I fate hian chaw thar a ei atanga darkar tlemte chhungin a luak tan emaw, a riltam emaw a nei tan em? A nih loh leh pum na mai mai a ni em? A châng chuan hei hi pum na mai ni lovin a tam thei bawk. Vawiin hian condition pakhat kan sawi dawn a, a danglam deuh hlek a, mahse hriat a pawimawh hle. Chu chu FPIES (Food Protein-Induced Enterocolitis Syndrome) an ti a. A hming hi a sei deuhin a lang thei a, mahse kan taksa, a bik takin intestines-a ei tur thenkhata protein awmte avanga thil thleng mai a ni.
FPIES chu eng nge ni? A awlsam zawngin i hrethiam ang u.
A awlsam zawngin sawi ila, FPIES (Food Protein-Induced Enterocolitis Syndrome) hi kan taksa immune system-in ei tur thenkhat a chhan dan pangngai lo a ni. Kan chaw ei dan (Gastrointestinal - GI system) a nghawng ber a ni. Chumi awmzia chu riltam leh riltam ang chi symptoms te hi a tam ber tihna a ni.
Food allergy ang lo takin FPIES symptoms hi chaw ei atanga darkar engemaw zat hnuah a lang tan thin . Hei hi he dinhmun hi a danglam bikna chhan chu a ni. Ngaihtuah teh, chawhmeh i ei a, chawhnu lam vel khan i na tan ta.
FPIES hi nausen leh naupang te zingah a tam ber a nih pawhin , a chang chuan puitlingte pawh a nghawng thei , chuvangin mi zawng zawng tan hriat a pawimawh.
Eng ei tur nge FPIES thlentu?
Chaw eng pawh hian FPIES thlen thei mahse, he natna thlentu tam ber ei tur tlemte a awm. Anni chu:
- Bawnghnute: Ran hnute bawnghnute leh kêl hnute ang chi.
- Nausen chaw ei: Nausen thenkhat chuan nausen chaw ei allergy an nei thei.
- Soy a ni.
- Oats a ni.
- Buhfai.
- Artui.
- Seafood: A bik takin shellfish ang chi crab, shrimp, leh sangha chi dang.
FPIES thlentu ei tur ber berte chu i awmna ram leh bial a zirin a danglam thei a, Sri Lanka-ah pawh heng ei tur avanga FPIES vei an awm tih hriat a ni bawk. Ngaihtuah teh, i naute chu buhfai i ei tan chauh a, a nih loh leh yogurt i pe a, darkar tlemte hnuah i naute chu a luak chhunzawm zel a, a pum a na bawk. Tichuan he thil hi i ringhlel tur a ni.
FPIES hi chi hnih a awm a, chungte chu:
FPIES hi chi hnih ah then theih a ni a:
1. Acute FPIES te chu:
- Chutiang a nih chuan, ei tur sawi tur ei atanga darkar khat atanga darkar li chhungin symptoms a lang thin.
- Luak leh ril\am hi a châng chuan a na hle thei a ni. Naute chu a luak chhunzawm zel ang a, hriatna a hloh phah ang.
- Mahse thil tha tak chu, heng symptoms te hi allergenic food tihtawp a nih atanga darkar 12 atanga darkar 24 chhungin a reh vek tlangpui.
2. 2. A rilru a hah lutuk chuan a rilru a buai em em a.FPIES rei tak takte chu:
- Hetiang dinhmun hi i allergy nei chaw chu ei chhunzawm zel leh ei fo a nih chuan a lo awm thin.
- Hei hian hun rei tak chhung chu intestine-ah inflammation a thlen thin.
- Acute FPIES angin natna lanchhuahna chu na lo mah se, a lo thleng thei a, a kal bo thei bawk. I naute hian natna lan chhuahna thenkhat a nei thei a, chu chu riltam, ei duh lohna, leh a rihna tlahniam te hi a ni.
- Allergenic ei tur i pek tawh loh hnuah heng symptoms te hi a bo theih nan ni thum atanga ni sawm vel a ngai thei.
FPIES natna lan chhuah dan chu engte nge ni? Engtin nge i hriat chian?
