I thinlung ruh a nghet em? Restrictive cardiomyopathy chungchang hi han sawi ila.

I thinlung chhunga pindan te te te hian hna a thawk tha tawh lo a nih chuan eng nge thleng ang tih i ngaihtuah ngai em? A chang chuan kan thinlung ruh te hi a nghet deuh a, thisen a khat tha thei lo. Chutih hunah chuan kan sawi tur, restrictive cardiomyopathy chu kan nei thei ang. Ngaihtuah buai suh, awlsam takin i vawng ang u.

Restrictive Cardiomyopathy hi eng nge ni?

A awlsam zawngin sawi ila, hei hi thinlung ruh (heart muscle) nena inzawm natna a ni. Kan thinlung hnuai lama chamber pahnih, ventricles , an tih, ruhte chu a nghet lo hle. Rubber band i hrual chuan a hmuna a snap leh ang kha a ni lo a, mahse a taksa ruhte chu a flex tha lo. Chumi awmzia chu heng chamber-te hian thisen mumal taka khat tur hmun an nei lo tihna a ni. Chutiang a lo thlen chuan thinlunga thisen kal chu a tichhe thin.

Hei hi hming dang a awm a, a chang chuan doctor-te pawhin heng hmingte hi an hmang thei bawk:

• `Idiopathic restrictive rilru lam natna`
• Infiltrative cardiomyopathy (thinlung ruh natna, taksa ruh chhunga thil dang lut avanga lo awm) .

He natna hi tuin nge vei tam ber? Engtiang chiahin nge a hluar?

Tu pawhin he natna, `(Restrictive Cardiomyopathy)` hi vei thei mahse, mi thenkhatah chuan a hnuaia awm thenkhat avang hian a tam zawk. Entirnan, `(Sarcoidosis)` (chu chuan `(Restrictive Cardiomyopathy)` a thlen thei bawk) hi hnam thenkhat hmeichhiaah a tam zawk.

Cardiomyopathy hi a awm fo thin. Mi 500 zinga 1 velin a nghawng a ni. Mahse, he cardiomyopathy chi hi a tlem ber . Cardiomyopathy vei zawng zawng zinga 5% vel a ni. Chuvangin, hei hi hriat fo loh thil a ni a, mahse hriat hlawh tak a ni.

Engtin nge restrictive cardiomyopathy hian thinlung a nghawng?

Kan thinlung hi taksa peng mak tak a ni. Chamber pali a nei a, a bik takin taksa ruh atanga siam a ni. Heng chamber te hian thisen chu contract hmangin an pump chhuak thin. Chamber chunglam pahnih chu `Atria` an ti a, a hnuai lam chamber pahnih chu `Ventricles` an ti bawk.

He `(Restrictive Cardiomyopathy)` dinhmunah hian thil thleng chu a hnuai lam chamber (`Ventricles`) ruhte chu a nghet lo va, an elasticity a hloh ta a ni. Tichuan chu pindan chu thisenin a khat kim thei lo. Balloon inflating ang maiin han ngaihtuah teh, balloon hi inflated tha a nih loh chuan boruak tlemte chauh a chelh ang. Hetah pawh hi chutiang chu a ni. Hei hian thinlung chhunga thisen kal dan zawng zawng a tikhawlo a ni.

Eng nge a lan chhuah dan? An hriat chian hma thei ang em?

A châng chuan symptoms a awm lo thei , a bik takin a tir lamah chuan. Mahse natna a zual zel chuan heart failure a awm thei a ni.Flu natna lan chhuah dan inang chiah chiah a lang tan thin. Chutiang chhinchhiahna thenkhat chu hetiang hi a ni:

• Pum khat emaw, rilru hahna emaw.
• Chest pain (chawlh lai emaw exercise lai emaw a awm thei).
• Luak chhuak emaw, muhil emaw.
• Ke leh ke a hring (`Edema`).
• Chau tih hriat reng (`Fatigue`).
• Heart rate dik lo (`Heart palpitations`) tih hriatna.
• Thâwk harsa (Dyspnea), a châng chuan thawhrimna tlêm tê pawhin.
• A taksa rihna a pung nghal.

