Lu na, na tak emaw, i taksa sir khatah rilru na tak emaw i nei ngai em? A chang chuan heng thilte hnung lamah hian i ngaihtuah phak loh chhan a awm thei. Vawiin hian damdawi lam natna hmuh tur awm lo mahse pawimawh tak kan sawi dawn a ni. Moyamoya Disease tih a ni. A hming hi a mak deuhin a ri a ni lawm ni? Eng nge a nih i en ang u.
Moyamoya Natna hi eng nge ni?
A awlsam zawngin sawi ila, Moyamoya Disease hi i thluaka thisen kalna kawng a tichhe thei a ni. A dik tak chuan thluaka thisen kalna natna a ni . I thluaka thisen petu thisen kalna kawng lian ber berte chu carotid arteries , i kawr sir atanga i thluak thlenga kal te hi an ni. He natnaah hian heng thisen kalna kawng pakhat emaw, pahnih emaw chu zawi zawiin a zim emaw, a inkhar vek emaw a ni. I thluak hmalam leh lai takah thisen pe chhuaktu cerebral arteries -te pawh a nghawng thei bawk.
Ngaihtuah teh, kan thluak hmalam hmun thuma ṭhena hmun hnih vel chu heng thisen kalna kawng lian tak takte hian thisen leh oxygen an pe chhuak a ni. Chuti a nih chuan hengte hi a tawi chuan eng nge thleng? Thluak mamawh thisen leh oxygen a tlem phah a. Tui pipe a inkhar chuan tui luang a tlahniam ang mai a ni.
Tunah chuan kan taksa hi mak a ti hle. Hetianga thisen kalna kawng lian tak a block hian thluak chuan a tlakchhamna chu siam that tumin thisen kalna kawng thar, te zawk siamin a bei thin. Mahse heng thisen kalna tharte hi thisen kalna bulpui angin an chak lo. An chak lo va , an te fo bawk . Kawngpui lian tak khap a, lirthei te chu side road te tak te hmanga divert an nih ang mai a ni. Heng thisen kalna kawng te tak te te hian thluak hi thisen tling an pe thei lo mai thei. Tin, heng thisen kalna kawng chak lote hi a chang chuan a puak thei bawk. Hei hian thluaka thisen chhuah leh stroke a thlen thei a ni .
"Moyamoya" tih hming hi eng nge a awmzia?
"Moyamoya" tih hi Japanese tawng a ni. A awmzia chu "meikhu plume" emaw "meikhu puff ang mai" emaw tihna a ni. Japanese doctor-te hian he natna hi an hmuchhuak hmasa ber a ni. Thisen kalna kawng scan bik, angiogram , an tih chuan, thisen kalna kawng te tak te lo piang tharte chu meikhu hrual ang maiin, a nih loh leh meikhu chhuak ang maiin a inher tih an hmu a. Chuvangin he natna hi "Moyamoya disease" tiin an vuah a ni. Chu chu hming mak tak a ni lo maw?
Moyamoya Disease hi engtiang chiahin nge a tlem?
Hei hi a takah chuan natna hmuh tur awm lo tak a ni. Japan ramah hmuh tur a tam ber. He natna vei mi sang za zingah a vaiin mi panga vel an awm niin an sawi. America ang ramah pawh he natna vei hi 5,000 aia tlem lo an awm. Chuvangin Sri Lanka-ah pawh hetiang hi a tlem hle niin a ngai thei. Mahse a chang chuan hetiang damlo hi an report thin.
Moyamoya Disease natna lan chhuah dan chu engte nge ni?
He natna lan chhuah dan hi thluaka thisen kal tlem vang a ni. Vawi tam tak chu, natna i hriat hmasak ber chu a niStroke a awm chuan, emaw, transient ischemic attack (TIA) a awm chuan . Heng TIA te hi doctor-te chuan "mini-stroke" an ti \hin. Chumi awmzia chu thluaka thisen kal chu hun eng emaw chen a titawp a, chumi hnuah a lo awm leh ta tihna a ni. Mahse hei hi vaukhânna a ni.
A lan chhuah dan dangte chu:
- Brain hemorrhage: Hei hi a hmaa kan sawi tawh thisen kalna kawng te tak te chak lo tak takte puak vang a ni thei.
- Lu na: Lu na fo, a chang chuan na tak tak a awm thei.
- Hmasawnna tlai: A bik takin naupang tê tête hian he natna hi an vei a nih chuan naupang dangte aiin an thanlenna a slow zawk thei.
