I fate mit i en hian thil danglam tak i hmu ngai em? Mit pakhat chu a mak deuhin a lang mai thei, a nih loh leh an mit hmuh chu a fiah deuh niin a lang mai thei em? Chutiang thil i hmuh chuan ngaihthah suh. Vawiin hian hetiang huna i rilruah harsatna lo thleng thei tur kan sawi dawn a, chu chu Coats Disease tih hming pu condition a ni. Hei hi mit natna hmuh tur awm lo tak a ni a, naupang te, a bik takin mipa naupangte a vei tlangpui.
Coats Disease hi eng nge ni? A awlsam zawngin i hrethiam ang u.
A awlsam zawngin sawi ila, Coats Disease hi i fa mit chhunga thisen kalna kawngte a lo thang tha lo a nih chuan a lo awm thin a ni. Hei hian a bik takin mit hnunglam retina a nghawng a ni. Hetiang hian han ngaihtuah teh: kan mit hi camera ang a nih chuan retina chu a chhunga film ang a ni. Mit chhunga eng a luh chuan thlalak a hmuchhuak a, he retina kaltlangin thluak hnenah thuchah a thawn thin.
Chuvângin, Coats Disease-ah chuan retina-a thisen kalna kawng te tak te chu a hring a, a inher a, plasma angin tui a leak emaw, a leak emaw ṭan a ni. Hei hi tui pipe-ah khur a awm a, tui a luang chhuak ang mai a ni. Thil chhiatna nasa tak thlen nghal lo mah se, hun kal zelah he leakage hian retina a tichhe thei a, mit hmuhna a tichhe thei bawk.
He natna hian mit pakhat a vei tlangpui. Mahse, a rualin mit pahnih a nghawng thei lo. Naupang tê leh tleirawlah hmuh chhuah tam ber ni mah se, kum eng pawhah a awm thei. Hei hian mitdelna a thlen thei a, retinal detachment ang chi harsatna lian tak tak a thlen thei a, a tawpah chuan chu mit chu mitdelna a thlen thei bawk. Chuvang chuan i fa mit emaw, mit hmuh danah emaw danglamna i hmuh chuan Doctor pan vat a pawimawh.
Heng symptoms te hi engte nge ni? Engtin nge i hriat chian?
Coats Disease hian a tir lamah chuan symptom a nei lo thei. Mahse, natna a zual zel chuan naupang hian a lan chhuah dan te chu:
- Mit hmuhna a tlahniam zauh zauh: I fa chuan mit pakhatah chiang taka hmu thei lo ang maiin a inhria mai thei. TV en laiin hnaih zawka inher emaw, lehkhabu chhiar laiin mitmeng hrual emaw ang chi thilte chu i hmu mai thei.
- Strabismus: Mit pakhat chu a dang aiin a hawi danglam niin a lang.
- Mit na: Naupang thenkhat pawhin mit na an complain thei bawk.
- Leukocoria: Hei hi a lan dan danglam deuh a ni. I fa mit mitmeng (pupil) i en hian , emaw, thlalak i lak hian, a var emaw, tangkarua emaw angin a lang thei. Hei hi "cat's eye" an ti \hin. He chhinchhiahna hi i hmuh chuan doctor pan nghal ngei ngei tur a ni.
Ngaihtuah teh, i fapa a inkhelh lai hian mit pakhatin chiang takin a hmu thei lo tih i hmu a, a nih loh leh zanah thlalak i lak chuan mit pakhat iris dum chhungah hian hmun dum a awm tih i hmu a. Chu chu hetah hian a thleng thei a ni.
Coats Disease hi eng stage nge ni?
Coats Disease hi a kal zel dan azirin stage hrang hrangah then a ni a, chu chu staircase ang mai a ni.
- Stage 1: Hei hi stage bulpui ber a ni. Hetah hian mit lam doctor chuan naupang mit chhungah thisen kalna kawng dik lo tak tak a nei tih a hmu thei a, mahse chu mi avang chuan naupang chuan hrehawmna emaw symptoms emaw a la tawng lo.
- Stage 2: Hei hi thisen kalna kawng dik lo atanga tui a chhuah tanna hmun a ni. Hei hian naupang mit hmuh dan a nghawng fo thin.
- Stage 3: Natna hian hetiang dinhmun a thlen chuan naupang mit (retina) chu a inthen tan thin. Hei hi dinhmun pawi zawk a ni.
- Stage 4: Stage palina-ah chuan naupang mit chu glaucoma , mit chhunga pressure a sanna natna a vei thei a ni.
- Stage 5: Hei hi Coats Disease na ber leh a tawp ber a ni. Hetih lai hian mit natna chu a mit a del vek thei a ni.
A pawimawh ber chu natna chu eng stage-ah pawh awm se, a hmaa hriat chhuah leh enkawl a nih chuan naupang mit hmuhna humhalh theihna chance a sang zawk a ni.