Pawimawh: Heng symptoms pakhat emaw a aia tam emaw i neih chuan `Restrictive Cardiomyopathy` anga ngaih suh. Amaherawhchu, doctor pan a, thurawn lak a tha ber.

Engvangin nge hetiang dinhmun hi a lo awm? A chhan engte nge ni?

Restrictive cardiomyopathy hi a chhan lian ber ber engemaw zat a awm a. Chu chu damdawi lam thil dang avanga lo awm thei a ni tihna a ni.

• `Amyloidosis` : Hei hi heart muscle-a protein a awm lai a ni.
• Connective tissue natna : Taksa tissue hrang hrang khawih thei natna.
• Hemochromatosis (iron overload) : Taksaah iron a tam lutuk.
• Sarcoidosis : Taksa peng hrang hranga cell chi hrang hrang granulomas an tih te lo awm.

Chu bakah, cancer enkawlna thenkhat hnuah pawh he natna hi a lo awm thei bawk:

• Chemotherapy hmanga enkawl a ni
• Radiation hmanga enkawlna a ni

Engtin nge doctor-te hian he natna hi dik taka an hriat theih? (Diagnosis) tih a ni.

Doctor i pan hunah i natna lan chhuah dan a zawt hmasa ang che a, taksa enfiahna a nei ang a, i thinlung thawk dan a ngaithla ang a, i thisen sang a enfiah ang.

Tichuan, a natna hriat chian nan leh heart chambers (ventricles) te chu a thawk tha em tih en turin echocardiogram (heart scan) an ti thin. Hei hian thinlung hnathawh dan leh ruhro thickness ang chi thil a check thei a ni.

I doctor chuan Restrictive Cardiomyopathy thlen thei tur underlying condition dangte enfiah nan test dang engemaw zat a rawt thei bawk. Chung zingah chuan:

• Thisen leh zun test a ni.
• Chest X-ray neih a ni.
• Thinlung `CT` scan (`Cardiac CT scan`) a ni.
• Exercise stress test neih a ni.
• Lung lam MRI.
• Thinlung PET scan a ni.
• Thinlung dinglam catheter hmanga siam a ni.
• Myocardial biopsy - Hei hi heart muscle sample tlemte lak a, test a ni.
• Genetic testing neih a ni.

Enkawlna a awm em? Engtin nge enkawl a nih?

Vanduaithlak takin he natna, `Restrictive Cardiomyopathy' tia koh hi he natna hi a bik takin a awm a ni.Damdawi a la awm lo. Mahse, doctor-te chuan a chhan bulpui chu an enkawl thei a, a natna lan chhuahna chu an thunun thei a ni.

Lung chak lohna nena inzawm symptom i neih chuan i doctor chuan a hnuaia enkawlna te hi a rawn rawt thei ang:

• Sarcoidosis i neih chuan corticosteroid (steroid-type damdawi) i ei thin.
• Taksa chhunga tui tam lutuk tihtlem nan Diuretics (Damdawi zun tamna thlentu) a ni.
• Heart rhythm mumal lo enkawlna atana damdawi (e.g. `Antiarrhythmics`, `Beta-blockers` emaw `Calcium channel blockers` emaw).
• Therapeutic phlebotomy hi hemochromatosis (iron overload) vei tan a ni.
• `(Amyloidosis)` chi thenkhat tan damdawi bik.

Mi thenkhat chuan a tawpah chuan natna a nasat chuan heart transplant surgery an mamawh mai thei. Symptoms control nan leh nunphung tha tak vawng reng turin palliative care -ah refer theih an ni bawk.

He natna hian eng harsatna nge a thlen theih?

