A chang chuan zawi zawiin i taksa thunun theih loh ang maiin i inhria em? I kal laiin i balance lo a, engkim a slow em em a, i aw chu a khur ang maiin... Hengte hi kum upat deuh deuha thil thleng pangngai ni mahse, a chang chuan kan sawi vak loh condition chhinchhiahna a ni thei a, mahse fimkhur a pawimawh hle. Vawiin hian hetiang nervous system natna hlauhawm tak, mahse na tak: Multiple System Atrophy, a nih loh leh MSA chungchang kan sawi dawn a ni.
A awlsam zawngin sawi ila, Multiple System Atrophy (MSA) hi eng nge ni?
Multiple System Atrophy (MSA) hi kan nervous system tichhe thei natna a ni. Kan taksa automatic process te a nghawng a, entîr nân, kan chetna control leh balance vawng reng . Natna hmuh tur awm lo tak a ni.
Thil lungchhiatthlak tak chu he natna hi damdawi famkim a la awm lo. Mahse lungngai suh, damdawi lam enkawlna dik leh kan nunphung tihdanglamna tenau te nen , heng symptoms te hi control theih a ni a, nun pawh a awlsam thei bawk.
MSA natna lanchhuahna chu engte nge ni?
He natna lan chhuah dan hi kum 50 leh 60 inkar a lo lang tan tlangpui a, mi thenkhat chuan natna pahnih hi an ti buai hle a, a chhan chu a lan chhuah hmasak dan hi Parkinson 's natna nen hian a inang deuh hlek a ni.
| Main symptoms hmasa ber a ni | |
|---|---|
| Movement lama harsatna a awm | Taksa che zawi, taksa ruh a nghet lo, leh khur. |
| Inbuktawk | Kea kal emaw hnathawh lai emawa balance hloh leh clumsiness. |
| Thusawi harsa | Aw ri nghing leh thu hrual hrual ang chi thil. |
| Thisen sang lama harsatna nei | Fainting emaw luak chhuak emaw, a bik takin thut atanga ding chhuak nghal a nih chuan. |
| Urinary system lama harsatna awm thei | Zun chhuah a ngai nghal emaw, zun (bladder) a chhuah vek theih loh emaw. |
Hei bakah hian nghawng dang pawh a awm thei bawk.
Heng symptom lian ber berte bakah hian taksaa thil kalphung bulpui dangte pawh a nghawng thei bawk.
- Thaw chhuak , mittui tla , leh hmui chhuah tlem.
- Constipation emaw bowel movement control theih lohna emaw .
- Erectile Dysfunction (ED) a awm thei.
- Mut laiin thawk chawlhsan (sleep apnea) emaw, mut laiin acting out emaw, au chhuah emaw, kut leh ke hrual emaw ang chi te.
- A rilru a buai hle.
- Kut leh ke lum emaw, rawng danglam emaw.
- Emotion, lungkhamna, a nih loh leh lungngaihna thunun harsa.
MSA natna hi chi hnih a awm a.
I symptoms ber berte a zirin i doctor chuan eng MSA chi nge i neih tih a rel ang.
| MSA chi hrang hrang | Thil langsar ber berte |
|---|---|
| Parkinsonian chi hrang hrang (MSA-P) 1.1. | Hei hi a tam ber chi a ni. A lan chhuah dan ber chu Parkinson natna nen a inang hle. Muscle stiffness, cheve slow, tremors, balance problems te hi a pawimawh ber a ni. |
| Cerebellar chi hrang hrang (MSA-C) 1.1. | A symptom ber chu coordination leh balance hloh a ni. Thusawi harsa, ei leh in, mit fim lo a thlen thei bawk. |
He natna hi engtin nge kan hriat theih ang?
MSA hi a tir lamah chuan hriat harsa deuh a ni thei. A chhan chu, a hmaa kan sawi tawh ang khan a natna lan chhuah dan hi Parkinson natna nen a inang hle a ni. Chuvangin, neurologist i hmuh a ngai ang .
I doctor chuan a enfiah ang che, i symptoms te a sawi ang che a, i thluak leh nervous system-a inthlak danglamna a zawng ang. MSA emaw Parkinson’s emaw i neih leh neih loh finfiah nan a hnuaia test te hi an ti thei ang:
- Autonomic testing: Test bik, nervous system hnathawh dan enfiahna a ni.
- MRI scan: Thluak ah danglamna a awm em tih en nan.
