Hemangioblastoma hi eng nge ni? Kan sawi dawn nia!

`Hemangioblastoma` tih thumal hi i hre tawh em? A buaithlak deuhin a lang thei a, mahse kan taksaah, a bik takin thluak, ruhro, mit chhunga lo awm thei tumor te tak te chi khat a ni. Ngaihtuah buai suh, awlsam takin kan sawi dawn a, i hriatthiam theih dan tur angin.

Hei hi cancer a ni em?

Mi tam tak chuan 'tumor' tih thumal an hriat hian an hlau nghal a, "Aw, hei hi cancer a ni em tih ka hre lo," tiin an ngaihtuah nghal vek a ni. Ka lawm hle mai, he `Hemangioblastoma` hi cancer a ni lo. Medical lamah chuan hengte hi benign emaw "non-malignant" emaw tumor an ni. Chumi awmzia chu cancer angin taksa peng dangah an darh lo tihna a ni.

Mahse, hengte hi cancer vei lo mah se, harsatna tenau engemaw zat a thlen thei a ni. Pakhat chu a chang chuan heng tumor zinga pakhat aia tam taksaah hian a awm thei tih hi a ni. A chhan dang chu he tumor hi a lo lian zauh zauh a, a chhehvela tissue leh nerve pawimawh tak takte chu a press tan thin a ni. Chutah chuan symptom chi hrang hrang a lo lang tan ta a ni. Pindan tenau takah thil lian tak awm a, a bak zawng atan hmun a awm lo ang mai a ni.

Hetiang hi tuin nge nei tam zawk?

Tunah chuan, "Tunge hetiang hi nei thei zawk?" Dik tak chuan `Hemangioblastoma` tih hi tu pawhah, kum eng pawhah a lo awm thei a ni. Mahse, doctor-te hmuh dan chuan he natna hi puitling ṭhalai zingah a tam zawk a ni .

Hei bakah hian special case dang a awm bawk. Chu chu genetic disease `Von Hippel-Lindau (VHL) disease` an tih chu a ni. Hei hi thil awm lo tak, thlahtute atanga lo chhuak a ni. `(VHL)` natna vei te hian midang aiin `Hemangioblastoma` tumor an nei tam zawk hle. Ngaihtuah teh, statistics atanga a lan dan chuan `(VHL)` natna vei zinga 60% vel chuan mit chhungah heng tumor te hi an nei thei a ni. Tin, 80% vel chuan thluak emaw, ruhro emaw-ah heng tumor te hi lo awm theihna an nei niin an sawi bawk. Chuvangin, `(VHL)` natna leh `Hemangioblastoma` hi inzawmna lian tak a awm a ni.

Hemangioblastoma hian engtin nge taksa a nghawng?

Tunah chuan he tumor hian kan taksa a nghawng dan hi i lo en ang u. A nghawng dan hi tumor awmna hmun leh a lian leh te a zirin a innghat ber a ni.

A bik takin he tumor hi thluak emaw ruhroah emaw a lo awm chuan kan thluak leh ruhro atana pawimawh `Cerebrospinal fluid (CSF)` luang chhuak chu a tikhawlo thei a ni. He `(CSF)` hi, a awlsam zawngin, tui thianghlim, tui ang chi, kan thluak leh ruhro vel hualtu, cushioning leh nourishment pe thin a ni. He `(CSF)` flow hi tumor in a tikhawlo a nih chuan thluak chhunga pressure a sang thei a, lu na na tak ang chi symptoms a thlen thei a ni. Tin, tumor awmna hmun azirin chu hmuna nerve te chu a compress a, chu chuan nerve te chu a thawk thei bawk.

Hei hi engtiang chiahin nge a hluar?

