I taksa ruhte chu a chak lo zauh zauh em? Primary Lateral Sclerosis (PLS) a ni tih i hre lo mai thei! Hemi chungchang hi han sawi ila!

A châng chuan i ke leh i kut chu zawi zawiin a hrual ang maiin i inhria em, a nih loh leh i chakna a tlahniam ang? I kal laiin a hma angin i chak lo niin i hria em, i balance pawh i hloh mai thei? Hengte hi i ngaihven vak lo mai thei symptoms ni mahse, a chang chuan a chhan lian zawk a awm thei. Chu chu Primary Lateral Sclerosis tih chu a ni a, a tawi zawngin PLS a ni.

He PLS hian eng nge a awmzia tih hi han en mai ila?

A awlsam zawngin PLS hi neuromuscular natna zual zel a ni. I taksa ruhte chu zawi zawiin a tichak lo va,/ emaw, a tichak lo bawk. I ke atang hian symptoms a intan fo thin. Hun a kal zel a, he chak lohna leh khauhna hi i taksa ruh dangteah pawh a darh thei a ni.

Hetiang hian han ngaihtuah teh: kan taksa ruhte hian electric hmanrua angin hna a thawk a. An mamawh ang chiaha ‘current’, thluak atanga thuchah lo lut chu an dawng tur a ni. PLS-ah chuan heng thuchah kengtu ‘wire’ ang maia Upper Motor Neurons (UMN) an tih nerve cell te hi a chhe vek a.

Vanduaithlak takin tun dinhmunah PLS damdawi a la awm lo. Chuvangin enkawlna hi i symptoms control leh nitin hna awlsam zawka tih theihna tura tanpui che hi a ni ber. Entîr nân, tiang emaw, kea kalna emaw hman ṭanpui che.

PLS hi engtiang chiahin nge a awm?

PLS hi a takah chuan a awm lo hle. Mi engzat nge an neih tih chiang takin statistics a la awm lo.

PLS leh ALS hi eng nge an danglamna? PLS hi ALS a ni thei ang em?

ALS, emaw Amyotrophic Lateral Sclerosis tih hi i hre tawh ngei ang. PLS leh ALS te hi nerve leh muscle natna a ni vek a. Mahse an pahnih inkarah hian danglamna pawimawh tak tak a awm.

A danglamna ber chu PLS hian i upper motor neurons (UMNs) chauh a nghawng a ni. Heng nerve te hi thluak atanga spinal cord thlenga thuchah phurtu te an ni. ALS-ah chuan heng UMNs te hi a nghawng bawk a, chutiang bawkin lower motor neurons (LMNs) , spinal cord atanga taksa peng hrang hranga thuchah thawn thin te pawh a nghawng bawk.

Tunah chuan, ‘Chuti a nih chuan, PLS vei tu emaw chuan a hnuah ALS a vei thei ang em?’ tiin i ngaihtuah mai thei. Ni e, a theih theihna chance a awm. A châng chuan ALS natna lan chhuah hmasak ber chu PLS nen a inang thei bawk. UMN chauh nghawng thei symptom i neih chuan a tir lamah PLS i vei tih hmuhchhuah a ni thei. Mahse a hnuah ALS symptoms i neih chuan UMN leh LMN pahnih a nghawng a nih chuan i doctor chuan i diagnosis chu ALS ah a thlak thei a ni.

Dik tak chuan PLS ang deuha lang tam tak hi UMN (`UMN-predominant ALS`) tichhe thei ALS chhinchhiahna hmasa ber an ni thei. Chuvangin doctor-te chuan PLS hi chiang taka hriat theih nan kum thum atanga kum li tal symptoms i neih a ngai a ni an ti .

PLS natna lan chhuah dante chu engte nge ni?

PLS symptoms hi a lang zawi zawi hle.Danglamna lian tak i hre nghal lovang.

A tir lama hmuh theih symptoms: 1.1.

A tirah chuan hetiang hi i hre mai thei:

• Ke ah a nghet lo. I ke a tang ang maiin a lang thei.
• I ke ruhte chu a chak lo ta hle mai. Tûn hma angin i chak lo niin i inhria mai thei.
• Kal a harsa ta a, a nih loh leh i balance vawng reng thei bawk. I tlu emaw, tlu emaw pawh a ni thei.
• Muscle spasm emaw, na tak tak emaw a awm thin.

