Aw, i naute hi a kut zungtang tawi deuh emaw, fused emaw neiin a piang em? Hei hi i hmuh hian nu i nih angin i lungngai hle a, i hlauthawng hle a, chu chu thil pangngai tak a ni. Damdawi lamah chuan he natna hi `(Symbrachydactyly)` kan ti a. A hming chu mak deuhin a lang thei a, mahse, i hriat chian chuan i hlauhthawnna chu nasa takin a tlahniam ang. Hemi chungchang hi chipchiar takin sawi ila, kan sawi dawn em ni?
Hei hi eng nge ni (Symbrachydactyly)? A awlsam zawngin i hrethiam ang u!
A awlsam zawngin, `(Symbrachydactyly)` hi pian tirh atanga awm thin natna a ni . Hei hi naute kut zungtang (leh a chang chuan ke ruh, mahse a tam zawkah chuan kut) a lo thang tha lo a nih chuan a ni. Chumi awmzia chu kut zungtang chu a tlangpui aia tawi zawk a ni thei a, kut zungtang pahnih emaw pathum emaw a inzawm khawm thei a, a chang chuan kut zungtang thenkhat chu a bo vek thei tihna a ni. Hei hian kut lan dan bakah a hnathawh dan a nghawng thei a ni.
Kan kut zungtang panga hian thil engzat nge a tih theih tih hi han ngaihtuah teh. Thil te tak te chelh, ziak, ei, engkim. Chuvangin, he natna neia piang naute hian a harsat deuh mai thei. Mahse lungngai suh, tunlaia damdawi hmanraw changkang tak takte nen hian he natna hi a tam zawkah chuan tihdam theih a ni.
He natna hi engtiang chiahin nge a awm (Symbrachydactyly)?
Hei hi a takah chuan thil awm lo tak a ni . Khawvel pumah kum tin nausen piang 32,000 zinga pakhat vel chauhvin he natna hi an vei (Symbrachydactyly). Chuvangin, hei hi i harsatna mai a ni lo va, a tlem hle bawk.
Engtin nge Symbrachydactyly hian naute taksa a nghawng?
A nghawng ber chu kut hnathawh leh hmel lan danah a ni . Kut zungtang chhiatna avang hian naute tan thil man thiam leh kut hnathawh a harsa thei hle. Kut lan dan pawh kut pangngai nen a danglam thei bawk.
Mahse hriat tur pawimawh tak chu a tam zawkah chuan he dinhmun hian kut pakhat chauh a nghawng (`(Unilateral)`) . Kut pahnih a nghawng hi a tlem hle.
Doctor-te chuan he natna (Symbrachydactyly) hi chi liah an ṭhen a. Chutiang chi hrang hrangte chu tlem han sawi ila.
(Symbrachydactyly) chi hrang hrangte chu engte nge ni?
He classification hi kut zungtang chunga a nghawng dan a zirin a ni.
1. Kut tawi tak nei symbrachydactyly (Type 1): .
Hetiang chiah hian naute hian kutpui leh kut zungtang pali zawng zawng a nei thei. Mahse, heng kut zungtang te hi a tlangpui aia tawi zawk an ni . Kut zungtang (`(Phalanges)`) ruh thenkhat pawh a bo thei bawk.
2. Oligodacylic symbrachydactyly (Type 2) a ni a, a chhuahna tur hmun leh a hmanna tur a awm lo.
Chutiang a nih chuan naute chuan kutpui leh pinky (kut zungtang te tak te) a nei thei a, mahse an inkar kut zungtang lai tak chu a awm lo thei a, a lo thang tha lo thei bawk . A chang chuan hei hi "atypical cleft hand" ang maiin a lang thei.
3. A rilru a hah lutuk chuan a rilru a buai em em a.A rilru a buai em em a, a rilru a hah em em bawk a. (Type 3):
A hming ang bawkin, hetiang dinhmunah hian naute hian kut zungtang pakhat chauh a puitling (a tlangpuiin kutpui) a nei a ni . Kut zungtang dang pali chu zung te te (`(Remnants or nubbins)`) emaw, a then lo thanglian deuh emaw pawh a ni thei. Chumi awmzia chu ruh leh ruh ang chi thil te hi a insiam tha lo tihna a ni.
4. Kut zungtang engmah nei lovin type (`(Peromelic symbrachydactyly - Type 4)`):
Hei hi a na ber a ni. Chutiang a nih chuan kutpui emaw kut zungtang dang emaw pawh a nghawng dawn lo .
I naute hian eng chi pawh nei se, doctor-te chuan a pian tirh atangin an hmuchhuak ang. Chumi hnuah chuan pediatric hand surgeon hnenah an refer mai thei che a ni .
