Engtin nge kan taksa hian hun engemaw chen ei lova kan kal hian, a nih loh leh exercise nasa taka kan tih hian engtin nge a mamawh chakna a hmuh theih tih i ngaihtuah ngai em? Battery a tlakchham huna hman tur power bank kan phone-ah kan dah ang bawkin kan taksa pawhin emergency-a kan hman theih tur energy reserve a nei bawk. Chu chu damdawi lam hawi chuan glycogen kan tih chu a ni. Hei hi kan taksa chakna hman dan tur pawimawh tak a ni.
Glycogen hi eng nge ni, a awlsam zawngin?
A awlsam zawngin sawi ila, glycogen hi kan taksaa glucose dahkhawm chi khat a ni. Tunah chuan glucose hi eng nge ni tih i ngaihtuah mai thei. Glucose hi sugar chi khat a ni a . Kan taksa hian kan ei leh in a\angin glucose a hmu a, a bik takin carbohydrates ( starch ) (buhfai, chhang, alu ang chi) awmna ei tur a\angin a hmu \hin. He glucose hi kan taksa chhunga cell te tana chakna petu fuel ber a ni.
Ngaihtuah teh, chaw kan ei zawh hian kan thisenah hian a mamawh aia tam glucose a awm a. Chuti a nih chuan taksa hian eng nge a tih? He glucose tam lutuk hi a la a, a hnua hman theih tur package-ah a dah a ni. Chu bungrua lian tak, glucose molecule sang tam tak inzawmkhawm atanga siam chu glycogen an ti a.
Hetiang kalphung hi kawng hnih in a thleng a:
1. Glycogenesis: Thisen a glucose tam lutuk lak a, glycogen anga dahkhawmna a ni.
2. Glycogenolysis : Kan taksain chakna a mamawh hian glycogen dahkhawm chu a tichhia a, glucose-ah a chantir leh a, thisenah a chhuah tir leh thin.
Heng thil pahnih hi a lo awm tak tak vang a ni a , chu chu kan taksain a mamawh hunah chakna a dawng a , a tul lo taka thisen sugar level a san loh nan a humhim a ni
Khawiah nge he energy store hi a awm?
Glycogen hi kan liver leh skeletal muscles ah a awm ber a, a tlem te chu thluak leh tissue dang ah pawh a awm bawk.
Hetiang hian han ngaihtuah teh, liver hian a lian leh te nena khaikhin chuan glycogen percentage sang zawk a khawlkhawm thei a ni. Mahse kan taksaah hian taksa peng tam tak kan neih avangin glycogen zawng zawng zinga a tam zawk ( hmun li a\anga hmun thum vel) chu taksa peng hrang hrangah hian a awm khawm a ni.
I taksaa glycogen awm zat hi thil engemaw zatah a innghat a ni:
- Carbohydrates i ei zat.
- Engzat nge i exercise tih leh engtiang chiahin nge i intense tih.
- Chaw ei inkar hun inthlauhna.
- Liver enzyme hnathawh dan.
He thil dahkhawmna, glycogenesis tia koh hi hormone insulin -in a thunun a ni. Kan ei hian kan thisen glucose level a sang chho zel a. Chumi hnuah kan pancreas chuan insulin a siam a, chu chuan kan cell-te chu glucose tam lutuk chu glycogen anga dahkhawm turin signal a pe a ni.
Glycogen, glucose, leh glucagon - heng pathumte hi eng nge an danglamna?
Heng hming pathumte hi ri inang mah se, an hnathawh dan erawh a inang lo. He danglamna hi chiang taka hrethiam tur chuan a hnuaia table hi en la.
| Hming | Chu chu eng nge ni? | Khawiah nge a awm? |
|---|---|---|
| Glucose a awm | Taksa cells te tana fuel ber. Sugar molecule awlsam ber. | A bik takin thisenah (thisen chhungah). |
| Glycogen a ni | Glucose molecule sang tam tak inzawmkhawm leh dahkhawm dan. (Energy khawlkhawmna) . | A bik takin liver leh muscle-ah a ni. |
| Glucagon a ni | Thisen sugar level a hniam chuan glucose siam chhuak turin glycogen a chhe tih hriattirna hormone a ni. | Pancreas atanga siam niin thisenah a chhuak thin. |
A awlsam zawngin glucose hi pawisa i hman ang mai a ni. Glycogen hi bank-a pawisa i neih ang a ni. Glucagon hi ‘message’ ang mai a ni a, pawisa i mamawh huna bank call turin a hrilh che a ni.
