Nausen piang thar in lama hruai luh hlimna chu sawifiah theih loh a ni lawm ni? Mahse, a chang chuan chu hlimna rual chuan hlauhna tlemte rilruah a lo lang fo thin. Nu emaw pa tu pawhin an naute hmui leh kut zungtang chu a sen deuh tih an hmuh chuan an buai hle ang. Hetiang thil hi an hmuh chuan congenital heart condition vang pawh a ni thei. Vawiin hian Pulmonary Atresia , thinlung natna khirh tak, mahse enkawl theih a nih thu kan sawi dawn a ni.
A awlsam zawngin, Pulmonary Atresia chu eng nge ni?
Hei hi a buaithlak deuhin a lang thei a, mahse a awlsam zawngin han sawi ila. Kan thinlung hi in te tak te, pindan pali nei ang mai a ni. He in dinglama pindan pahnih (atrium dinglam leh ventricle) hnathawh ber chu taksa pum puia a kal kual vela oxygen tlakchham tawh thisen "bawlhhlawh" chu khawlkhawm a, chu chu lung chhunga tihfai turin thawn chhuah a ni.
Thisen hi thisen kalna kawng lian tak Pulmonary Artery an tih hmangin lungah a thawn thin a ni . He thisen kalna bul tannaah hian kawngkhar ang maia thawk valve a awm a. Pulmonary Valve kan ti a . He kawngkhar hi a inhawng chuan thisen chu lung chhungah a lut a.
Tunah chuan han ngaihtuah teh, he kawngkhar, pulmonary valve hi pian tirh lamah a lo piang lo a nih chuan, a nih loh leh khar vek a nih chuan eng nge thleng ang? Chu chu Pulmonary Atresia kan tih hi a ni .
A awlsam zawngin, hetiang dinhmunah hian thinlung atanga lung atanga thisen oxygenated thawn chhuahna kawngkhar lian ber chu pian tirh atangin a khar a ni. Chumi avang chuan oxygen tlachham, blue-colored thisen chu taksa pum puiah a kal kual a.
Hei hi thil awm lo tak a ni. America ang ramah pawh nausen piang 6,700 zinga pakhat chauhvin he natna hi an nei a ni.
Hetiang dinhmun nena hmuh theih tur thinlung chhiatna dang
Naute pulmonary atresia vei chuan he chhiatna ber bakah hian thinlung lam harsatna dang engemaw zat a nei thei bawk.
- Thinlung dinglam a thang tha lo: Ventricle dinglam, lung chhunga thisen pumptu leh a chunga tricuspid valve te chu a lo thang tha lo thei a, a te hle bawk.
- Thinlung khur: A tlangpuiin naute hian a pum chhunga a awm laiin thinlung pindan chunglam (atria) pahnih inkarah khur te tak te (Foramen Ovale) a nei a. Hei hi pian hnuah a khar thin. Mahse, naute thenkhatah chuan a khur chu a inhawng reng thei. Tin, thinlung hnuai lam (ventricles) pahnih inkarah hian bang chhungah khur a awm thei bawk (Ventricular Septal Defect - VSD). He hole hian oxygen level hniam thisen chu oxygen level sang thisen nen a inhmeh tir thei a ni.
Engtin nge i naute hian he natna hi a nei tih i hriat theih ang? Natna
Pulmonary Atresia symptoms hi nau piang atanga darkar engemaw zat emaw, ni engemaw zat emaw chhungin a lang tan tlangpui. A lan chhuah dan ber leh hriat awlsam ber chu:A natna pakhat chu cyanosis an ti a .
