A chang chuan i hmui a vawt hle, cotton wool ball ang maiin i hria em? A nih loh leh i mitmengah hian kang emaw, i hrual emaw, i mitmengah sand awm ang maiin i kang reng em? Hengte hi thil pangngaiah kan ngai a, mahse a chang chuan kan taksa chhunga thil dang thleng chhinchhiahna a ni thei. Vawiin hian chutiang dinhmun pakhat, Sjogren’s Syndrome chungchang kan sawi dawn a ni. Hei hi hun rei tak chhunga awm tur ni mahse, ngaihtuahawm tur a ni lo. Inenkawlna mumal tak i neih chuan nun pangngai, hlim takin i nung thei a ni.
A awlsam zawngin, Sjogren’s Syndrome hi eng nge ni?
Hei hi hriatthiam a awlsam hle. Kan taksa hian defense system a nei a, chu chu immune system kan ti a ni . Kan taksaa lut hrik leh virus dotu leh natna laka min vengtu thisen var (white blood cells) te hi a ni. Mahse, Sjogren’s Syndrome hi autoimmune natna a ni .
A awlsam zawngin, kan defense system ngei pawh a thawk tha lo a, ramdang hrik ni lovin kan cell hrisel tak takte chu a bei tan ta a ni. Hetah hian he attack hian kan taksaa tui siamtu glands te a target ber a ni. Chu chu mittui siamtu gland leh ka chhunga hmui siamtu gland te tihna a ni . Chuvangin heng glands te hi an chhiat chuan mittui leh hmui te an siam tha thei lo. Chumi avang chuan mit, hmui leh taksa peng dangte chu a lo vawt ta a ni.
Hei hi dam chhung zawnga natna a nih thu i hriat hian tlem a lungkham hi thil pangngai a ni. Mahse, Sjogren’s vei tam zawk hi hriselna tha takin an khawsa a, harsatna lian tham an nei tlem hle tih hre reng ang che.
Engvangin nge hetiang hi a lo awm? Risk factors te chu engte nge ni?
Doctor-te chuan hei hi eng nge a thlen tih chiang takin an la hre lo a, mahse thil engemaw zat a awm nia ngaih a ni.
- Genetic influence : I genes hian he natna hi a vei duhna tlem a nei thei.
- Trigger: Bacteria emaw virus emaw infection hian he natna lo chhuahna tur trigger angin hna a thawk thei a ni.
Hetiang hian han ngaihtuah teh. Sjogren natna nena inzawm genetic defect i nei a, viral fever ang chi i nei bawk. Tichuan i immune system a kick in. Mahse, chu genetic defect avang chuan thisen var te chuan natna hrik chauh ni lovin, kan hmui leh mittui siamtu gland te pawh an rawn bei tan ta a ni. A chhan chu he indona hi a la chhunzawm zel a, enkawlna i hmuh loh chuan a symptoms a la awm chhunzawm zel dawn a ni.
Chu bakah, risk factor dang engemaw zat a awm bawk:
- Kum: Kum 40 chunglam ah a tam zawk tlangpui a, mahse tleirawl leh naupangah pawh a awm thei bawk.
- Gender: Hmeichhiain he natna hi mipa aiin a let 10 in an vei tam zawk.
- Autoimmune natna dang: Sjogren’s vei zinga a chanve vel chuan autoimmune natna dang, lupus emaw rheumatoid arthritis emaw an nei bawk.
Sjogren’s Syndrome natna lan chhuah dan chu engte nge ni?
Heng symptoms te hi mi zawng zawng tan a inang vek lo. Mi thenkhatin pakhat emaw pahnih emaw an nei a, thenkhat erawh chuan tam tak an nei thei thung. Heng symptoms te hi eng nge ni tih han thlir ila.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Symptoms Main leh Most Common | |
| Kawng a vawt | Kawng chhung lam chu chalk emaw cotton wool emaw ang maiin a lang. Thusawi leh chaw ei a harsa thei hle. Hei hian ha a tichhe thei a, ha natna a thlen thei a, oral thrush (candidiasis) a thlen thei bawk. |
| Mit a vawt | Kang, itching, mit ah gritty feeling a awm. Light sensitivity (mit blue) leh blurred vision a awm thei. |
| Symptoms awm thei dang | |
| Taksa hmun dangah a vawt | Thlarau, hmui, vun, leh hnar vawt. Vagina a vawt. |
| Taksa na leh a hring | Joint swelling, na, leh stiffness te a awm bawk. Muscle na a na. Kawng leh hmaiah glands a hring chhuak. |
| A tlangpuiin a dangte | Chauhna awm reng. Thil ngaihtuah leh hriatreng harsa. Lu na. Skin rashes leh ni êng laka sensitivity. Dry cough emaw thawk harsa emaw. |
Sjogren’s Syndrome chi hnih a awm
Doctor, he natna chi hnih hi ka hrilh thei ang che:
1. Primary Sjogren’s syndrome: Chumi awmzia chu Sjogren’s chauh i nei tihna a ni a, immune disease dang a awm lo.
2. Secondary Sjogren’s syndrome: Chumi awmzia chu Sjogren’s syndrome hi immune system natna dang, rheumatoid arthritis emaw lupus emaw nen a inzawm tihna a ni.
