Naupang tê ṭhenkhat chu thunun theih loh khawpa chein an inher leh inhnim hrual i hmu tawh em? I fa ngei pawhin he harsatna hi a nei ve mai thei. Hetiang dinhmun i hmuh hian lungngaihna leh hlauhna i neih hi thil pangngai a ni. Vawiin hian natna pakhat Athetoid Cerebral Palsy tih kan sawi dawn a, chu chuan heng symptoms te hi a lantir a ni.
He Athetoid Cerebral Palsy hi eng nge ni?
A awlsam zawngin sawi ila,
Athetoid Cerebral Palsy hi naupang taksa ruhte chu a duh loh zawnga che (doctor-te chuan dyskinesia an ti bawk) movement disorder a ni. Hei hi
cerebral palsy chi hnihna a ni . Cerebral palsy hi thluak leh nervous system tichhe thei natna a ni. Hei hian che leh inrualna lama harsatna a siam a, chu chu kal leh ding ang chi te a ni. Athetoid hian cerebral palsy chi dang aiin
naupang chetna a nghawng nasa zawk thei a ni. Chuvangin, a then phei chuan he natna hian naupang dam rei zawng a ti tawi thei a ni. I doctor pawhin he natna hi
dyskinetic cerebral palsy an tih hi a hre tawh mai thei bawk .
Hetiang dinhmun hi engtiang chiahin nge a awm?
Khawvel pumah naupang 1,000 zinga 1 leh 4 inkar chu cerebral palsy vei an ni. Chung zinga
12% atanga 14% vel chuan athetoid cerebral palsy an nei a ni. Chumi awmzia chu he chi hian cerebral palsy vei naupang 10,000 zinga 1 leh 3 inkar a vei tihna a ni.
Hei hi eng symptoms nge ni?
Naupang Athetoid Cerebral Palsy vei chuan a chetna thunun theih loh a nei thei a, chu chu:
- Taksa twsting leh turning .
- Wriggling, twisting nature, rulhut ang maia lantir.
- Sudden jerking emaw convulsive movement emaw a awm.
- Movement ang chiah kha tih leh zel .
Hetiang ang chetna thunun loh hian harsatna dang a thlen thei a ni:
- Taksa natna .
- Posture tha lo tak .
- Drooling a chhuak .
- Movement hrang hrang inkara inremna awm lo .
Naupang tê tête zînga chhinchhiahna hmuhte chu engte nge ni?
Naupang tê tê Athetoid Cerebral Palsy vei chuan a hnuaia chhinchhiahnate hi a lantîr thei a ni:
- I hnungzang chunga i mut lai hian i kut leh ke chu a inbeng kang chhunzawm zel a .
- An kum nena inmil thil tih tlai (entir nan, hmasawnna lama thil thleng tlai tak tak , crawling leh walking te).
- Taksa inher leh inher reng, a bik takin lu chu a sir khata hawitir hunah. I naute chu a inkhelh lai pawhin a lu chu a sir khatah a inher nghal tih i hmu mai thei a, a nih loh leh a kut emaw, a ke emaw chu a inher mai mai tih i hmu mai thei.
Heng athetoid ang chi movement an tihte hi engte nge ni?
Doctor-te chuan heng thunun theih loh chetnate hi chi hrang hrangah an thliar hrang a:
- Dystonia : Hei hi duh loh zawnga chetna, twisting movement a ni. A châng chuan taksa chu hmun khata awm ang maiin a awm thei.
- Chorea : Hei hi zai, rang, repetitive movement ang a ni. Taksa chu a inher chhuak mai mai a, hmun khatah a awm thei lo ang mai a ni.
- Athetosis : Hei hi zawi zawiin, rulhut ang maia inher chhuak a ni.
Ngaihtuah teh, heng chetnate hi puppet pakhat, a hrui inzawm khawm ang mai a ni a, naupang taksa pengte chu a duh angin ni lovin, a takin a che a ni. Hei hi naupang leh nu leh pa tan pawh a harsa hle.
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Athetoid Cerebral Palsy thlentu ber chu
naupang thluak chhung thuk taka awm basal ganglia leh thalamus tihchhiatna a ni . He basal ganglia hian kan chetna control tu thluak hmun atanga spinal cord thlenga thuchah thawn turin a pui thin. Chuvangin hei hi a chhiat chuan chetna thunun a harsa ta hle. Hetiang chhiatna hi nausen pum chhunga a awm lai emaw, a pian lai emaw, a pian hnu rei vak lovah emaw a thleng thei a ni. A hnuaia mite hian a thlen thei a ni:
- Thluaka thisen chhuak (Hemorrhage).
- Thai .
- Thluaka thisen emaw oxygen emaw tling tawk lo (`(Perinatal Asphyxia)` an ti bawk).
- Thisena bilirubin tam lutuk (hei hian Hyperbilirubinemia emaw Kernicterus emaw tih ang chi natna a thlen thei).