- Aneurysm: Thisen kalna kawng thenkhata balloon ang maia bulge awm. Chungte chu a puak thei.
- Duhthusam lova chetna: Ke leh ke ang chi thilte thunun theih loha tihnghing.
- Cognitive abilities lama harsatna: Entirnan, zirlai, hriatrengna leh ngaihtuahna seng harsa.
- Hriatna lama harsatna: Mit hmuhna, hriatna, rim, khawih leh thlum dan inthlak danglamna a awm thei.
- Seizures: Seizure ang chi dinhmun.
Heng symptoms zinga pakhat emaw a aia tam emaw i nei thei. Mi zawng zawng hian heng symptoms te hi a inang vek lovang.
Eng thilin nge Moyamoya Natna hi a thlen?
Dik tak chuan zirchiangtute chuan he natna hi eng nge a thlen tih chiang takin an la hre thei lo. Mahse, genetic influence a nei tih hmuhchhuah a ni a, a chang chuan chhan dang vangin acquired condition a ni thei bawk. He natna hi nu leh pa atanga fate hnena thlen thei genes chungchangah hian zirchianna an la nei mek a ni. Tin, taksaa inflammation emaw infection emaw ang chi thil thenkhatin a thlen thei nia rinhlelh a ni bawk.
A châng chuan, heng Moyamoya symptoms te hi damdawi lam thil dang nen pawh a awm thei bawk. Hei hi Moyamoya syndrome emaw Moyamoya phenomenon emaw an ti a. Entir nan:
- Down syndrome tih hi a ni
- Graves natna ( thyroid gland nena inzawm natna) .
- Neurofibromatosis type 1 (genetic condition) a awm a, a natna hi a tha lo hle.
- Sickle cell natna ( thisen natna) .
- Atherosclerosis (thisen kalna kawnga thau awm) .
Hetiang natna dang nei te hian Moyamoya symptoms an nei tam zawk.
Moyamoya Disease hi genetic a ni em?
Ni e, zirchiangtute chuan RNF213 an hmuchhuak taRNF213 an tih gene-a mutations, a nih loh leh inthlak danglamna hi fibromyalgia vei thenkhatah hian a mawhphurtu a ni thei. He gene atanga protein siam RNF213 hi thisen kalna kawng siamnaah a inrawlh niin an ngai.
Japanese mi Moyamoya natna vei zinga 15% vel chuan an chhungte zingah he natna vei an nei a, hei hian genetic link a nih thu a tarlang. Mahse, rochan dan dik tak erawh hriat chian a la ni lo.
Tute nge Moyamoya Disease vei tam zawk?
Kan sawi tawh ang khan hei hi natna hmuh tur awm lo tak a ni. Genetic factors avanga lo awm moyamoya natna hi Japanese mite zingah a tam zawk nachungin, tunah chuan hnam dang zingah pawh a vei nasa hle.
Scientist-te chuan a chhan dik tak chu la hrethiam lo mah se, hmeichhiate hian mipa aiin a let hnih velin he natna hi an vei tam zawk a ni.
Moyamoya natna hi kum eng pawhah a lo awm thei. Amaherawhchu, naupang kum 5 leh 10 inkar leh puitling kum 30 leh 50 inkar te hi an vei tam ber a ni.
He natna hian eng harsatna nge a thlen theih?
Moyamoya natna hi uluk taka enkawl a nih loh chuan harsatna chi hrang hrang a awm thei a ni. Chung zingah chuan:
- Paralysis a awm
- Mit hmuhna lama harsatna a awm
- Thusawi lama harsatna a awm
- Movement disorder a awm thei
- Thluak a tichhe vek
Hei vang hian natna hriat chian leh enkawl vat a pawimawh.
Engtin nge Moyamoya Disease i vei tih i hriat theih ang?
Moyamoya natna lanchhuahna i neih chuan doctor-in a enfiah ang che a, i natna lan chhuah dan a zawt ang che. Tichuan, moyamoya natna nia rinhlelh a nih chuan hetiang test hi an ti thei ang:
- Cerebral arteriography: He test-ah hian tube te tak te, catheter an tih chu i kut emaw ke emaw artery-ah dah a ni. Chumi hnuah chuan iodine (contrast dye) awmna tui bik chu catheter hmangin thisenah an inject leh a. Chumi hnuah chuan X-ray an la a, chu tui chu thisen kalna kawngah engtin nge a kal tih an en a ni. Hei hian thisen kalna kawng a zim zia leh thisen a kal dan te a hriat theih phah a ni.