Chumi awmzia chu naute hmui, kut zungtang leh ke ruhte chu thisenah oxygen a tlakchham avangin a sen angin a lang tihna a ni. He rawng dum hi mi thenkhat chuan he natna hi "blue baby syndrome" an tih chhan a ni.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Vun rawng sen (Cyanosis) . | Ka hmui, kut zungtang leh nail hnuai lam rawng blue emaw purple emaw a inthlak. |
| Thâwk harsa | Thâwk rang, thawk hah (Dyspnea). |
| Chauhna danglam tak | Naute hian hnute pe turin chakna pawh a nei lo va, a muhil reng bawk. |
| Bawnghnute in harsat | Tlemte in hnuah pawh lu a tihbuai avangin bawnghnute in duh loh. |
| Vun lum, clammy tak a ni | Naute ke leh ke i khawih chuan a vawt a, a hnim a, thawk hah ang maiin a awm. |
| Tap/chawlh fo thin | Naute chu a lungawi lo hle a, chhan awm lovin a tap reng bawk. |
Engvangin nge hetiang hi a lo awm? A chhan leh a hlauhawmna
Hetiang dinhmun hi a chhan dik tak hi hriat a la ni lo . He heart defect hi nausen pum chhunga a lo seilian atanga kar 8 hmasa berah a awm thin. Mahse, thil engemaw tak chuan a hlauhawmna a tipung tih hmuhchhuah a ni.
- Genetic factors: Chhungkaw zinga mi pakhatin congenital heart disease emaw, genetic disease thenkhat (e.g. DiGeorge’s syndrome) a neih chuan a hlauhawmna a sang zawk.
- Naupai laia nu hriselna: 1.1.
- Naupai laiin meizuk .
- Diabetes hi uluk taka control theih loh a ni.
- Naupai laia hman tlak loh damdawi thenkhat (teratogenic drugs) hman.
- Nu leh pa thilte: 1.1.
- Nu leh pa zinga pakhatah congenital heart disease a neih.
- Nu kum upa lam.
Engtin nge doctor-te hian he natna hi dik taka an hriat theih?
A tam zawkah chuan heng dinhmunte hi naute pian hmain hriat theih a ni a, chu chu naupai lai scan hmanga hriat theih a ni.
- Naupai lai: Doctor chuan routine scan (ultrasound) neih laiin naute thinlung chungchangah rinhlelhna a neih chuan, fetal echocardiogram tih, special scan atan a refer ang che. Hei hian naute thinlung hnathawh leh insiam dan chu chiang takin a hmu thei a ni.
- Naute pian hnuah: Doctor-in naute thinlung a ngaihthlak laiin thawm danglam (heart murmur) a hriat chuan, a nih loh leh naute chu a sen a nih chuan he natna hi rinhlelh a ni. Tichuan, he natna hi finfiah nan test eng emaw zat an nei leh thin.
| Fiahna | Hei hian eng nge a tih? |
|---|---|
| Pulse Oximetry hmanga tih a ni | Naute ke ruh lianah hian clip ang chi hmanrua te tak te an bun a, thisenah oxygen awm zat a teh thin. |
| Chest X-ray neih a ni | A lian leh te, a pianzia leh a thisen chu lung chhunga a kal dan te chu a rough idea a pe a ni. |
| Electrocardiogram (ECG) hmanga tih a ni. | Thinlung electrical activity hi heart muscle-ah pressure a awm em tih emaw, rhythm pangngai lo a awm em tih emaw an teh thin. |
| Echocardiogram (Echo) hmanga tih a ni. | Hei hi test pawimawh ber a ni . Heart scan ang mai a ni. Thinlung insiam dan te, valve hnathawh dan te, thisen kal dan te, khur a awm leh awm loh te chu chiang takin a lang thei a ni. |
Hei hi eng enkawlna nge ni?
Pulmonary Atresia hi a hriat veleh enkawl nghal tur a ni. Damdawi hmanga tihdam kim theih a ni lo. Mahse, damdawi leh hmanraw dang hmangin naute nunna chhanhim a, operation atana a inpeih hma loh chuan a dinhmun a nghet thei a ni. A tawp berah chuan surgery hrang hrang tih hi a ni .
1. Enkawlna (damdawi leh tih dan tur) .
- Enkawl dan: Naute a pian hnuah thisen kalna kawng bik (Ductus Arteriosus) a awm a, chu chu a tlangpuiin a khar thin. He thisen kalna kawng hi a inhawng reng theih nan damdawi pakhat Alprostadil an tih chu vein (IV) kaltlangin pek a ni. He thisen kalna kawng hi a inhawng chuan oxygen tlachham thisen thenkhat chu lungah oxygen la turin a kal thei a ni. Hei hi hun eng emaw chen atana chinfelna a ni.
- Thiltih dan: A chang chuan, thisen kalna kawng hawn reng turin stent dah a ni. A nih loh leh thinlung chunglam chamber pahnih inkar khur chu tihzauh nan septostomy tih a ni. Hengte hi thisen kal dan tlem a tihchangtlun nan tih a ni.