`Restrictive Cardiomyopathy` vang hian harsatna dang engemaw zat a awm thei bawk. Chungte chu:

• Heart arrhythmia : Thinlung thawk mumal lo.
• Heart failure : Thinlung hian taksaah thisen a pump tling thei lo.
• Thisen zam leh stroke (`Thromboembolism` or `Stroke`) : Thisen zam hian stroke a thlen thei.

A hlauhawmna tihziaawmna turin eng nge kan tih theih ang?

Hetiang dinhmun, ``Restrictive Cardiomyopathy,'' tih hian i thinlung hian thisen pump turin a thawkrim zawk a ngai tihna a ni. Chuvangin, i thinlunga hnathawh tur tihtlem nan i doctor nen inbiakna neih a pawimawh hle.

Restrictive Cardiomyopathy thlentu damdawi lam dinhmun hnuaia awmte ven a harsat laiin, i thinlung hriselna atana a hnuaia mite hi i ti thei ang:

• I thisen sang control rawh .
• I taksa rihna hrisel tak vawng reng rawh .
• Stress tihziaawm rawh .

He natna nen hian eng nge i beisei ang?

Restrictive Cardiomyopathy hi natna khirh tak a nih avangin i thinlung hriselna atana i tih theih dan tur chungchangah doctor nen inbiakna neih fo a pawimawh.

He natna hi eng chen nge i dam theih ang tih hi mi hrang hrangah a inang lo. I doctor chuan nang leh i chhungte hnenah natna a zual zel dan tur leh eng nge i beisei tur tih a hrilhfiah ang che.

Engtin nge ka in enkawl ang? (Mahni inenkawlna) .

A pawimawh ber chu doctor thupek dik taka zawm a, a hun taka damdawi pek zawng zawng ei hi a ni. Chu bakah, i doctor chuan nunphung tihdanglam turin a hrilh thei bawk che a, chungte chu:

• Chaw hrisel chi tlem (sodium-controlled) .Lak tur chuan.
• Exercise tih (doctor-in a hrilh ang chauh).

Engtikah nge damdawi lam thurawn i lak nghal ang?

I heart failure symptoms chu a na zual nia i hriat emaw, symptom thar i neih chuan i doctor ko nghal rawh .

Tin, hetiang emergency a lo thlen chuan damdawi inah kal nghal tur a ni (Sri Lanka-a awm a nih chuan 1990 ang chi emergency number call rawh):

• I rilru natna nasa tak i neih chuan .
• I faint a nih chuan .
• Vawikhatmah thawk harsatna nasa tak i neih chuan .

Hriat reng tur: Thinlung hi kan nunah taksa peng pawimawh tak a nih avangin kan enkawl a pawimawh hle.

Take-Home Thuchah a ni

Okay, chuvangin kan sawi tawh `(Restrictive Cardiomyopathy)` chungchanga hriat reng tur awlsam tak tak te chu hetiang hi a ni:

• Hemi kawngah hian thil thleng chu thinlung hnuai lam (ventricles)-a ruhte chu a nghet lo va, an inthlak danglam theihna a hloh ta a ni .
• Chuvângin, chu cell-te chuan thisen an khat ṭha thei lo .
• Tichuan thinlung hian taksaah thisen pump turin nasa zawkin hna a thawk a ngai a , chu chuan ``Heart failure`` a thlen thei a ni.
• Hei hi damdawi chiang tak awm lo mah se, a chhan bulpui enkawl leh a lan chhuah dan control hmanga enkawl a ni .
• Hemi chungchangah hian zawhna emaw rinhlelhna emaw i neih chuan i doctor nen inbiakna neih hlau suh .

Hriselna tha neih duhsakna kan hlan e!

` Restrictive Cardiomyopathy, lung natna, thinlung ruh natna, thawk harsa, rilru na, thinlung natna, damdawi hmanga enkawl