Copper, mineral copper hi kan zavaia hrisel taka kan thawh theih nan a pawimawh hle a, a tlem hle. Mahse, he dâr pawimawh tak hi taksaah a mamawh aia tam a pung khâwm chuan eng nge thleng ang tih han ngaihtuah teh? Chu chu Wilson’s Disease tia koh, natna hlauhawm tak, mahse na tak ni thei tak a lo awm hun a ni. He thu hi hre hlau suh. A chungchang dik taka hriattir a, enkawlna mumal zawnga hlawhtling taka enkawl theih a ni. Vawiin hian he thu hi awlsam takin, i hriatthiam theih tur tawng hmangin kan sawi dawn a ni.
Wilson natna hi eng nge ni tak tak?
A awlsam zawngin, Wilson-a natna hi genetic disease a ni . Chhuan hrang hrangah a kal zel a ni. Kan taksa chhunga copper lut tur filter chhuaktu ber chu thin (liver) a ni. Tui filter ang mai a ni. Mahse Wilson natna vei miah chuan he copper filtering process nena inzawm gene (`ATP7B` gene) ah hian chhiatna a awm a.
Hei hian thin (liver) hian a hna a thawk tha thei lo a ni. Chuvang chuan copper tam zawk chu taksa atanga paih chhuah ai chuan liver, thluak leh mit ang chi organ lian tak takah a pung khawm tan ta a ni. Hun a kal zel a, he copper pungkhawm hian heng taksa peng hrang hrangte hi a tichhe thei a, symptom hrang hrang a thlen thei bawk.
Thil pawimawh tak chu hei hi thlahtu natna a nih avangin natna lo awm tur chuan naupangin he gene chhia hi nu leh pa hnen atangin a rochun a ngai a ni. Nu leh pa pakhat chauh atanga rochun a nih chuan a natna lan chhuah dan a lang lovang, mahse chu mi chu natna kengtu a ni thei. Chumi awmzia chu he gene hi an fate hnenah an pe chhuak thei tihna a ni.
He natna lan chhuah dan engte nge ni?
Wilson natna lanchhuahna hi a lang nghal lo. Taksaah hian copper a awm khawm theih nan hun engemaw chen a mamawh avangin hun engemaw chen hnuah natna lanchhuahna a lo lang tan thin. Tin, copper awmna organ a zirin a natna lan chhuah dan pawh a inang lo thei bawk. Heng symptom lian ber berte hi eng nge ni tih i lo en ang u.
| Organ/system a nghawng | Hmuh theih symptoms te |
|---|---|
| Liver nena inzawm natna lan chhuah dan | |
| Thin |
|
| Thluak leh nervous system nena inzawm neurological symptoms te | |
| Thluak |
|
| Mit lam natna lan chhuah dan | |
| Mit | Hei hi symptom bik tak a ni. Mit dum vel chu rangkachak rawng dum ring a rawn lang a. Doctor-te chuan hei hi Kayser-Fleischer rings tiin an sawi thin. Hei hi mit chhunga copper awm zat chhinchhiahna ber a ni. Mi thenkhat chuan sunflower cataract an nei thei bawk a, chu chu sunflower ang mai a ni. |
Thil dang pawh a awm
A chunga kan sawi tak symptoms lian ber berte bakah hian taksaa copper a pun avangin harsatna dang engemaw zat a awm thei bawk.
- Kidney-ah lung a awm
- Hmeichhiaah thlasik hun mumal lo
- Ruh density hniam leh arthritis natna
- Nail-te chu blue discoloration a ni
Tute nge he natna vei theihna sang zawk?
Hei hi genetic disease a nih avangin, a hlauhawm ber chu chhungkaw history a ni .
I chhungkuaa mi tu emaw, a bik takin i nu leh pa, i unaupa emaw, i unaunu emaw chuan Wilson natna a vei a nih chuan, he natna hi i vei thei emaw, carrier i nih theihna tur emaw a ni.
Kum 5 leh 40 inkarah hian natna lan chhuah tan a ni tlangpui a, mahse, kum naupang zawkah pawh a lan chhuah thu report a awm a, naute thla 9 mi leh puitling kum 70 mi te pawh a tel.
I chhungkuaa mi tu emaw hian he natna hi an vei a nih chuan i doctor hmu a, inhnialna awm lova sawipui hi a tha ber a ni. A tul chuan genetic testing hmangin a natna hi finfiah theih a ni.
Engtin nge enkawl a nih?
Wilson-a natna chungchang hriat chu hlauhawm tak ni thei mah se, thu lawmawm tak chu a enkawlna \ha tak tak a awm tih hi a ni . Enkawlna hian tum lian pahnih a nei a.
1. Taksa a copper tam lutuk lo awm tawh chu paih chhuah:
Chumi atan chuan Doctor ten damdawi chi khat bik an pe thin. Chungte chu `chelating agents` an ti a. Heng damdawi te hian taksaa copper particle dang awmte chu an inzawm khawm a, zun hmangin taksa atangin an paih chhuak thin. Hetianga enkawl chhunzawm a nih chuan taksaa copper level chu control theih a ni. Amaherawhchu, heng damdawi ei lai hian hliam damna a tlai thei. Chuvangin, zai tur i nih chuan i doctor hnenah i hrilh lawk tur a ni.
2. Chaw atanga copper taksaa a luh loh nan:
Chumi atan chuan Zinc supplement pek a ni. Zinc hian chaw ei kawng (digestive system)-a copper lakluhna a ti tlem a ni. A châng chuan, he zinc enkawlna hi doctor-te chuan he natna vei nia hriat tawh, mahse a lan chhuahna la nei loteah pawh an ṭan ṭhin.
It is very important to take this treatment for the rest of your life , i doctor-in a rawt angin, ni khat pawh tlai lovin. I doctor chuan copper tamna ei tur (e.g. shellfish, liver, chocolate, nuts) ei tlem turin a fuih thei bawk.
Take-Home Thuchah a ni
- Wilson’s Disease hi taksaa copper awmkhawm avanga lo awm, genetic disease hmuh tur awm lo tak a ni.
- Hei hian thin, thluak leh mit a nghawng ber a ni.
- A lan chhuah dan ber chu sawifiah theih loh jaundice, mize inthlak danglam, leh mit dum (Kayser-Fleischer ring) vel rangkachak rawng ring (golden-brown ring) te a ni thei.
- I chhungkuaa tu pawhin he natna hi an vei a nih chuan, a lan chhuah loh pawhin doctor rawn la, thurawn la rawh.
- A hmaa hriatchhuah leh dam chhung enkawlna hian nun hrisel, pangngai tak i neih theih nan a pui thei che a ni. Damdawi lam thurawn tel lo chuan enkawlna titawp ngai suh.
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