'Schwannoma' tih thumal hi i hre ngai em? Hei hi i tan chuan thumal thar a ni mai thei. A nihna takah chuan kan nervous system-a tumor chi khat a ni. Lungngai suh, a hlauhawm reng reng lo. A awlsam zawngin, i hriatthiam theih dan tur angin sawi ila.
‘Schwannoma’ tih hi eng nge ni?
A awlsam zawngin sawi ila, he ‘Schwannoma’ hi kan taksaa ‘Schwann cells’ atanga lo piang chhuak tumor a ni. Tunah chuan heng ‘Schwann cells’ te hi eng nge an nih i ngaihtuah mai thei, a dik em? Hengte hi kan ‘peripheral nervous system’ cell te an ni a, chu chu thluak leh ruhro atanga chhuak nerve fiber vel a sheath siamtu cell chi khat a ni. Electric wire vel plastic khuh ang mai a ni. Heng cell te hian kan nerve te hi an venghim a, nerve message te chu rang taka kal tir turin an pui bawk. Chuvangin heng ‘Schwann cells’ te hi heng tumor te hi ‘Schwannomas’ an tih te siamtu an ni.
A tam zawkah chuan 90% vel chu heng ‘Schwannomas’ te hi benign an ni . Chumi awmzia chu taksa pum puiah an darh lo, hmun khatah an awm reng tihna a ni. Mahse, a tlem hle a, malignant an lo ni thei . Chutiang a nih chuan tlem tal i fimkhur a ngai a ni. Heng tumor te hi a tlangpuiin an lo thang zawi zawi hle .
Heng tumor te hi taksa khawi hmunah pawh, nerve awmna hmun apiangah a lo awm thei a ni. Entirnan, kan thluak atanga kan beng thlenga kal nerve-ah an tam ber. Hei hi ‘vestibular schwannoma’ emaw ‘acoustic neuroma’ emaw an ti bawk. Malignant schwannomas hian kea ‘sciatic nerve’, kut chhunga ‘brachial plexus’, leh hnungzang hnuai lam ‘sacral plexus’ te a nghawng tam ber.
Schwannomas hi neurilemmomas emaw neuromas emaw an ti \hin. Cancer vei an nih chuan soft tissue sarcomas tia sawi theih a ni.
A tha ber chu, 90% vel chu he ‘Schwannoma’ hi tumor pakhat chauh angin a awm thin .
‘Vestibular Schwannoma’ tih hi eng nge ni?
Vestibular schwannoma chungchang hi tlem kan sawi tawh a. Hei hi schwannoma chi khat a ni a, kan hriatna leh balance siamtu beng chhunga nerve atanga intan a ni. Hei pawh hi a tlangpuiin cancer a ni lo va, a thang zawi zawi bawk.
Mahse, he tumor hi a lo lian chhoh zel chuan hriatna leh balance nena inzawm nerve te chu a press tan ta a ni. Chu chu a ni:
- Beng natna a hriatna chu zawi zawiin a tlahniam tan thin .
- Tinnitus hi beng chhunga ring (ringing...like sound) a ni .
- AchanginLuak chhuak ang maiin a awm.
‘Schwannoma’ hi thluaka tumor a ni em?
Tunah chuan he ‘schwannoma’ hi thluaka tumor a ni reng em tih i ngaihtuah mai thei. Dik tak chuan a ni lo. Thluak chhungah emaw, lu chhungah emaw a lo thang lian thei a, mahse taksa hmun dangah pawh nerve-ah a lo thang lian thei bawk. A chhan chu, kan sawi tawh ang khan hengte hi ‘Schwann cells’ atanga lo piang an ni a, chu cell te chu kan ‘peripheral nervous system’ ah a awm a, chu chu thluak atanga taksa peng dang thlenga kal nerve-ah te a awm a ni.
Mahse, kan sawi tam ber chi, ‘Vestibular Schwannoma’ tih chu thluaka tumor anga ngaih a ni .
