Mi thenkhat mitmeng var, chu chu sclera var chu a sen deuh tawh tih i hmu ngai em? He inthlak danglamna hi nangmah ngei pawhin i hmu tawh mai thei. Hei hi naute tê têah chuan a awm fo ṭhîn. Chuvangin, damdawi lamah chuan mit var hian blue, gray emaw purple emaw rawng a neih chuan ‘Blue Sclera’ kan ti thin. A tam zawkah chuan hei hi ngaihtuahawm tur a ni lo. Mahse, a chang chuan hei hi kan taksa chhunga damdawi lam dinhmun dang chhinchhiahna a ni thei. Chuvangin vawiinah hian engkim hi a awlsam zawngin sawi ila.
‘Blue Sclera’ hi eng nge ni tak tak?
A awlsam zawngin kan mit peng var hi sclera an ti a. A nihna takah chuan connective tissue fiber chak tak tak atanga siam khuhna thuk tak a ni. A hna ber chu mit venhim leh a pianzia vawng reng hi a ni.
Ngaihtuah teh, he bang dum, sclera an tih hi eng emaw chhan vanga a lo hring deuh a nih chuan eng nge thleng ang? Chutih lai chuan he bang dum te tak te hmang hian tissue dum (uvea) leh a hnuaia thisen kalna rawng chu a lang chhuak ta a ni. Puan dum te tak te hnuaia thil dum i dah chuan a chungah blue rawng i hmu thei ang mai a ni. Chuvangin Blue Sclera kan ti a ni. A tlangpuiin he natna hian mit na leh chhinchhiahna dang a thlen lo.
Hei hi dinhmun khirh tak a ni fo em?
Ni lo, a tam zawkah chuan a ni lo. Hei hi a nasat dan chu mit sen chhanah a innghat a ni.
- Nausen naupang: Nausen piang thar leh nausen te sclera hi a pianphungah chuan a hring deuh a ni. Chuvangin an mit var te hi tlem a sen deuha lang hi thil pangngai a ni. Naute a lo seilian chuan he sclera hi a thim a, a rawng dum chu a bo ta a ni.
- Puitling: Hetiang dinhmun hi puitling thenkhatah iron tlakchhamna ang chi chhan awlsam tak vang a ni thei.
Mahse, a châng chuan hei hi damdawi lam dinhmun khirh tak chhinchhiahna a ni thei tih hre reng ang che. Chuvang chuan i mit emaw, i fa emaw mitah danglamna i hmu a nih chuan ngaihthah lova Doctor pan mai a tha ber. I doctor chuan a chhan dik tak hriat nân mit enfiahna, thisen test, a nih loh leh genetic testing a ti mai thei.
Mit hring (blue eyes) awm chhan berte chu engte nge ni?
Blue Sclera awm chhan hi chi hrang hrangah then theih a ni. Table pakhatah han en ila, chutichuan hriatthiam a awlsam zawk ang.
| A chhan Category a ni | Entirna leh A chipchiar zawk |
|---|---|
| Genetic Condition hrang hrangte | Hengte hi pianpui (congenital conditions) a ni a, thlah kal zelah a kal zel thei a ni.
|
| Natna leh dinhmun dang |
|
| Damdawi leh pawn lam thil dang |
|
Hei hi eng enkawlna nge ni?
Hei hi hriatthiam a pawimawh hle. Blue Sclera hi natna a ni lo va, a symptom a ni. Chuvang chuan Doctor te chuan mit rawng dum hi an enkawl lo va, a hnuaia natna hnuaia awm, mit sen a thlentu chu an enkawl zawk a ni.
- Iron tlakchhamna i rinhlelh chuan , i doctor chuan iron supplement emaw iron tamna ei tur emaw a rawn rawt thei ang. I iron level a normal leh chuan i mit a blueness chu a bo zauh zauh thei.
- Osteogenesis Imperfecta awm chhanGenetic disease a nih chuan Alzheimer’s ang bawkin enkawlna chu natna enkawl danah a innghat a ni. Hei hian specialist doctor team puihna a ngai mai thei.
