' Mad Cow Disease ' tih hming hi i hre tawh a, i hlau tawh em? Chu hming i hriat chuan horror movie-a awm ang maiin a awm a ni lawm ni? Mi tam tak chuan a ṭul lovah an hlau hle a, a chhan chu an hriat tam loh vang a ni. Mahse vawiinah hian eng nge a nih tak tak te, mi a nghawng dan te, kan hlauh tak tak tur em tih te hi han sawi mai ila.
A hmasa berin ‘mad cow disease’ tih hi eng nge ni?
A awlsam zawngin sawi ila, mad cow disease hi bawng nervous system natna a ni. Damdawi lama a hming chu Bovine Spongiform Encephalopathy (BSE) a ni. Bacteria emaw virus emaw avanga lo awm a ni lo. Protein pangngai lo prion an tih avanga lo awm a ni.
Ngaihtuah teh, chhan awm lovin, kan taksaa awm tlangpui protein pakhat chu ‘tha lo takin’ a fold nghal a, a pianzia dik lo a nei a, a tichhe thei hle. He misfolded protein (prion) hian protein tha dang pawh amah ang bawkin protein tha lo ah a chantir thei bawk. Zawi zawiin he protein tha lo hi thluak leh ruhroah a awm khawm a, nerve tissue a tichhia a ni. Bawngte hian he natna hi an vei chuan an ding thei lo va, an kal tha thei lo va, an rilru hahdam lo leh chetsualna an nei thei bawk. Amaherawhchu, bawng pakhatin hri kai a nih hnua heng symptoms te hi a lan chhuah theih nan kum 4-6 vel a ngai a ni.
He natna hi United Kingdom-ah a darh ber a, kum 1980 leh 1990 chhoah khan bawng hriselte chu ran hri kai sa leh ruh atanga siam ran chaw pek an ni. Mahse, khawvel ram tam takah dan khauh tak leh himna tur ruahmanna siam a nih avangin tunah chuan bawnghnute zingah he natna vei hi a tlem hle tawh a ni.
Okay, chuti a nih chuan hei hian engtin nge mi a nghawng?
Ni e, he natna hian mihring a kai thei bawk. Mahse chutih lai chuan ‘mad cow disease’ an ti lo. Mihringah hian he natna hi Variant Creutzfeldt-Jakob Disease (vCJD) an ti a.
vCJD hi natna hmuh tur awm lo tak a ni. BSE vei bawnghnute nervous system hmun thenkhat, a bik takin thluak emaw ruhro emaw awmna bawnghnute ei avanga lo awm a ni.
Mahse hetah hian thil pawimawh tak i tihbuai loh tur a awm. Natna dang pakhat CJD tih a awm bawk. Classic CJD (Sporadic CJD) tih a ni. Chu leh he vCJD hi thil hrang hrang pahnih a ni.
- Classic CJD: Hei hi bawngsa ei avanga lo awm a ni lo. Hei hi natna hmuh tur awm lo tak a ni a, a pianphungah, a chhan hriat loh, khawvel hmun dangah, bawnghnute ei leh ei lo apiangah a lo awm thei a ni. Kum 65 chunglamte a nghawng tlangpui.
- Variant CJD (vCJD): Hei hi BSE vei bawnghnute ei nen a inzawm a ni. Kum eng pawh a nghawng thei a ni.
Sri Lanka ang ramah chuan bawnghnute ei avanga vCJD vei theihna hi zero hnaih tak a ni . Hei hi a chhan chu kan ramah bawng leh sa lakluh kawngah quality control khauh tak a awm a, kan rama bawng zingah BSE vei report a la awm lo.
vCJD natna lan chhuah dante chu engte nge ni?