Natna a zual zel angin a lan chhuah theih dan:

Natna a lo zual zel chuan heng ang chi natna dang a lo lang thei a ni:

• Kut zungtang, kut leh kut ruh te pawh a nghet a, a chak lo bawk. Thil tê tête man a harsa thei a, ziak pawh a harsa thei bawk.
• Zun chhuah control harsat. Hei hian zun hmanhmawhthlak leh insum theih lohna a thlen thei a ni.
• Natna hi hnungzang hnuai lam leh kawr ah a awm thin.

Lei ruh (muscles) tichhe thei symptoms hmuh tur awm lo:

Hei hi a tlem hle a, mahse mi thenkhat chuan an lei thau (tongue muscle) te pawh a nghawng thei bawk. Chutiang a nih chuan:

• Thusawi thiam lo (dysarthria) a awm thin. Thumal sawi thiam a harsa ta hle mai.
• Chaw ei harsa (dysphagia). Chaw emaw, in emaw i ei hian i rilru a buai ang maiin i inhria mai thei.

PLS hi eng thilin nge a thlen?

A tam zawkah chuan PLS hi a chhan dik tak kan la hre lo. Chu chu thudik chu a ni.

Mahse, a tlem hle a, naupang tê leh puitling naupang (`juvenile primary lateral sclerosis`) vei thei PLS chi khat a awm. Hei hi nau pai laia an DNA inthlak danglam vang a ni.

PLS atang hian kan taksaah eng nge thleng?

PLS hi neuromuscular condition a ni a. I thluaka motor neurons leh chu neurons atanga spinal cord thlenga nerve fibers te a nghawng ber a ni. Chungte chu upper motor neurons (UMN) an ti bawk.

Ngaihtuah teh, i ke i sawn duh hian i thluak hian thuchah a thawn thin. He thuchah hi nerve fiber kaltlangin spinal cord-a neurons thlengin a kal a, chuta tang chuan i kea voluntary muscles-ah a kal bawk. Muscle te hian he thuchah hi an dawn hian an che thin.

PLS-ah chuan heng UMN nerve cell te hi an thi zauh zauh (degeneration). Tichuan, taksa ruhte hian thuchah tul tak tak an dawng lo a, chuvangin taksa ruhte hian beisei angin hna an thawk lo.

Hei hi thlahtu natna a ni em?

PLS hi a tlangpuiin rochun atanga lo chhuak a ni lo. Chumi awmzia chu i chhungkuaa tumahin an la nei lo a nih pawhin i tipung thei tihna a ni. A tam zawkah chuan random takin a thleng a, chhungkaw history-ah natna hi a awm lo.

Tute nge PLS vei theihna chance sang zawk?

PLS hian a takin tu pawh a nghawng thei. Kum 50 vel atanga hmuhchhuah a ni tlangpui a, mahse, kum 50 hnuai lam, kum upa lam, naupang thlengin a nghawng thei a ni. Mipaah ​​a tam deuh hlek a.

PLS vang hian eng harsatna nge awm thei?

PLS a kal zel chuan tanpuina tel lova kal harsa i ti mai thei. Tiang, kea kalna, a nih loh leh wheelchair i hman a ngai mai thei . Chu bâkah, i taksa ruhte a chak loh zêl chuan i balance a hloh thei a , i tlu awlsam zâwk thei bawk. I tih chuan i hliam mai thei.

Engtin nge PLS hi hmuhchhuah a nih?

Doctor chuan taksa enfiahna, thluak enfiahna leh specialized test dangte hnuah PLS a nei tih a hmuchhuak thin. I symptoms te chu an enfiah ang a, symptoms inang nei condition dang, ALS emaw multiple sclerosis emaw te chu paih chhuah an tum ang. Test-ah hian:

• Thisen test a ni.
• Electrodiagnostic examination - Hengte hian i nerve leh muscle te hnathawh that dan a enfiah thin. Entirnan, nerve conduction zirchianna leh needle electrode zirchianna te hi a ni.
• MRI (Magnetic Resonance Imaging) hmanga thluak leh ruhro test a ni.
• Cerebrospinal fluid (CSF) hmanga enfiah a ni. Hei hi i ruh (lumbar puncture emaw spinal tap) atanga tui tlemte lak a, neuromuscular natna bik atana thil dik lo awmte zawn chhuahna hmanga tih a ni.

PLS enkawl dan tur chu engte nge ni?

PLS enkawlna hian i natna lan chhuah dan tur i enkawl theih nan a tum a ni. Hei hian a huam thei ang:

• Muscle stiffness, limping, leh ei harsa tihziaawmna damdawi.
• Physical therapy hmanga taksa chak lohna tihziaawmna tur, taksa ruh inthlak danglam theihna tur leh ruh inzawmna (joint range of motion) tihchangtlun nan te.
• Nitin hnathawh leh kal theihna tura pui thei device. Entîr nân, tiang, kea kal, a nih loh leh wheelchair.
• Speech therapy emaw, thusawi harsatna nei tura puitu hmanrua emaw.

