I emaw, i fa emaw taksaah chuan thau a tlahniam nghal em, a bik takin vun hnuaiah chuan, chu hmunte chu a hnim hring angin a lang em? A nih loh leh i hmai leh kut thau chu a bo nghal vek a, upa zawkin a lang che em? Heng inthlak danglamna rual hian taksaah hriselna lama harsatna dang a lo awm a nih chuan tunlaia kan sawi mek dinhmun avang pawh a ni thei.
A awlsam zawngin, Lipodystrophy hi eng nge ni?
Lipodystrophy hi kan taksain thau a hman dan leh a khawlkhawm danah a lo awm thin a ni. Pian tirh atanga awm thil a nih loh chuan ‘Acquired Lipodystrophy’ kan ti thin. Chumi awmzia chu kan dam chhung hian eng emaw chhan vangin he dinhmun hi a lo awm tihna a ni. Hei hian kan vun hnuaia thau layer a nghawng ber a ni. Chuvangin mi hmel chu a danglam vek thei a ni. Tin, hei hi a lan danah chauh a ni lo va, taksa chhungah hriselna lama harsatna engemaw zat a thlen thei bawk.
HIV vei thenkhat pawhin he natna (LD-HIV) hi an nei thei bawk. Damdawi an ei vang emaw, natna hrim hrim vang emaw pawh a ni thei.
A chi dangte hi han en ila.
| Lipodystrophy chi hrang hrang | A sawifiahna awlsam tak |
|---|---|
| A rilru a buai em em a, a rilru a hah em em bawk a. | Hei hian taksa pum puiin vun hnuaia thau a tihniam phah a ni. Lawrence syndrome an ti bawk. |
| A rilru a buai em em a, a rilru a hah em em bawk a. | Thau hloh hi taksa chunglam (hmai, kawng, kutphah)-ah chauh a awm thin. Barraquer-Simons syndrome tia hriat bawk. |
| Localized Lipodystrophy natna a awm | Thau hloh hi taksa hmun khatah emaw hmun tlemteah emaw a awm a, chu chuan dimple te te a siam thin. |
AGL leh APL pahnih hi mipa aiin hmeichhiaah a let thum zetin a tam zawk tlangpui. Hei hian naupang chu a hmai thau a tihtlem phah thei a , an kum tak tak aiin a upa zawkin a lang thei bawk . Hei hian naupang leh nu leh pate tan pawh lungngaihna nasa tak a thlen thei a ni.
A pawimawh ber chu thau hi kan hmel lan nan chauh a pawimawh lo va, taksa hormone balance atan pawh a pawimawh hle. Fat tissue hian hormone leptin an tih chu a siam chhuak thin. He hormone hian kan thluak chu kan ei tling tawh tih signal a pe a.
Thau a bo chuan he leptin hormone hi a tlahniam bawk. Chu mai ni lovin, thisen, thinlung, thin, leh kal ang chi hmunah thau a awm tan thin. Hei hian harsatna lian tak tak , zunthlum, cholesterol sang, thin natna, leh kal (kidney failure) te a thlen thei a ni .
Engvangin nge hetiang hi a lo awm? (A chhan) .
Vawi tam tak chu doctor-te pawhin he natna hi a chhan chiang tak hmuh an harsat phah ṭhin. Mahse, a lo awm chhan tur thil engemaw zat hmuhchhuah a ni a:
- Infection: He natna hi natna hrik kai hnuah a lo awm thei a, chu chu measles, pneumonia, infectious mononucleosis, emaw hepatitis te hi a ni.
- Autoimmune disease: Hei hi taksa ngeia immune system-in taksa thau cells a beih hian a lo awm thei a ni.
- Hmun khata inject chhunzawm zel emaw, pressure pek emaw: Entirna tha ber chu zunthlum tan insulin ei thinte hi an ni. Nitin hmun khatah i inject chuan hun kal zelah chu hmun vel thau chu a hmin ang a, khur te tak te a siam ang. Chuvangin doctor te chuan nitin insulin i inject na hmun chu thlak danglam turin an ti fo thin.
- Thil engemaw accident emaw hliam emaw.
Hei hi eng symptoms nge ni?
Heng chi zawng zawng hian taksa thau a tichhe vek a, mahse mi hrang hrangah a inang lo. I fain eng chi nge a neih a zirin a natna lan chhuah dan a inang lo ang.
AGL (Taksa thau zawng zawng hloh) .
Heng naupangte hian an hmai, kut, ke, kut leh a chang chuan an kephah thlengin vun hnuaiah thau an nei lo tluk a ni. Hei hian taksa ruh ( muscular appearance) a pe a , an vein pawh a ti langsar hle . Heng naupangte hi an riltam reng a, an puitlin thuai thin.
APL (Taksa chunglam thau tihtlem) .
Chutiang a nih chuan thau hloh hi hmai atang hian a intan thin. Tichuan zawi zawiin a kawr, a kut leh a rilruah a darh zauh zauh a. Taksa hnuai lam hi a nghawng lo tlangpui.