- Magnetic Resonance Angiography (MRA): Hei hi natna nei lo test a ni a, magnetic field, radio wave leh computer hmangin i thisen kalna kawngte chu enfiah a ni.
- Magnetic Resonance Imaging (MRI): Hei hi MRA nen a inang reng a ni. I taksa chhungril thlalak a la a, natnain i thluak a nghawng dan a teh thei bawk.
Heng test te hian doctor te chuan Moyamoya natna i vei leh neih loh chiang takin an hre thei a ni.
Moyamoya Disease hi eng stage nge ni?
Moyamoya natna hi a zual zel a.Natna a ni. Chu chu enkawl loh a nih chuan natna chu a zual zel dawn tihna a ni. Doctor-te chuan natna nasat dan sawi nan "Suzuki stages" tih classification an hmang a. MRA scan atanga information an hmuh hmangin natna stage eng nge i awm tih an hre thei a, heng Suzuki stage te hi, a awlsam zawnga sawi chuan, hetiang hi a ni:
- Stage 1: Carotid artery chhung lam chauh a narrowing emaw blockage emaw a awm.
- Stage 2: Carotid artery apical branch zawng zawng chu a thim tan vek tawh. Chu thisen kalna "smoky" (a te, meikhu ang maia lang) chu angiogram-ah chuan hmuh tur a awm lo.
- Stage 3: Angiogram-ah hian thisen kalna kawngte chu chiang takin a lang. Chu "smoke plume" hmel chu chiang takin i hmu thei.
- Stage 4: Thluaka thisen kalna kawngte chu zawi zawiin a tlahniam tan a. An aiah chuan thisen kalna kawng dang (transdural collateral vessels) a lo awm tan ta a ni.
- Stage 5: Thisen kalna kawng a tlahniam lehzual a, thisen kalna kawng dang tam zawk a lo piang ta a ni.
- Stage 6: Thluaka thisen kalna kawngte chu a bo vek tawh mai. Carotid artery chu a zim vek emaw, a block vek emaw a ni.
Heng stage hrang hrangte hi dik taka hriatthiamna hian doctor-te chu enkawl dan tur ruahmanna siam turin a pui thin.
Moyamoya Disease enkawlna tur engte nge ni?
Moyamoya natna enkawl hian a tum ber chu a natna lan chhuah dan control a, a natna zual zel tur ven tum a ni. Chumi atan chuan i doctor chuan damdawi thenkhat a pe thei che a ni:
- Aspirin: Aspirin hian chutiang thisen kalna kawng te tak te, chak lo tak tak lo piang tharte thisen zam chu a veng thei a, a ti tlem thei bawk.
- Antiseizure damdawi: Hengte hi epilepsy vanga epileptic seizures (convulsions) venna atana pek a ni.
- Anticoagulants: Hengte hi thisen tithianghlimtu an ni. Thisen a inzawm loh nan an pui thin. Amaherawhchu heng damdawi te hian hlauhawmna a nei a, chu chu thisen chhuah a awm chuan tihtawp a harsa thei hle. Chuvangin doctor ten hengte hi fimkhur takin an pe thin a, special case-ah chauh an pe thin.
- Calcium channel blockers: Hengte hian migraine vanga lu natna tihziaawmna kawngah a pui thei a ni. Mahse, heng damdawi te hian thisen sang a tihniam thei bawk a, chu chuan stroke hlauhawmna a tipung thei a ni. Chuvangin special case-ah chauh hman an ni.
Mahse, heng damdawi te hian thisen kalna kawng a zim chu a titawp thei lo tih hre reng ang che. Chuvangin natna hi a zual zawi zawiin a zual thei a ni. Chutiang a nih chuan i doctor chuan bypass surgery neih a rawt thei ang . He surgery hi:
- Lu vunah thisen kalna kawng hrisel tak tak hmanga thisen kalna kawng thar siam, thisen kalna kawng khar chu bypass.
- Thisen kal dan chu thluak hmuna a nghawng danah a inthlak danglam (redirect).
- Thisen kalna kawng tawi te hawn.
I doctor chuan i dinhmun atana surgical procedure eng nge a inmil ber tih chipchiar takin a hrilhfiah ang che, a side effects leh harsatna awm thei te.
Moyamoya Disease hi a veng thei ang em?