Liver leh muscle-a glycogen tihchhiat danah hian danglamna tlem a awm a. Liver hian glycogen a tichhia a, taksa pumin a hman theih tur glucose a siam a ni. Mahse muscle glycogen siam glucose hi chu muscle te chauhvin an hmang thei a ni . A chhan chu taksa ruh (muscle) te hian exercise an tih laiin chakna nasa tak an mamawh a ni. Taksa pum puia thisen atanga glucose an lak chhuah chuan thluak ang chi taksa peng pawimawh tak takte hian glucose an nei tlem dawn lo. Chuvangin taksa ruhte hian anmahni chakna khawlkhawm chu an vawng reng a ni.
Ka glycogen level hi ka check thei ang em?
Dik tak chuan glycogen level direct-a teh hi a buaithlak deuh a, tih dan pangngai a ni lo. A chhan chu he level hi kan ei leh in leh exercise kan tih zat a zirin nitin a inthlak reng a ni. Thil bik takah chuan a tul chuan doctor chuan liver emaw muscle emaw atanga tissue te tak te a la thei a, chu chu a enfiah thei a (hei hi biopsy an ti a ) glycogen level a enfiah thei bawk.
Mahse a tlangpuiin doctor-te chuan glucose nena inzawm harsatna a awm leh awm loh enfiah nan test awlsam zawk an ti thin.
- Thisen test a , thisen glucose level leh liver leh muscle function te enfiah thin a ni.
- Liver a lian leh lian loh enfiah nan ultrasound scan .
- Genetic test hi thlahtu natna a awm nia rinhlelh a awm chuan an ti thin.
A vaiin puitling hrisel tak chuan an taksaah glycogen gram 600 vel a dahkhawm a ni. Hei hi mi taksa lian leh te, ei leh in leh exercise level a zirin a danglam thei.
Glycogen kaihhnawih natna
Glycogen Storage Disease (GSD) hi natna hlauhawm tak, rochun atanga lo chhuak a ni a, glycogen siam chhuah emaw tihchhiat emaw theihna a tichhe thei a ni. Genetic defect avanga lo awm a ni. Taksain glycogen metabolism atana enzyme mamawh a tlakchham chuan a thleng thin.
Hei hian liver ang chi taksa peng hrang hrangah glycogen hlauhawm takin a pung thei a, mi thenkhatah chuan taksain glycogen a siam thei lo tak tak thei bawk. Hei hian symptom hrang hrang a thlen thei a, chu chu muscle chak lohna te hi a ni.
GSD hi damdawi awm lo mah se, enkawlna hian a natna lan chhuah dan a thunun thei a ni. Chi thenkhat tan enzyme replacement therapy a awm a, chi tam tak tan chuan cornstarch treatment a awm bawk.
I thisen sugar level, chakna tlakchhamna, emaw, taksa ruh na lutuk chungchangah ngaihtuahna i neih chuan i doctor nen inbiakna neihpui ngei ang che.I doctor nen inbia ang che. Internet-a information zawn ai chuan damdawi lam thurawn dik tak lak a pawimawh zawk.
Take-Home Thuchah a ni
- Glycogen hi kan taksain glucose (sugar) a khawlkhawm dan a ni. Kan taksaah ‘power bank’ ang mai a ni.
- He chakna hi liver leh muscle-ah a awm ber a ni.
- Glycogen hi thisen sugar level nghet taka awm reng tur leh exercise leh chaw nghei laia chakna pe turin a pawimawh hle.
- Hormone insulin hian glucose a khawlkhawm theih nan a pui a, hormone glucagon hian energy dahkhawm chu a hmang leh thei bawk.
- I thisen sugar level emaw taksa chakna emaw chungchangah ngaihtuahna i neih chuan ngaihtuah suh la, i doctor hnenah thurawn dil ngei ang che.











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