I fa hian a vunah hian a dum, a rawng danglam tak tak a nei em? (Juvenile Localized Scleroderma) tih hi a awm lo.

I fa taksaah, an ke emaw, an pum emaw-ah pawh ni thei, rawng a inthlak nghal a, khawih pawh a harsa deuh tih i hmu ngai em? Nu leh pa i nih angin i hmuh chuan hlauhna leh lungkhamna tlem i nei a ni mai thei. "Hei hi eng nge ni? Engvangin nge hetiang thil hi a lo awm?" I ngaihtuah tawh mai thei. Hlau suh. A tam zawkah chuan he natna hi tunlaia kan sawi tak natna, `Juvenile Localized Scleroderma` vang a ni thei. A hming hi a buaithlak deuh nachungin, a awlsam zawngin, i hriatthiam theih dan tur angin sawi ila.

A awlsam zawngin, Juvenile Localized Scleroderma chu eng nge ni?

A hming atang hian tan ila. `Scleroderma` tih thumal hi Greek tawng pahnih atanga siam a ni a: "sclera" tih awmzia chu 'hard' tihna a ni a, "derma" tih awmzia chu 'vun' tihna a ni. A awmzia chu "vun khauh" tihna mai a ni. "Juvenile" tih hi naupang leh tleirawlah a awm vang a ni. "Localized" tih hi taksa hmun bik, vun, vun hnuaia tissue, leh a chang chuan ruh leh ruh te chauh a nih vang a ni. Chumi hming dang chu `Morphea` a ni.

Hei hi autoimmune condition a ni a . A awlsam zawngin kan taksa invenna system, immune system chu a â deuh a, a vun hrisel tak chu a rawn bei tan ta a ni. He beihna chhanletna atan hian naupang vun chu a hring tan a, a nih loh leh a hring tan a ni.

Hetianga a hring hian vun chhunga connective tissue cells te hian protein `collagen` an tih chu a siam tam lutuk thin. `Collagen` hi taksa chhunga tissue tam tak, kan vun telin chakna leh nghetna pe thei thil a ni. Mahse a pung lutuk chuan, hliam hnua hliam ang maiin, vun chu a thim a, a khauh ta hle mai. Hei hi `fibrosis` kan ti bawk. Hei hi i fa taksaah hian hetiang hmun khauh tak, rawng danglam tak angin i hmu thei a ni.

Hetiang dinhmun hi eng chi hrang hrang nge ni ber?

Localized Scleroderma hi chi hrang hrang lian tak tak a awm a. Type tin hian symptoms a inang lo deuh vek a. Eng nge an nih i han thlir teh ang.

A chi bik: "En coup de sabre".

Hei hi `Linear Morphea` tih subtype a ni. Naupangin a hmai emaw lu vunah emaw heng streak ang chi hi a neih chuan chu natna chu "en coup de sabre" kan ti thin. Hei hi French tawng a ni a, a awmzia chu "khadaih hmanga tihhlum ang mai" tihna a ni. A chhan chu a hmai hnuai lam line rawng danglam, a chang chuan sunken line ang mai a nih vang a ni.

Naupangin eng symptoms nge a lantir?

Heng symptoms te hi hun kal zelah a danglam thei a ni. Hmun te tak te, hliam ang maia lang atanga tan an ni thei.

• Early stage: Naupang vunah hian red emaw purple emaw patch emaw plaque emaw a lo lang thin. Hetiang dinhmunah hian vun a khauh lo va, a pangngai angin a lang.
• Middle stage: Hun a kal zel a, a hmun chu a khauh a, a hring a, a lian deuh bawk. A hmun lairil chu a var emaw, a sen emaw a lo ni a, waxy angin a lo lang a, a eng chhuak bawk. A chhehvelah hian pink emaw purple emaw halo a awm thei.
• Nakinah: Hun a kal zel a, inflammation a reh hnuah vun natna chu a sen (hyperpigmented) emaw, a var (hypopigmented) emaw a ni thei. A chang chuan vun pawh a hring thei bawk.

A nasat chuan heng spot te hian tissue thuk zawk a nghawng thei a, symptoms a awm thei a, chungte chu:

• Natna leh hrehawmna.
• Ke leh ruh leh taksa peng tha taka che thei lo.
• Hmaiah a lo awm a nih chuan ha emaw mit lamah emaw harsatna a thlen thei a ni.

Engvangin nge naupangte hian hetiang hi an lo neih?

Dik tak chuan hei hi a chhan dik tak chu hmuhchhuah a la ni lo , mahse doctor-te chuan thil hrang hrang inzawmkhawm vang a ni thei niin an ngai.

