I naute hian thinlung natna hlauhawm tak a vei em? Ebstein-a Anomaly chungchang hi a awlsam zawngin i zir ang u.

I fate hian a chau reng em? Thâwk lamah harsatna a nei niin a lang em? A vun hi a chang chuan a sen angin a lang em? Chûngte chu thil pangngai a nih fo laiin, a châng chuan pianpui thinlung lama harsatna vang pawh a ni thei. Vawiin hian chutiang thinlung natna hmuh tur awm lo mahse pawimawh tak pakhat chu kan sawi dawn a ni. Ebstein’s Anomaly tih a ni.

Ebstein-a Anomaly hi eng nge ni tak tak?

A awlsam zawngin sawi ila, hei hi pianpui thinlung natna a ni. Chu chu nausen pum chhunga a la awm laia thinlunga chhiatna lo awm chu a ni. Kan thinlung hian pindan pali, pindan chunglam pahnih leh pindan hnuai lam pahnih a nei a. Heng chamber inkarah hian kawngkhar ang maia thawk valve te a awm a. Chûngte chuan kawng khat chauha thisen kal chu an thunun a ni.

Ebstein’s Anomaly hian tricuspid valve a nghawng ber a, chu chu thinlung dinglamah upper chamber (right atrium) leh lower chamber (right ventricle) inkarah a awm a ni. Hetiang dinhmunah hian thil pawimawh pahnih a thleng thin:

1. Valve chu a awm dik lo: He tricuspid valve hi a awm dan pangngai aia hniam zawkah dah a ni a, dinglam hnuai lam chamber chhungah a awm a.

2. Valve leaflet te hi a insiam tha lo: Valve leaflet te hi a pianzia pangngai lo tak a ni. A châng chuan thinlung bang-ah pawh an innghat thei bawk.

Kawngkhar a khar mumal loh chuan eng nge thleng tih han ngaihtuah teh. Chutiang bawkin he valve hi a khar tha tawk lo a, a hnuai lam atanga thisen pump ngai chu upper chamber ah a leak leh thin.

Hei hian thinlung dinglama upper chamber chu a ti lian a ni. Tin, a hnuai lam chamber, a hnuai zawka awm valve nei chuan hnathawh thatna tur hmun a nei tlem zawk bawk. Hun a kal zel a, he thinlung dinglam zau tak hi a chak lo thei a, thinlung chak lohna pawh a thlen thei a ni.

Vawi tam tak chu naupang `Ebstein's Anomaly` vei te hian thinlung lam natna dang an nei thin. A tam ber chu thinlung chunglam pindan pahnih inkar bang chhunga khur awm hi a ni. Hei hi `(Atrial Septal Defect - ASD )` an ti a.

Hetiang natna lan chhuah dan hi engte nge ni?

Symptoms hrang hrang hi a zau hle. A chang chuan natna hi a na hle a nih chuan nau pian atanga ni rei lo te chhungin a lan chhuah dan a lang thei. Amaherawhchu, he natna hi a nasat loh chuan tleirawl lai thlengin a lanchhuahna a awm lo thei.

Engvangin nge hetiang hi a lo awm? Eng nge a chhan?

Dik tak chuan, hei hi a chhan chiang tak zawn chu a harsa fo thin. Mahse doctor-te chuan genetic changes hian chanvo a nei thei niin an ngai. Naupai laiin damdawi thenkhat lithium emaw benzodiazepines emaw ei hian hlauhawmna tlemte a thlen thei tih rinna a awm bawk. Mahse hengte hi research stage-ah an la awm a ni.

Engtin nge doctor hian hei hi a hmuh theih? (Thil test a ni) .

I fa hian heng symptoms te hi a neih chuan doctor in uluk takin a enfiah hmasa ang. Tichuan, thinlung hnathawh dân dik tak hriat nân test engemaw zât an ti thei a ni.

• Echocardiogram: Hei hi test pawimawh ber a ni. Nausen pum chhunga ultrasound scan ang bawkin thinlung chhungril chipchiar takin a la chhuak a ni. Valve awmna hmun, an pianzia, thisen hnunglam a luang em tih, engzat nge, heart chamber te hi engzat nge a lian tih te a entir thei a ni.
• Electrocardiogram (EKG): Hei hian thinlunga electric hnathawh dan a teh a. Hei hian heartbeat mumal lo (arrhythmias) a hriat theih nan a pui thin.
• Cardiac MRI: Hei hian thinlung leh valve te chu chiang zawk, three-dimensional image a siam thei a ni. Hei hi operation hma ang chi dinhmunah chuan a pawimawh hle.
• Exercise Stress Test: Naupang kum upa zawk tan chuan treadmill-a an kal laiin EKG an ti thin. Hei hian thinlungin thawhrimna a chhân lêt dân hriat nân a ṭanpui a ni.
• Holter Monitor: Hei hi hmanraw te tak te a ni a, darkar 24 atanga darkar 48 chhung taksaah bun theih a ni. Nitin heart rate a record a, nitin heartbeat mumal lo awm apiang hriatchhuah nan hman a ni.

Hei hi eng enkawlna nge ni?

Enkawlna chu natna nasat dan leh naupang natna lan chhuah danah a innghat a ni.

Damdawi hmanga enkawl

A natna lanchhuahna a nasat loh chuan doctor chuan naupang dinhmun enfiah turin thutlukna a siam thei a ni. Heart failure chhinchhiahna a awm chuan thinlung hnathawh thatna tur emaw, taksa atanga tui tam lutuk paih chhuah nan emaw damdawi an pe thei a ni. Lungphu a mumal lo a nih chuan a thunun theihna tur damdawi a awm bawk.

Inzai

Symptoms a nasat emaw, thinlung a chak lo zawi zawi emaw a nih chuan zai a ngai mai thei.

• Valve Repair: Surgeon-te duhthlanna hmasa ber chu naupang valve siam that leh siamthat tum hi a ni fo thin. Naupang tissue ngei hmangin valve flap te chu a thawk tha thei turin an siamrem thin.
• Valve thlak dan: Valve chu siamthat theih loh khawpa a chhiat chuan a hmunah artificial valve dah a ni. Chungte chu thir (Mechanical valve) emaw, rannung tissue (Biological valve) atanga siam emaw a ni thei. Metal valve dah a nih chuan i dam chhung zawng thisen tithianghlimtu i ei a ngai dawn a ni.
• Thil tih dan dang: Surgery neih lai hian thinlung chhunga khur (ASD) chu khar theih a ni a, thinlunga thinlung thawk mumal lo (irregular heartbeat) thlentu (catheter ablation) chu enkawl theih a ni.

Fimkhur tur bikte chu engte nge ni?

Hetiang natna nei naupang hi a dam chhung zawnga cardiologist enkawl a ngai a ni . Surgery hnuah pawh clinic-a kal a, a hun ruatah checkup neih a pawimawh hle.

I fain he natna hi a neih chuan a hnuaia symptoms te hi lo thlir reng ang che:

• Vun a rawn sen tam zawk chuan.
• Naupang thiltih, tlan leh inkhelh a tlahniam chuan.
• Taksaah hliam a awm chuan.
• I thinlung a na zual tih i hriat chuan.

Hetiang ang inthlak danglamna i hmuh chuan i doctor hnenah hriattir nghal rawh .

Tin, a then phei chuan ha chhuah hma ang chiah hian doctor chuan naupangte chu thinlung natna laka inven nan antibiotics ei turin a fuih thei bawk. Doctor thupek dik takin zawm fo ang che.