He pūnaha parepare whakamiharo kei roto i ō tātou tinana, kāore? Koinei te mea e kīia nei e tātou ko te pūnaha ārai mate. Ka tiaki i a tātou mā te whawhai ki ngā iroriki, ngā huakita, me ngā huaketo e puta ai te mate. Engari whakaarohia, me pēhea mēnā ka pōhēhētia tēnei pūnaha parepare o tātou ki ngā pūtau pai o roto i tō tātou tinana, ā, ka tīmata te whakaeke i a rātou? Koinā te wā ka puta, e kiia nei ko te "Pankreatitis Autoimmune". Ki te kī noa, ka tīmata tō ake pūnaha parepare ki te mahi ki tō repe taiaki.
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He aha te "Pankreatitis Ā-tinana"? He māmā noa iho...
Whakaarohia te pūnaha ārai mate o tō tinana hei ope taua e tiaki ana i tētahi whenua. Ko te mahi a tēnei ope taua he tiaki i te whenua mai i ngā hoariri o waho (pērā i ngā iroriki me ngā huaketo). Engari i roto i te (Autoimmune Pancreatitis), ka hē tēnei ope taua, ka whakaeke i ngā tāngata harakore o tōna ake whenua (arā, ngā pūtau hauora i roto i te repe taiaki) me te whakaaro he hoariri rātou. Nō reira, ka mumura te repe taiaki, ka whara, ā, ka ngoikore tana mahi. Koinei te mea e kiia nei e tātou he autoimmune pancreatitis .
He pēhea te noa o tēnei mate?
He mate tino onge te (Pankreatitis Autoimmune). I te nuinga o te wā ka pā ki te kotahi i roto i te kotahi rau mano tāngata. Ki te tangohia ngā mate mumura roa o te repe taiaki (pankreatitis mau tonu), tata ki te 2% noa iho o rātou ka taka ki tēnei wāhanga (Pankreatitis Autoimmune). Nō reira, ehara tēnei i te mate e pā ana ki te katoa.
He momo (Pankreatitis Autoimmune)?
Ae, e rua ngā momo matua o te (Pankreatitis Autoimmune). Kia kite tātou he aha ēnei.
1. Momo 1 Pancreatitis Ārai Mate
Koinei te momo tino noa . I roto i tēnei, he nui ake te pūmua e kiia nei ko te (Immunoglobulin G4), ko te (IgG4) rānei i roto i tō tātou tinana. He momo paturopi tēnei (IgG4). Ina pupuhi, ina mumura rānei i tētahi wāhi o te tinana, ka piki ake te taumata o tēnei (IgG4).
Engari i tēnei momo tuatahi, ehara i te mea ko te repeure anake te raruraru. Ka pā pea ki ētahi atu okana o tō tātou tinana. Hei tauira:
- Ngā awaawa au: He ngongo rite ki te ngongo ēnei e kawe ana i te au mai i te ate ki te whekau iti.
- Ngā ngongo whatukuhu: Ngā ngongo i roto i ngā whatukuhu.
- Ate
- Ngā pūkahukahu
- Pūngāwerewere
- Ngā repe huware
- Repe tairoiti
Ka puta hoki te pupuhi me te kino i ngā wāhi pēnei.
2. Momo 2 o te Pancreatitis Ārai Mate
Ko te repe taiaki anake te pānga o tēnei momo. Ko te mea e tupu ana i konei, ko te pakaru o te repe taiaki me ngā awa taiaki e te momo toto ma e kiia nei ko te "neutrophils". Ko te nuinga o te wā ka kitea tēnei āhuatanga i roto i te hunga rangatahi.He nui ake te tūponotanga ka pāngia rātou e te mate puku mumura (IBD).
He aha ngā take o te (Pankreatitis Ā-tinana)? He āhuatanga mōrearea kei reira?
