Naupai laiin doctor kan biak hian a châng chuan kan hriat ngai loh thu, emaw, damdawi lam dinhmun hmuh tur awm lo tak tak emaw kan tawk ṭhin. Chutiang hunah chuan hlauhna leh lungkhamna nasa tak nei hi thil pangngai a ni. Vawiin hian chutiang piansualna tlemte leh na tak pakhat chu kan sawi dawn a ni. Hetiang dinhmun hi Ectopia Cordis kan ti a. He thu i hriat hian hlau suh. Hemi chungchang hi awlsam takin, pakhat hnu pakhatin i hrethiam vek ang u.
Ectopia Cordis chu eng nge ni tak tak?
A awlsam zawngin, Ectopia Cordis chu naute chu an thinlung zawng zawng emaw, a then emaw chu an taksa pawn lama awm a pian hi a ni. Hei hi thil awm lo tak a ni. Ngaihtuah teh, khawvel puma naute maktaduai khat zinga pariatah chauh he natna hi a awm a ni.
Hei hi natna khirh tak a nih avangin Ectopia Cordis natna vei nausen piang tam tak chu an pum chhungah emaw, an pian atanga ni thum chhungin an thi thin. Mahse, he thawnthuah hian beiseina lam a awm. Doctor, nurse, physiotherapist leh specialist dangte telna medical team thiam tak takte chuan he natna neia piang naute thenkhat chu kar tam tak chhung, a then phei chuan kum tam tak chhung pawh an nung thei a ni.
Hei hi eng nge a chhan?
Dik tak chuan mithiamte chuan hei hi chhan chiang tak pakhat mah an la hmu lo a, mahse ngaihdan tlemte an nei tho.
- Hmasawnna lama harsatna: Theory pakhat chu naute chu nausen pum chhunga a lo seilian chhoh zel chuan taksa lama inthlak danglamna a awm a, chu chuan naute than dan pangngai a tibuai a ni. Entirnan, naute hual veltu fluid-filled sac (amniotic sac)-ah fibrous band a lo awm a, chu chuan naute thanlenna a tikhawtlai thei a ni.
- Chest development problem: Theory dang pakhat chu naute rilru a thang tha lo tih hi a ni. Hei hian thinlung chu rilru chhunga a hmun dik takah a kal thei lo. Hei hian Ectopia Cordis leh thinlung lama harsatna dang a thlen thei a ni.
- Natna dang nena inzawmna: Ectopia cordis hi piansualna dang, taksa lairil lama awmte nen a inzawm tih hmuh a ni fo. Entirnan, sternum, pericardium leh abdominal wall-a chhiatna nen a inzawm a ni. Chromosomal condition Trisomy 18 leh Turner syndrome te nen pawh a inzawm thei bawk.
- Genetic causes : Tun hnaia theory pakhat chu nausen thenkhatah chuan ``(BMP2)'' tih gene bik an nei lo tih a ni. He gene hi thinlung leh rilru hmalam hmasawnna dik tak neih nan a pawimawh hle. Chuvangin a tlakchhamna hi a chhan a ni thei niin an ngai.
Eng symptoms nge hriat theih?
Ectopia Cordis natna lan chhuahna ber leh langsar ber chu thinlung hi taksa pawn lama awm a ni. Mahse, heng naute hian taksa lairil ( lu atanga hnuai lam line)-ah hian midline defect dang an nei thei bawk.
| Harsatna dang hmuh tur a awm | A sawifiahna awlsam tak |
|---|---|
| Cranial cleft a awm | Hmai ang chiaha cleft emaw split emaw neih. |
| Hmai/kham (palate) a inthen | A hmui chunglam emaw, a hmui emaw-ah cleft awm. |
| Lungs a lo thang kim lo | Naute lung hi a lian tawk lo hle. |
| Scoliosis natna (Scoliosis) a ni | Spine curvature emaw scoliosis emaw nei. |
| Great Wall-a khur pakhat | Diaphragm-a khur pangngai lo, rilru leh pum inthenna muscle. |
Engtin nge doctor-te hian hei hi an hriat chian?
A tam zawkah chuan i naute hian Ectopia Cordis a vei a nih chuan naupai laiin ultrasound scan pangngai (routine ultrasound scan) hmangin a hriat theih a ni. Naupai thla thum khatna atang tawhin hriat theih a ni. Diagnosis finfiah nan ultrasound scan round dang i neih leh a ngai mai thei. Heng test result hi i tan a pawimawh hle a, eng nge i tih leh tur tih i rel thei a ni.
