Naupan lai atang tawh khan thinlung natna i nei tih i hre lo mai thei. Mahse, i upat deuh deuh emaw, i lo upat deuh deuh emaw chuan i chau tan em, thawk i hah a, i rilru a na tan em? Mi tam tak chuan thinlung natna hi kum upat ruala lo thleng thin niin an ngai. Mahse thudik tak chu thinlung natna thenkhat hi rochun a ni. Vawiin hian congenital heart diseases kan sawi dawn a, chu chu puitling atanga hmuhchhuah emaw enkawl emaw a ni.
Puitling pianpui thinlung natna (ACHD) chu eng nge ni?
A awlsam zawngin, hei hi i pian tirh laia i thinlung pianzia emaw, a awm dan emawa chhiatna a ni. “Pianpui” tih thumal hi “pian a\anga” tihna a ni. Heng tlin lohnate hi nausen pum chhunga a la awm laiin a lo awm thin. Heng chhiatna te hian thinlung chhunga thisen kal dan a nghawng thei a ni . Chûngte chu “pianpui thinlung lama harsatna” kan ti bawk.
Heng thinlung natna thenkhat hi a na lo hle. Mi dangte chu an serious hle thei bawk. A chhiatna chi leh a nasat dan azirin mi thenkhat chuan puitling an nih hma chuan symptom engmah an nei lo mai thei. Mi dangte chuan an dam chhungin symptom engmah an nei lo thei bawk. Mi dangte chu naupan laiah enkawl an ni thei a, mahse puitling an nih chuan hun rei tak chhung nghawng an nei thei bawk.
Mahse, lungkham a ngai lo. Tunlai damdawi lam thiamna a lo thang chho zel a, heng natnate hi hriatchhuah leh enkawl dante chu nasa takin a lo tha chho ta a ni. Dik tak chuan naupan lai atanga heng thinlung natna enkawltu zinga 90% aia tam chuan nun hrisel tak an hmang zui zel a ni. Naupang emaw, puitling emawa he natna hi i vei tih hmuhchhuah i nih pawhin, i dinhmun enfiah turin dam chhung zawng damdawi lam thurawn leh test i mamawh ang.
Chu chuan thinlung pêng engte nge a nghawng theih?
Heng pianpui thinlung chhiatna te hian thinlung hmun eng pawh a nghawng thei a ni. A nghawng theihna hmunpui berte chu:
- Thisen kalna kawng : Thinlung chhunga thisen kalna kawngte hian taksa pum puiah thisen a phur a, thinlungah a kir leh thin. Arteries hian oxygen tamna thisen chu thinlung atanga taksaah a phur lut thin. Vein hian thisen deoxygenated chu thinlungah a phur kir leh thin.
- Heart chambers: Lungphun leh thisen kal danHeng chamber te hian an thunun a ni. Upper chamber pahnih (right leh left atria) leh lower chamber pahnih (right leh left ventricles) a awm bawk. Heng chamber te hi wall (septum) hmanga inthen a ni.
- Heart valve : Heng valve pali te hian thisen chu heart kaltlangin kawng khatah chauh a kal tir thin. Kawng dik lova thisen luang chhuak tur titawptu kawngkhar ang an ni.
Congenital heart disease chi hrang hrangte chu engte nge ni?
Puitling zingah hian pianpui thinlung natna chi hrang hrang a awm a. Eng nge an nih i han thlir teh ang.
| Thil tihsual awmzia | Entirna leh sawifiahna awlsam tak |
|---|---|
| Thisen kalna kawng a chhiat | Hmun \henkhatah thisen kalna kawng a zim chuan thinlungin thisen pump turin nasa zawkin hna a thawh a ngai a ni. A châng chuan thisen kalna kawngte chu a inmil lo thei a, chu chuan oxygen tlachham thisen chu taksaah a luang lut thei a, oxygen tamna thisen chu lungah a luang lut thei bawk. Entirnan: Aortic coarctation, Patent ductus arteriosus (PDA), Pulmonary artery stenosis . |
| Heart valve a chhiat avangin | Heart valve te hi a zim thei a, a khar tha lo thei a, a khar vek thei a, a insiam tha lo thei bawk a, chu chuan thinlung tan taksa pum puia thisen pump chhuah a harsat phah thei a ni. Entirnan: Bicuspid aortic valve natna, Ebstein-a thil danglam, Mitral valve prolapse (MVP) . |
| Septal defects (heart chamber inkar bang a chhiatna) 1.1. | Chûngte chu kan hriat vek tawh “thinlung khur” te chu an ni. Hei hi a chunglam chamber pahnih (atria) emaw, a hnuai lam pahnih (atrium) emaw inkar bang chhunga khur a ni. Hei hian oxygen tamna thisen chu oxygen tlakchhamna thisen nen a inhmeh tir thei a ni. Hei hian thisen chhunga oxygen awm zat chu thinlung atanga taksa panna a tihtlem phah a ni. Entirnan: Atrial septal defect (ASD), Patent foramen ovale (PFO), Ventricular septal defect (VSD) . |
Tute nge heng dinhmunte hi vei tam zawk?