FPIES natna lan chhuah dan ber chu:
- Diarrhea: A chang chuan tui a ni thei a, thisen tlem pawh a awm thei bawk.
- Pum natna: Nausen te te chu an tap a, an pum an chelh a, an bei nasa hle.
- Pallor: Taksa chu a rawn sen nghal a, thisen tel lo rawng a rawn chang ta a ni.
- Lethargy: Naute chu a lethargic mai mai a, a khel lo va, a mit a chhing vek niin a lang.
- Tum loh taka taksa rihna tihtlem: Hei hi a bik takin hun rei tak chhunga FPIES-ah hmuh theih a ni.
- Hypothermia: Taksa a vawt a.
Pawimawh tak chu FPIES-ah chuan heng natna lan chhuah dan hi chaw sawi tur ei atanga darkar engemaw zat hnuah a lang thin , a tlangpuiin darkar 1 leh darkar 4 inkar a ni. Chronic FPIES-ah chuan symptoms a lo thleng thei a, a kal bo thei bawk.
I naute chuan zing lamah bawnghnute bottle khat a in tih han mitthla teh. Chawhnu lamah chuan a luak chhuak chhunzawm zel a, a pum a na a, a taksa chu a hring vek a, nunna nei lo ang maiin a lang. Chutiang a nih chuan FPIES rinhlelh a pawimawh.
Engvangin nge FPIES hi a lo awm? Eng nge a chhan?
FPIES kan neih chhan ber chu kan taksa hriselna (immune system) hian ei tur thenkhata protein awmte hi "a tichhe thei" tiin a ngaihtuah sual a, a bei nasa hle a ni. Immune system chuan heng ei tur te hi hmelma ang maiin a en thin.
Hemi kawngah hian thil thleng chu kan chaw ei dan (ril leh intestines)-a immune cells te hian ei tur "chhiatthlak" nia an ngaihte chu paih chhuah tumin an bei thin. Hei hian pum leh intestines-ah a hring leh inflammation a thlen thin. Hei hian luak chhuak leh luak chhuak a thlen thin.
FPIES hi reaction chi khat a ni a, `non-IgE-mediated` an ti a. A awlsam zawngin, kan hriat tam tak allergy (e.g., peanut allergy) siamtu `IgE antibodies` te hi a huam lo. Chu ai chuan immune cell dangte chu an inrawlh zawk a ni. Thil pawimawh dang chu FPIES hian allergy na tak dang thenkhatah chuan taksa pum pui inflammation a thlen lo tih hi a ni. Chumi awmzia chu thawk harsatna thlentu `anaphylaxis` na tak, nunna atana hlauhawm tak chu a awm tlem zawk tihna a ni (dehydration nasa tak leh shock hian natna khirh tak dang a thlen thei nachungin).
FPIES vang hian eng harsatna nge thleng thei?
FPIES reaction hian a chang chuan natna khirh tak, nunna atana hlauhawm tak pawh a thlen thei bawk. Chung zinga pawimawh ber chu:
- Shock: Hei hi rang taka thisen sang hniam tak a ni. Hei hi a hlauhawm hle mai.
- Dehydration: Luak leh riltam chhunzawm zel chuan taksa atanga tui leh chi tam tak a bo thin. Hei hi naupang tê têah a thleng thuai thei a, chuvangin fimkhur hle a ngai a ni.
Engtin nge doctor hian FPIES hi a hriat theih ang?
Doctor chuan nangmah emaw i fa emaw chu an natna lan chhuah dan chipchiar taka a zawh hnuah FPIES hi a ringhlel ang . Eng ei tur nge i ei te, eng chen nge a lan chhuah tan tirh te, a natna lan chhuah dan te chu eng nge ni tih te hi a pawimawh hle.
A châng chuan doctor chuan ``food challenge test'' a ti thei bawk.Hei hian naupang chu, damdawi lam enkawlna hnuaiah, ei tur rinhlelh zinga tlemte pek a, a chhanna a awm leh awm loh enfiah a ni. Hei hi in lama tih a tha lo hle a, a nasat chuan damdawi lam pan vat a ngai a ni.