Hetiang dinhmun hi tute nge hlauhawm zawk? (Risk Factor hrang hrang) 1.1.
Thil engemaw takah chuan nu nghawngtu thilte hian naupang cerebral palsy vei theihna a tipung thei bawk:
- Naupai laiin harsatna (entir nan, uterine rupture) a awm thin.
- Nausen pum chhunga awm chu twins, triplets angin a rualin.
- Nau pai theih lohna enkawlna.
- Chemical thenkhat ( tuipui thila methylmercury ang chi) nena inzawmna.
Tin, naupang nghawngtu a hnuaia thilte hian Athetoid Cerebral Palsy vei theihna a tipung bawk:
Hei hian eng harsatna dang nge a thlen theih?
Athetoid Cerebral Palsy hi hriselna lama harsatna dang nen a inzawm thei a ni. Chung zinga ṭhenkhat chu:
- Thinlung lama hmasawnna lama harsatna (doctor-te chuan ``Intellectual Disability'' an ti bawk).
- Epilepsy natna a ni.
- Thusawi leh tawng hman harsa.
- Hriatna emaw, mit hmuhna lama harsatna emaw.
- Orthopaedic malformations hi ruh emaw, ruh leh ruh emaw a nghawng thei dinhmun a ni.
- Mut lama harsatna nei.
- Rilru lam harsatna, entirnan, lungngaihna.
- Kum leh san zawng nena inmil rihna neih loh.
- Chaw emaw tui emaw chu thawkna kawngah aspiration hian thawkna a tichhe thei a ni.
Heng harsatna thenkhat hi nunna atana hlauhawm pawh a ni thei tih hriat reng a pawimawh. Engtin nge doctor-te hian hei hi an hriat chian?
Cerebral Palsy hi nausen a la naupan laiin doctor-in a hriat chhuah a ni tlangpui. Chumi atan chuan naupang chu endik a ni a, test chi hrang hrang tih a ni. Doctor chuan nang (naupang enkawltu) hnenah naupangin a lan chhuah dan leh a lan dan te chu a zawt ang che. Tin, naupang chu a kum a zirin a lo thanglian em tih leh thil a ti em tih a enfiah bawk ang (`Developmental Milestones`). Taksa endikna neih chhung hian naupang motor skill leh coordination te pawh enfiah thin a ni.
Eng ang test nge i tih thin?
- Brain imaging test: `(Magnetic Resonance Imaging - MRI)` ang chi test hian thluak chhiatna hmun a hriat theih.
- Thisen test: Hengte hi natna dang, chutiang bawka natna lan chhuah theihna tur chu paih chhuah nan hman a ni.
Engtin nge enkawl ang? (Tihdamna)
Athetoid Cerebral Palsy enkawlna atana thil pawimawh ber chu
naupang natna lan chhuah dan tihtlem te, nitin nun awlsam zawk te, naupang nunphung tihchangtlun te hi a ni Hei hi enkawl dan hrang hrang a awm a:
- Physical Therapy, Occupational Therapy, leh Thusawi Therapy te . Chûngte chuan naupang chetna te, ni tin hna thawh theihna te, leh thusawi thiamna te a tichak a ni.
- Assistive devices , crutches, leg supports (`braces`) emaw wheelchairs (`wheelchairs`) te pawh a awm thei.
- Naupangin a mamawh ei tur dik tak a dawn theih nan ei leh in lama inthlak danglamna siam.
- Damdawi hman dan .
- Botulinum Toxin injection hmanga tihdam theih a ni.
- Enkawlna hmanrua pakhat Deep Brain Stimulation (DBS) tih a ni.
- A hman dan chu Intrathecal Baclofen Therapy (IBT) tih a ni.
- A châng chuan operation pawh a ngai mai thei.
Doctor chuan i fa tan eng enkawlna kawng nge tha ber tih a hrilhfiah ang che, chutiang chuan i fa hriselna chungchangah thutlukna dik tak i siam thei ang.
He natna hi damdawi a awm loh avangin dam chhung zawnga enkawl a ngai dawn a ni. Eng ang damdawi nge hman thin?
Athetoid Cerebral Palsy damdawi hman tlanglawn tak tak thenkhat chu:
- Baclofen `(Baclofen)` tih a ni
- Trihexyphenidyl `(Trihexyphenidyl)` tih a ni
- Levodopa a ni
- Diazepam `(Diazepam)` tih a ni
- Tetrabenazine `(Tetrabenazine)` tih a ni
- Carbamazepine a ni
Enkawlna hian side effect a nei em?
Enkawlna zawng zawng ang bawkin heng enkawlna hian side effect engemaw zat a thlen thei a ni. I fa doctor chuan enkawl tan hmain heng side effects te hi a hrilhfiah ang che. Side effects tlangpui chu:
- Symptoms a zual zel.
