I kut i en tawh em, i fa kut i en a, i kut zungtang pakhat chu a dang ang bawka dinglam ni lovin, hruihrual ang maia ben tlem a ni tih i hmu ngai em? Kut zungtang te tak te pawh a ni thei a, kut zungtang dang pawh a ni thei bawk. Damdawi lamah chuan hei hi ``Clinodactyly'' an ti a, chu chu kut zungtang pakhat chu nail bula joint atanga kut zungtang dang thlenga hetiang hian a ben a ni. Hei hi dinhmun pawi tak a ni lo va, a chungchang tlem tal hriat a tha.
`(Clinodactyly)` tih hi eng nge ni tak tak?
A awlsam zawngin `(Clinodactyly)` tih hi kan kut zungtang-a ruh te tak te, chu chu ruh chi khat, deformity te tak te a ni. Kut zungtang ruh a thang tha lo a nih chuan a awm thin. In this , kut zungtang, nail hnaih ber joint atang chuan chhung lam, chu chu kut zungtang dangte lam hawiin, hrui ang maiin a inbeng a ni. A tam zawkah chuan hei hian kan kut zungtang te tak te (pinky finger) a nghawng thin . Mahse, a chang chuan he natna hi kut zungtang eng pawhah a awm thei a, kut chauh ni lovin ke ruh thlengin a awm thei bawk.
Kan kut zungtang te hi a ben deuh hi thil pangngai a ni. Bend 10 degree aia tlem a nih chuan harsatna lian tak a ni lo. Mahse, a bik takin ``Clinodactyly`` kan ti a, chu chu kut zungtang chu degree 10 aia tam a inbeng chuan . Ngaihtuah teh, kut zungtang chu 'C' letter ang maia ben ang maia lang a nih chuan chu chu a dinhmun chu a ni.
Hei hi a chang chuan pianpui a ni thei a, a nih loh leh naupan laia kut zungtang ruh a lo thang chhoh lai accident dang vang pawh a ni thei bawk.
He dinhmun hian tute nge a nghawng ber?
Hetiang kut zungtang hrual, ``Clinodactyly'' tia koh hi tu chungah pawh a thleng thei . Amaherawhchu, zirchianna atanga a lan dan chuan mipa zingah a hluar deuh hlek a ni.
A châng chuan he crookedness hi amah chauhin a thleng thei a, hriselna lama harsatna dang a awm lo. Hei hi ``Isolated clinodactyly`` kan ti a. Mahse, ṭhenkhatah chuan genetic syndrome -ah pawh a tel thei bawk . Entir nan:
- `Down syndrome` tih a ni
- `Turner syndrome` tih a ni
- `Klinefelter syndrome` tih a ni
Tuna zirchianna atanga a lan dan chuan Down syndrome vei mi pali zinga pakhat vel chuan he natna hi Clinodactyly an tih hi an nei a ni.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Hei hi engtiang chiahin nge a awm tih hi statistics dik tak a awm lo. Zirna hrang hrangah chuan mipui 1% leh 2% inkar chuan he natna hi an nei thei tih hmuhchhuah a ni a, zirchianna thenkhatah chuan 20% vel a ni thei tih an sawi bawk. Chuvangin, hetiang kut zungtang i neih chuan nangmah chauh i ni lo tih hre reng ang che.
`(Clinodactyly)` hian taksaah eng nge nghawng a neih?
Mi tam tak chuan hei hian harsatna a thlen dawn em tih an ngaihtuah thin. Dik tak chuan a tam zawkah chuan ``Clinodactyly`` hi natna hlauhawm lo tak a ni.Hei hian a bik takin i kut zungtang hmel a tidanglam deuh chauh a ni. Chumi awmzia chu kut zungtang hnathawh that dan a nghawng lo tihna a ni. I kut zungtang chu a pangngaiin i hmang thei.
`(Clinodactyly)` natna lan chhuah dan chu engte nge ni?
Hetiang natna lan chhuah dan hi i kut zungtang pakhatah a lang tlangpui. Sawi tawh ang khan pianpui a ni thei. Mahse, a chang chuan heng natna lanchhuahna te hi naupan lai hian ruh a lo thang lian a, a puitlin chuan a lang chhuak thin. Clinodactyly hi i kut pakhat emaw, kut pahnih emawa kut zungtang eng pawhah hmuh theih a ni. Ke ruh a nghawng thei bawk.