FPIES hi a chang chuan hriat a harsa thei a, a chhan chu a natna lan chhuah dan chu natna dang, bacteria infection ang chi nen a inang thei a ni. Chuvangin, i doctor chuan allergy thisen test emaw, allergy skin test emaw a ti thei a, allergy dang a awm leh awm loh a enfiah thei bawk. Mahse, heng test-te hian FPIES vei hian allergy a nei tih a tilang hauh lo.
FPIES enkawl dan tur chu engte nge ni?
Doctor-te chuan FPIES vanga acute symptoms enkawlna atan a hnuaia mi hi an hmang thei ang:
- Steroids: Hengte hi intestine-a inflammation (swelling) tihziaawmna atana pek a ni.
- Intravenous fluids (IV fluids): Saline ang chi thil hi tui tlakchhamna venna atan emaw, tui tlakchhamna a awm chuan enkawl nan emaw pek thin a ni.
- Antiemetics: Entirnan, damdawi ``Ondansetron (Zofran®)`` ang chi hian luak chhuak a titawp thei.
Heng enkawlna zawng zawng hi damdawi inah pek vek a ni a, damdawi lam enkawlna hnuaiah pek vek a ni.
Kei emaw ka naute emaw hian FPIES kan neih chuan eng nge thleng ang?
Thu lawmawm tak chu naupang tê tam zawk chuan kum 3 emaw kum 4 emaw an tlin meuh chuan FPIES an outgrow tawh a ni. Chumi awmzia chu a hmaa an allergy thin ei tur chu a hnuah an ei thei tihna a ni. Mahse, chu ei tur te chu i rawn luh tir leh hmain doctor nen inbiakna neih a tha ber a, ``food challenge test'' tih pawh a tha ber.
Chumi hma chuan a pawimawh ber chu eng ei tur nge hetiang hi thlentu dik tak hriatchhuah a, chaw pek tawh loh hi a ni. Luak chhuak na tak leh riltam hi a hlauhawm hle thei a, chuvangin chu pawh chu lo thlir reng ang che.
Puitlingten FPIES an vei a nih chuan a enkawl dan tha ber chu an allergy nei ei tur te hriatchhuah a, ei loh hi a ni. A châng chuan, puitlingte chuan hun kal zelah FPIES an outgrow thei bawk. Mahse, thil tam takah chuan puitling atanga intan FPIES hi dam chhung zawng a daih thei a ni.
FPIES hi ven theih a ni em?
Nangmah emaw i fa emaw hian FPIES i nei tih i hriat chuan reaction ven dan tha ber chu an allergy nei ei tur pek loh vek hi a ni.
Food diary vawn hian eng ei tur nge harsatna thlentu tih hriatna kawngah a \angkai hle thei a ni. Hei hian i fain a ei zawng zawng leh engtikah nge a ei tih ziak vek tihna a ni. Tichuan, symptoms a lo awm chuan an tan hmaa an ei kha i en thei ang. A châng chuan, doctor chuan ‘elimination diet’ (ei tur ṭhenkhat enchhin ngai diet) pawh a rawt thei bawk .
I naute hian FPIES a neih chuan, i doctor chuan a hnuaia thilte hi a rawt thei ang, chutih rualin i naute chu a mamawh ei tur a la pe reng a ni:
- Hypoallergenic nausen formula hman dan . Hengte hi allergenic tlem zawka siam a ni.
- I naute tana solid foods i tan dawnin thlai chi (e.g., buhfai, oats) ai chuan thei leh thei chi hrang hrang dah hmasa phawt ang che.
- FPIES ei tur inhriattirna ladder zawm a ni . Hei hian i naute hnena ei tur thar pek dan tur leh a hman dan tur a sawifiah a ni.
FPIES nei mi ka nih angin eng nge ka tih ang?
FPIES i neih chuan – emaw i neih nia rinhlelh i nih chuan – i ei leh in tur uluk taka i chhinchhiah a ngai dawn a ni. Hei hian eng ei tur nge i reaction thlentu tih chiang taka hriat theih nan a pui ang che. A chhan i hriat chian hnuah chuan chutiang ei tur chu i ei loh tur a ni.