Dik tak chuan `Hemangioblastoma` hi tumor chi khat a ni lo. Thluaka tumor lo awm zawng zawng kan lak chuan `Hemangioblastoma` hian 0.5% a luah a, chu chu percentage hniam tak a ni a, za hnih zinga pakhat vel a ni. Spinal cord-a tumor chi hrang hrang lo awmte kan lak chuan 2% vel a ni. America ang ram statistics kan en chuan puitling 100,000 zinga 24 velin thluak emaw nervous system-ah emaw tumor chi khat emaw an nei niin an sawi. Chuvangin `Hemangioblastoma` hi an zinga za zela tlemte chauh a ni. Chuvang chuan hei hi mi zawng zawng tibuaitu natna a ni lo.

Eng nge a lan chhuah dan?

He `Hemangioblastoma` tumor hi a lo chhuahna hmun azirin a symptoms hi a danglam deuh thei. Chu chu engtin nge a thawh tih i en ang u.

Spinal cord hemangioblastoma i neih chuan:

He tumor hi i ruhro, i ruh chhunga nerve cord-ah a lo awm a nih chuan heng ang symptoms hi i nei thei ang:

• Constipation emaw fecal incontinence emaw a awm thei.
• Zun harsatna (urinary retention) emaw, zun control theih lohna (urinary incontinence) emaw.
• Taksa peng emaw, taksa peng hrang hrang emawa rilru hahna emaw, rilru hahna emaw hriatna.
• Muscle weakness , a chang chuan kal a harsat phah thin.

Thluaka Hemangioblastoma i neih chuan:

Hetiang tumor hi thluak chhungah a lo awm chuan thluak tumor anga ngaih a ni. Tichuan, hetiang symptoms te hi i hmu thei ang:

• Balance problems, zu rui ang maiin a awm thei.
• Lu na fo thin , a chang chuan zing lamah a na zual thin.
• Nausea or vomiting , a bik takin zing lamah.

Retina-a hemangioblastoma i neih chuan:

Kan hmuh thlalakte record tu mit hnung lama tissue layer retina-ah tumor a lo awm a nih chuan mit tumor anga ngaih a ni. Thil thleng thei thenkhat chu hetiang hi a ni:

• Retinal detachment , chu chuan mitdelna a thlen thei.
• Zawi zawiin emaw mit a hloh vek emaw .
• Mit na leh a hring .

A chhan engte nge ni?

A tam zawkah chuan `Hemangioblastoma` lo awm chhan chiang tak, chiang tak hmuh a harsa thin. Chu chu chhan bik (sporadic) nei lovin an lo awm thei tihna a ni. Mahse, a hmaa kan sawi tawh ang khan damlo pali zinga pakhat velin he natna hrik hi thlentu `Von Hippel-Lindau (VHL)` tih hming pu genetic condition an nei tih hmuhchhuah a ni. Chu chu `(VHL)` vei te hian he tumor hi an vei theihna chance a sang zawk tihna a ni.

Engtin nge hei hi i hriat chian? (Diagnosis) tih a ni.

A chunga kan sawi tak symptoms pakhat emaw a aia tam emaw i neih chuan doctor i hmuh hunah i symptoms chungchang a zawt hmasa ang che. I damdawi lam dinhmun dangte leh i chhungte zingah hetiang dinhmun (family history) nei tawh leh awm loh a zawt bawk ang. Tichuan, test eng emaw zat tih a ni thei a, chu chuan a natna chu a finfiah thei a, tumor awmna hmun leh a lian zawng hriat theih a ni bawk.

• CT scan (Computed Tomography scan): Hei hian X-ray hrang hrang leh computer bik hmangin taksa chhunga tissue hrang hrangte cross-sectional image a la thin.
• MRI (Magnetic Resonance Imaging): Hei hian magnetic field chak tak leh radio wave hmangin taksa chhunga taksa peng leh tissue nem tak takte thlalak chiang tak, chipchiar tak tak a siam chhuak thin. Hei hi hemangioblastoma ang chi natna hriat theihna atana test pawimawh tak a ni.
• Angiography: Hei hi thisen kalnaah dye bik inject a, thisen kalna kawnga hemangioblastoma ang chi tumor te chu X-ray emaw MRI/CT scan emaw hmanga hmuh theih zawka siam a ni. Heng tumor te hi thisen kalna kawngah (vascular tumors) a lo thang lian avangin he test hian an thisen supply dan tur pawh a hriat chian theih bawk.