A lan chhuah dan tlangpui thenkhat han thlir ila.
- Kut zungtang chu hook emaw letter ‘C’ angin (degree 10 aia sang angle-ah) bent angin a lang .
- Kut zungtang ben chu kut zungtang dang lam hawiin (a tam zawkah chuan kut zungtang te tak te chu ring finger lam hawiin) a inher a ni.
- Kut zungtang pahnih inkarah hian bend a lo lang a.
- A châng chuan, ke ruh ben chu ke ruh dangte chungah a kal thei bawk.
- A pawimawh ber chu he kut zungtang ben hian a tlangpuiin natna leh hliam a thlen lo.
Clinodactyly vei te hian an kut zungtang chu a pangngaiin an la hmang thei tih hre reng ang che. Mahse, a tlem berah chuan kut zungtang chu degree 30 aia tam a ben chuan kut zungtang chetna (range of motion) a tlem thei hle. Chutiang a nih chuan doctor-te chuan siamthat nan operation neih an rawt mai thei.
Engvangin nge hetiang hian kut zungtang hi a hrual? A chhan engte nge ni?
``Clinodactyly'' awm chhan ber chu i kut zungtang ruh awm dan pangngai lo vang a ni.
A awlsam zawngin: Kan index, middle, ring, leh little fingers te hian ruh pathum ``phalanges'' an ti vek a. Heng ruhte hi a chungah an inzawm khawm a, chuvang chuan ruh pahnih a awm a ni. A châng chuan, i kut zungtang lai takah ruh, a lai leh nail hnaih ber inzawmna (``distal phalanx'') inkar ruh chu, square ang maia lian ai chuan, wedge ang maia lian, trapezoid emaw triangle emaw-ah a lo thang lian zawk ṭhin. Chuvangin, he ruh hi a lo thang dik loh chuan ruh dangte nen line dik takah a line up thei lo. Chuvang chuan kut zungtang tip chu a hrual ta a ni. Hmu?
Hei hi nu leh pa atanga genes atanga lo chhuak thil a ni em?
Ni e, `(Clinodactyly)` awm chhan hi engemaw zat a awm. Chumi zinga pakhat chu he mizia hi rochun a ni.
A châng chuan, Clinodactyly hi i ruh a la ṭhan laiin kut zungtang hliam vang a ni thei. Hliam hian kut zungtang ruh chu a pangngai lo takin a tipung thei a ni. Ruh chu square shape pangngaiah a lo thang lian ai chuan wedge angin a lo thang lian thei a ni.
Mahse, a tam zawkah chuan ``Clinodactyly`` hi accident mai mai a ni lo.Hei hi random takin a thleng thei a, a nih loh leh i nu leh pate hnen atangin chu mizia chu i rochun thei bawk. I nu leh pa zinga pakhatin `(Clinodactyly)` thlentu gene a neih chuan chu gene chu i hmu thei bawk. Hei hi `(Autosomal dominant)` genetic pattern kan ti a. Chumi awmzia chu, chu gene chu i nu leh pa hnen atanga i hmuh chuan `(Clinodactyly).` pawh i hmu dawn tihna a ni
A châng chuan clinodactyly hi genetic condition complex zawk symptom pakhat chauh a ni thei a, chu chu symptom dang pawh a awm ve ve tih hmuh a ni tihna a ni.
Eng dinhmun dang nge `(Clinodactyly)` symptom hi a thlen theih?
Clinodactyly hi ruh thanna tichhe thei genetic condition engemaw zat chhinchhiahna a ni thei. Chung dinhmun thenkhat chu:
- `Down syndrome` tih a ni
- `Fanconi thisen tlakchhamna`
- `Klinefelter syndrome` tih a ni
- `Turner syndrome` tih a ni
- `Triple X syndrome` tih a ni
Hetiang dinhmun hi i neih chuan ``Clinodactyly`` nen hian symptom dang pawh i nei thei bawk. Chuvangin, doctor chuan hei hi ``Clinodactyly`` chauh nge condition dang a tel tih a hre thei ang.
Engtin nge doctor-te chuan hei hi ``Clinodactyly'' tia an hriat?
I doctor chuan i medical history enfiahin i kut zungtang taksa enfiahna hmangin ``Clinodactyly`` natna hi a hmuchhuak ang.