Heng dinhmunte hian mipa leh hmeichhia, kum leh chi hrang hrang thliar lovin tu pawh a nghawng thei a ni. Mahse, natna thenkhat chu mipa aiin hmeichhiaah a tam zawk. Entirnan, `Atrial septal defect (ASD)` leh `Mitral valve prolapse (MVP)` ang chi hi hmeichhiaah a tam zawk. `Aortic coarctation` ang chi hi mipaah a tam zawk. Tin, `Down syndrome` emaw `Turner syndrome` ang chi genetic condition nei te pawh hi congenital heart disease vei theihna a sang zawk bawk.
Engvangin nge hetiang hi a lo awm? Risk factors te chu engte nge ni?
Vawi tam tak chu doctor-te pawhin hetiang congenital heart defect hi engvangin nge a awm tih chiang takin an sawi thei lo. Thenkhat chu rochun theih a ni. Chu chu genes hmanga tih a ni.
Tin, naupai laiin nuin a hmachhawn tur dinhmun thenkhat chuan naute tan he hlauhawmna hi a tipung thei bawk.
- Nuin a naupai tirh thla thum chhunga virus infection rubella emaw influenza emaw a vei chuan.
- Nuin zunthlum (Type 1 emaw Type 2 Diabetes) a neih chuan .
- Natna atana hman tur damdawi thenkhat , acne leh epilepsy te hi naupai laiin hman theih a ni.
- Naupai kar 30 hnua ibuprofen ang chi natna tidamtu i ei chuan.
Nang pawhin heng symptoms te hi i nei ve em?
ACHD symptoms hi mi hrang hrangah a inang lo. I kum, i thinlung natna i neih zat, natna nasat dan leh i chhiatna chi hrang hrangah a innghat a ni. Mi thenkhat chuan symptom engmah an nei lo mai thei. Symptoms a awm tak tak a nih chuan:
- Nail, hmui leh vun rawng blue discoloration (Cyanosis): Hei hi taksaa thisen luang chhuak zingah oxygen a awm loh vang a ni.
- Luak chhuak thei.
- Chau awlsam taka inhriatna: Hna tlemte thawh emaw, kea kal emaw hnu pawha tlu mai tur ang maia inhriatna.
- Thinlung mur: Hei hi i hre thei lo. He thawm danglam tak hi doctor-in i rilruah stethoscope a dah hian a hriat chauh a ni.
- Heart palpitations: Thinlung chu nasa tak leh rang takin a thawk tih hriatna a ni.
- Thinlung thawk mumal lo (Arrhythmia).
- Thâwk harsa (Dyspnea).
- Ke ruh, ke, kut zungtang (edema) a lo hring (edema).
A pawimawh ber chu heng symptoms nei zawng zawng hian congenital heart disease an nei vek lo. Mahse heng symptoms te hi i neih chuan Doctor hmu a, sawipui a pawimawh.
Engtin nge hei hi i hmuh theih, Doctor?
Doctor i pan dawnin i symptoms te leh i chhungte zingah lung natna nei an awm leh awm loh a zawt hmasa ang che. Tichuan taksa enfiahna a nei ang a, i thinlung ri chu a ngaithla ang.
Diagnosis confirm nan a hnuaia test pakhat emaw a aia tam emaw tih tir i ni thei ang:
- Chest X-ray: A rilru a buai em em a, a rilru a hah em em bawk a.
- Echocardiogram (echo): Hei hi thinlung scan ang a ni. Thinlung pianzia te, chamber te leh valve te hnathawh dan te chiang takin a hmu thei a ni.
- Electrocardiogram (EKG): Hei hian thinlung electrical activity, chu chu heartbeat rhythm a test a ni.
- Exercise stress test: EKG hi treadmill-a i kal emaw, i tlan laiin emaw tih a ni a, exercise i tih hian i thinlungin a chhan dan en a ni.
- Heart MRI leh Heart CT scan: Scan hmanga thinlung thlalak chiang zawk, three-dimensional image siam chhuah a ni.
- Cardiac catheterization: Hei hi natna hriatchhuah leh enkawlna atan pawh hman a ni. Test, tube (catheter) te tak te tak mai chu thigh chhunga thisen kalna kawng atanga thinlung lam pan a ni.