- Damdawi avanga lo awm a nih chuan chu damdawi chu thlak emaw, tihtawp emaw chu doctor chuan a ngaihtuah ang.
Chumi awmzia chu enkawlna chu a chhan bulpuiah a innghat vek tihna a ni. Chuvang chuan damdawi lam thurawn lak a pawimawh a, mahni invenna neih loh a pawimawh.
Engtikah nge damdawi lam thurawn i lak nghal ang?
I mit var rawng inthlak danglamna i hmuh chuan hlauthawng lova doctor pan a tha ber. Mahse, mit sen hring hian a hnuaia chhinchhiahnate hi a zui a nih chuan damdawi in Emergency Department (ETU)-ah i kal nghal tur a ni .
- Mit hmuhna a inthlak nghal zung zung
- Mit hmuh a fiah lo
- Mit atang hian mittui ang tui a luang chhuak thin.
- Eng laka sensitivity (mit dum) .
- Mit na lutuk
Hengte hi mit lama harsatna lian tak chhinchhiahna a ni thei a, chuvangin hun khawhral lova inenkawlna zawn a pawimawh.
Take-Home Thuchah a ni
- Blue Sclera chu mit var (sclera) chu a sen, a sen emaw, a sen emaw a nih chuan a ni.
- Hei hi sclera a thinning vang a ni a, chu chuan a hnuaia tissue te chu a rawn lang chhuak thei a ni.
- Hei hi thil hlauhawm lo tak a nih fo laiin, a châng chuan natna hnuaia awm, iron tlakchhamna emaw, genetic disorder emaw ang chi chhinchhiahna a ni thei bawk.
- Enkawlna hian mit rawng dum a ngaihtuah lo va, a thlentu damdawi lam dinhmun hnuaia awm chu a ngaihtuah zawk a ni.
- I mitah heng inthlak danglamna te hi i hmuh chuan, a bik takin mit na emaw, mitdel emaw ang chi natna dang a awm chuan doctor pan nghal rawh.
👩🏽 ⚕️ Zawhna dang (FAQ)
💬 Selexipag / Uptravi tablets hi eng natna atana damdawi bik tak tak pek a ni?
Hei hi damdawi pangngai a ni lo! Hei hi khawvela damdawi hlawhtling tak leh man to tak (Prostacyclin receptor agonist) a ni a, ‘Pulmonary Arterial Hypertension (PAH)’ natna thihna thlen thei, thinlung atanga lung lam panna thisen kalna kawngte chauh a zim a, chuta thisen sang chu a pangngai lo takin a sang a, ‘lung leh thinlung a thi’ a ni!
💬 Lung lama thisen a kal loh lai hian engtin nge heng pills (Uptravi) ei hian thisen kalna kawng a tihzauh?
chemical pakhat ‘Prostacyclin’ tih hi taksaah hian a pianphungah a awm a, chu chuan lung (Pulmonary arteries)-a thisen phurtu thisen kalna kawng a tizau/zai a, mahse PAH vei te chuan an nei lo. He pill hi taksaa a luh chuan lung kawng chhunga receptor (IP receptor)-ah direct-in a kal a, button pakhat a hmet a ni! Tichuan thluak chu ‘Prostacyclin’ a lo thleng ta tih ngaihtuahin an bum a, chutah chuan lung chhunga thisen kalna kawngkhar (constricted blood vessels) zawng zawng chu a relax nghal vek (Vasodilation), thinlung chunga phurrit chu a bo nghal vek a ni.
💬 He natna khirh tak tan damdawi (Selexipag) pek hi eng nge a tuar theih loh?
Hei hian a side effect tam zawk chu taksa pum puia thisen kalna kawng (Prostacyclin effect)-a button awmte a hmet vang a ni! Side effects awm tam ber chu tuar theih loh ‘lu na’ (thisen kalna a lian zel vang), taksa ruh leh hmui natna nasa tak (Jaw pain / Myalgia), leh ril\am te hi a ni! Tin, sudden flushing (flushing) hi harsatna lian tak a ni thei ngei ang.











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