Chu bakah, doctor chuan:
- I kut X-ray la rawh. Hei hian i kut zungtang chhunga ruh awmte pianzia leh awmna chu chiang takin a tarlang ang.
- I kut zungtang chetna (range of motion test / flexibility test) test rawh. Chu chu i kut zungtang inzawmna chu eng chen nge i ben theih leh i tihdik theih ang tihna a ni.
Heng test atang hian doctor chuan hei hi ``Clinodactyly'' a nih leh nih loh, thil dang emaw, surgery ang chi thil a ngai em tih emaw a rel thin.
Hei hi eng enkawlna nge ni?
Mi tam tak tan chuan thu lawmawm tak chu hetiang hi a ni: A tam zawkah chuan clinodactyly hi enkawlna a ngai lo. A chhan chu, a hmaa kan sawi tawh ang khan, a tlangpuiin kut zungtang hnathawh a nghawng lo.
Mahse, a tlem hle, na tak takah chuan , kut zungtang curvature degree 30 aia tam a nih a, kut zungtang chu a pangngaia i hman theih lohna hmunah chuan i doctor chuan reconstructive surgery neih a rawt thei ang. He surgery hi naupang tê tê, ruh la ṭhang chho zelteah a hlawhtling ber a ni.
`(Clinodactyly)` lo awm tur ven dan tur a awm em?
Dik tak chuan ``Clinodactyly'' hi a tam zawk hi chu ven theih a ni lo, a chhan chu random occurrence emaw, i genes inthlak danglamna avanga lo awm emaw a nih vang a ni.
Clinodactyly thlentu genetic condition i neih chuan, emaw, i nu leh pa zinga pakhatin clinodactyly a neih chuan, i doctor emaw, genetic counselor emaw chuan i fain a rochun theihna tur a hrilhfiah thei che a ni.
`(Clinodactyly)` i neih chuan eng nge i beisei ang?
Clinodactyly hi a tlangpuiin dam chhung daih tur a ni. Mahse, i kut zungtang ruh awm dan chauh a nghawng a, kut zungtang hnathawh dan a nghawng lo. Chuvangin, kut zungtang hrual vangin i hman theih loh phawt loh chuan enkawl a ngai lo.
I kut zungtang chunga he curve te tak te hi i tana thil danglam bik, midang zawng zawng aiin i danglam bikna angin ngaihtuah rawh. I identity-ah a tel ve a ni!
Engtikah nge Doctor i hmuh ang?
Hei hian damdawi lam enkawlna a ngai lo tlangpui a, mahse heng ang case-ah hian doctor pan a tha:
- I kut zungtang chu a ben avangin i hmang thei lo a nih chuan.
- Bent finger range of motion a tlahniam tih a hriat chuan .
- Clinodactyly hi a na lo tlangpui. Mahse, i kut zungtang ben (bent finger)-ah natna emaw, nuam lo emaw i neih chuan doctor pan ngei ngei tur a ni.
I doctor hnenah eng zawhna nge i zawh tur?
Nangmah emaw i fa emaw hian ``Clinodactyly'' an nei tih i hriat hnu chuan i doctor hnenah hetiang zawhna hi i zawt thei ang:
- Ka kut zungtang "straighten" turin operation ka mamawh em?
- Hei hi ``Clinodactyly`` hi damdawi lam thil dang chhinchhiahna a ni em?
- `(Clinodactyly)` ka neih chuan ka fa hian he mizia hi a rochun theihna chance engzat nge awm?
Hêng zawhnate chhânna i hriat hnu chuan he dinhmun hi i hrethiam lehzual thei ang.
A tawp berah chuan hriat reng tur pawimawh ber
``(Clinodactyly)`` hi a tlangpuiin a hlauhawm lo, natna a thlen lo va, i kut zungtang i hman dan pawh a thlak danglam lo. Doctor-te chuan i kut zungtang angle chu degree 30 aia tam a ben loh chuan surgical treatment an rawt lo. Chu i kut zungtang hrual tlemte chu i tan thil danglam leh danglam bik angin ngaihtuah rawh. I nitin hnathawhna a tibuai loh chhung chuan lungkhamna tur a awm lo. Rinhlelhna emaw, harsatna emaw i neih chuan damdawi lam thurawn la hreh suh.
` Kut zungtang curvature, clinodactyly, kut zungtang tihzauh, ruh deformities, genetic diseases, Down syndrome, kut zungtang surgery te











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