I chau reng em, i lu a buai reng em, a nih loh leh stairs chhoh harsa i ti em? Mi pakhatin, "Engvangin nge tunlai hian i sen em em?" Hengte hi thisen tlakchhamna (anemia) chhinchhiahna a ni fo thin. Mahse vawiinah hian natna hlauhawm tak, thisen tlakchhamna thlentu, mi tam takin an hriat ngai loh, mahse kan hriat chian a ngai tih kan sawi dawn a ni. Chu chu Pure Red Cell Aplasia , a tawi zawngin PRCA a ni.
A awlsam zawngin, Pure Red Cell Aplasia (PRCA) hi eng nge ni?
Kan taksa ruh lian tak tak chhungril, ruhro hi thisen siamna factory lian tak ang mai a ni tih han ngaihtuah teh. He factory hi kan taksa mamawh cell chi thum, thisen sen, thisen var, leh platelet siamna hmun a ni. Thisen zam (red blood cells) hna ber chu kan thawk chhuah huna lung chhunga oxygen lo lut chu la in, taksa pum puia cell dang zawng zawngah a sem darh vek a ni.
Tunah chuan Pure Red Cell Aplasia (PRCA) tih dinhmunah chuan thisen sen siamtu factory-a production line chuan hna a thawk tawh lo nghal a ni. Cell chi dang, thisen var leh platelet siam chhuah hi a tlangpuiin a danglam vak lo. Thisen sen siam chhuah chauh a reh chuan taksaa thisen sen awm zat chu a tlahniam zauh zauh a. Hei hi anemia kan tih chu a ni . Taksa pum puia oxygen phur thei tur cell a awm loh chuan a hmaa kan sawi tawh ang chi, hahna leh chak lohna te chu a lo lang tan thin.
PRCA natna lan chhuah dan tlangpui chu engte nge ni?
PRCA hi thisen tlakchhamna nasa tak thlentu a nih avangin thisen tlakchhamna pangngaia hmuh aiin a natna lan chhuah dan a langsar zawk.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Chau | Hna hahthlak tak tak thawh chu sawi loh, ni khat pawh i paltlang thei lo khawpa chau taka inhriatna. |
| Thâwk harsa (Dyspnea) . | Thil tih pangngai tih lai te, kea kal lai te, stairs chhoh lai te pawhin thawk hah lutuk. |
| Luak chhuak thei | Thluak mamawh oxygen a tlem avangin luak chhuak tih hriat. |
| Vun dum (pale skin) a ni | Thisen sen a tlakchham avangin vun, hmui leh nail te chu a sen hring angin a lang a, chu chuan vun chu a rawng pink a pe a ni. |
| Lu na | Lu na hi thluaka oxygen pek tlem vang a ni. |
| Beng chhunga thawm hriat (Pulsatile Tinnitus) . | Lungphun ri ang zela beng chhunga thawm hriat. |
| A rilru natna (Angina) . | Lung ruh (heart muscle)-a oxygen tlakchham vanga rilru natna. |
Engvangin nge hetiang dinhmun tlemte hi a lo awm?
PRCA hi chhan pakhat chauh a awm lo. A thlentu thil engemaw zat a awm. A châng chuan damdawi lam dinhmun dang hnuaia side effect angin a awm thei bawk.
- Autoimmune Diseases: A awlsam zawngin sawi ila, hei hi kan taksa defence system (immune system)-in kan taksa ngei a rawn beih palh hi a ni. A châng chuan he attack hian ruhro chhunga thisen sen siamtu cell te pawh a target thei bawk. Entirnan, PRCA hi natna `(Systemic Lupus Erythematosus - SLE)` leh `(Rheumatoid Arthritis)` te nen a awm thei.
- Thisen Cancer: Thisen kaihhnawih cancer chi hrang hrang, a bik takin Chronic Lymphocytic Leukemia (CLL) leh Large Granular Lymphocytic Leukemia (LGL) te nen chuan PRCA vei theihna a awm.
- Cancerous Tumors: Thymoma hi cancer natna a ni a, chu chu kan rilru chhunga thymus gland-ah a lo awm a. Hei hi PRCA thlentu lian tak a ni thei bawk.
- Viral atanga kai theih: Parvovirus B19PRCA thlentu virus hi a chhan ber a ni. He virus hian ruhro (bone marrow) a stem cells te chu direct-in a bei a, chu chu red blood cells siamtu a ni. HIV, Epstein-Barr virus, leh hepatitis virus vang te pawh a awm thei bawk.
- Bacterial Infection: Bacteria infection na tak, TB ang chi pawhin PRCA a thlen tam lo hle.
- Damdawi thenkhat: PRCA hi damdawi thenkhat side effect angin a awm thei bawk.
- Naupai: A tlem hle a, hmeichhe thenkhat chuan naupai laiin PRCA hun eng emaw chen an nei thei. Mahse, nau neih hnuah chuan a takin a reh tlangpui thung.
He natna hi engtin nge doctor hian a hriat theih ang?
A chunga kan sawi tak symptoms i neih chuan doctor chuan a enfiah hmasa ang che a, chutah chuan test eng emaw zat neih a rawt ang che a, chu chu i natna hriat chian nan a ni.
- Complete Blood Count (CBC): Hei hian i thisen chhunga thisen sen, thisen var leh platelet awm zat a teh a ni. PRCA-ah chuan thisen zam (red blood cells) hi a tlem hle.
- Reticulocyte Count: Hei hian thisen sen puitling lo, ruhro (bone marrow)-a lo piang thar leh thisena dah belh zat a teh a ni. PRCA-ah pawh he zat hi a tlem hle.
- Peripheral Blood Smear: Thisen tla khat lak a, microscope hmanga enfiah a, thisen sen (red blood cells) pianzia leh awm dan enfiah a ni.
