I hmui chu a hring nghal vek a, ei laiin chaw ei harsa i ti em? Mahse, rei vak lo hnuah chuan i hrehawmna chu a reh a, pangngai takin i ei leh thei ta em ni? Hetiang thil tawn hi i lo tawng tawh a nih chuan he thupui kan sawiho tur hi i tan a pawimawh hle ang. Hei hi Myasthenia Gravis an tih natna a ni .
Myasthenia Gravis chu eng nge ni?
A awlsam zawngin sawi ila, myasthenia gravis hi natna rei tak a ni a, kan taksa ruhte chu a chau a, a chak lo nghal vat thin. Hei hi a danglamna ber chu hman a nih chuan taksa ruhte chu a chak lo a, chawlh hnuah a chak leh ta a ni. Battery i hnathawh laiin a thi a, mahse hun engemaw chen i dah chuan a recharge leh thin ang a ni.
Hetiang dinhmun hian taksa peng hrang hrang a nghawng thei a ni. A awm chuan `generalized myasthenia gravis` kan ti thin. Hei hian chaw ei te, ei te, nuih te, kekawrte hrual te, kut phar te, thil pakhat nghet taka chelh te, ding leh stairs chhoh te a ti harsa thei a ni.
Pawimawh tak: A châng chuan he natna hian thawk chhuahna atana mamawh taksa ruhte pawh a nghawng thei bawk. Hei hi emergency hlauhawm tak, nunna atana hlauhawm tak a ni. Hei hi myasthenic crisis kan ti a. Chutiang a nih chuan damdawi in pakhat Emergency Treatment Unit (ETU) -ah dah nghal tur a ni.
He natna hian tu pawh a vei thei a, mahse hmeichhia kum 20 leh 40 inkar leh mipa kum 50 leh 70 inkar ah a tam ber a, he natna vei nuin nau a hrin chuan nu thisena protein (antibodies) thenkhat chu naute hnenah a kal thei a, chu chuan hun engemaw chen atan taksa ruh a tichak lo thei a ni. Mahse ngaihtuahawm tur a awm lo, a tlangpuiin kar tlemte chhungin naupang taksain heng thilte hi a paih chhuak ang a, naupang ruhte chu a pangngaiin a lo let leh ang.
He natna lan chhuah dan tlangpui engte nge ni?
Mi tam tak tan chuan natna hi mit atanga intan a ni. Chuvangin a lan chhuah hmasak ber chu mitmeng tlahniam, mit hmuh lohna, emaw, mit pahnihna emaw a ni thei. Kum khat emaw kum hnih chhungin he chak lohna hi taksa ruh dangteah a darh thei a ni.
Heng symptoms te hi a hnuaia table-ah hian sawifiah belh leh ila.
| Symptom a ni | Hei hi eng nge thleng? (Eng nge thleng?) |
|---|---|
| Mit ruh chak lohna | Mit pakhat emaw, mit pahnih emawa mitmeng tlak, double vision, emaw blurred vision. |
| Hmel lan dan inthlak danglam | Nuih emaw, hmel siam emaw ang chi thil tih hian hmai ruh (facial muscles) control harsat. |
| Thusawi harsa | Aw a inthlak thin. Rei vak lo kan sawi hnu chuan a aw chu a hrual a, a hnar a lo awm zauh zauh a. |
| Chaw ei harsat | Chaw, in tur leh hmui ei harsa. A châng chuan, i hnar a\angin i ei leh in thil a lo chhuak thei bawk. |
| Thâwk harsa | Hei hi emergency a ni! (Myasthenic Crisis) tih a ni. Chhung ruh chak loh vangin thawk a harsa thin. |
| Limb leh neck chak lohna | Kawng dinglam vawn harsa, kal harsa, kut chawi sang thei lo, rit phur thei lo. |
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Hei hi hrethiam tur chuan kan nerve leh muscle te hnathawh dan tlem kan hriat hmasak a ngai a ni. I kut i phar duh chuan i thluak atang hian nerve kal tlangin thuchah a lo chhuak ang tih han ngaihtuah teh. He thuchah hi nerve tawp leh thau inzawmna tenau takah taksa ruh (muscle) hnenah a thleng a ni. He thuchah kengtu chemical messenger hi acetylcholine an ti a . He chemical, acetylcholine hian taksa peng chhunga receptor-te a inzawm chuan taksa ruh chu a inzawm khawm a, chu chu a thawk tihna a ni.
Myasthenia gravis hi autoimmune disorder a ni a, a natna hi a ni.. Chu chu kan taksa venghimtu immune system hian tihsual a siam a, kan taksa peng hrisel tak takte a bei thin tihna a ni. He natnaah hian thil thleng chu immune system atanga antibodies siam hian ka sawi tawh ang khan acetylcholine receptor te chu a block emaw, a tichhia emaw a ni. Tichuan nerve atanga thuchah lo chhuak chuan taksa ruh (muscles) a thleng tha lo. Chuvang chuan taksa ruhte chu a chak lo ta hle a ni.
Immune system-in hetianga a tih chhan dik tak hi hriat a la ni lo. Mahse a chang chuan thymus gland nen a inzawm nia ngaih a ni a, chu chu rilru chunglam a ni. He gland hian antibody siam nan a pui thin. Myasthenia gravis vei zinga 15% vel chuan he gland-ah hian tumor (thymoma) an nei a. Heng tumor te hi cancer ni lo mahse, surgery hmanga gland lakchhuah (thymectomy) hian damlo thenkhatah symptoms a tihziaawm thei a ni.