Schwannoma hi tuin nge vei?
Heng ‘Schwannomas’ te hi kum 50 leh 60 inkar ah an lo awm tam ber a, naupang te te ah an tlem hle.
Schwannomas hi mi hrisel tak takah random takin a lo awm fo thin. Mahse, a then phei chuan schwannomas hi genetic conditions neurofibromatosis type 2 (NF2) , schwannomatosis , emaw Carney complex te avang pawhin a lo awm thei bawk. Heng genetic condition nei te hian schwannoma pakhat aia tam an vei tam zawk.
Schwannoma hi engtiang chiahin nge a awm?
Schwannoma hi tumor a awm lo hle a ni . Ngaihtuah teh, America ang ramah pawh kum tin mi sanghnih aia tlem loin he natna hi an vei thin. Cancer nei lo (benign) Schwannoma zinga 60% chauh hi a hmaa kan sawi tawh ‘vestibular Schwannoma’ an ni.
Schwannoma natna lan chhuah dan chu engte nge ni?
Because these Schwannomas grow very slowly , kum tam tak chhung chu symptoms an lantir lo mai thei. Tin, heng tumor te hi taksa hmun hrang hrangah a lo awm theih avangin, a lan chhuah dan chu mi hrang hrangah a inang lo thei hle bawk . Mi thenkhat chuan symptom engemaw zat an nei thei a, a na lo hle thei a, thenkhat erawh chu a na hle thei bawk.
Heng a lan chhuah dan tlangpui thenkhat chu hetiang hi a ni:
- Lump emaw tumor emaw hmuh theih . Hei hi khawih emaw, hmet emaw chuan a hrehawm deuh thei.
- A rilru a buai em em a .
- Muscle chak lohna .
- Ant crawling emaw pin leh needle emaw ang maiin a lang (doctor-te pawhin hei hi ‘paresthesia’ an ti bawk).
- Natna nasa tak, kang, hliam, emaw, hliam na tak ang maia hriatna .
Pawimawh: Heng symptoms te hi natna dang vang pawh a ni thei a, chuvangin hetiang thil i neih chuan doctor pan a, thurawn lak a tha ber.
Tumor awmna hmun a zirin symptoms a danglam dan
- Vestibular Schwannoma natna a niKan sawi tawh ang khan, a vei te hian hriatna leh balance lama harsatna an nei thei a , beng ri (tinnitus) pawh an nei thei bawk.
- Heng tumor te hi i hmai nerve -ah a lo awm a nih chuan, i ei theihna te, i mit a tihchet theihna te, leh i ei theihna te a nghawng thei a ni . I hmai sir khat hman theihna pawh i hloh thei (facial paralysis) .
- Kea sciatic nerve -ah schwannoma a lo awm chuan hnungzang natna leh ke hnuai lam atanga chhuak natna a thlen thei a, chu chu herniated disc ang chi a ni
Eng thilin nge Schwannoma hi a thlen?
Dik tak chuan, a tam zawkah chuan Schwannoma hi a chhan dik tak hi hriat a ni lo . 90% chauh hi a chang chuan a thleng thin.
Mahse, a hmaa kan sawi tawh ang khan Schwannomas hi Carney complex, Neurofibromatosis type 2 (NF2), leh Schwannomatosis te ang chi genetic condition avang hian a lo awm thei bawk. Genetic study-ah chuan kan chromosome 22-a NF2 gene hi Schwannomas lo awm chhan ber a ni tih hmuhchhuah a ni.
Engtin nge Schwannoma hi hmuhchhuah a nih?
Heng tumor te hi an lo thang zauh zauh avangin kum tam tak chhung chu symptom i neih hmain an awm thei a ni. Chuvangin diagnosis neih nan hun rei tak a ngai thei . Symptoms i neih chuan i doctor chuan test thenkhat a order mai thei. A châng chuan, chhan dang vanga scan an tih laiin tumor chu accident-in hmuh a ni ṭhin.
