Doctor-in i fate taksa chu a sen a ni tih a hrilh che a, a chhan chu liver-a bile ducts a block vang a ni tih a hrilh che khan i hlau hle a ni ngei ang, chu chu Biliary Atresia an ti a ni. Tunah chuan doctor hian ‘Kasai’ tih surgery chungchang a sawi a ni mai thei. He surgery hi eng nge ni tak tak? Naute tan a tha ang em? I lu-ah zawhna tam tak i nei ngei ang. Lungngai suh. A awlsam zawngin, i hriatthiam theih dan tur angin sawi ila.
Kasai Procedure chu eng nge ni?
A awlsam zawngin, hei hi Biliary Atresia tih natna enkawlna atana surgery bik tih a ni. Kan thin (liver) hian tui ‘bile’ an tih chu a siam chhuak thin. He bile hi taksain kan ei leh in a thau leh vitamin thenkhatte a digest a, a hip lut thei a ni. Biliary Atresia vei nauteah chuan liver atanga intestines thlenga bile phurtu fine tubes (bile ducts) te chu a pian tirh atangin a block emaw, a lo insiam lo emaw a ni.
Chuvangin he Kasai procedure-ah hian surgeon chuan heng bile ducts blocked, dysfunctional te hi a paih chhuak thin. Tichuan, naute chhungril te tak te atanga a then chu an la a, chu chu liver nen direct in an thlunzawm a, bile kalna tur kawng thar an siam a ni. Tui luang chhuak thei lo pipe block chu lakchhuah a, a thar dah ang mai a ni.
Engvangin nge naute hian he surgery hi a mamawh?
Ngaihtuah teh, liver atanga bile lo chhuak hian chhuahna tur kawng a neih loh chuan eng nge thleng? Chu bile zawng zawng chu liver chhungah a khawlkhawm vek a ni. He bile accumulated hian zawi zawiin liver cells a tichhia tan thin. Hun a kal zel a, thin chu a hliam a, a khauh a, a thawk thei lo. Hei hi cirrhosis kan ti a ni .
Enkawl loh chuan biliary atresia hi thla engemaw zat chhungin liver failure vek a ni thei. Hei hi nunna atana hlauhawm tak a ni.
He Kasai surgery hian liver chhiatna chu a titawp emaw, a ti hniam emaw a ni. Hei hian naute nunna chhanchhuahna chance ropui tak a pe a ni.
Operation hma leh operation neih chhung hian eng nge thleng?
Zai a nih hma hian doctor-te chuan naute chu tui a tlakchham theih nan IV fluid an pe ang a, natna kai theihna tur tihziaawmna turin antibiotics an pe bawk ang.
Surgery tan hmain surgeon chuan naute hian Biliary Atresia a vei tih 100% a hriat chian a ngai a ni. Hei hian ‘Cholangiogram’ tih test tih a huam a ni. Hemiah hian naute pum chhungah incision te tak te an siam a, gallbladder chhungah tube te tak te an thun a, X-ray atanga hmuh theih damdawi bik an inject a ni. Hei hian doctor chuan bile duct a block leh block loh chiang takin a hmu thei a ni.
Biliary atresia a awm tih finfiah a nih chuan doctor chuan operation a kalpui ang. Naute gallbladder leh bile ducts blocked te chu lakchhuah a ni ang a, small intestine (jejunum) section hmangin liver nena inzawmna thar siam a ni ang. He surgery hian darkar engemaw zat a daih thei.
Surgery hnuah eng nge thleng?
Surgery zawhah naute chu intensive care unit (ICU)-ah ni 5 atanga ni 10 vel dah a ni a, uluk taka enkawl a ni.
- Nutrition: Ni hmasa berah ei tur engmah pek a ni lo va, hliam a dam theih nan. Nutrition mamawh chu saline hmanga pek a ni. Chumi hnuah chuan bawnghnute chu nasogastric tube hmangin an tan tir leh thin. Zawi zawiin oral feeding hi an practice ta a ni.
- Enfiahna: Doctor leh nurse te chuan naute chu uluk takin an en a, thisen a chhuak em tih emaw, bile a chhuak em tih emaw an en a. Naute ek chu a sen emaw, green emaw a lo ni ang a, hei hian bile a luang tan tawh tih a tilang ang.
- In lama haw: Hliam a dam tan a, thin hnathawh a tha a, naute chu a hnute a pe tha thei a nih chuan in lama haw phalsak i ni ang.
Kasai operation hi engtiang chiahin nge a hlawhtlin?
Hei hi zawhna pawimawh tak a ni. Surgery hlawhtlinna chu thil engemaw zatah a innghat a ni:
- Hun: He surgery hi naute chu kar 6 leh thla 2 inkar a nih chuan a hlawhtling zawk a ni . Chuvangin, natna lan chhuah dan i hriat veleh Doctor pan vat a pawimawh hle.
- Liver condition: Operation lai hian liver chhiatna a tlem ber a nih chuan a result a tha hle.
- Medical team: Tin, surgery thiam tak leh medical team, heng surgery hrang hranga tawnhriat nei te’n an tih a pawimawh hle bawk.