(Symbrachydactyly) natna lan chhuah dan chu engte nge ni?
Hetiang dinhmun chhinchhiahna awmchhun leh ber chu naute kut zungtangte chu a tawi emaw, a inzawm khawm emaw, a pian tirh atanga a bo emaw hi a ni . Hei hi kawng khatah hmuh tur a tam ber.
Heng finger deformities avang hian heng underlying tissue-ah hian thil danglam a awm thei bawk:
- Ruh (`(Ruh)`) .
- Muscles (`(Muscles)`) te hi a tha hle.
- Ligaments (ligaments) te
- Tendons a ni
- Nerves (`(Nerves)`) te hi a awm a.
Eng thilin nge Symbrachydactyly hi a thlen?
Dik tak chuan `(Symbrachydactyly)` awm chhan dik tak hi hmuh a la ni lo . Specialist thenkhat chuan nausen pum chhunga naute a lo thanglian mek laia naute kut a thisen kalna tibuaitu `(Vascular dysgenesis)` an tih natna avanga lo awm a ni thei niin an ngai. Chumi awmzia chu thisen kal dan a that loh chuan kut peng hrang hrang a thang tha lo tihna a ni.
A pawimawh ber chu hei hi genetic disorder emaw, hereditary issue emaw a ni lo. Chumi awmzia chu nu leh pa pakhat mah nei lo mah se naute chuan a nei thei tihna a ni a, chutiang natna nei chuan an fate hnenah a pe chhuak dawn lo tihna a ni. Hei hi random occurrence a ni. Chuvangin, lungngai suh la, "Ka sualna a ni em?"
Engtin nge (Symbrachydactyly) hi kan hriat theih ang?
A tam zawkah chuan doctor-te chuan naute a pian veleh he natna hi an hmuchhuak thei a ni . ``Symbrachydactyly`` a nih leh nih loh leh, a nih chuan eng chi nge tih chu naute kut a inthlak danglamna enin an hre thei a ni.
A châng chuan, naupai laia ultrasound scan (`(Prenatal ultrasound)`) i neih lai hian he natna hi hriat hmasak theih a ni.
Enkawl tan hmain naute kut chhunga ruh awm dan enfiah nan X-ray tih theih a ni.
(Symbrachydactyly) hi eng enkawlna nge ni?
A tam zawkah chuan Symbrachydactyly enkawlna ber chu operation a ni.Mahse, naute zawng zawng hian operation an mamawh vek lo va, nausen hrang hrangah surgery mamawh chi hrang hrang a inang lo va, an dinhmun a zirin a inang lo.
Surgery hmanga enkawl a ni
A tlangpuiin, doctor-te chuan naute kum khat emaw kum hnih emaw vel a tlin hma chuan operation an rawt lo , a chhan chu chutih lai chuan naute tissue te chu a lo thang lian deuh tawh a, tunah chuan operation pawh a tuar thei tawh a ni.
Surgery tum ber chu naute kut chu a hnathawh dan leh a lan dan pangngaia siam leh hi a ni . A châng chuan, zai vawi khat chauh pawh a tawk lo thei a, vawi tam tak zai a ngai thei bawk.
Surgery an tih lai hian doctor-te chuan vun flap emaw, kut atanga tissue dang emaw hmangin kut zungtang inkar gap te chu khar nan emaw, kut zungtang then hran tum nan emaw an hmang thei bawk. Hei hian naute tan thil man leh kut hman a awlsam phah a ni.
Thil na tak tak thenkhatah chuan, a bik takin kut zungtang a bo vek chuan ``Toe transfer`` tih dan pawh a awm a, chutah chuan naute ke atanga ke ruh pakhat lak chhuah a, kut ah dah a ni He thu i hriat hian i hlauthawng mai thei, "Aw, ke chu engtin nge a awm ang?" Mahse, hlau suh. Hetianga ke atanga ke ruh lak chhuah ni mah se, naute hian ding, kal, tlan leh zuang harsa a nei lovang. Amaherawhchu, kut hnathawh chu nasa takin a tha chho dawn a ni.
Surgeon chuan i naute hian eng ang surgery nge a mamawh tih leh a hnua eng nge i beisei tur tih chipchiar takin a hrilhfiah ang che. Chutiang hunah chuan naute hi enkawl hmasak a pawimawh hle a, chu chu a puitlin hmaa enkawl a pawimawh hle.
Surgery hmanga enkawlna ni lo
Naupang thenkhat pawhin operation hma emaw, operation hnu emawa non-surgical treatment an neih hian hlawkna an hmu bawk.
- Brace emaw splint emaw bun: Hengte hi bun hian i kut zungtangte chu a sei thei a, a tichak thei bawk.