- Thisen sang tehna: Thut leh ding chunga thisen sang tehna a ni.
- ECG test: Thinlung electrical signal awm dan enfiah nan.
- Sweat tests: Taksa a thawh dan test.
Eng thilin nge MSA hi a thlen?
A awlsam zawngin sawi ila, MSA vei chuan thluaka nerve cells thlawptu cell-ah protein bik a siam chhuak thin. Hei hian thluak leh ruhro hmun thenkhat chu zawi zawiin a tichhe emaw, a thi emaw a siam thin. Mithiamte chuan he natna hi a chhan dik tak hi hriat a la ni lo niin an sawi.
Natna avanga harsatna awm thei te
Mi tam tak tan chuan kum tlemte chhungin symptoms hi harsatna lian takah a lo chang thei a, chuvangin heng thilte pawh hi hriat chian a pawimawh hle.
- Nitin hna thawh harsat.
- Thâwk lak harsatna, a bik takin `Sleep apnea` ang chi dinhmun.
- Tlu fo thin.
- Hmasawnna harsatna a pung zauh zauh a, wheelchair hman a ngai a, a tâwpah chuan khum aṭanga tho thei lo a ni ta a ni.
- Vocal cords a paralysis thin.
- Chaw ei theih lohna.
- Lung infection, pneumonia ang chi te.
- Zun kawng natna a awm.
- Thisen a chhuak thin.
Mi pakhatin he natna a vei theih hun chhung hi mi hrang hrangah a inang lo. Mi thenkhat chu kum 15 emaw a aia rei emaw an dam thei. Thihna hi thawk harsatna avanga harsatna awm vang a ni fo thin.
Enkawl dan leh enkawl dan
MSA damdawi bik a awm loh avangin enkawlna tum ber chu a natna lan chhuah dan control leh nun nuam thei ang bera siam a ni.
Damdawi leh damdawi lam enkawlna
- Parkinson natna enkawlna atana hman thin levodopa ang chi damdawi te hian a chang chuan khur, rilru hahna leh chet slow te chu a thunun thei a ni.
- Doctor chuan thisen sang control nan damdawi `droxidopa`, `fludrocortisone`, emaw `midodrine` te a pe thei a.
- A chang chuan heart rate tihreh nan pacemaker a ngai thei bawk.
- Damdawi mirabegron emaw oxybutynin emaw te hian zun control nan a pui thei a ni. A chang chuan zun chhuah theihna tura pui turin catheter a ngai thei bawk.
- Mipat hmeichhiatna lama harsatna nei tan damdawi pawh a awm bawk.
Therapies hrang hrang
- Physical therapy leh exercise hian taksa ruhte a tichak thei a, a tidanglam thei bawk.
- Occupational therapy hian nitin hna awlsam zawka thawh dan zir turin a pui thei che a ni.
- Speech therapy hian kea kal leh tawng harsatnaah a pui a ni.
In lama nangmah ngeiin i tih theih thil
Heng thilte hian i nun chu tlem a awlsam phah thei a, mahse eng thil pawh i tih hmain i doctor nen inbiakna neih hi theihnghilh suh.
- Thisen sang tihsan nan i chaw eiah chi tlem tal dah la, tui tam tak in rawh.
- Thisen kal dan tur atana pui turin special compression stockings ha.
- Thut leh mut atanga tho thut loh tur. Zawi zawiin tho rawh.
- Mut laiin khum lu chu tlem a sang taka dah.
- Constipation atan fiber tamna ei tur, thlai leh thei chi hrang hrang ei thin ang che.
- Taksa lum lutuk loh tur.
- Thisen zam a awm loh nan a theih ang anga che.
Take-Home Thuchah a ni
- Multiple System Atrophy (MSA) hi natna khirh tak, zual zel, nervous system tichhe thei a ni.
- A lan chhuah hmasak dan hi Parkinson natna nen a inang em avangin, a natna hi dik taka hriat theih nan neurologist pan a pawimawh hle.
- He natna hi tihdamna famkim awm lo mah se, damdawi te, damdawi lam enkawlna te, leh nunphung tihdanglamna te hian a natna lan chhuah dan a thunun thei a, nun a ti awlsam thei bawk.
- Nangmah emaw, i hriat miin emaw heng symptoms te hi i neih chuan hlau suh la, a rang thei ang bera doctor thurawn la rawh. Hetih lai hian damlo tan chhungte tanpuina leh hmangaihna hi a pawimawh hle.











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