I nau piang thar chu a blue ta em? Nau hnute pek kawngah harsatna a nei em? Thâwk a harsat em? Hengte hi a chang chuan pianpui thinlung natna chhinchhiahna a ni thei bawk. Nu emaw pa emaw hian hetiang thil an hmuh hian an hlauthawng em em thin hi thil pangngai tak a ni. Vawiin hian thinlung natna hmuh tur awm lo tak, mahse hriat tur pawimawh tak kan sawi dawn a ni. Chu chu Double Inlet Left Ventricle an tih condition a ni.
Double Inlet Left Ventricle (DILV) tih hi eng nge ni?
A awlsam zawngin sawi ila, hei hi pian tirh atanga lo awm thin, pianpui heart defect hmuh tur awm lo tak a ni. Hei hi hrethiam tur chuan thinlung hrisel hnathawh dan hi han thlir hmasa ila.
Kan thinlung hi pindan pali nei in ang maiin han ngaihtuah teh. A chung lamah pindan pahnih a awm a, a hnuai lamah pindan pahnih a awm bawk.
- Upper two chambers (Atria): Hei hi taksa atanga thisen lo lut leh khawlkhawmna hmun a ni. Chamber dinglam (Right Atrium) hian taksain a hman tawh thisen "bawlhhlawh" a dawng a, oxygen a tlem hle. Left chamber (Left Atrium) hian thisen "thianghlim" a dawng a, chu chu lung atanga oxygen a khat a ni.
- Chamber hnuai lam pahnih (ventricles): Hengte hi thinlung chhunga pump lian ber pahnih an ni. Ventricle dinglam hian oxygen tlakchhamna thisen chu lungah a pump lut a, oxygen a la thei a ni. Left ventricle hian oxygen tamna thisen chu lung atanga taksa peng dang zawng zawngah a pump chhuak thin.
Tunah chuan Double Inlet Left Ventricle (DILV) vei naute thinlunga thil thleng hi han en teh. Heng naute zingah hian lower chamber (ventricle) pakhat chauh hian hna a thawk tha hle. Chu chu left ventricle a ni . Ventricle dinglam hi a te lutuk a, a thawk thei lo fo thin.
Buaina lian ber chu upper chamber pahnih (right leh left atria) atanga thisen chu lower chamber hnathawk awmchhun (Left Ventricle)-ah a inzawm khawm a ni. Chumi awmzia chu oxygen tlachham thisen leh oxygen tamna thisen pahnih hi a inzawm khawm tihna a ni . Tichuan he thisen inhmeh tak hi naute taksa leh lungah pump luh a ni. Hei vang hian harsatna tam tak a awm thin.
Hetiang natna lan chhuah dan hi engte nge ni?
Heng symptoms te hi naute pian hnu ni engemaw zat emaw, kar tlemte chhungin a lang tlangpui. Nu i nih angin hengte hi i hriat chian a pawimawh hle.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Vun leh hmui a sen (Cyanosis) . | Naute vun, hmui leh kut zungtangte chu a sen angin a lang a, a chhan chu a taksa pum puia oxygen tlakchhamna thisen a kal kual vang a ni. Hei hi a lan chhuah dan ber pakhat a ni. Mi thenkhat chuan "blue baby" an ti bawk. |
| Chaw pek \ha lo | Naute hian bawnghnute a pai hian a chau hle a, thaw pawh a harsat phah thin. Chuvang chuan tlem a in a, a chawlhsan ta a ni. |
| Thâwk harsa | Naute chu a thaw chak hle. A rilruah a lut ang maiin a lang mai thei. |
| Thau tihpun loh | Naute hian bawnghnute in tam atanga chakna a hmuh theih loh avangin a thau tha lo ang. |
| Thawmhnaw hak | A bik takin bawnghnute i in hian i hmai vel i thawkrim a, a chhan chu i thinlung hian a thawhrim zawk a ngai a ni. |
| Lungphun pangngai lo | Thinlung hi a na chak hle emaw, a rhythm mumal lo emaw a nei thei bawk. Doctor chuan examination neih laiin extra sound (heart murmur) a hre thei. |
Engvangin nge hetiang hi a lo awm? Hei hi eng nge a chhan?
Hei hi a chhan dik tak hi hriat a la ni lo . Naupai kar tir lamah, naute thinlung a lo thang lian lai hian a thleng fo thin. Nu leh pa sualna a ni lo.
Vawi tam tak chu DILV hian thinlung lama harsatna dang engemaw zat a keng tel a, chu chuan thisen kal dan a tibuai zual sauh a ni.
- Aortic coarctation: Thinlung atanga taksa thlenga thisen phurtu thisen kalna bulpui (aorta) a tawi.
- Pulmonary atresia: Pulmonary valve, lung chhunga thisen phurtu chu a siam tha tawk lo.
- Pulmonary valve stenosis: Lung chhunga thisen phurtu valve a tawi.
He natna hi Doctor ten engtin nge an hriat chian?
He natna hi hriat theih dan kawng hrang hrang a awm a.
Naupai lai hian
A chang chuan nausen pum chhunga a la awm laiin hei hi hriat theih a ni. I doctor-in i routine scan (ultrasound)-a i thinlungah thil danglam a hmuh chuan special scan-ah a refer ang che. Fetal Echocardiogram an ti a . Hei hian naute thinlung insiam dan leh hnathawh dan chipchiar takin a entir thei a ni.
Naute a pian hnuah
Vawi tam tak chu naute pian hnuah natna hi hriatchhuah a ni.