Condition tha ber hnuaiah chuan he surgery hian naute 60% aia tam zingah jaundice telin symptoms a tihziaawm thei a ni. Doctor-te chuan zai a nih atanga thla 6 chhunga naute hian jaundice a nei leh lo a nih chuan surgery hi hlawhtlingah an ngai a ni.
Surgery chu hlawhtling lo ta se engtin nge ni ang?
A chang chuan Kasai operation hnuah pawh bile ducts te hi a chhuak tha lo thei. Chutiang a nih chuan naute chu liver transplant a ngai dawn a ni . Hei hian hlauthawng suh. Dik tak chuan Kasai operation nei naute zinga a chanve vel chuan kum 2 an tlin hunah chuan liver transplant an mamawh dawn a ni. Kasai operation hi liver transplant a ngai hma chu hun lei nan bridge a ni.
I naute i rawn hruai haw hnuah engtin nge i enkawl?
Naute a dam kim theih nan thla 3-4 vel a ngai thei. In lama naute i enkawl dawnin heng thilte hi i fimkhur hle a ngai a ni.
- Damdawi hi dik takin pe rawh:I damdawi ei tur chu i doctor-in a tih ang chiah chiah, a hun takah ei thin ang che. Infection laka inven nan oral antibiotics hi thla engemaw zat pek a ngai mai thei. Bile flow tihchangtlunna tur damdawi hi kum tam tak chhung pek a ngai mai thei.
- Hliam enkawl rawh: I doctor emaw nurse emaw hnenah hliam tihfai dan tur leh eng bandage nge hman tur tih chiang takin zawt rawh.
- Clinic tlawh loh tur: Operation hnu ni ruat saah clinic-ah kal ngei ngei tur a ni. Naute dam leh dan tur hi doctor hnenah hriattir reng a pawimawh hle.
- Nau hnute pek hi a pawimawh hle: A theih chuan naute hnute pe rawh. Nu hnute tui chhunga thau awmte hi awlsam takin thin (liver) hian a hip lut thei a ni. Nau hnute pek theih loh chuan doctor-in a rawt angin special formula hmang ang che.
- Thianghlim rawh: Naute i khawih hmain i kut chu uluk takin silfai fo ang che. Chhungkaw zingah tu emaw khawsik emaw khawsik emaw an neih chuan i naute nena inhnaih loh tur.
| Risk symptoms awm thei chu doctor hnenah hriattir nghal tur a ni | |
|---|---|
| Vaukhânna chhinchhiahna | Hrilhfiahna |
| Khawsik | Khawsik 38 Celsius (100.4 Fahrenheit) aia sang a ni. Hei hi infection chhinchhiahna a ni thei. |
| Chaw ei duh lohna | Naute chuan hnute a in duh lo vek a nih chuan. |
| Hliam a inthlak danglam thin | Surgery hliam chu a hring a, a sen a, a nih loh leh fluid/pus a chhuak bawk. |
| Pum natna | Naute pum a khawih chuan na taka tap emaw, puar emaw. |
| Jaundice natna lo lang leh thin | Naute mit emaw vun emaw var chu a sen leh emaw, a sen zual emaw a ni. |
| Stool rawng rawng | Pale emaw clay-colored stools tih hian bile flow a tawp tawh tihna a ni. |
| Thisen chhuak | Thisen chu bawlhhlawh chhungah emaw, luak chhuak nen emaw. |
| Heng symptoms te hi i hmuh chuan doctor hnenah hriattir nghal la emaw, i naute chu damdawi in hnai ber Emergency Department (ETU)-ah hruai la. | |
I naute hian hetiang thil hi a paltlang a ngai tih i hriat chuan i mangang, i lungngaihzia leh i hlauhthawn zia chu ka hrethiam. Engkim a lo thleng thuai hunah chuan tanpuina i mamawh ngei ang. I chhungte, i thiante leh i hmangaih tak takte hnen atangin tanpuina dil rawh. He zinkawngah hian nangmah chauh i ni lo tih hre reng ang che. He zinkawngah hian nangmah pawh hi ngaihtuah ve teh. Beiseina nei la, hriatna nei reng la, i chhehvela mite hnen atangin tanpuina zawng rawh.
Take-Home Thuchah a ni
- Kasai procedure hi naute zinga thin natna, biliary atresia enkawlna atana surgical procedure ber a ni.
- Hei hian bile duct blocked chu lakchhuah a, intestine section pakhat hmanga bile kal theihna tur kawng thar siam a huam a ni.
- Surgery tih hma (naute thla 2 a tlin hma) chuan hlawhtlinna chance a sang zawk.
- Naute zai zawhah in lama enkawl a pawimawh hle. Doctor thupek dik takin zawm rawh.
- Surgery a hlawhtlin loh chuan liver transplant a ngai mai thei a, hei hi he natna enkawl danah pawh a tel ve a ni.
- Khawsik, ei duh loh, jaundice lo lang leh emaw, bawlhhlawh var emaw ang chi natna hlauhawm tak tak i hmuh chuan doctor hnenah hriattir nghal rawh.











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