Engtin nge natna hi kan hriat theih ang?
He natna lan chhuah dan hi natna dang (e.g., fibromyalgia) nen a inang a, immune natna dang nen a awm dun fo avangin, a chang chuan diagnosis hi a buaithlak deuh thei a ni.
I doctor chuan a enfiah ang che a, hetiang zawhnate hi a zawt ang che:
- I mit a na reng em? An kang em?
- I ha hi a chhe fo em?
- I hmui leh hmui a vawt em?
- I ruh natna emaw, i ruh (stiffness) i nei em?
Tichuan, an diagnosis finfiah nan test eng emaw zat an order ang.
- Thisen test: Hengte hian i thisena antibody awm zat a teh a, chubakah i taksaa inflammation awm zat a teh bawk. Sjogren’s vei tam tak chuan an thisenah antibody chi hrang hrang an nei a.
- Mit leh hmui test: 1.1.
- Schirmer test: I mit a vawt zia hriat nan lehkha phek te tak te chu mitmeng hnuai lam hnuaiah dahin mittui tlak zat teh thin a ni.
- Slit lamp examination: Mit chunglam chu magnifying device hmanga enfiah a ni.
- Salivary gland biopsy: Salivary gland te tak te tak te hi hmui hnuai lam atanga lak chhuah a ni tlangpui.
Engtin nge enkawl leh enkawl dan?
He natna hi a dam kim thei lo a, mahse a natna lan chhuah dan thunun thei tur leh nun hrisel tak nei thei tur enkawlna tam tak a awm a ni.
Mit vawt enkawlna
I doctor chuan mittui tlakna tur `artificial tears` an tih chu a pe thei ang. Nitin i hman a ngai a ni. Zanah hman tur gel thick tak tak a awm bawk. Hengte hian a puih loh chuan `(Restasis)` ang damdawi hi pek theih a ni. Enkawlna dang chu `punctal occlusion` a ni. Hetah hian tear duct-ah hian plug te tak te dahin a block a ni. Hei hian mittui chu mit chungah rei zawk a awm thei a, a hnim reng bawk.
Kawng vawt tan enkawlna
Doctor chuan pilocarpine ang chi damdawi a rawt thei a, hei hian ka chhunga hmui siam chhuahna a tichak a ni. Tin, artificial saliva spray pawh a awm bawk. A pawimawh ber chu ha enkawltu pan fo a, i ha hriselna enkawl hi a ni. A chhan chu hmui a tlakhniam chuan ha chhe theihna a sang chho zel a ni.
Symptom dang a awm chuan enkawlna
Joint pain hi painkiller emaw natna tidam thei damdawi hydroxychloroquine emaw hmanga enkawl theih a ni. A chang chuan taksa chhungril peng hrang hrangte a nghawng a nih chuan steroid prednisone emaw methotrexate emaw te hi hun rei lote chhung atan pek theih a ni. Heng zawng zawng hi i doctor-in a rel vek a ni.
In lama i tih theih tur damdawi awlsam tak tak
Damdawi lam enkawlna rual hian in lama i tih theih thil awlsam tak takte aṭangin hahdamna nasa tak i hmu thei bawk.
- Kawngkhar vawt:
- Nilengin tui tlem tlem in in thin ang che.
- Sugar tel lo gum ei emaw, lozenge ei emaw hian hmui a tipung thei a ni.
- Chaw rimtui, chi, hnim, leh a vawt (biscuit ang chi) ei loh tur.
- Ni khatah vawi hnih ha sil thin ang che. Zu awmna mouthwash hmang suh.
- Meizial zu leh cigarette meikhu laka inhriat loh vek tur a ni.
- Mit leh vun vawt:
- Meikhu, leivut, leh thli tleh nana hmunte chu pumpelh rawh.
- Computer i hman hunah chawlh hahdam fo thin ang che.
- In chhunga humidity awm reng nan humidifier hmang ang che.
- Inbual dawnin tui lum aiah tui lum hmang zawk ang che.
- Nitin i vunah moisturizer tha tak hnawih thin ang che.
Take-Home Thuchah a ni
- Sjogren’s Syndrome hi keimahni taksa hriselna (immune system) a tha lo vanga lo awm a ni. Lungngai suh, kai theih a ni lo.
- A lan chhuah dan ber chu hmui leh mit vawt hi a ni . Tin, ruh natna leh hahna ang chi symptoms te pawh a awm thei bawk.
- He natna hi tihdam kim theih ni lo mah se, damdawi inenkawlna mumal tak leh nunphung awlsam taka tihdanglam a nih chuan a natna lan chhuah dante chu uluk taka thunun theih a ni a, nunphung pangngaia nunpui theih a ni.
- Heng symptoms te hi i neih chuan, chiang takinDoctor hmu la, thurawn la rawh.
- I ha hriselna hi a bik takin enkawl rawh. Ha enkawltu hmu fo ang che.
Sjogren’s Syndrome, hmui ro, mit ro, autoimmune natna, ruh natna, autoimmune natna











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