- Parvovirus B19 Test: He test hi Viral infection nia rinhlelh a awm chuan tih thin a ni.
- CT Scan: He test hi rilruah ``Thymoma'' ang chi tumor rinhlelhna a awm chuan tih theih a ni.
- Bone Marrow Aspiration/Biopsy: Hei hi natna finfiah nan test pawimawh ber a ni. Anesthesia hnuaiah hip ruh ang chi hmun atanga ruhro sample lakchhuah nan needle te tak te hman a ni. PRCA-ah chuan hei hian ruhro (bone marrow)-ah thisen sen (red blood cells) a tlakchham vek tih a nemnghet thei a ni.
PRCA hi engtin nge enkawl a nih?
PRCA hi natna thlentu hriatchhuah a, chu chhan chinfelna hmanga enkawl a ni.
A pawimawh ber chu he enkawlna hi doctor enkawlna hnuaiah chauh tih tur a ni. Mahni damdawi ei hian nghawng pawi tak a nei thei a ni.
Enkawl dan hrang hrang a awm a:
- Immunosuppressants: Natna thlentu chu immune system hnathawhna lama harsatna a nih chuan a control nan damdawi `(Corticosteroids)` (e.g. Prednisone) leh `(Cyclosporine)` te pek thin a ni.
- Thisen pek dan: 1.1.Thisen zat a tlem hle a, a natna lanchhuahna a nasat chuan a reh thuai nan thisen pek a ni. Mahse hei hi hun eng emaw chen atana chinfelna a ni. Thisen pek chhunzawm zel hian taksaah iron a lo pungkhawm thei a, chuvangin iron tam lutuk paih chhuah nan a hranpaa enkawl (Chelation Therapy) a ngai a ni.
- Surgery: Natna thlentu chu thymus gland tumor (Thymoma) a nih chuan a gland (Thymectomy) lakchhuah nan surgery neih thin a ni.
- Stem Cell Transplant: Genetic condition thenkhatah chuan mi hrisel tak atanga lak chhuah stem cell te chu ruhro hrisel thar siam tumna atan an thlak thin.
- Immunoglobulin Therapy: PRCA hi Parvovirus B19 infection avanga lo awm a nih chuan he enkawlna hian virus hi a control thei a ni.
Enkawlna hrang hrangte hian a side effects te pawh i zir dawn bawk ang.
Treatment zawng zawng ang bawkin PRCA treatment hian side effect engemaw zat a nei thei a ni. Mahse i doctor chuan heng zawng zawng hi a hrilhfiah lawk ang che.
Immunosuppressant damdawi hmansualna (side effects) te
- Acne a lo awm thin
- Zunthlum vei theihna a awm
- Thisen sang lutuk
- Ruh natna (Osteoporosis) a awm
- Rihna a sang chho zel
- Pum natna leh rilru hahna
Thisen pek avanga side effects awm thei
- Khawsik leh allergy (itching) .
- Hri kai theihna a awm
- Thir a tam lutuk
Heng side effects te hi mi zawng zawngah a thleng vek lo va, i doctor chuan a enkawl theih nan a pui ang che. Chuvangin ngaihtuah buai a ngai lo.
PRCA nena khawsak hi eng ang nge ni a, engtin nge ka in enkawl ang?
PRCA hi a chang chuan natna khirh tak a ni thei bawk. Natna hi enkawl hnuah a reh vek thei a, a lo lang leh thei bawk. Chuvangin, he natna nena kan nun hian ngaihtuah tur engemaw zat a awm.
- Doctor hmu fo rawh: Enkawlna hnuah i natna lan chhuah dan a bo a nih pawhin, i doctor-in a tih hun chhungin checkup turin kal ngei ngei tur a ni. Hei hian natna lo kir leh hmaa hlauhawmna awm thei chu a hriat theih nan a pui ang che.
- Maintenance doses: Mi thenkhat chuan natna a lo let leh loh nan damdawi dose hniam zawk an ei chhunzawm a ngai mai thei.
- Nunphung hrisel: 1.1.
- Ei leh in tha: Doctor hnenah iron tamna ei tur leh ei leh in tha tak chungchang zawt la.
- Tui in tam: Taksa tui tlakchhamna tur venna.
- Exercise: I doctor thurawn angin i tana tha tur exercise him tak ti rawh.
- Hri kai laka invenna tur:Kut sil fo thin ang che. Mipui tamna hmunah fimkhur rawh. Vaccine pek ngai awm apiang chu i doctor nen sawiho rawh.
- I natna lan chhuah dan ngaihven rawh: I taksaah inthlak danglamna emaw, chhinchhiahna thar emaw i hmuh chuan doctor hnenah hriattir tur a ni.
Take-Home Thuchah a ni
- Pure Red Cell Aplasia (PRCA) hi natna awm lo mahse na tak a ni a, ruhro hian thisen sen a siam chhuak tawh lo.
- Chumi atanga harsatna lo chhuak ber chu thisen tlakchhamna nasa tak a ni. A lan chhuah dan ber chu hah lutuk, vun rawng hring leh thawk harsa te hi a ni.
- Hei hi chhan tam tak a awm a, immune system lama harsatna, cancer, leh virus infection te hi a pawimawh ber a ni.
- Thisen test leh bone marrow examination te hi a dik taka hriat theih nan a pawimawh hle.
- Natna awm chhan a zirin enkawlna tha tak tak a awm a. Amaherawhchu, natna a lo awm leh theih avangin doctor thupek anga follow-up a pawimawh hle.
- Nangmah emaw, i hriat miin emaw heng symptoms te hi i neih chuan hlau suh la, doctor thurawn la nghal rawh.
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