Schwannoma hriat theihna tura pui thei imaging test te chu:
- MRI (Magnetic Resonance Imaging) scan : Hei hi test na tak a ni. Magnet lian tak, radio wave leh computer hmangin taksa chhunga taksa peng leh thil awmte chu chiang takin a tarlang a ni. Hei hi Schwannoma hmuhchhuah leh hriatchhuahna atana test tha ber a ni .
- CT (Computed Tomography) scan : Hei hian X-ray leh computer hmangin taksa chhunga thil awmte thlalak a la thin.
- Ultrasound scan : Hei hian high-frequency sound wave hmangin taksa chhunga taksa peng emaw soft tissue emaw live thlalak emaw video emaw a la thin. Doctor te chuan hei hi vun hnuaia schwannomas hmuh nan an hmang thin.
I doctor pawhin schwannoma emaw cancer emaw a nih tak tak theih nan biopsy a ti thei bawk. Hei hian needle hmanga lump sample tlemte lak a huam a ni. Pathologist pakhat a ni, chu chu hetianga tissue sample enfiahtu specialist doctor chuan he sample-a cell awmte hi microscope hmangin a en a, chutah chuan test dang a nei leh a, hei hi eng ang tumor nge a nih chiah tih a hriat theih nan.
Schwannomas hi engtin nge an enkawl?
Schwannoma enkawlna chu tumor awmna hmun, a lo thang chak dan, leh i natna lan chhuah dan te a innghat a ni .
Enkawlna kawng hrang hrang a awm a:
- Observation/watch and wait : Tumor hi cancer (benign) a nih loh chuan, a lo thang zawi hle a, symptoms i neih loh emaw, a tlem lutuk emaw a nih chuan i doctor chuan enkawl ai chuan ngun taka enfiah a rawt thei ang. Chumi awmzia chu tumor a lian chho zel em tih emaw, symptom thar a lo lang em tih emaw an scan fo ang che tihna a ni. Mahse, a lian deuh emaw, a hnua symptom i neih chuan enkawl an rawt mai thei.
- Surgery : Tumor chu a lo thang chak lutuk a, symptoms a tihbuai che a nih chuan emaw, harsatna dang a thlen a nih chuan doctor chuan operation tihchhuah a rawt thei ang. A tlangpuiin tumor pumpui chu lakchhuah vek a ni a, mahse a chang chuan tumor awmna hmun azirin surgeon chuan tumor thenkhat chauh a la chhuak thei a ni. Schwannomas hi nerve chhehvel sheath-ah a lo awm a, chuvangin nerve tichhe lovin operation pawh tih theih a ni fo . Mahse, vestibular schwannomas avanga operation hnuah hriatna hloh theihna a sang zawk .
- Radiation therapy : Hei hian technique bik, stereotactic radiosurgery (SRS) , hmangin, radiation beams focused tak tak thawn chhuakin tumor chu a tichhia a ni. If the tumor is near important blood vessels or nerves , i doctor chuan operation avanga harsatna awm thei lo turin he radiation therapy chi hi a rawt thei ang.
Hemi bakah hian , immunotherapy leh chemotherapy damdawi te hi malignant schwannoma tan pawh hman a ni.
Schwannoma hi ven theih a ni em?
Vanduaithlak takin tunah hian heng ‘schwannomas’ te hi ven dan tur a awm lo . A tam zawkah chuan random takin an lo thang lian a, a chhan hriat loh. Case 10% vel chu genetic condition thenkhat nena inzawm a ni a, hei vang hian miten heng tumor te hi an nei tam zawk a ni.
I chhungkuaa mi tu emaw chu neurofibromatosis type 2 (NF2), schwannomatosis, a nih loh leh Carney complex vei nia hriat a nih chuan i doctor nen inbia ang che . Nang pawhin he natna hi i vei em tih enfiah turin genetic counselling neih a rawt thei bawk.
Schwannoma natna vei tur chu eng nge ni?
