I thut mai mai a, rang takin i hnungzang ruhte chu lungpui ang maia nghet lo, che thei lo ang maiin han ngaihtuah teh. A nih loh leh, thawm tlemte emaw, mi pakhatin a rawn vuak che emaw pawhin i taksa a ti na a, i taksa ruhte chu natna nasa tak avangin a ti na hle tihna a ni. Chûngte chu hnungzang natna emaw, taksa ruh natna pangngai emaw chauh a ni lo thei. Vawiinah hian mi tam takin an la hriat ngai loh dinhmun hmuh tur awm lo tak mai kan sawi a, mahse hriat a pawimawh hle. Hei hi Stiff Person Syndrome , a tawi zawngin SPS an ti a.
A awlsam zawngin, Stiff Person Syndrome (SPS) hi eng nge ni?
Stiff Person Syndrome hi thluak lama natna awm lo tak a ni. Kan thluak leh ruhro (spinal cord) a nghawng a ni. A awlsam zawngin, autoimmune disorder a ni . Chumi awmzia chu natna laka kan taksa venhimtu tur immune system hian tihsualin kan cell hrisel tak takte chu a rawn bei tan tihna a ni. He natna hi a tlem em em a, United States ang ramah pawh he natna vei hmuhchhuah hi 5,000 aia tlem lo an ni.
He natna vei chuan a taksa peng lai tak, chu chu a taksa ruh (tronk area)-ah a tight tih hriat hmasak ber a ni . Hun a kal zel a, he tightness hi kut leh ke thlengin a darh thei a ni. Hetiang tightness bakah hian muscle spasm na tak tak pawh a awm thei bawk. Hetiang tightness avang hian taksa dinhmun hi hun kal zelah a danglam thei a, hmalam pan deuhin a inbeng kang thei a, hunched over angin a lang thei bawk .
Heng taksa ruh (muscle spasms) te hi a takin a lo awm thei a, thil engemaw avanga lo awm pawh a ni thei. Entirnan, thawm ri nasa tak, mi pakhatin a rawn tawk che emaw, stress nasa lutuk emaw chuan heng spasms te hi a thlen thei a ni.
He natna lan chhuah dan berte chu engte nge ni?
He natnain a nghawng dan hi mi hrang hrangah inang lo deuh mah se, a lan chhuah dan tlangpui thenkhat hmuh theih a awm. Table pakhatah han en ila.
| Symptom a ni | Eng thil nge thleng? |
|---|---|
| Muscle stiffness nasa tak a awm | Trunk atang hian a intan a, chutah chuan taksa peng hrang hrangah a darh leh thin. He stiffness hi a tir lamah lo kal leh kal mahse hun kal zelah a awm reng thin. |
| Muscle Spasms na tak tak | Heng khur hian darkar tam tak a daih thei a , a chang chuan a na lutuk a , ruh tliak pawh a thlen thei bawk . |
| Kal harsa & Tlu | Muscle stiffness hian kal emaw, che emaw a ti harsa hle. Ding emaw, kal emaw laiin i balance i hloh thei a, i tlu thei bawk. He tlak hi "like a log falling over" tia sawi a ni a, a chhan chu taksa hi a nghet vek a, tlu chu i thunun thei lo a ni. |
| Rilru lama nghawng a neih dan | He natna hian lungkhamna leh lungngaihna a thlen fo thin. Seizure i neih i hlauh avangin in chhuahsan i hlau mai thei. |
Heng symptoms te hi a lo lang nghal thin avangin damlote chuan vantlang hmuna kal leh lirthei khalh an hlau thin. Chuvangin, zawi zawiin khawtlang atanga inhlat an tum thin.
Engvangin nge hetiang thil hi a lo thlen?
Doctor-te chuan hei hi a chhan chiang tak an la hmu lo a, mahse a theory ber chu kan immune system-a harsatna a ni tih hi a ni.
Kan taksa peng hrang hrangte chetna control thei tur neurotransmitter GABA tih a awm a. Kan taksa ruhte hnena ‘relax’ tura signal thawntu ‘switch’ angin han ngaihtuah teh. He GABA siam nan hian enzyme `glutamic acid decarboxylase (GAD)` tih hi a pawimawh hle. SPS vei tam zawkah chuan taksain he GAD enzyme hi beitu antibodies a siam chhuak thin. Heng antibodies te hian an kal a, GAD enzyme an tihchhiat chuan GABA hi a siam tha lo hle. Tichuan taksa ruhte hian ‘relax’ tih thuchah chu a dawng tha lo va, an inthlau reng a, an inhnim hrual reng bawk.