PLS symptoms nei tan damdawi pek dan:

PLS symptoms natna atana damdawi an pek tlangpui thenkhat chu:

• Muscle stiffness atan chuan: `(Baclofen)` leh `(Tizanidine)` te hi a ni
• Taksa ruh natna: `(Quinine)`
• Taksa tih hahdam nan: `(Diazepam)`

Enkawlna hian side effect a nei em?

Ni e, damdawi zawng zawng ang bawkin he damdawi hian side effect a nei thei. Damdawi a zirin side effect a inang lo. Chuvangin, damdawi eng pawh i ei tan hmain i doctor nen a side effect awm thei chungchang sawipui hmasak a pawimawh hle.

PLS hi ven theih a ni em, tihdam theih a ni em?

PLS awm chhan dik tak hriat a nih loh avangin tun dinhmunah chuan a lo awm lohna tur kawng a awm lo.

Tin, lungchhiatthlak takin tunah hian PLS tidam kim thei tur damdawi a awm lo.

PLS vei dam rei zawng chu engzat nge ni? Engtin nge an beisei theih ang?

PLS hian i dam rei zawng direct-in a nghawng lo. PLS vei chuan dam chhung pangngai a nei thei a, natna nei lo ang bawkin.

I natna lan chhuah dan leh a zual chak dan hi mi hrang hrangah a inang lo. A tlangpuiin primary lateral sclerosis hi zawi zawiin a kal zel a, kum tam tak chhung, a then chu kum sawm tam tak chhung a ni. Mahse, i symptoms a zual zel tih i hriat thut chuan doctor pan nghal rawh.

Damdawi hian i natna lan chhuah dan a tihziaawm thei a, nitin hnathawh tur pawh tihtawp lohvin i kalpui thei bawk. I kal kual hunah him leh inrintawkna nei zawka i awm theih nan tiang, kea kalna, a nih loh leh wheelchair hman i ngaihtuah mai thei.

Engtikah nge Doctor i hmuh ang?

I taksa peng hrang hrangah zawi zawiin inthlak danglamna , a nghet emaw, a chak lo emaw i hmuh chuan i doctor nen inbia ang che. PLS i vei tih hmuhchhuah a nih chuan, damdawi i ei lai pawhin i natna lan chhuahna a tizual a nih chuan, a nih loh leh side effect i neih chuan chu chu i doctor hnenah pawh hrilh bawk ang che.

A pawimawh ber: I tlu emaw, accident-a i hliam emaw chuan emergency room-ah kal nghal rawh.

I doctor zawh tur zawhna

PLS i neih chuan i doctor zawh tur zawhna tam tak i nei ang. Entir nan:

• Eng enkawlna nge ka natna lan chhuahna control-na atana ṭanpui thei?
• Enkawlna hian eng side effect nge a neih?
• Engtin nge hun kal zelah ka dinhmun hi a zual zel dawn tih ka hriat theih ang?
• Ka taksa ruh (muscle function) tichak turin eng exercise nge ka tih theih ang?
• Cane emaw, walker emaw hman a ngai em?

A tawp berah chuan Take-Home Message kan rawn thawn leh ta

I taksa tihchet theihna tichhe thei dinhmun hmasawn takah insiamrem chu thil harsa tak a ni thei tak zet a ni. Hmanlai thil tih nuam i tih thin ṭhenkhat chu zawi zawiin a harsa thei hle. Primary lateral sclerosis (PLS) hi zawi zawiin a kal zel a, mahse nitin nun a nghawng thei a ni.

Hêng taksa inthlâk danglamnate hian i rilru put hmang pawh a nghawng a nih chuan, rilru lam hrisêlna lama mithiamte biak chuan hahdamna i hmu thei a ni .Zahpui tur a ni lo, mi tam tak chuan hetiang hunah hian tanpuina an mamawh a ni.

I taksa chakna a danglam tih i hriat chuan doctor pan nghal rawh. Independent leh comfortable zawka i awm theih nan damdawi emaw mobility device emaw an pe thei che a ni. He zinkawngah hian nangmah chauh i awm lo tih hre reng ang che.

` Primary lateral sclerosis, PLS, taksa ruh chak lohna, neuropathy, motor neurons, ALS, natna lan chhuah dan