Localized (hmun khata thau hloh) .
Hei hi vunah khur te tak te ang mai a ni. Heng khur zinga pakhat aia tam a awm thei. A châng chuan heng hmunte hi a na thei a, bump na tak tak a nei thei bawk.
Engtin nge doctor hian hei hi a hriat chian?
Doctor hmu tura i kal hunah chuan taksa enfiahna kimchang tak a nei ang a, nang leh i fate nen zawhna tlemte a zawt ang.
- Eng symptom nge i hmuh?
- Engtikah nge heng inthlâk danglamnate hi i hriat hmasak ber?
- Hetianga a lan dan inthlak danglamna hi taksa hmun tlemteah chauh a ni em, a nih loh leh taksa pum puiah a awm em?
- I vun hnuaiah hian hring hring emaw, vun sen (panniculitis) i nei tawh em?
- Zunthlum i nei em? Tun hnaiah i thisen sugar leh cholesterol level i enfiah tawh em?
Diagnosis finfiah nan a hnuaia test te hi tih theih a ni:
- Skin biopsy: Vun te tak te tak tak lak a ni a, microscope hmangin an enfiah thin.
- Taksa thau tehna test: Skinfold thickness tehna emaw special X-ray leh MRI scan hmangin taksa thau insem dan hriat theih a ni.
- Thisen test: Thisen sugar, kal hnathawh, cholesterol, thin enzyme, leh uric acid level te enfiah thin a ni.
- Zun test: Kal lama harsatna a awm leh awm loh enfiah thin ang che.
Engtin nge enkawl a nih?
Vanduaithlak takin thau hloh tawh chu tihpun leh theihna tur a awm lo. Chuvangin, enkawlna tum ber chu natna avanga harsatna lo awm thei tur ven hi a ni. Chumi atan chuan nunphung hrisel zawm hi a pawimawh hle.
- Diet: Hetiang natna vei zawng zawng hian low-fat diet an zawm tur a ni . Mahse, naupang a nih chuan an thanlenna tur calorie leh nutrient dik tak an dawng em tih pawh i fimkhur tur a ni. Hemi chungchangah hian nutritionist rawn hmasak a tha ber.
- Exercise: Exercise hian thisen sugar level a control thei a, taksaa thau hlauhawm tak tak awm tur a veng thei bawk.
- Damdawi: AGL vei te chu leptin hormone bo thlak nan metreleptin (Myalept) tih shot pek theih a ni. Statins leh omega-3 fatty acids te hian cholesterol sang control nan a pui thei a ni. Zunthlum i vei chuan insulin emaw damdawi dang emaw i ei a ngai mai thei.
Pawimawh: I hmel danglamna i ngaihtuah a nih chuan i doctor nen plastic surgery ang chi duhthlan tur chungchang i sawi thei ang. Fillers inject emaw, taksa peng dang atanga thau lak emaw hian hmai a tikhat thei a, a lan dan thenkhat chu a siam tha leh thei a ni.
Naupang rilru lamah engtin nge kan enkawl ang?
He natna hian hmel lan dan a nghawng nghal avangin naupang chu damdawi pek bakah hmangaihna, ngilneihna leh rilru chakna pek a pawimawh hle.
1. Entawn tlak ni rawh: Positive takin awm reng rawh. Miin i fa chanchin a zawt a nih chuan, muangchangin leh awlsam takin thil awmdan chu hrilhfiah rawh.
2. I fate mahni inngaihhlutna siam rawh: I fate pianzia sawi reng ai chuan an thiamna te, an theihna te, an mizia tha te chu fak la.
3. Ṭhiante chu inpawh tawn turin fuih rawh:Amaherawhchu, naupangte hi an danglam a. A châng chuan naupang dangte thusawi ṭha lo an hre thei a, hnawhchhuah an ni thei bawk. Chutiang dinhmunte hmachhawn dan tur chu i fate chu zirtir lawk rawh.
4. Professional counseling zawng rawh: Naupang leh chhungte pawhin he harsatna hmachhawn avanga lungkhamna lo awm thinte enkawl turin counselor tanpuina an dil thei a ni.
Take-Home Thuchah a ni
- Acquired Lipodystrophy hi nau piang hnua taksa thau dahkhawm leh hmanna lama harsatna a ni.
- Hei hian hmel a tidanglam thei a, harsatna lian tham tak tak, zunthlum, cholesterol sang, thin leh kal natna te a thlen thei a ni.
- Hei hi enkawlna bik awm lo mah se, nunphung hrisel leh damdawi hmanga harsatna awmte chu thunun theih a ni.
- I emaw i fate taksa thau a tlahniam dan danglam tak i hmuh chuan doctor pan vat la, thurawn la rawh.
- Hetiang dinhmun nena kan nun hian taksa hriselna leh rilru hriselna pawh ngaihtuah a pawimawh hle.











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