Naupai chhunzawm zel tura i rilru i siam chuan i doctor chuan i naute hmasawnna chu uluk takin a enfiah ang. Hei hian MRI ( magnetic resonance imaging) a huam thei bawk.)` leh `(Echocardiography)` test hman a ni ang. Echocardiography hi test bik a ni a, sound wave hmanga thinlung thlalak chipchiar tak tak lak a ni.
Doctor-te pawhin he natna hi thinlung awmna hmun azirin an thliar hrang bawk.
| Thinlung awmna hmun | Awmzia | Indaih |
|---|---|---|
| Thoracic a ni | A rilru chhunga ribs leh sternum bulah, pum chung lamah. | 64% vel a ni. |
| Thoracoabdominal a ni | A rilru hnuai lam, pum lam hawiin. | 18% vel a ni. |
| Pum chhunga awm | Pum chhungah chuan. | 15% vel a ni. |
| Cervical a ni | Kawr lam, ruhro lam hawia rit lutuk. | 3% vel a ni. |
Ectopia Cordis natna hmuhchhuah hi chhungkaw eng tan pawh thil buaithlak tak a ni. Hetiang hunah hian rilru lama chak taka awm reng a pawimawh hle.
Hei hi eng enkawlna nge ni?
When talking about treatment options , ngaihtuah hmasak ber tur chu naute himna hi a ni. Chuvang chuan naute hrin dan awmchhun chu cesarean section (C-section) a ni. Chu chu pawn lama thinlung tichhe lovin naute chhuah tir dan tha ber a ni.
Pian hnuah i naute hian thawk lakna kawngah tanpuina dang a mamawh mai thei. Chutiang ti tur chuan doctor-te chuan i naute thlipuiah plastic tube flexible tak an dah ang a, chu chuan boruak a luang chhuak thei ang. Tin, lungte khuh tube kaltlangin tui bik an inject thei bawk a, chu chuan oxygen a lakluh that theih nan a pui thei bawk.
Ectopia Cordis enkawlna tum ber chu a rilru chhunga kawngkhar chu surgery hmanga khar a, thinlung chu rilru chhunga dah leh a, thinlung chhiatna dang awm apiang siamthat a ni. Heng surgery te hi vawi khatah tih vek a ni lo fo thin. Stage engemaw zatah an ti thin.
Harsatna hmasa ber leh lian ber chu thinlung chu a tlangpui aia te zawka dah luh hi a ni. Doctor chuan chutianga a tih zawh chuan a hnute ruh (sternum) chu a dah leh ta a ni. Hetiang hunah hian heart transplant hi duhthlan tur a ni lo tlangpui.
"Comfort Care" tih hi eng nge ni?
A then phei chuan surgery hi a risky lutuk a, hlawhtlinna chance pawh a tlem hle. Chutiang hunah chuan i doctor chuan "Comfort Care" tih option chungchang a sawipui ang che.
A tum ber chu naute hian hrehawmna leh hrehawmna a tawh thinte tih tlem a, an dam chhung zawng thlamuanna leh thlamuang taka an nun theihna tura phalsak a ni. Hei hi enkawlna bik a ni a, naute leh chhungte enkawl leh tihdam ai chuan, he hun harsa karah hian thlamuanna pek tumna a ni.
Take-Home Thuchah a ni
- Ectopia Cordis hi piansualna a awm lo hle a, nausen thinlung chu taksa pawnah a awm a.
- Hei hi a chhan dik tak hriat chhuah ni lo mah se, nu pum chhunga naute lo seilian laia harsatna lo awm leh genetic factors te hian hei hi a thlen niin an ngai.
- Naupai lai hian ultrasound scan hmanga hriat theih a ni fo.
- Step engemaw zat awmna surgery buaithlak tak tak chu enkawlna atan tih ni mah se, naute zawng zawng hi operation an nei thei vek lo mai thei.
- Hetiang diagnosis hi chhungkaw tan chuan harsatna lian tak a ni. Chuvangin, surgery leh "Comfort Care" telin duhthlan tur zawng zawng, i doctor nen zalen taka sawiho a, i naute leh chhungte tana thutlukna tha ber siam a pawimawh hle.
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