- Pulse Oximetry test: Tunah chuan Sri Lanka rama damdawi in zawng zawngah te hian nausen piang tharte chungah he test hi tih a ni tawh. Hei hian naute thisena oxygen level a teh a ni. Oxygen level a hniam chuan thinlung natna chhinchhiahna a ni thei.
- Damdawi lam endikna: Doctor-in naute thinlung a ngaihthlak laiin thawm danglam tak (murmur) a hriat chuan, a nih loh leh vun a sen a nih chuan rinhlelhna a nei thei.
Tichuan, a natna hriat chian nan test eng emaw zat an nei leh a.
| Fiahna | Hei hi engtin nge i tih? |
|---|---|
| Chest X-ray neih a ni | A rilru X-ray a ni. Hei hian thinlung lian leh te leh lung chhunga thisen kal zat hriat theihna a pe thei a ni. |
| Electrocardiogram (ECG) hmanga tih a ni. | Thinlung electrical activity tehna test. Heart rhythm lama harsatna awmte a hmuchhuak thei. |
| Echocardiogram (Echo) hmanga tih a ni. | Hei hi fiahna pawimawh ber a ni. Scan ang mai a ni. Thinlung pindan te, valve te leh thisen kal dan te chiang takin a hmu thei a ni. |
| Cardiac Catheter hmanga tih a ni | Test complex tak, naute rilru chhunga thisen kalna kawng khata tube te tak te tak tak kal tlanga thinlung chhunga pressure leh oxygen level tehna. |
Hei hi eng enkawlna nge ni?
He natna hi damdawi hmanga tihdam kim theih a ni lo. Enkawlna ber chu operation hrang hrang a ni.Hei hian naute thinlungah chamber pahnih a siam lo. Chu ai chuan ventricle pakhat awmsa hmangin taksa chhungah thisen a kal chak thei ang bera a kal tir zawk a ni.
Hei hi vawi khat surgery a ni lo. He surgery series hi naute kum a zirin stage hrang hrangah tih a ni.
| Surgery neih dan tur stage hrang hrang | Kum (a tlem berah) . | Surgery hnuah eng nge thleng? |
|---|---|---|
| A hmasa ber atan: Blalock-Taussig (BT) Shunt | Pian hnu ni engemaw zat emaw, kar hmasa emaw chhungin | Lung chhunga thisen kal tlem a nih chuan he surgery-ah hian tube te tak te (shunt) dah a ni a, chu chuan lungah thisen a kal tling thei ang. |
| Stage pahnihna: Glenn Shunt Procedure tih a ni | Thla 4 - 6 chhung a ni | Naute taksa chunglam atanga oxygen tlachham thisen lo chhuak chu lung lam pan nghal a ni a, thinlung chu a paltlang a ni. Hei hian thinlunga hnathawh tur a tihtlem phah a ni. |
| Stage Pathumna: Fontan kalphung | Kum 2 - 3 chhung | Hei hi surgery hnuhnung ber a ni. Taksa hnuai lam atanga thisen deoxygenated lo chhuak pawh hi lung nen direct-in a inzawm bawk. He surgery hnuah hian deoxygenated leh oxygenated thisen inzawmkhawm chu a tawp vek tawh mai. |
Surgery bakah hian doctor chuan naute tan damdawi thenkhat a pe thei bawk.
- Digoxin: Thinlung inzawmna (contraction) a tichak.
- ACE inhibitors: Thisen sang tihhniam.
- Anticoagulants: Thisen zam a veng.
- Diuretics: Taksa atanga tui tul lo a paih chhuak thin.
A nasat ber lai chuan heng surgery te hi tih theih a nih loh chuan heart transplant ngaihtuah theih a ni.
Nakin hun chu eng nge ni ang? Beiseina kan nei thei ang em?
Hetiang natna chungchang i hriat hian hlauhthawn hi hriatthiam theih a ni. Mahse i hriat tur pawimawh ber chu medical science hmasawnna avang hian heng naute hian nun tha zawk neih theihna hun remchang an nei ta a ni . Operation hnua kum 10 chhunga damchhuah zat hi 70% - 80% vel a ni. Naupang tam tak chuan puitling an thleng hial a ni.
Mahse heng naupangte hian an dam chhung zawnga cardiologist enkawlna an mamawh a ni . Clinic kal a, a hun taka test neih a pawimawh hle. Complication thenkhat a awm thei bawk.
- Ke ruhro (ingrown toenails) leh kut zungtang lian (clubbing) te.
- Lung infection tam tak, pneumonia ang chi te.
- Heart rhythm lama harsatna nei.
Tin, heng naupangte hian naupang dangte ang bawkin tlan, zuang, leh infiamna lama tihkhawtlai engemaw zat an nei thei bawk. Heng zawng zawng hi doctor nen sawiho leh thutlukna siam tur a ni.
Take-Home Thuchah a ni
- Double Inlet Left Ventricle (DILV) hi thinlung natna hmuh tur awm lo, na tak, mahse enkawl theih, pianpui lung natna a ni.
- I nau piang thar vun a rawn sen (cyanosis), chaw pek harsatna a neih emaw, thawk harsa emaw a nih chuan tihkhawtlai suh la, doctor pan nghal rawh.
- Enkawlnaah hian naute kum a zirin stage hrang hranga operation complex tak tak tih a ni.
- He zinkawng hi harsa viau mah se, damdawi lam thiamna lama hmasawnna avang hian heng naupang tam tak hi tunah chuan puitling thlengin an nung thei tawh a ni.
- Nun chhung zawnga enkawl leh cardiologist-in a enkawl dan dik a pawimawh hle.











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