I fa emaw, chhungte emaw chuan primary hemophagocytic lymphohistiocytosis (HLH) ang chi natna hlauhawm tak, natna hlauhawm tak a nei tih i hriat chuan hlauhna leh mangang taka awm hi thil pangngai a ni. Hetiang hunah hian i doctor-in a rawtna enkawlna tur chungchang hi hriat chian a pawimawh hle. Vawiin hian vaccine bik Emapalumab tih kan sawi dawn a, hei hi he natna lan chhuah dan control nan hman a ni.
A awlsam zawngin Emapalumab hi eng nge ni?
Emapalumab hi damdawi chi khat bik a ni a , chu chu monoclonal antibody an ti a . Kan taksa immune system peng bik hnathawh control nana lab-a a bik taka siam protein angin han ngaihtuah teh.
Tunah chuan hei hian HLH tan engtin nge a puih tih kan en ang. HLH ah hian kan taksa immune system chu a overactive a, cell hrisel te chu a bei tan thin. Emapalumab hian he overactivity siamtu chemical signal interferon-gamma an tih chu a block a, immune system a ti reh a ni.
Thil pawimawh ber: Hei hi HLH damdawi a ni lo a, mahse natna lan chhuah dan na tak takte control-na atan a pui a, taksa chu a dam lehna kawngah a pui bawk.
He damdawi hi i ei tan hmaa i doctor hnena i hrilh tur thilte
He enkawlna hi i tan hmain doctor hnenah i emaw damlo emaw hriselna chanchin kimchang pek hmasak a pawimawh hle. Hêng thute hi a bîk takin sawi chhuak ngei ang che.
- Tuna hri kai mek: Tunah hian khawsik, khuh, khawsik ang chi natna i neih chuan.
- Vaccine chungchang: Tun hnaia vaccine eng emaw i dawng tawh a nih chuan, emaw, nakin lawkah i dawng dawn a nih chuan.
- Tuberculosis (TB): Tuberculosis i lo vei tawh emaw, vun test positive i neih tawh emaw, tun hnaia tuberculosis vei nena inkawp hnai tak i neih chuan doctor hnenah i hrilh tur a ni.
- Allergy: He Emapalumab damdawi emaw, damdawi dang emaw, ei tur emaw, dye dang emaw allergy i neih chuan.
- Naupai leh nau hnute pek: Naupai, nau pai tum emaw, nau hnute pek emaw i nih chuan.
Heng thute a\ang hian i doctor chuan he damdawi hi pek che a \ha em tih leh fimkhurna bik eng nge i zawm tur tih a rel ang.
Engtin nge he damdawi hi pek a nih?
Emapalumab hi injection a ni a, chu chu vein (infusion)-ah pek a ni. In lamah i hmang thei lo. Hospital emaw clinic emaw-a healthcare professional trained-in a pek a ni. I enkawl lai leh enkawl zawhah uluk takin an enkawl ang che.
He damdawi hi naupang kum eng pawh, nau piang thar atanga naupang thlengin, a tul hunah pek theih a ni. Mahse, naupang hnena pek dawnin fimkhur bik a ni. I pediatrician nen chipchiar zawkin i sawi thei ang.
Damdawi dose khat ka ei loh chuan engtin nge ni ang?
He enkawlna hi hun ruat saah pek thin a ni. Chuvang chuan Doctor appointment pelh loh a pawimawh hle. Eng emaw chhan vanga ni ruat saah i kal thei lo a nih chuan i doctor emaw damdawi in emaw ko nghal la, hriattir rawh.
Damdawi ka ei tam lutuk chuan engtin nge ni ang?
Hei hi damdawi inah pek a nih avangin hetiang thil thleng theihna chance hi a tlem hle. Mahse, damdawi i ei tam lutuk mai thei nia i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah call nghal la, a nih loh leh Emergency Treatment Unit (ETU) hnai ber pan rawh.
Enkawl laia ngaihtuah tur thil
- Tuberculosis (TB) test: He damdawi hi i tan hma hian Tuberculosis (TB) test i ni ang. I doctor-in TB damdawi a pek chuan Emapalumab i ei hmain i ei tan tur a ni a, a pek hun chhung zawng chu i ei zo tur a ni.
- Infection hlauhawmna: He damdawi hian immune system a titawp avangin natna kai theihna hi a sang deuh thei a ni. Chuvangin, khawsik, khawsik, rilru na, khuh ang chi symptoms i neih chuan mahni invenna nei suh la, i doctor hnenah hriattir nghal rawh. Damlote laka inthiarfihlim tum ang che.
- Damdawi dang: Damdawi dang, vitamin emaw, herbal remedies emaw i ei lai chu i doctor hnenah hrilh rawh. A bik takin he damdawi hi i ei lai hian virus nung vaccine lak loh tur a ni.
Eng side effect nge ka neih theih ang?
Damdawi zawng zawng ang bawkin Emapalumab hian side effect a nei thei a, mahse mi zawng zawngin an vei lo.
| Side Effects awm thei te | |
|---|---|
| Side effect na tak tak, doctor hnenah report nghal tur a ni | |
| Allergy natna a awm thei | Vun vun rawng, hnim hring, hmai, hmui emaw lei emaw a hring. |
| Thâwk harsa | Thâwk a tawi, thawk chakna a sang. |
| Lungphun a rawn ri ta | I thinlung chu a na hle tih hriatna. |
| Thisen sang a sang | Thisen sang a sang. |
| Hri kai theihna chhinchhiahna | Khawsik, khawsik, khuh, ril na, zun laiin na. |
| Side effects nasat loh tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur a ni | |
| Digestive system lama harsatna awm thei | Pum na, chaw ei kham, luak chhuak, luak chhuak. |
| Thil dang pawh a awm | Khuh, rilru hahdam lo (a bik takin naupang), injection na hmuna natna, sen, emaw, vun emaw. |
He list-ah hian side effect awm thei zawng zawng a tel lo. Thil danglam tak i tawn chuan damdawi lam thurawn la rawh.
Take-Home Thuchah a ni
- Emapalumab hi damdawi bik a ni a, HLH na tak symptoms control nan vein-ah inject a ni.
- Hei hian natna hi a tidam kim lo nachungin, natna lan chhuah dan control nan a pawimawh hle.
- Enkawl i tan hmain i hriselna chungchang zawng zawng, a bik takin natna hrik, allergy, leh TB chungchangte chu doctor hnenah hrilh hmasa phawt ang che.
- Enkawl lai hian hri kai chhinchhiahna, khawsik, khuh, leh allergic reaction te hi fimkhur hle ang che. Harsatna i neih chuan doctor hnenah hriattir nghal tur a ni.
- He damdawi hi damdawi inah pek a nih avangin ni ruat saah enkawl turin kal ngei ngei tur a ni.











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