Kei te ngana tonu ngā kairangahau ki te rapu i te tino take , engari he maha ngā wā ka pā mai tēnei mate ki te hunga i waenga i te 50 me te 60 tau te pakeke. Heoi anō, ka taea te pā mai i mua atu. E rua ngā wā ka nui ake te tūponotanga o te pāngia o ngā tāne e tēnei mate i ngā wāhine.
I ētahi wā, e whakaarohia ana he tauhohenga tēnei o te pūnaha ārai mate o te tinana ki tētahi mate huakita. Hei tāpiri, ko te hunga whai mate pūnaha ārai mate he nui ake te mōrearea ki te pāngia e tēnei mate. Hei tauira:
- (Te mate tairoiti a Hashimoto): Ka iti ake te mahi a te repe tairoiti (te mate hypothyroidism).
- (Mate puku mumura - IBD): Ina koa ko ngā mate pēnei i te (ulcerative colitis).
- (Te mate pāwera o te ate me te ate tuatahi)
- Te fibrosis retroperitoneal: Te hanganga o te kiko rite ki te koha i roto i te arai o te tuara o te puku.
- Rūmātiki: Te mumura o ngā hononga.
- (Te mate pāwera)
- (Te mate a Sjögren)
Mena kei a koe ētahi atu mate pūnaha ārai mate pēnei i tēnei, he mea pai kia āwangawanga koe mō te mate Pancreatitis Pūnaha Ārai Mate.
He aha ngā tohu o te (Pankreatitis Autoimmune)?
I ngā wāhanga tōmua o tēnei mate , kāore pea he tohu e kitea . Heoi, i te haere whakamua o te mate, ka tīmata te whaiti o ngā awa repeure, ka kore ai e taea e ngā whākōkī e hunaia ana e te repeure te haere tika.
Ka puta pea ngā tohu pēnei i te aukati i te awa pancreatic:
- Mamae o te puku o runga
- Mamae tuara o waenganui
- Korere
- Whakapairuaki/ruaki
- Te whakahekenga taumaha
He mea nui: Ka kitea anō hoki ētahi o ēnei tohu i roto i te mate pukupuku repe. Nō reira, ki te pāngia koe e ēnei tohu, he mea whakaaro nui kia kaua e mataku, engari me toro atu ki te tākuta tonu kia kitea ai te take o te raruraru . Mēnā kei a koe te (Autoimmune Pancreatitis), ehara i te mea he mate pukupuku tōu.
Hei tāpiritanga, ka taea e te pancreatitis ā-tinana te pupuhi, te tipu kore-matepukupuku, me ngā whēwhe kī tonu i te wai i roto i te repeure. Mena ka puta ēnei pupuhi, ngā puku, ngā whēwhe rānei i roto i te pane o tō repeure, ka taea e rātou te aukati i te awaawa o te au, ka ārai i te au mai i te rere tika ki roto i te whekau iti. Kei roto i te au he tae e kiia nei ko te bilirubin. Ina kohia tēnei bilirubin ki roto i te toto, ka taea e ia te puta te jaundice.Ka kōwhai te kiri me te mā o ngā kanohi (jaundice), ā, ka ngenge pea koe. Ina piki te bilirubin i roto i te mimi , ka pōuri te mimi . Ina puta te bilirubin ki roto i ngā whekau , ka mā te tae o ngā tūtae .
He aha ngā raruraru ka pā mai i te (Pankreatitis Autoimmune)?
Ka taea e te mumura mau tonu o te repe taiaki te whakapōrearea, te whakaheke taumaha, me te mamae tonu i te puku o runga me te tuara. Waihoki, ki te pakaru ngā pūtau whakaputa insulin i roto i te repe taiaki , ka pāngia pea e te mate huka .
Ka taea e ngā paturopi IgG4 te whakaeke i te repeure, tae atu ki ētahi atu okana, inā koa i te Momo 1. Ko ēnei okana ko:
- Ngā awaawa au
- Ngā repe huware
- Ngā repe wai
- Te repe tairoiti ('Tairoiti')
- Ngā whatukuhu
- Ngākau
- Ngā pūkahukahu me te pleura (te arai o ngā pūkahukahu)
Me pēhea te tautuhi i te mate pāwera autoimmune?
