I naute piang thar chu i en lai hian a thawk danah danglamna tlem a awm tih i hmu ngai em? A tap lai hian a thaw tha viau maithei, mahse a muthilh lai leh a rilru a hahdam lai chuan a hnar atanga thawk a harsat deuh niin a lang em? A nih loh leh, thawk turin a hmui a hawn reng avangin nau a hnute a chawlhsan em? Nu emaw pa emaw hian hetiang thil an hmuh hian tlem a hlauhthawn hi thil pangngai tak a ni. Vawiin hian congenital condition, symptoms ang chi, mahse hriat lar vak lo chungchang kan sawi dawn a ni. Chu chu `Choanal Atresia` a ni.
A awlsam zawngin, Choanal Atresia chu eng nge ni?
Choanal Atresia (pronounced: ko-a-nal atre-sia) hi naute pian tirh lamah an hnar hnung lamah blockage a awm a, chutah chuan an hmui (choana an tih) nen a inzawm a, chu chu membrane emaw ruh emaw a ni. Hnar chu chamber pahnih angin ngaihtuah la, chamber tin hnung lamah kawngkhar pahnih khar a ni. He blockage hi ruh vang a ni thei a, ruh leh soft tissue inzawmkhawm vang pawh a ni thei.
Hetiang dinhmun hian naute hnar kawngkhar pakhat (`Unilateral`) emaw, hnar kawng hnih (`Bilateral`) emaw chauh a nghawng thei a ni. Engtiang chiahin nge a nasat leh enkawl vat a ngai tih chu a blockage chu a sir khatah emaw, a sir lehlamah emaw a awm leh awm loh leh a hlat danah a innghat a ni.
A pawimawh ber chu nausen piang tharte hian an hnar atanga thaw an chhuah tam ber hi a ni. An tap lai chauhvin an hmui hmangin an thawk a, chuvangin hnar hrual hian nghawng lian tak a nei thei a ni.
Choanal Atresia chi hnih lian ber berte chu engte nge ni?
Hemi chi hnih hi chiang takin i hrethiam ang u. Table-a i en chuan i tan a awlsam zawk ang.
| Quality chi hrang hrang | Hei hi eng nge thleng? | A nasat dan leh a lan chhuah dan |
|---|---|---|
| Unilateral Choanal Atresia (a sir khatah block a awm) . | Naute hnar sir khat chauh a inkhar a. A lehlamah a thaw thei. | Hei hi dinhmun pawi tak a ni lo. Naute hian hnar dang atanga a thaw a chhuah avangin naupan lai thlengin a natna lan chhuah dan a lang lo thei. A lan chhuah dan tlangpui chu hnar luang chhuak, a sir khat atanga chhuak chauh a ni. |
| Bilateral Choanal Atresia (A sir lehlamah blockage a awm) . | Naute hnar sir lehlamah a inkhar a. A hnar atang chuan thaw a la thei lo. | Hei hi thil hmanhmawhthlak tak, nunna atana hlauhawm tak a ni! Naute hi a thaw thei lo a, chuvangin damdawi in Emergency Treatment Unit (ETU)-ah dah vat a ngai a, thawk tura tanpuina pek a ngai bawk. Naute chu a ṭah chauhvin a thaw chhuak thin. |
Choanal atresia hi nau piang 7,000 zinga 1 vel ah a awm thin. Chung zinga 60% aia tam chu unilateral an ni. Hmeichhiaah pawh mipa aiin a let hnih zetin a tam zawk bawk.
Hetiang natna lan chhuah dan hi engte nge ni?
A hmaa kan sawi tawh chi hnih a zirin symptoms a inang lo.
Hnar sir lehlamah a inkhar (Bilateral Choanal Atresia) .
Doctor ten naute a pian veleh heng symptoms te hi an hmu nghal thei a ni.
- Thâwk harsa na tak: Naute chu a tap loh laiin thawk a harsat hle.
- Vun leh hmui dum (`Cyanosis`): Naute vun, hmui, leh kut zungtangte chu a sen tan a, a chhan chu taksain oxygen a hmuh tlem vang a ni.
- Tap lai chauh thawk: Naute hian a ṭah chauhin a hmui a hawn avangin chutih lai chauh chuan a thawk a, vun sen hring chu a tlahniam a, pink a lo ni ta a ni. Tap a reh chuan thawk a harsa leh a, a rawn sen leh thin.