Doctor hmuh hun tha ber berte chu engte nge ni?
I naute hian food reaction a nei nia i hriat chuan, formula emaw, bawnghnute emaw pawh nise, doctor pan ngei ngei tur a ni. Reaction tenau tak pawh hian i naute mamawh ei tur a hmuh theihna a tibuai thei a ni. Reaction na tak a awm chuan doctor lam pan nghal tur a ni.
Engtikah nge Emergency Treatment Unit (ETU) ah i kal a ngai ?
Nangmah emaw i fa emaw hian a hnuaia symptoms te hi i neih chuan damdawi in emergency room-ah kal nghal rawh:
- Buaina emaw rilru dinhmun danglam emaw .
- Peeing tlem lutuk emaw, pee lo tak tak emaw.
- Mit sunken – Hei hi tui tlakchhamna chhinchhiahna a ni.
- Hmai, hmui emaw lei emaw a hring chhuak .
- Thâwk lak emaw ei leh in emaw harsatna .
Heng symptoms te hian thil awmdan chu a pawi hle tih a tilang a ni.
Doctor hnena zawhna pawimawh zawh tur
Doctor i tlawh hunah heng zawhnate hi zawh a \angkai hle ang:
- Hei hi ei leh in lama allergy tlanglawn tak a ni em, FPIES nge?
- Eng eitur nge FPIES thlentu tih engtin nge i hriat theih ang?
- Engtin nge heng allergenic foods te hi ka/ka fa mamawh ei tur dik tak ka la hmuh rualin ka pumpelh theih ang?
- Kei/ka fa hian hetiang reaction hi a neih chuan engtin nge ka tih ang?
FPIES chungchang tlem han zir belh ila?
- FPIES lo awm tan kum: FPIES hi naute thla 4 vel atanga tan a ni tlangpui , a nih loh leh allergy avanga ei tur an rawn luh tirh atanga tan a ni. FPIES hi puitlingah a lo awm a nih chuan kum 40 hnuah hmuh tur a awm tlangpui .
- Puitlingah FPIES hi engtiang chiahin nge a awm?: Naupang tête aiin puitlingah FPIES hi a tam lo hle. Puitling 450 zinga pakhat vel (0.22%) chuan FPIES an nei a ni. Puitlingah FPIES thlentu ei tur ber chu shellfish a ni .
- Nausen hnute pe chauhvin FPIES an nei thei em?: Hei hi a tlem hle a, mahse a ni, a theih tho. A châng chuan nu hnute pe lai ei tûra protein awmte chu nu hnute hmangin a naute hnênah a kal thei a, FPIES a thlen thei bawk. Mahse, hemi chungchanga zirchianna hi a la chiang lo hle.
- FPIES hi autoimmune disease a ni em?: Ni lo, FPIES hi `autoimmune disease` a ni lo. FPIES hi ei tur digestive tract chhunga lut tur immune system response a ni.
A pawimawh ber - take-home message
FPIES hi a awm lo hle a, mahse a chang chuan na tak a ni a, chu chuan i fa emaw nangmah emaw tan an mamawh ei leh in tur i hmuh harsat phah thei a ni. A chang chuan natna dang a entawn thei a, chuvangin eng ei tur nge a thlen tih hriat nan test leh experiment engemaw zat a ngai a ni.
Lungngai suh. Doctor chuan eng ei tur nge ei loh tur tih ngaihtuah turin a pui thei che a, hrisel taka awm dan tur leh i mamawh ei tur i hmuh theih dan tur a sawipui thei bawk che a ni. I man hma a, uluk taka i enkawl chuan he natna nen hian i hrisel thei ang. A pawimawh ber chu ngaihtuahawm i neih chuan damdawi lam thurawn lak hi a ni.
` FPIES, ei leh in lama allergy, nausen luak chhuak, nausen luak chhuak, ei leh in protein, enterocolitis syndrome, immune system











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