Hei tātaritanga tika i tēnei mate, me te whakarite ehara i te matepukupuku repeure, me whai whakamātautau maha. Me whai whakamātautau pēnei i ēnei:
- Ngā whakamātautau toto: Ka tirohia e ēnei ngā taumata tiketike rawa o te IgG4, tae atu ki te mahi ate me ngā taumata o ētahi momo pūtau toto.
- Ngā whakamātautau whakaahua: Ka tirohia e ēnei te rahi o te repe taiaki, mēnā he koha kei roto, mēnā rānei kua whaiti ngā awaawa. Ko ngā tauira o ēnei whakamātautau ko te (matawai CT) me te (matawai MRI).
- Biopsy: Ko te tango i tētahi wahi iti o tō repe taiaki ka tirotirohia i raro i te karuārai. Ko te tikanga ka mahia tēnei mā te tikanga endoscopic iti rawa te whakaekenga e kiia nei ko te Endoscopic Ultrasound (EUS). I roto i tēnei tikanga, ka whakauruhia e tō tākuta tētahi ngongo roa, ngāwari (me te rama me te taputapu ultrasound i tētahi pito) ki roto i tō puku me ō whekau hei tirotiro i tō repe taiaki. Kātahi ka tangohia he tauira biopsy mā roto i tō puku, i ō whekau rānei. I ētahi wā, me tapahi iti pea tō kiri e te taote pokanga (laparoscopy) hei tango i tētahi tauira biopsy.
- Whakamātautau corticosteroid: Ka āwhina hoki tēnei ki te whakaū i te mate. Ka hoatu he steroids ki a koe mō te wā poto hei tirotiro mēnā ka heke ō taumata IgG4, ā, ka pai ake ō whakamātautau whakaahua.
Me pēhea te rongoā i te (Pankreatitis Autoimmune)?
He mea whakamiharo, mō te tokoiti noa iho o te tangata, ka memeha noa iho tēnei mate, kāore he rongoā . Engari mō te tokomaha, me whai rongoā .
Ko te mate pukupuku autoimmune ka rongoatia nuitia ki ngā corticosteroids.He momo rongoā e kiia ana he steroid. Hei tauira, he rongoā pēnei i te (prednisone) me te (prednisolone) rānei. Ko te mahi a ēnei rongoā mā te whakaiti i te pupuhi me te whakamarie i te pūnaha ārai mate e kaha rawa ana te mahi. Ko te tikanga ka tīmata te maimoatanga me te horopeta nui o ngā steroid. Kātahi ka whakaitihia mārire te horopeta (tapered).
Mena kāore he raruraru, kāore koe e hiahia ki tētahi atu maimoatanga. Ko te maimoatanga e hiahiatia ana ka whakawhirinaki ki te momo raruraru. Mena he whaiti te awaawa repeure ('awaawa whakawhāiti'), ka taea te mahi i tētahi tikanga hei whakatuwhera i te awaawa me te whakapakari mā te whakamahi i tētahi taputapu mata kōhao ('stent').
Ka taea e au te ārai i te mate pāwera (Autoimmune Pancreatitis)?
Kāore he mea e taea te mahi hei ārai i te whanaketanga o tēnei mate nā te mea he raruraru kei roto i tō tātou ake pūnaha ārai mate.
He aha te tirohanga mō te hunga e pāngia ana e te (Pankreatitis Autoimmune)?
Ka ora pai te nuinga o te tangata i muri i te maimoatanga corticosteroid , ā, kāore he raruraru. Kāore te mate pāwera ā-tinana e pā ki tō roanga o te oranga .