A pawimawh ber chu kan sawi tawh ang khan immune system activation hi a ni . Chu bakah, environment factor thenkhat, entirnan, infection, vunah trauma, etc. te hi he natna thlentu nia rinhlelh a ni. Mahse hei hi natna hrik kai theih a ni lo.

Engtin nge doctor hian hei hi a hriat chian?

Doctor hnena i fa i hruai dawnin a tih hmasak ber tur chu naupang chu uluk taka enfiah a, a symptoms te zawt che a ni. Hei hi `Localized Scleroderma` a ni em tih chu vunah a hnah awm dan enin i chhut thei fo.

Diagnosis confirm tur chuan hetiang test hi i tih a ngai mai thei bawk:

• Skin Biopsy: Hei hi vun natna hmun te tak te tak te lak a, microscope hmanga enfiah a ni. Hei hian vun cell-ah eng inthlak danglamna nge thleng tih chiang takin kan hmu thei a ni.
• MRI scan (Magnetic Resonance Imaging): Hei hian vun natna chu eng chen nge a thuk tih leh a hnuaia taksa ruh emaw ruh emaw a nghawng em tih a hriat theih.

Hei hi eng enkawlna nge ni?

Enkawlna tum ber chu vunah a hring (inflammation) control a, natna darh zel tur tihtawp a, vunah hliam (fibrosis) tihziaawm te hi a ni. Enkawlna chu naupang natna chi leh a nasat danah a innghat a ni.

Enkawlna kawng hrang hrang a awm a:

• Corticosteroids: Hengte hi topical cream, oral tablet emaw, intravenous injection emaw angin pek theih a ni.
• Vun tana cream chi dang: Damdawi `Calcipotriene`, `tacrolimus`, `pimecrolimus` te awmna cream.
• Immunomodulating agents: Natna a nasat zawk chuan immune system overactivity control nan damdawi `Methotrexate` emaw `Mycophenolate Mofetil` emaw pek thin a ni.
• Physical therapy leh massage: Hengte hi taksa ruh tichak tur leh ruh inzawmna tha tak neih nan a pawimawh hle a, a bik takin `Linear Morphea` ang dinhmunah chuan.
• Light therapy (Thlalak hmanga enkawlna):He enkawlna hian ultraviolet rays hmangin vunah hmun dum awmte chu a ti nem a ni. Amaherawhchu, hei hian vun a tar emaw, vun cancer emaw a thlen thei a, chuvangin he thu hi doctor in uluk takin a hrilhfiah ang.
• Plastic surgery: Natna hi a thawk lo vek tawh chuan vun hmel siam that leh nan surgery tih theih a ni.

Nu leh pa angin engtin nge i fate i ṭanpui theih?

Damdawi inenkawlna bakah hian naute vun venhimna atan in lama tih theih eng emaw zat a awm bawk.

• Sahbawn na tak leh detergent hman loh tur: Thil rimtui rit tak tak awmna product hian i naute vun a ti vawt lehzual thei a, a ti na zual thei bawk.
• Skin-friendly moisturizer hmang rawh: Vun sensitive tana tha tur moisturizer tha tak ni khatah vawi eng emaw zat hnawih thin ang che.
• Tui lum takah inbual: Tui lum lutuk emaw, tui vawt lutuk emaw ei loh tur.
• Ni laka invenna: Pawn lama i chhuah dawnin sunscreen tha tak i hnawih ngei ngei tur a ni.
• I in chhungah humidity vawng reng rawh: Thli a vawt chuan humidifier hman hian vun a vawt loh nan a pui thei a ni.

He dinhmun hian engtin nge naupang nun a nghawng?

Hei hian a ti hlauhawm thei che a nih pawhin, thudik tak chu Juvenile Localized Scleroderma vei naupangte hian nun pangngai tak an hmang thei a ni .

Naupang tan sikul kal te, thiante nena inkhelh te, infiamna te, a tih dan pangngai anga chhungkaw thiltih hrang hranga tel te tan daltu a awm lo. Dik tak chuan exercise hi thil tha tak a ni a, a chhan chu taksa ruh a tichak a ni. Chaw leh in tur bik a ngai lo va, ei leh in tha leh inthlau tak pek chauh hi a tawk.

A châng chuan, vunah hliamte hian naupang chu khawtlângah tlem a ti nuam lo a, a ti mualpho thei bawk. Chutiang hunah chuan nu leh pa i nihna anga i tih tur chu naupang chu hmangaihna nena inbiakna neihpui a, hei hi a sualna a ni lo tih hrethiam tir a, mahni inrintawkna siam hi a ni.