SPS vei te hian autoimmune natna dang an nei tam zawk bawk.
- Vitiligo - vunah a var a awm
- Type 1 Diabetes a ni
- Pernicious anemia - Vitamin B12 tlakchhamna avanga thisen tlakchhamna
- Thyroiditis (Thyroid gland natna hrik kai) .
Tin, cancer chi hrang hrang nei te chu SPS (e.g. lung, kidney, breast, thyroid, colon cancer) vei an hlauhawm hle bawk.
Engtin nge doctor hian he natna hi dik taka a hriat theih ang?
SPS symptoms hi kum 30 leh 60 inkarah a lang tlangpui a, hmeichhiain mipa aiin a let hnih zetin he natna hi an vei tam zawk.
He natna lan chhuah dan hi natna tlanglawn dang nen a inang avangin , SPS hi natna dang anga ngaih a ni fo thin.
- Multiple Sclerosis natna a ni
- Parkinson natna a ni
- Fibromyalgia natna a ni
- Muscular dystrophy a awm thin
- Hlauhthawnna
Chuvang chuan diagnosis dik tak hmuh theih nan hun engemaw chen a la ngai thei a ni. I doctor chuan a enfiah hmasa ang che, i medical history a zawt ang che, chutah chuan test eng emaw zat a ti ang a, chu chuan natna dang a neih loh nan a ti ang.
1. Thisen test a GAD antibodies: Hei hi test pawimawh ber a ni. Heng GAD antibodies hi SPS vei zinga 60% - 80% thisenah hian a sang hle.
2. Electromyography (EMG): Hei hian i taksa ruhte electrical activity a teh a, chu chu a relax lai leh a tense lai a ni. SPS vei te taksa ruh hi an relax lai pawhin an thawkrim reng a ni.
Hei hi eng enkawlna nge ni?
Sawi hmasak ber tur chu he natna hi damdawi a la awm lo . Mahse, natna lan chhuah dan control thei tur leh nitin hnathawh chhunzawm zelna tur enkawlna tha tak tak a awm nual. Treatment plan hi damlo tinte tana siam a ni a, an symptoms a zirin a ni.
I doctor chuan a natna leh taksa ruh natna (muscle spasms) control nan damdawi hrang hrang a enchhin ang. Mi zawng zawng taksa hian damdawi ei hi a chhan dan inang vek lo a, chuvangin i tana damdawi inkawp dik tak zawn nan hun engemaw chen a la ngai mai thei.
- Muscle stiffness atan: Benzodiazepines (e.g. diazepam, clonazepam) leh baclofen te hi hman a ni tlangpui.
- Natna atan: Natna tidamtu leh anti-seizure damdawi thenkhat hian natna control turin a pui thei a ni.
- Intravenous Immunoglobulin (IVIG) therapy: Hei hian mi hrisel atanga lak antibody te chu thisenah pek a ni. Hei hi SPS symptoms control nana damdawi tha tak a ni tih hmuhchhuah a ni bawk.
Damdawi bakah hian taksa lam enkawlna, stretching exercise, massage, leh acupuncture te pawh a awm bawkHetiang thil hian natna a tihziaawm bakah taksa ruhte a tichak thei bawk.
Take-Home Thuchah a ni
- Stiff Person Syndrome (SPS) hi taksa ruh natna chauh a ni lo va, autoimmune neurological disease a awm lo hle.
- A lan chhuah dan ber chu ruh (muscle stiffness) nasa tak leh trunk area atanga tan spasm na tak tak te hi a ni.
- Hei hi natna dang nena inthlau fo a nih avangin, dik taka hriat theihna turin doctor tawnhriat ngah tak puihna a pawimawh hle.
- He natna hi tihdam kim theih ni lo mah se, i natna lan chhuah dan thunun thei tur leh nun pangngaia nunpui thei tur enkawlna tha tak tak a awm a ni.
- Nangmah emaw i hriat emaw hian heng symptoms hi i neih chuan ngaihthah suh, "Muscle strain mai a ni" ti rawh. Doctor hmu nghal la, doctor rawn la.
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