Hei hi eng enkawlna nge ni?
Congenital heart defects tenau tak tak thenkhat chu enkawlna engmah a ngai lo. Mahse, chutiang titu tan pawh cardiologist hnenah checkup neih fo a ngai dawn a, chu chu an dinhmun a na zual em tih enfiah a ngai dawn a ni.
Mi dangte chuan enkawl an ngai a ni. I natna chi leh a nasat dan hian i enkawl dan tur a hril ang.
Damdawi chi hrang hrang
I doctor chuan thinlung hnathawh that nan leh symptoms control nan damdawi chi hrang hrang a pe thei ang. Entirnan, thisen sang control thei, heart rate control thei, taksa atanga tui tam lutuk paih chhuak thei damdawi (diuretics) an pe thei bawk.
Heart Devices dah theih a ni
- Pacemaker: He device hi vun hnuaiah dahin heart rate control a ni a, a bik takin heart rate a slow a nih chuan.
- ICD (Implantable Cardioverter Defibrillator): Nunna atana hlauhawm heartbeat mumal lo hriat theihna tur leh electric shock pe chhuaktu, chu chu siamthat theihna tur hmanrua a ni.
Cardiac Catheterization hman dan tur
Hei hi surgery aiin procedure awlsam zawk a ni. Sawi tawh ang khan thinlung chhungah hian tube te tak te dahin thinlung chhunga khur (ASD ang chi) te khar nan an hmang thin. Thisen kalna kawng emaw, valve emaw zim deuhte tihzauh nan pawh hman a ni.
Inzai
Defect thenkhat chu siamthat nan operation a ngai thin. Heart valve siamthat emaw thlak emaw theih a ni a, a nih loh leh a chhiatna complex zawkte chu open-heart surgery emaw minimally invasive surgery emaw hmangin siamthat theih a ni bawk.
Lungphun thlak a ni
Hei hi tih a tlem hle. Lung natna khirh ber, nunna atana hlauhawm ber, damdawi dang hmanga tihdam theih loh nei tan chuan heart transplant hi a tawp ber a ni.
Engtin nge i in enkawl ang?
ACHD nena i khawsak hian i hriselna pawh i enkawl a ngai a ni.
- Nun hrisel tak hmang rawh: Ei leh in inthlau tak ei la, doctor rawn la, i tana tha tur exercise ti la, meizuk leh zu in loh vek rawh.
- I doctor zawng zawng hnenah hrilh rawh: Ha enkawltu emaw, doctor dang emaw hmu turin i kal emaw, ACHD i vei tih hrilh ngei ang che.
- Cardiologist hmu fo ang che: Symptoms nei lo mah la, doctor-in a tih angin check-up la.
- I ha enkawl dan: I ha te chu vawn fai rawh. I hmuiah natna hrik a awm chuan natna hrik te hian i thisen kal tlangin i thinlung (endocarditis) a nghawng thei a ni.
- Naupai hmain damdawi lam thurawn la rawh: Hmeichhia fa beisei i nih chuan i cardiologist nen sawiho la, nau pai i tum hmain thurawn la hmasa phawt a pawimawh.
Engtikah nge doctor pan nghal i mamawh?
A hnuaia symptoms te hi i neih chuan heart failure chhinchhiahna a ni thei a nih chuan, damdawi in hnai ber Emergency Department (ETU)-ah kal nghal vat rawh .
- Thâwk harsa na tak.
- Pum emaw ke hnuai lam emaw a hring.
- A chhan hriat loha chau lutuk, danglam tak.
Tin, symptom thar i neih emaw, i symptom awmsa chu a zual zel nia i hriat emaw chuan doctor pan nghal rawh.
Take-Home Thuchah a ni
- Adult-onset congenital heart disease (ACHD) hi i thinlunga structural defect, pian tirh atanga awm thin a ni.
- Mi thenkhat chuan puitling an nih hma chuan symptom engmah an nei lo mai thei.
- Thâwk harsa, general fatigue, rilru tightness, leh vun dum (bluish skin) te hi a lan chhuah dan tlangpui a ni.
- Tunlai damdawi hmanlai (damdawi, surgery, catheter hman dan) avang hian mi tam tak chu nun pangngai, active takin an nung thei a ni.
- Hetiang natna hi i neih chuan, symptoms nei lo mah la, i dam chhung zawng cardiologist enkawlna hnuaia awm reng a pawimawh hle.
Congenital heart disease, heart disease, ACHD, Adult Congenital Heart Disease sinhala, thinlunga khur, thawk harsa, rilru na, thinlung surgery, thinlung natna lan chhuah dan











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