Chutiang a nih chuan doctor-te chuan an rawn inrawlh nghal ang a, naute thlipuiah hian tube te tak te an dah lut ang a, chu chuan a thawk thei ang. Naute dinhmun a nghet tawh chuan operation chungchanga thutlukna siam a ni ang.
Hnar sir khat chauh a block chuan (Unilateral Choanal Atresia) .
Heng symptoms te hi a langsar lutuk loh avangin i naute i hruai haw hnuah chauh i hre lo mai thei. Kum tam tak hnuah chauh pawh i hre lo mai thei.
- Nau hnute pek laiin chawlh hahdam loh: Naute hian hnute a pek laiin a hnar atanga thawk a mamawh a ni. A sir khat a inkhar tlat avangin thawk a harsat a, hnute pek a chawlhsan a, a hmui a hawng ta a ni. Hei hian naute chu a ti hahdam lo hle thei a, a hnute pawh a pe tha thei lo bawk.
- Hnar khata hnar luang chhunzawm zel: I naute hnar chu chhan hriat loh, khawsik awm lovin a sir khatah chauh a luang chhunzawm zel a nih chuan chu chu he natna lan chhuahna ber leh tlanglawn ber a ni.
- Tap laiin chhung lam hawia pil:Naute a tap loh chuan thawk a harsat laiin a rilru chu a pil lut ang maiin a lang.
- Chronic sinusitis: Naupang kum upa zawkte chuan hnar sir khatah mucus a awm avangin sinus infection an nei fo thei.
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Hetiang dinhmun hi a chhan dik tak hi hriat a la ni lo. Amaherawhchu, Doctor-te chuan nausen pum chhunga nausen lo pian tirh lamah chuan hnar leh hmui inthenna (membrane) a awm niin an ngai. A tlangpuiin he membrane hi naute a lo seilian chuan a mah chauhin a inthiar chhuak thin. Mahse, naute thenkhatah chuan he membrane hi a awm reng a, a awm reng a, chu chu `Choanal Atresia` tia hriat a ni.
A kaihhnawih dinhmun dangte
Choanal Atresia vei naute zinga a chanve vel chu genetic disease dang emaw, pianpui harsatna emaw an nei a ni. A chhan dik tak hriat ni lo mah se, he natna hi syndrome dang nen a awm dun fo thin.
Chung zingah chuan a hnuaia mite hi a pawimawh ber a ni:
- CHARGE syndrome: Naute bilateral nasal obstruction nei zinga 60% vel chuan CHARGE syndrome an nei a.
- `Treacher Collins syndrome` tih a ni
- `Crouzon syndrome` tih a ni
- `Pfeiffer syndrome` tih a ni
Choanal Atresia hi hetiang genetic condition dang nen hian hmuh theih a ni. Chuvangin, hei pawh hi doctor in a enfiah ang.
Enkawl loh chuan eng harsatna nge awm thei?
A bik takin a sir khatah blockage a awm chuan hriat loh chuan enkawlna a tikhawtlai thei a ni. Hei hian hun rei tak chhung nghawng a nei thei a ni.
- Beng natna awm fo: Hnar leh beng inzawmna a awm avangin hnar sir khat a inkhar reng a, mucus a khat reng chuan beng a nghawng thei a, beng natna a thlen fo bawk.
- Hriatna hloh: Hun rei tak chhunga beng natna hian beng a tichhe thei a, hun kal zelah hriatna hloh a thlen thei bawk.
- Aspiration: Bawnghnute emaw ei tur emaw aspirate a hlauhawm hle a, a bik takin nau hnute pek laiin thawk harsat vangin a awm thei.
Heng hlauhawmna te avang hian doctor chuan a hun takah enkawl a rawt ang.
Engtin nge he dinhmun hi kan hriat theih ang?
Naute a sir lehlamah hnar khar chu a pian tirh atangin damdawi inah hmuhchhuah a ni tlangpui. Mahse, a sir khatah blockage a awm chuan test neih a ngai a, chu chu a hriat theih nan a ni.
1. Thâwk test: Doctor chuan naute hnar bulah glass te tak te a vawn ang a, chuta tang chuan steam a chhuak em tih a enfiah ang. Side khat atanga steam a chhuak lo a nih chuan chu sir lamah chuan blockage a awm tih a tilang thei.