Eng nge a enkawl dan?

Okay, tunah chuan `Hemangioblastoma` enkawlna tur eng nge awm tih kan en ang u.A enkawl dan tur hi thil tam takin a hril a, chu chu tumor lian tham tak, a awmna hmun leh i hriselna zawng zawng te hi a ni.

• Surgical resection: Hei hi doctor-te’n an rawt ber a ni. Hetah hian doctor emaw nurse emaw chuan vunah incision a siam a, surgical instrument hmangin tumor chu a paih chhuak thin. Hetah hian thil tum ber chu a chhehvela tissue hrisel, a bik takin nerve te tihchhiat tlem nan tumor a tam thei ang ber paih chhuah a ni.
• Radiation therapy: A chang chuan, surgery hmanga tumor chu a chhuak kim thei lo a nih chuan, a nih loh leh tumor chu a lo let leh tawh a nih chuan radiation therapy hman a ni. Hei hian tumor cells tihchhiat emaw, tumor tihtlem emaw nan targeted tak tak, radiation beam chak tak tak hman a huam a ni. Hei hi hmanraw bik a awm a, chu chu stereotactic radiosurgery an ti a ni. Radiation therapy pek hun chhung leh pek zat hi tumor awmna hmun leh i medical history kal tawh ang chi thil hrang hrangah a innghat a ni.
• Enfiahna: A châng chuan, tumor hi a te lutuk a, a lan chhuahna a awm lo a nih chuan, emaw, tumor awmna hmunin operation hmanga lak chhuah a hlauhawm lutuk a nih chuan, doctor-te chuan tunah chuan engmah ti lo turin an rawt mai thei a, mahse MRI scan leh follow-up visit neih reng chungin en reng ang che. Hei hi tumor a lian chho zel em tih leh symptom thar i neih leh neih loh en nan a ni. Tumor tam tak i neih a, a lo thang lian zel a, a lo thang zauh zauh a nih chuan he approach hi i ngaihtuah mai thei.
• Ruihhlo hmanga enkawl dan:Tunah hian heng tumor te hi a lo thang lian zel tur titawp thei emaw, a tihtlem thei emaw damdawi chungchangah zirchianna kalpui mek a ni. A bik takin `(VHL)` natna vei tan chuan damdawi pakhat `(Belzutifan)` tih chu tunah hian `(VHL)` nena inzawm tumor-ah hlawhtlinna a lantir mek a, `Hemangioblastoma` pawh a tel. Amaherawhchu, hengte hi enkawl dan thar a la ni a, mi zawng zawng tan a tha lo a, doctor thurawn chauha ei tur a ni.

A dam kim thei ang em?

Hei hi mi tam tak tan chuan zawhna pawimawh tak a ni. `Hemangioblastoma` vei zawng zawng hi an danglam vek a, chuvangin mi zawng zawng tan chhanna pakhat pek a harsa hle.

Ngaihtuah teh, mi pakhatin `Hemangioblastoma` tumor pakhat chauh a neih a, chu chu operation hmanga a pum pui leh him taka lakchhuah theih a nih chuan, chu hmun khatah chuan a lo thang leh theihna chance a hniam hle. Chumi awmzia chu dam leh theihna chance a sang hle tihna a ni.

Mahse mi thenkhat chuan tumor pakhat aia tam an nei thei (a bik takin VHL nei te). A nih loh leh, tumor hi thluak thuk takah emaw, hmun sensitive tak, lakchhuah harsa takah emaw a awm thei bawk. Chutiang hunah chuan damna famkim chungchang sawi chu a buaithlak deuh. Chuvangin, i dinhmun a zirin i medical team te nen i beisei tur chungchang sawipui a pawimawh hle.

Risk factor dang a awm em?