He natna hi engtin nge doctor hian a hriat theih ang?
Heng symptoms te hi i neih chuan Doctor i pan hmasa phawt tur a ni. I nervous system chungchangah a enfiah ang che. Tichuan, chu natna hriat theih nân test engemaw zât neih an rawt thei a ni.
- Thisen test: He test hi i thisenah hian ka sawi tawh acetylcholine receptor beitu antibodies bik a awm em tih hriat nan tih a ni.
- Ice pack test: I mitmeng a tlak chuan minute hnih vel ice pack dah a ni. Hei hi khawsik hian hun engemaw chen atan taksa chak lohna a tihziaawm em tih enfiah nan an ti thin .
- Repetitive nerve stimulation tests: Electrode vunah dahin electrical signal te te thawnin nerve atanga taksa peng hrang hranga thuchah thawn chak leh thawh that dan tehna a ni.
- EMG (Single-fiber electromyography) test: Electrode tha tak tak, needle ang chi chu vun kaltlangin taksa ruh pakhatah dahin thluak leh ruh inkara electrical activity chu enfiah a ni.
- Imaging scans: Thymus tumor (thymoma) a awm leh awm loh enfiah nan CT scan emaw MRI scan emaw neih tir i ni thei.
- Pulmonary function tests: Heng test te hi natnain lung hnathawh a nghawng em tih hriat nan an ti thin.
Enkawlna leh in lama tih theih thilte
He natna enkawl dan hi i kum, i natna lan chhuah nasat dan leh natna a darh chak dan azirin a innghat a ni.
Damdawi chi hrang hrang
I doctor chuan damdawi te chu a rawn rawt thei ang:
- Cholinesterase inhibitors: Heng damdawi te hian nerve leh muscle inkara inbiakpawhna a tichak a, chu chuan taksa ruh tichak turin a pui a ni.
- Corticosteroids: Hengte hian immune system hnathawh a control a, antibody tha lo siamchhuahna a ti tlem bawk.
- Immunosuppressants: Heng damdawi te hi immune system-in a chhanletna a tihziaawm lehzual nan pek a ni bawk.
Therapies bik hrang hrang
A natna lan chhuahna a lo zual nghal vat emaw, operation hma emaw chuan i doctor chuan intravenous (IV) therapy a rawt thei ang.
- Plasmapheresis: Hei hian i thisen chu machine hmanga thawn chhuah a, antibody tha lo tak takte filter chhuah a huam a ni. A result chu rang viau mah se, rei vak lo chauh a daih.
- Intravenous immunoglobulin (IVIg): He enkawlna hi i thisenah antibody hrisel tak tak inject a ni. Hengte hian i immune system hnathawh dan a tidanglam a, i symptoms te pawh a control bawk.
Surgery - Thymectomy tih a ni
Thymus gland-a tumor awm avanga natna lo awm a nih chuan surgery hmangin gland chu a chhuak vek a ni. Tumor awm lo a nih pawhin damlo thenkhatte symptoms chu thymus gland lakchhuah a nih chuan a tha zawk.
Nunphung a inthlak danglam thin
Damdawi bakah hian i nunphungah inthlak danglamna tenau te siam hian natna lan chhuah dan tur a thunun thei bawk.
- Chaw ei laiin chakna humhalh rawh: Chaw ei harsa i tih chuan ni khata chakna i neih tam ber hunah ei thin ang che. Chaw lian ei ai chuan nilengin chaw tenau engemaw zat ei thin ang che. Chaw bland tak tak thlang rawh.
- Hriselna hmanrua hmang rawh: Toilet leh khum bulah grab bar dah la, etc. Mats leh thil dangte chu lei atangin la chhuak la, chu chuan a tlu leh tlu theihna a ti tlem ang.
- Machine atanga tanpuina dawng rawh: Kut hnathawh ai chuan electrical appliances (electric toothbrush, can opener) hmangin i chakna humhim rawh.
- Mit patch hmang rawh: Hei hian double vision-ah a pui thei. TV en emaw, lehkha chhiar emaw hian mit pakhat kha khar la, mit pahnih hi a inthlak danglamin hmang ang che.
- I ni chu ruahman rawh: I chakna chu fing takin hmang rawh. Ni khata i chak ber hun zawng la, in chhung leh pawn lam thil i tih hun tur chu zawng rawh.
Take-Home Thuchah a ni
- Myasthenia Gravis natna hi taksa chakna (muscle) atanga lo chhuak a ni a, chu chuan taksa ruh a tichak lo hle. Chawlh hahdam hnuah chak lohna a tlahniam thin.
- Mit (blurred vision, double vision) atang hian symptoms hi intan fo mahse, taksa chhunga muscle eng pawh hi a nghawng thei a ni.
- Thâwk harsa (myasthenic crisis) hi medical emergency a ni a, enkawl vat a ngai a ni. Chutiang a nih chuan damdawi in pakhata Emergency Treatment Unit (ETU) pan nghal mai tur a ni.
- Hei hi damdawi lam enkawlna dik leh nunphung thlak danglam a nih chuan a thunun theih hle. Hlau suh, i Doctor nen inbia la, a tul anga inenkawlna dawng rawh.
- Nitin hnathawh tur ruahmanna siam a, chakna humhalh hmangin symptoms nena nun chu i ti awlsam thei a ni.
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