Hei hi Schwannoma natna a ni.Prognosis, chu chu natna hian hun rei tak chhunga a nghawng dan tur che hi thil engemaw zatah a innghat a ni:
- Taksa chunga tumor awmna hmun .
- Tumor hi engtiang chiahin nge a lian .
- Surgery tih a nih chuan tumor engzat nge lakchhuah a nih .
- Tumor chu cancer (malignant) emaw, benign (benign) emaw a nih pawhin .
A tlangpuiin, schwannoma awm theihna tur hmalam hun chu a tha hle . A tam zâwk chuan, tumor chu lak chhuah vek a nih chuan a lo ṭhang leh tawh lo vang .
He ‘Schwannoma’ avanga harsatna awm thei tam zawk hi chu tumor lakchhuahna tur operation hnuah a thleng thin . A bik takin a hnuaia mite hian operation hnuah harsatna a thlen thei a ni:
- Tumor a lian hle a nih chuan .
- Tumor chu taksa chhung thuk takah a awm chuan .
- Tumor hi i kut a nerve lian pathum zinga pakhat ulnar nerve atanga tan a nih chuan.
Schwannoma chungchangah hian engtikah nge doctor i hmuh ang?
Schwannoma i vei tih hmuhchhuah a nih chuan, i doctor pan nghal a pawimawh a, i schwannoma enkawl dan tur , symptom thar i neih emaw, i symptoms awmsa a zual emaw pawh nise .
I doctor chuan enkawl lohvin tumor chu enfiah turin a rawt che a nih chuan kum khatah vawi khat tal checkup turin i hmu tur a ni . Chumi hnuah chuan imaging test (MRI ang chi) a ti thei a, tumor lo thang chak dan leh a dinhmun a enfiah thei bawk.
Tumor i nei tih i hriat chuan hlauhna i neih hi thil pangngai a ni. Mahse thu lawmawm tak chu schwannoma hi tumor chi khat a ni a , a tlangpuiin cancer a ni lo va , a lo thang zawi zawi a ni . I medical team chuan i tana enkawlna tur ruahmanna tha ber tur ngaihtuah turin an pui ang che. Tumor enfiah mai mai emaw, surgery hmanga lak chhuah emaw, thil dang emaw pawh a ni thei. Zawhna zawh hlau suh, eng pawh ni se . I doctor chu tanpui turin a awm reng a ni.
Take-Home Thuchah a ni
Okay, chuti a nih chuan tunah chuan kan sawi tawh kha ngaihtuahna tha tak i nei ta a ni, Schwannoma. Hriat reng tur pawimawh thenkhat chu hetiang hi a ni:
- Schwannoma chu nerve vel Schwann cell atanga lo chhuak tumor a ni. A tam zawkah chuan hengte hi cancer vei an ni lo .
- These grow very slowly , chuvangin a chang chuan kum tam tak a ngai thei a, symptoms a lan theih nan.
- Taksa chhunga tumor awmna hmun a zirin symptoms a inang lo hle . Entîr nân, hriatna hloh, beng ri, bengchheng, natna, leh taksa ruh chak lohna te a awm thei.
- Hengte hi lo thang lian rawh se.A chhan dik tak chu hriat a ni lo fo va, mahse, chu chu genetic condition ṭhenkhat nêna inzawm a ni thei .
- Hengte hi MRI scan hmanga hriat theih dan ber leh tha ber a ni.
- Enkawlnaah chuan tumor enfiah te, operation hmanga lak chhuah te, a nih loh leh radiation therapy te pawh a tel thei a ni. Enkawlna chu tumor chi leh awmna hmunah a innghat a ni.
- Don’t worry , Schwannoma hi a tam zawkah chuan enkawl tha, tihdam theih a ni. Thil ngaihtuah leh zawhna i neih chuan i doctor nen inbia ngei ang che.
` Schwannoma, neuromas, Schwann cells, vestibular schwannoma, nervous system, cancer nei lo tumor, MRI scan te hi a awm thei











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