- Prosthesis: Naupang thenkhat chuan thil an man theih nan leh hna an thawh theih nan kut lem (prosthetic arm) an hmang thei a.
- Physical therapy: Surgery zawhah i naute chu a kut hman dan tur tha thei ang bera zirtir nan physical therapy hi a pawimawh hle. Hei hian kut ruh a tichak a, range of motion a ti sang bawk.
I naute tan eng enkawlna nge tha ber tih ngaihtuah turin i doctor nen inbia ang che.
(Symbrachydactyly) surgery atanga dam leh theih nan eng chen nge a ngaih?
Hei hi i naute surgery chi hrang hrangah a innghat tak zet a ni. I doctor emaw surgeon emaw chuan operation hnua i naute kut enkawl dan tur a hrilh ang che. Chu thupekte chu dik taka zawm a pawimawh hle.
Engtin nge Symbrachydactyly hi ka ven theih ang?
Dik tak chuan i naupai lai hian he natna (Symbrachydactyly) hi a lo awm loh nan engmah tih theih a awm lo . A chhan chu, kan sawi tawh ang khan, a chhan chiang tak hmuh a la ni lo.
Amaherawhchu, a tlangpuiin, piansualna tipungtu thil engemaw zat a awm. Naupai lai hian hengte hi pumpelh a tha ber:
- Zu in a in thin.
- Meizial zu emaw, zuk leh hmuam thil dang hman emaw.
- Intihhlimna atana ruihhlo hman.
Naupai laiin i ei leh in tur leh i in tur chungchangah i doctor nen inbia ang che.
Ka naute hian Symbrachydactyly a vei a nih chuan eng nge ka beisei ang?
I naute chu `(Symbrachydactyly)` vei nia hriat ni mah se, he natna hian naute than dan pangngai emaw, rilru lama hmasawnna emaw a nghawng dawn lo . Chumi awmzia chu, i naute chu a lo seilian tha ang a, naupang dang ang bawkin a hlim ang.
Mahse, Symbrachydactyly nen hian piansualna dang emaw, damdawi lam dinhmun dang emaw hmuhchhuah a nih chuan i naute hian enkawlna dang emaw, enkawlna dang emaw a mamawh thei a ni. I doctor chuan hei hi a hrilhfiah ang che.
Engtikah nge Doctor ka hmuh ang?
I naute kutah danglamna i hmuh chuan i doctor nen sawipui rawh. A bik takin operation an neih tawh chuan surgery na hmunah hian a hnuaia chhinchhiahna te hi zawng rawh:
- Thisen chhuak.
- A rawng inthlak danglam (blueness, redness).
- A hring chhuak.
- Pus emaw tui dang emaw chhuak.
- Naute chu a na ang maia a lan emaw, a danglam bik taka a rilru a hahdam loh emaw chuan.
Hetiang thil i hmuh chuan Doctor pan nghal rawh.
Doctor hnenah eng zawhna nge ka zawh ang?
Zawhna emaw, ngaihtuahna emaw i neih chuan doctor zawt rawh. Entir nan:
- Ka naute hian eng chi Symbrachydactyly nge a neih?
- Eng ang surgery nge a mamawh?
- Surgery engzat nge neih a ngai dawn?
- Kum engzat nge operation a neih ang?
- Ka naute hian physical therapy emaw, non-surgical treatment dang emaw a mamawh ang em?
Nang leh i naute tan hetiang zawhna hi zawh a, engkim chiang taka hriatthiam a pawimawh hle.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Symbrachydactyly hi naute pian tirh atanga a kut zungtang te tawi emaw, inzawm khawm emaw a ni. Hei hian naute dam chhung atana an kut hman theihna a nghawng thei a ni. Mahse, pianpui kut piansualna neia piang i nih chuan i fa chu a hlim lo ang a, a hrisel lo ang tihna erawh a ni lo.
Kut hnathawh tihchangtlun nan surgery neih a ngai fo thin. Chumi hnuah chuan kut hnathawh tihchangtlun nan physical therapy ang chi thil a ngai mai thei. Amaherawhchu, `(Symbrachydactyly)` natna hian naute taksa peng dang eng emaw zat thanna emaw, rilru lama hmasawnna emaw a nghawng lo.
I naute chuan naupang dang ang bawkin a duh danin khawvel a hmachhawn dan a zir ang. I hmangaihna te, i thlawpna te, leh i fuihna te hi a tân a pawimawh ber a ni.
Hemi chungchang hi hriat belh i duh chuan i Doctor nen inbiak pawh hlau suh. I kalna apiangah an pui ang che.
`Symbrachydactyly, nau piangsual, kut piansual, kut zungtang hrual, kut zungtang hrual, naupang hriselna, surgery











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