Engvangin nge Coats Disease hi a lo awm?
Dik tak chuan mithiamte chuan Coats Disease (idiopathic ) awm chhan hi an la hmu thei lo . Chu chu, a chhan chiang tak awm lovin, a takin a thleng fo tihna a ni.
Thil pawimawh dang chu Coats Disease hi genetic disorder a ni lo tih hi a ni . Chu chu, thlah khat atanga thlah khata inthlunzawm, thlah kal zel natna a ni lo tihna a ni. I chhungkuaa tumahin an nei lo a nih pawhin i fain a la nei thei tho. Tin, i fate zinga pakhatin a neih vang mai mai chuan naupang dangte pawhin an nei ve ang tih ngaihtuah a ngai lo.
Hetiang hi tuin nge nei tam zawk? (Risk factor hrang hrang) 1.1.
Tu pawhin Coats Disease vei thei mahse, mi thenkhat chu an hlauhawm zawk.
- Hmeichhia aiin mipa naupangin he natna hi a let thum velin an vei tam zawk tih hmuhchhuah a ni.
- Kum thlir chuan:
- Doctor te chuan naupang leh puitling kum 16 hnuai lam ah hetiang hi an hmuchhuak fo thin .
- A tlem hle a, naute thenkhat chu he natna hi neiin an piang thei a, a nih loh leh an pian hnu thla engemaw zat hnuah pawh a lo lang thei bawk.
- Coats Disease vei hmun thuma ṭhena hmun khat vel chu kum 30 chunglam puitling an nih thu an sawi bawk .
Engtin nge doctor hian hei hi a hriat theih? (Diagnosis) tih a ni.
Doctor, a bik takin mit lam doctor , i fa mitmenga thil danglam tak i hriat hnua i hmuh chuan, a tih hmasak ber tur chu naupang mit uluk taka enfiah hi a ni.
- Naupang mit chu pawn lam a\ang pawhin a chhung lam a\angin hmanraw bik hmangin a enfiah \hin.
- Naupang mit hmuh dan enfiah nan visual acuity test an nei thin. Hei hian lehkha leh thlalak entir a, chhiar tir a huam a ni.
Chu bakah, Coats Disease finfiah nan a hnuaia special imaging test pakhat emaw a aia tam emaw pawh tih theih a ni bawk:
- Optical Coherence Tomography (OCT) scan: Hei hian mit (retina) cross-section thlalak a la a.
- Angiography test: Hei hian i kut zungtang pakhatah dye bik inject a, i mit chhunga thisen kalna kawng a kal lai thlalak lak a ni . Hei hian leak awm zawng zawng chiang takin a hriat theih a ni.
- Ultrasound scan: Hei hian mit chhung lam a en thei.
- MRI (Magnetic Resonance Imaging) hmanga enfiah a ni.
- CT scan (Computed Tomography scan) hmanga tih a ni.
Heng test te hian doctor chuan mit chhunga thil thleng dik tak te, thisen kalna kawng a chhiat nasat dan te, tui a leak leh chhuah loh te a hre thei a ni.
Enkawlnate chu engte nge ni?
Coats Disease enkawl dan hi naupang natna stage a zirin a innghat a ni. Entirnan, natna hi hriat hma lutuk (stage 1 emaw early stage 2 emaw) , naupang chuan enkawlna engmah a mamawh lo mai thei. Chutiang hunah chuan mit lam doctor chuan naupang mit a enfiah fo ang a, retina-a thisen kalna kawng hrang hranga inthlak danglamna a en reng ang.
Mahse, naupangin natna lan chhuah dan na tak a neih chuan, emaw, natna chu a na zawka a awm chuan, enkawl dan tur a awm a, chungte chu:
- Cryotherapy: Hei hian thisen kalna kawng pangngai lote chu a vawt lutuk a, a tichhia a, chu chuan tui a chhuah loh nan a titawp a ni.
- Damdawi hmanga enkawl dan: Mit lam doctor chuan anti-VEGF (Anti-vascular endothelial growth factor) damdawi chu naupang mit (retina)-ah direct-in a inject thei a. He damdawi hian chu thisen kalna atanga tui chhuak tur chu a titawp a, retinal detachment a veng bawk.
- Surgery: Naupang chu natna khirh tak a nih chuan, emaw, retinal detachment ang chi natna a lo awm a nih chuan, a chhiatna siamthat nan operation neih a ngai mai thei.
Ka fa hian Coats Disease a vei a nih chuan eng nge ka beisei theih ang?
Coats Disease hian naupang mit leh mit a nghawng dan hi natna hi engtikah nge a awm tih hriat a nih dan leh mit hian enkawlna a dawn danah a innghat a ni. Zirna hrang hrangah chuan naupang chu natna a lo awm chuan a upa poh leh a nasat zawkna hmunah a kal chak lo zawk tih hmuhchhuah a ni .