Ni e, vawi tam tak kan sawi tawh ang khan, genetic condition `Von Hippel-Lindau (VHL)` natna i neih chuan `Hemangioblastoma` vei theihna chance a sang hle. Chuvangin, doctor-in `Hemangioblastoma` a hmuhchhuah chuan, a bik takin i naupang emaw, tumor tam tak i neih chuan `(VHL)` natna an test thei bawk.

Dam lehna tur prognosis chu eng nge ni?

Hemangioblastoma prognosis hi a tlangpuiin a tha a, a bik takin medical team ten tumor hi an paih chhuak vek thei a nih chuan. Tin, tumor hian hun rei tak chhunga symptoms, permanent nerve damage ang chi a thlen loh chuan a dam leh theihna chance a sang hle bawk.

Tumor chu lakchhuah a nih hnuah pawh i doctor pan a ngai dawn a, regular check-up neih a ngai dawn a ni . Heng check-up-ah hian MRI scan ang chi thil te pawh a tel thei. Chutianga tih chuan a lo lang leh thei (a bik takin VHL vei te tan) a hmain hriatchhuah leh enkawl theih a ni ang. Chuvangin, i doctor thupek dik taka zawm leh a hun taka clinic-a kal hi i damna atan a pawimawh hle.

Doctor hnenah eng zawhna nge i zawh tur?

Hemangioblastoma i vei a nih chuan, emaw, i vei mai thei nia i ngaih chuan, i doctor hnenah hetiang zawhna hi zawh a tha ang:

• "Ka symptoms awm chhan ber chu eng nge ni?"
• " `Hemangioblastoma` ka neih chhan (entir nan, VHL natna) underlying medical condition dang (entir nan, VHL natna) ka neih theihna chance chu eng nge ni?".. tiin a sawi.
• "Ka `Hemangioblastoma` enkawl dan tur chu engte nge ni? Enkawlna tin hian eng nge a thatna leh a that lohna?"
• "Hetiang enkawlna te hnuah hian eng side effect nge ka beisei theih ang?"
• "Tumor lakchhuah hnuah `Hemangioblastoma` a lo awm leh theihna chance chu engzat nge ni?"
• "Engzat nge check-up turin ka lo kal ang?"

Heng zawhnate hi zawh hian i dinhmun hriatthiamna chiang tak i neih theih nan a \angkai hle ang. I rilrua thil awm zawng zawng, eng ang pawhin tenau pawh ni se, i doctor hnenah sawipui hlau suh. Chumi hnuah chauh chuan enkawlna tha ber i hmu thei ang.

Thuhmahruai angin hre reng ang che (Take-Home Message) .

Okay, chuvangin kan sawi tawh kha han khaikhawm ila.

Hemangioblastoma hi cancer ni lo (benign) tumor a ni a, thisen kalna atanga lo chhuak a ni. I thluak, i ruhro, a nih loh leh i mit (retina) -ah an awm tam ber .

He tumor hi a lo lian chhoh zel chuan a chhehvel tissue te chu a nawr thei a, neurological symptoms a thlen thei bawk.

A tam zawkah chuan doctor-te chuan operation hmangin tumor chu an la chhuak ang. Tumor chu lakchhuah vek a nih chuan a lo let leh theihna chance a tlem . Mahse, `Von Hippel-Lindau (VHL)` ang chi genetic condition nei te chu heng tumor te hi an vei theihna a sang zawk a, tumor tam tak pawh a awm thei a, an lo kir leh duh zawk bawk.

Chuvangin, he thuziak-a kan sawi tak symptoms te hi i neih chuan, a bik takin a awm reng emaw, a na zual emaw a nih chuan, a rang thei ang bera doctor pan a, thurawn lak a tha ber. Diagnosis a hma poh leh enkawlna a hlawhtlin theihna a sang zawk tih hre reng ang che. Ngaihtuah buai suh, damdawi lam enkawlna leh kaihhruaina dik tak nen chuan heng dinhmunte hi enkawl theih a ni a, hlawhtling taka nunpui theih a ni bawk.

` hemangioblastoma, thluaka natna hrik, ruhro natna, mit natna, Von Hippel-Lindau, benign tumor, thisen kalna kawng natna