɛm a fɔ go to dɔktɔ?
Dipen pan yu kɔndishɔn, yu dɔktɔ kin sɛtul fɔ fala yu ɔltɛm fɔ wach yu ɔl wɛlbɔdi. If dɛn bin du ɔpreshɔn pan yu fɔ pul wan tumbu, dɛn kin tɛl yu bak fɔ du imej tɛst fɔ chɛk if di tumbu dɔn kam bak ɔ if nyu tumbu dɔn fɔm.
Di tin we impɔtant pas ɔl na fɔ go to dɔktɔ ɛnitɛm if yu gɛt sayn dɛn fɔ wan tumbu we yu bin dɔn gɛt trade, ɔ if yu notis ɛni nyu chenj we yu go sɔprayz pan na yu bɔdi . No put am off, okay? Bikɔs di mɔ yu no di sik kwik kwik wan, na di mɔ i go izi fɔ mek yu trit am.
Di tin dɛn we impɔtant pas ɔl fɔ mɛmba frɔm wetin wi dɔn tɔk bɔt (Take-Home Message) .
gangliocytoma εn pineocytoma na tu tכmכro dεm we rili rεs, we de gro sloslo, bεnεn bren tכmכro dεm we de divεlכp na yu sεntri nεv sεstem (CNS) εn pineal gland.
Pan ɔl we dɛn tin ya nɔto kansa, dɛn kin mek yu gɛt difrɛn kayn sik dɛn we kin afɛkt yu layf. Dipen pan di kayn tumbu we yu gɛt, dɔktɔ dɛn kin trit am wit ɔpreshɔn ɔ redyushɔn tɛrapi. Dɛn tumbu ya nɔ kin rili kam bak afta dɛn dɔn pul dɛn wit ɔpreshɔn.
If yu gɛt benign tumor lɛk dis, tɔk to yu dɔktɔ bɔt yu tritmɛnt opshɔn dɛm, wetin fɔ ɛkspɛkt afta tritmɛnt, ɛn wetin yu nid fɔ no bɔt fɔ liv wit dis kayn tumor. Nɔ ol ɛnitin bak, lisin to ɔltin . I go gi yu trɛnk. Nɔr frayd, di tin wae impɔtant pas ɔl na fɔ no bɔt dɛn tin ya ɛn fala yu dɔktɔ in instrɔkshɔn.
` Bren tכmכro, gangliocytoma, pineocytoma, CNS, pineal gland, simptom dεm, tritmεnt











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