2. CT scan hmanga tihchhuah a ni:Hei hi a danglamna tak tak chu a ni. I hnar chhung lam 3D thlalak lak ang mai a ni. Blockage awmna hmun, ruh emaw membrane emaw a nih leh nih loh leh a thuk zia chiang takin a hmu thei.
3. Nasal endoscopy: Hetiang tih dan hian tube hmangin hnar chhungah camera tha tak tak dahin doctor chuan hnar chhung lam chu screen-ah direct-in a en thei a ni.
Medical team hian heng test neih chhung hian naute hi a thawk tha em tih an enfiah thin a, chuvangin naute tan hlauhawm a awm lo.
Engtin nge enkawl a nih?
Choanal Atresia enkawlna nghet awmchhun chu surgery a ni.
- Hnar sir lehlamah a inkhar a nih chuan: Naute chu a rang thei ang bera zai a ngai dawn a ni.
- Hnar sir khat a inkhar a nih chuan: Naute hian thawk emaw, ei leh in lama harsatna nasa tak a neih loh chuan, doctor chuan naute chu tlem a lo puitlin hma chu sawn a rel thei a ni.
Inzai
Surgery-ah chuan ruh emaw, membrane emaw blocked chu lakchhuah a, thawk chhunzawm zel theih nan thawkna kawng chu siamrem leh a ni. Hei hi hnar (transnasal) emaw, palate (transpalatal) emaw hmangin tih theih a ni.
A then phei chuan a khar leh tawh loh nan operation hnua kawngpui siam thar kaltlangin tube te tak te (`stent`) dah a ni. He tube hi thla engemaw zat hnuah operation tenau tak hmangin lakchhuah leh a ni. He operation hi full anesthesia hmanga tih a nih avangin naute hian natna a nei lo.
In lama enkawl dan tur
I naute hian unilateral obstruction a neih a, doctor chuan operation sawn a tum a nih chuan in lama symptoms enkawl dan tur a pe ang che. Entirnan, hnar a thianghlim theih nan saline drops hmang turin an ti mai thei che.
I doctor zawh tur zawhna
I naute hian he natna hi a nei tih i hriat chuan i rilruah zawhna tam tak awm hi thil pangngai tak a ni. Heng zawhnate hi i doctor zawh hreh suh.
- "Doctor, ka naute hnar hi a sir khatah nge a sir lehlamah a block em?"
- "He natna hi `CHARGE syndrome` ang natna dang nen a inzawm em?"
- "Naute hi engtikah nge operation a neih a ngaih ang?"
- "Doctor hian eng ang surgery nge a rawt?"
- "Engtin nge surgery chu a hlawhtling tih chiang taka kan hriat theih ang?"
I naute hian Choanal Atresia a vei tih hriatchhuah chu, a bik takin a pian tirh atanga thawk harsa an tih chuan nu leh pate tan chuan a hlauhawm hle thei a ni. Mahse, he natna hi operation hmangin hlawhtling takin enkawl theih a ni tih hre reng ang che. Operation an neih hnuah naute tam zawk chu an dam kim vek a, an dam chhungin harsatna awm lovin an thawk chhuak thin. Chuvangin, i naute hian heng symptoms te hi a nei tih rinhlelhna tlemte pawh i neih chuan doctor pan nghal la, enfiah nghal rawh.
Take-Home Thuchah a ni
- Choanal atresia hi hnar hnung lama kalna kawng (pasageway) pianpui atanga inkharkhip (congenital blockage) a ni.
- Bilateral nasal obstruction hi damdawi lam emergency a ni. Naute hian a pian tirh atangin thaw a harsat phah dawn a ni.
- Unilateral nasal congestion hi thil thleng nghal mai a ni lo. Simptoms chu a sir khat atanga hnar atanga chhuak chhunzawm zel leh ei harsa tih te hi a hnuah a lo lang thei a ni.
- Hei hi enkawlna nghet tak chu surgery a ni a, chu chuan result hlawhtling tak a pe a ni.
- I naute thawk danah emaw, nau hnute pek danah emaw thil dik lo i hmuh chuan tihkhawtlai suh la, doctor rawn nghal rawh.











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