2. Surgery (surgery) tih a ni.
Naute surgery chi hrang hrang mamawh chu a thinlung dinglam lo thanglian dan leh thinlungah khur a awm leh awm lohah a innghat a ni.
A pawimawh ber chu heng surgery te hian natna hi a "tidam" kim lo tih hi a ni. Chu ai chuan a theih ang anga thinlung hnathawhna chu an siam ṭha leh a, naute chu nun pangngaia a awm theih phah a ni.
Naupang tam tak chuan open-heart surgery , stage thum hrang hrang an nei a, chu chu naute dam kum hmasa berah an ti ṭhin.
1. First surgery (BTT Shunt): Hei hi naute pian hnu ni hmasa berah tih a ni tlangpui. Hetah hian artificial tube te tak te (shunt) chu taksaa thisen petu main artery branch pakhat nen an inzawm a, chu chu lung chhunga thisen phurtu artery a ni. Hei hian lung chhunga thisen kalna tur kawng thar a siam a ni.
2. Second surgery (Glenn Procedure): He surgery hi naute thla 4 leh thla 8 inkar a nih chuan tih thin a ni . Hetah hian a hmaa tube dah tawh chu lakchhuah a ni a, taksa chunglam atanga oxygen tlakchhamna thisen chu lung nen direct-in a inzawm a ni.
3. Third surgery (Fontan Procedure): Hei hi he surgery series hnuhnung ber a ni . Naute hi kum 2 leh kum 4 inkar a ni.Hei hi a inkar ah tih a ni. Hetah hian taksa hnuai lam atanga oxygen tlachham thisen lo chhuak pawh hi lung lam pan nghal a ni.
Heng surgery pathumte hi an tih zawh chuan taksaa oxygen tlachham thisen zawng zawng chu lung dinglamah kal lovin, oxygen dawng turin lungah direct-in a kal ang.
Surgery hnuah eng nge thleng?
Hengte hi operation lian tak tak a nih avangin naute chu damdawi inah, intensive care unit (ICU)-ah, kar khat emaw kar hnih emaw vel a awm a ngai dawn a ni. Thâwk lakna tur ventilator, an thinlung hnathawh enfiahna tur monitor, leh natna tidamtu damdawi ang chi thil an mamawh dawn a ni.
Nausen thenkhat chu operation hnuah hnute an pe thei lo mai thei. Chutiang hunah chuan bawnghnute hi nasogastric tube hmangin pek thin a ni. In lama i haw hnuah pawh i naute rih zawng leh a than dan hi ngun takin i ngaihven tur a ni.
A pawimawh ber chu he naupang hi a dam chhung zawng cardiologist enkawlna hnuaiah a awm a ngai dawn a ni . Hun ruat saah clinic-ah checkup neih a pawimawh hle.
I upat deuh deuh chuan operation tam zawk emaw, enkawlna dang emaw i mamawh mai thei. Tin, medical checkup neih fo hi a pawimawh hle a, a chhan chu arrhythmia leh heart failure ang chi harsatna a awm theih avangin.
Take-Home Thuchah a ni
- Pulmonary atresia hi pianpui lung natna khirh tak a ni a, thinlung atanga lung thlenga thisen phurtu valve chu a block ta a ni.
- A lan chhuah dan ber chu naute hmui leh kut zungtang blue discoloration (cyanosis) a ni. Thâwk harsa leh bawnghnute in duh lohna pawh hmuh tur a awm thei bawk.
- He natna hi naupai lai emaw, naute pian hnu lawkah emaw scan hmangin hriat theih a ni.
- He enkawlna hi open-heart surgery hrang hrang, stage hrang hranga tih thin a ni. Chûngte chuan natna chu tidam lo mah se, naupang chu nun ṭha neih theihna hun remchâng a pe a ni.
- Heng naupangte hian dam chhung zawng enkawl leh cardiologist enkawl an mamawh a ni.
- I fain heng symptoms te hi a neih chuan hlauthawng suh la, a rang thei ang bera doctor pan rawh. Naupang nunna chhanhim nan rang taka hriatchhuah leh enkawl hi a pawimawh hle.











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