He natna hi hriat a harsa deuh a, a chhan chu a lan chhuah hmasak dan hi rilru lama harsatna nen a inang a ni. Natna a zual zel chuan nervous system nena inzawm symptoms a lo lang chhuak thin.
| Hunbi | Symptoms lo lang chhuak te |
|---|---|
| A lan chhuah hmasak ber (Rilru lam hriselna nena inzawm) |
|
| A hnu lama a lan chhuah dan (Nervous system nena inzawm) . |
Natna chu a tawp ber thlenga a kal zel chuan damlo chu a rilru a buai a, hun leh hmun a hre lo. Vanduaithlak takin vCJD kai atanga thla 13 chhungin thihna a thleng tlangpui.
Engtin nge he natna hi hriatchhuah leh enkawl a nih?
Mi pakhatin a dam laiin vCJD a nei tih hi 100% chiang taka sawi a harsa hle. A chiang tawk tur awmchhun chu thih hnua thluak biopsy neih hi a ni.
Mahse, mi pakhatin he natna hi a vei nia rinhlelh a nih chuan doctor-te chuan damdawi lam thil dang a awm loh nan test hrang hrang an nei ang.
- MRI thluak scan a ni
- EEG test hmanga thluak hnathawh enfiah thin
- Lumbar Puncture tih a ni
- Thisen test a ni
- Genetic test neih a ni
Enkawlna a awm em?
Vanduaithlak takin vCJD emaw prion natna dang emaw tidam kim thei tur damdawi hmuh tur a la awm lo.
Tunah hian tih tur awm chhun chu a natna lan chhuah dan control a, damlo tan hahdamna pek a ni. Entîr nân, natna, rilru hahna, leh mut theih lohna damdawi an pêk a.
Engtin nge he thil lakah hian kan inven theih ang?
Hei hi a chinfel dan tha ber chu bawngtein BSE an vei loh nan a ni. Khawvel ram hrang hrangin chutiang ti tur chuan khauh takin hma an la a ni.
- BSE testing neih a ni.
- Ran damlo tihchhiat.
- Mihring ei leh in leh ran chawah hian bawng thluak leh ruhro (spinal cord) ang chi thil hlauhawm tak tak telh khap tlat a ni.
Mimal anga i hriat tur pawimawh tak tak:
- Chaw siam hian prions a that lo: A tlangpuiin kan chaw siam hian heating hian natna hrik a that thin. Mahse, heng proteins prion an tih te hi temperature sang, acid leh radiation te hian a tichhia lo.
- Bawnghnute leh bawnghnute atanga siam thilte hi a him: Zirchianna atanga a lan dan chuan hri kai bawnghnute in hian vCJD a kai lo. Chuvangin bawnghnute, yogurt, cheese, etc. ngaihtuah buai a ngai lo.
- Thisen pek: A tlem berah chuan hri kai thisen hmanga kai theih a ni. He hlauhawmna tihziaawm nan hian thisen petu, BSE vei tawhna ram-a awm tawhte chu thisen pe thei lo turin hun eng emaw chen atan an tel lo.
Thutawp atan chuan Sri Lanka ang ramah kan cheng a, vCJD chungchangah hian a tul lova hlauhna kan neih chhan tur kan nei lo. Kan ram hian ei leh in himna tehfung sang tak a nei a.
Take-Home Thuchah a ni
- ‘Mad cow disease’ (BSE) hi bawnghnute natna a ni. Mihringte nghawng thei chi tlemte tak chu vCJD an ti a.
- Bawng hri kai atanga nervous tissue, thluak emaw spinal cord emaw ang chi sa ei atanga kai a ni. Beef steak pangngai atang chuan a hlauhawmna a hniam zawk.
- He natna thlentu prion hi a lum emaw, chawhmeh emaw a tihchhiat theih loh.
- Bawnghnute leh bawnghnute atanga siam te hian he natna hi a kai lo. An him vek a ni.
- Sri Lanka ramah hian kan tan he natna vei theihna hi a tlem hle. Chuvangin tul lovah hlau suh.
- Nangmah emaw, i hriat miin emaw sawifiah theih loh rilru lam emaw, nervous system lama inthlak danglamna (hriatrengna hloh, kal harsat ang chi) i neih chuan i chhungkaw doctor (doctor) hnenah thurawn dil nghal rawh.











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