Heoi, ka taea e te (Aunoa-Imune Pancreatitis) te hoki anō (ka hoki anō) . He mea tino noa tēnei i roto i te hunga whai momo tuatahi (Momo 1). Ko te mea pea ka hoki anō te mate i roto i ngā tau tuatahi e toru i muri i te tātaritanga. Ko te tangata kua pāngia e te mate ka nui ake te tūponotanga ka pāngia e ngā raruraru.
Ka aha mēnā ka hoki anō te mate?
Ki te whakahaeretia pai, ka taea e te hunga e pāngia ana e te mate anō te ora i ngā oranga oraora me te hauora .
Me tīmata anō pea koe ki te whakamahi i ngā corticosteroids. Ka haere tonu ētahi tāngata ki te rongoā steroids mō ētahi tau hei ārai i te hokinga mai o ngā tohu. Ka whakamātau pea ngā tākuta i ētahi atu rongoā hei rongoā i te pūnaha ārai mate e kaha rawa ana te mahi (ngā rongoā immunomodulatory me ngā rongoā immunosuppressive).
He aha ngā kare ā-roto mōku i te wā e rongoatia ana?
Tērā pea ka puta ētahi pānga taha i te whakamahinga o ngā steroids. Hei tauira, te mamae o te puku, te hiahia nui, te kore okiokinga, me te uaua ki te moe. Tērā pea ka pā kino ēnei pānga ki te oranga o ia rā, engari he wā poto noa iho . Kia tino whai hua ai tō maimoatanga mō te Autoimmune Pancreatitis, he mea nui kia mau tonu te tango i ngā steroids e ai ki te whakahau a tō tākuta .
Mena he tino hoha rawa ngā pānga taha, me whakamōhio atu ki tō tākuta i mua i te whakamutu i te maimoatanga. Tērā pea ka tohua e ia ētahi atu maimoatanga hei āwhina i a koe kia ora, hei whakarerekē rānei i tō mahere maimoatanga.
Āhea ahau ka taea te hoki ki ngā mahi o ia rā i muri i te maimoatanga mō te (Pankreatitis Autoimmune)?
Ko te tikanga ka whakaora te rongoā steroids i ngā tohu o te '(Autoimmune Pancreatitis)' i roto i ētahi wiki.He tokomaha te hunga e hoki ana ki ā rātou mahi o ia rā ina memeha haere ō rātou tohu.
He mate mumura onge te mate pāwera ā-tinana ka pā ki te mahi a te repe taiaki. Mā te toro atu ki tētahi tākuta e mōhio ana ki ngā mate repe taiaki ka taea e koe te whiwhi i te tiaki pai rawa atu e hiahiatia ana e koe. He maha ngā tāngata ka ora katoa i muri i te tango i ngā steroids . Tērā pea ka hiahia ētahi tāngata ki ētahi atu maimoatanga mate pāwera ā-tinana hei whakatutuki i te whakaoranga mō te wā roa.
Hei whakamutunga, kia maumahara ki tēnei (Karere hei tango ki te kāinga)
- He mate onge te mate pāwera ā-tinana (Aunoa-pūnaha Mate Pāwera) e whakaekea ai tō ake repe taiaki e tō ake pūnaha ārai mate.
- Mena kei a koe ngā tohu pēnei i te mamae o te puku, te ngaronga taumaha, te kiriuhi rānei o te kiri , me rapu tohutohu hauora koe .
- Ehara tēnei i te mate pukupuku repeure, engari he rite tonu ngā tohu, nō reira he mea nui kia tika te tautuhi mate .
- Ko te rongoā matua ko ngā corticosteroids.
- He tokomaha te hunga e ora pai ana i te rongoā, engari ka taea e te mate te hoki mai anō.
- He mea tino nui kia tino whai i ngā tohutohu a te tākuta kia tere ai te ora .
Kia maumahara, kāore koe i te mokemoke. He mea noa te maha o ngā whakaaro e rere ana i roto i tō hinengaro i roto i tēnei āhuatanga. Nō reira, kia tuwhera ki tō tākuta, ka pātai atu i ō pātai. Kei konei rātou hei āwhina i a koe.
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