- Mutthilh theih lohna.
- Lu na.
- Muscle chak lohna.
- Luhai.
Hetiang dinhmun nei naupang hi eng ang nge ni ang?
Athetoid cerebral palsy hi
damdawi a awm lo . Chumi awmzia chu dam chhung zawnga dinhmun a ni tihna a ni. Mahse, naupang a lo puitlin chuan a na zual lo (nonprogressive). Cerebral palsy chi dang aiin chetna thunun loh
hian a nghawng nasa zawk tlangpui. Hei hian naupang tan nitin hna, sam hrual leh inchei te chu a ti harsa thei a ni. Wheelchair ang chi puitu hmanrua tel lo chuan kal a harsa thei bawk. Mahse, enkawlna hian naupang natna lan chhuah dan a thunun thei a, nuam zawka nun a pui thei bawk. Hetiang natna vei naupangte hian an thau a tlahniam thei. Hei hi a chhan chu heng chetna thunun lohte hian an ei tur atanga an hmuh aia chakna an hmang tam zawk vang a ni. Chuvangin, Doctor chuan naupang rihna leh ei leh in dan chu a enfiah fo ang a, ei leh in tur dik tak an dawng em tih a chiang ang.
Dam rei zawng chungchangah eng nge i sawi theih ang? (Nun rei zawng) .
Naupang dam rei zawng
hi a natna nasat dan azirin a inang lo . Naupang zawng zawng hi a nghawng dan inang vek an ni lo. Symptoms leh complications a nasat em em chuan dam rei zawng a ti tawi thei a ni. Cerebral palsy chi dang nena khaikhin chuan athetoid cerebral palsy vei te dam rei zawng hi a tawi deuh tlangpui.
Hei hi ven dan tur a awm em? (Invenna) 1.1.
Athetoid Cerebral Palsy vei zawng zawng hi ven theih a ni lo. Amaherawhchu, naupai lai hian fimkhur theih a ni.
Checkup neih fo hian i fain cerebral palsy a vei theihna chu i tihtlem thei a ni. I doctor chuan nang leh i naute tan hrisel leh him taka awm theihna tura i mamawh thurawn a pe ang che. Doctor hmuh hun tha ber berte chu engte nge ni?
I fain athetoid cerebral palsy chhinchhiahna a lantir a, chu chu an kum anga thil tih tlai emaw, taksa chetna danglam tak emaw a nih chuan doctor pan nghal rawh . Naupang cerebral palsy vei tawhin symptom thar a neih chuan, symptom awmsa chu a na zual a nih chuan, emaw, enkawlna avanga side effect a awm chuan doctor hnenah hrilh nghal rawh. Doctor hnena zawh tur pawimawhte chu engte nge ni?
I fa dinhmun i hriat dawnin zawhna i neih hi thil pangngai tak a ni. Doctor hnenah hetiang zawhna hi zawt hreh suh:- Ka fa tan hian eng enkawlna nge i rawt?
- Chutiang enkawlnate hian side effect a nei em?
- Ka fain an mamawh ei tur dik tak a hmuh theih nan ei leh in lama inthlak danglamna ka siam a ngai em?
- Ka fa natna lan chhuah dan hi engtiang chiahin nge a nasat?
- Eng harsatna nge ka hriat bik tur?
- Eng ṭanpuitu hmanrua nge ka fate ṭanpui thei?
I fa hian dam chhung zawnga natna damdawi nei lo a nei tih hriat a harsa thei hle. Athetoid Cerebral Palsy hian naupang chu tui atanga sangha chhuak ang maiin a ti thei a . An thluak hian an taksa peng hrang hrang, chetna thunun tha tak takte hnenah message a thawn theih loh avangin thunun theih lohvin an writhe leh writhe thei a ni. Hetiang Cerebral Palsy hian i fate tan nitin hna thawk tur leh wheelchair tel lovin khawvel a kal harsa thei hle. Mahse, nangmah chauh i ni lo tih hre reng ang che. I fa medical team te puihnain i fa chu a natna lan chhuah dan tur enkawl leh hrisel taka awm turin i pui thei ang.
A tawi zawngin, hre reng ang che (Take-Home Message) .
Athetoid Cerebral Palsy hi naupang nunah nghawng lian tak a nei thei a ni. Mahse, hriatthiamna dik tak, a hun taka enkawl, leh hmangaihna nena enkawl chuan i fa chu a theih ang anga nun pangngaia nung tûrin i ṭanpui thei a ni. I fa hian heng symptoms te hi a neih chuan doctor thurawn lak hreh suh. Naupang tin hi an hlu a, naupang tin hian hlim taka awm theihna an nei tih hre reng ang che. Athetoid Cerebral Palsy, Cerebral Palsy, Cerebral Palsy, Thluak lama harsatna, Naupang natna, Chevekna lama harsatna, Thluak lam natna
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