Coats Disease hi a hmaa hriat chhuah a nih chuan (stage 1 emaw 2 emaw) naupang hian nghawng na tak, hun rei tak chhunga nghawng a nei tlem zawk. Mahse, enkawl a nih pawhin mit natna chu eng emaw chen chu mit hmuhna hloh (low vision) a la nei thei tho.
Natna hi a na zawka a lo kal tawh chuan mit natna chu mitdelna a sang zawk a ni. Chuvang chuan a rang thei ang bera doctor pan turin kan rawt a, a danglamna tlemte pawh i hmu a nih pawhin.
Hei hian eng harsatna dang nge a thlen theih?
Coats Disease lai hian naupang chu mit lam natna dang a vei theihna a sang hle a, chungte chu:
- Glaucoma natna (Glaucoma) a awm
- Mit (cataract) a awm
- Uveitis ( mit chhunga tissue inflammation) .
- Neovascularization tih a ni
Chuvang chuan Doctor thupek fimkhur taka zawm a, a hun taka test tura kal hi a pawimawh hle.
Coats Disease hi ven theih a ni em?
He natna hi random takin a lo awm thin avangin, a chhan chiang tak awm lovin, Coats Disease venna tur hian kan tih theih tur a awm tak tak lo.
Mahse, natna hi hriat chhuah a nih hnuah mit lam doctor-in naupang mit (retina) a inthlak danglamna enfiah nan mit lam doctor-in a rawt angin mit enfiahna (follow-up eye exam) neih fo a pawimawh hle. Hei hian natna a zual zel tur hriatchhuahna leh a tul anga hmalak a pui dawn a ni.
Engtikah nge Doctor ka hmuh ang?
I fa mit emaw, mit hmuh danah emaw danglamna i hmuh chuan doctor emaw mit lam doctor emaw pan nghal ang che. Tikhawtlai suh.
Tin, heng symptoms te hi i neih chuan hospital emergency department ah kal nghal rawh :
- Mit hmuhna hloh nghal mai.
- Mit na tak.
- Eng eng hmuh emaw, mit hmaa floater hmuh emaw angin sawi theih a ni.
Doctor hnenah eng zawhna nge i zawh tur?
Doctor hmu tura i kal hian hetiang zawhna hi i zawt mai thei:
- Ka fa hi Coats Disease hi eng stage-ah nge a awm?
- Follow-up exam atan engzat nge ka lo kal ngai?
- Naupangin enkawlna a mamawh em?
- Eng ang enkawlna nge a mamawh?
- Coats Disease hian eng chen nge a mit hmuhna a nghawng dawn?
Hetiang zawhna hi zawt la, i rinhlelhna zawng zawng chu tifai rawh. Doctor chuan engkim a hrilhfiah ang che.
Coats Disease leh Retinoblastoma hi eng nge an danglamna?
Coats Disease leh Retinoblastoma hi naupang tê tête mit (retina) tichhe thei natna pahnih a ni.
- Coats Disease hi naupang mit (retina)-a thisen kalna kawng dik lo taka lo thanglian a, mit chhunga tui a luang chhuak thin a ni.
- Retinoblastoma hi cancer chi khat, mit (retina)-a lo awm thin a ni. Cancer ni mah se, mit pawnah a darh lo a nih chuan naupang tam zawk chu enkawl hnuah cancer nei lovin an khawsa thei a ni.
Natna pahnih lan chhuah hmasak dan hi a inang hle. A bik takin, black iris (leukocoria) rawng dum hi an pahnih ah hian hmuh theih a ni. Chuvangin, i fate mitah danglamna emaw, a lan chhuah dan emaw i hmuh chuan eng nge a nih chiang taka hriat theih nan mit lam doctor pan nghal a pawimawh hle. Doctor chuan test a ti thei a, heng natna pahnih zingah hian eng nge ni tih chiang takin a hrilh thei che a ni.
Take-Home Thuchah a ni
Coats Disease hi natna awm lo tak a ni a, i fa mit hnunglam retina-a thisen kalna kawng te tak te te a nghawng a ni. Hei hian chu thisen kalna atang chuan tui a luang chhuak a, mit a tichhe thin.
Hriat reng tur pawimawh tak chu he natna hian naupang mit leh mit a nghawng dan tihziaawmna tur tha ber chu natna hi a naupan lai atanga man hi a ni.
Chuvangin, i fate mitmeng emaw, thil an hmuh danah emaw inthlak danglamna tlemte pawh i hmuh chuan ngaihthah suh la , doctor emaw mit lam doctor emaw pan nghal rawh. A hmaa hmuhchhuah a nih chuan i fate mit hmuhna chu enkawlna hmanga chhanchhuah theihna chance a sang zawk hle. Ngaihtuah buai suh, nang leh i fate tanpui turin doctor te an awm reng a ni.
` Coats natna, naupang mit natna, mit chhunga thisen kalna kawng, mit (retina), mit hmuh lohna, mit enkawlna, naupang hriselna











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