Genetic factors avanga lo awm Moyamoya syndrome hi ven theih dan finfiah a la awm lo. Mahse, thisen kalna kawng nena inzawm risk factors control a, atherosclerosis hlauhawmna tihziaawmna hmangin Moyamoya syndrome vei theihna chu tihziaawm theih a ni.
Tin, Moyamoya natna i neih chuan i doctor-in damdawi a pek ang chiah leh a tih ang taka ei hian i natna lan chhuah dan a thunun thei a, harsatna i neih loh nan a pui thei bawk.
He natna vei hian eng nge a beisei theih ang?
Mi tam tak tan chuan Moyamoya natna hi hun kal zelah a zual zauh zauh thin. Thisen kalna kawng a zim deuh deuh chuan stroke pawh an nei thei . Moyamoya natna hi enkawl loh chuan thluak lam chhiatna nasa tak a thlen thei a, stroke a thlen thei a, thihna thlengin a thlen thei bawk.
Mahse, mi thenkhat chu kum tam tak chhung chu natna lanchhuahna nei lovin an awm thei a ni. Symptoms a lan tan chuan doctor chuan operation neih a rawt thei bawk.
Moyamoya Disease vei dam rei zawng chu engzat nge ni ang?
He natna hi hriat hmasak a nih a, enkawl tan thuai a nih chuan Moyamoya natna vei te chu nun pangngaiin an nung thei a ni.
Amaherawhchu, enkawl loh chuan he natna hi a thihpui thei a ni. Chuvang chuan natna hriat hmasak leh enkawl hi a pawimawh em em a ni.
Moyamoya Disease vei chuan engtikah nge emergency medical attention a zawn ang?
Stroke chhinchhiahna i neih chuan emergency medical attention i pan nghal tur a ni . Hetah hian hun hi a pawimawh ber a ni.
American Stroke Association chuan miten an hriatreng awlsam nan FAST tih acronym an hmang a. Sinhala tawnga a awmzia hi han thlir ila:
- F - Face droop: I hmai sir khat chu a hlim hmel em? Nui i tum chuan i hmai sir khat chu a tla thla em?
- A - Kut chak lohna: Kut pahnih i chawi sang thei em? Kut pakhat chu a tla thla em?
- S - Thusawi harsa: I thusawi a slur em? Nge a slow em? Thumal awlsam tak chu i sawi nawn leh thei ang em?
- T - Emergency services biak hun: Heng stroke chhinchhiahna te hi i hmuh chuan 911 call nghal la, ambulance la la, a nih loh leh damdawi inah kal nghal rawh. Hun hi a pawimawh ber a ni!
Stroke chhinchhiahna dangte chu a lo lang nghal mai thei:
- Rilru tibuai
- Taksa sir khatah natna hrik awm
- Mit hmuhna lama harsatna a awm
- Kal harsat
- Lu na na tak a ni
Moyamoya Disease hi natna hlauhawm tak a ni a, stroke leh thluaka thisen chhuak a thlen thei a ni. Zirchiangtute chuan a chhan dik tak chu la hre chiang lo mah se, Japanese mite zingah a tam zawk. Moyamoya symptoms i neih chuan doctor pan nghal rawh. Moyamoya Disease hi a hmaa hriatchhuah leh enkawl hi nunna leh thihna inthlauhna a ni thei. Stroke symptoms hriat a pawimawh bawk a, a lo awm a nih chuan hmalak nghal a pawimawh bawk.
Thupui tawi (Take-Home Message) 1.1.
Chuvangin, tunah chuan vawiin a kan sawi Moyamoya Natna chungchang hi hriatthiamna engemaw chen in neih ka beisei. Hriat reng tur pawimawh thenkhat chu hetiang hi a ni:
- Hei hi natna hmuh tur awm lo tak a ni a, thluaka thisen kalna kawng a ti zim a.
- Stroke , lu na , leh seizures ang chi symptoms a awm thei.
- Natna hriat chian leh enkawl vat a pawimawh hle .
- Enkawlnaah hian damdawi leh, a tul chuan bypass surgery te pawh a tel a ni.
- Stroke (FAST) chhinchhiahna hriat chian hi nunna chhanhimna a ni thei.
Nangmah emaw, i hriat miin emaw heng symptoms te hi i neih chuan doctor rawn la. Ngaihtuah buai suh, engkim tan solution a awm vek. A pawimawh ber chu hmalak vat hi a ni.
` Moyamoya, thluak natna, stroke, thisen kalna, thluak natna, genetic natna, lu na
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