Kua rongo koe i tētahi āhua e kite ana koe i ngā mea pango ririki e rere ana i mua i ō kanohi? Kāore rānei, he pōuriuri pea tō tirohanga? He mea noa ēnei, engari i ētahi wā he tohu pea nō te raruraru kei roto i tō kanohi. I tēnei rā ka kōrero tātou mō tētahi mate kanohi onge ka taea te whakahaere mēnā ka rongoatia tika.
He aha tēnei (Te Kōrioretinopathy o te Manu)?
Ki te whakarapopoto, ko te Birdshot Chorioretinopathy, ko te BSCR rānei, he mate mumura onge e puta ana i roto i te kanohi. Ehara i te mate mau tonu , arā, kāore e pai ake i roto i te wā poto, engari he mate pumau. Ki te kore e rongoatia tika, ka arahi pea ki ngā huringa tirohanga tuturu , ki te ngaro katoa rānei o te tirohanga .
(BSCR) he mate kino kei roto i tētahi rōpū mate e kiia nei ko te "Uveitis", e kino ai ngā kiko o roto i te kanohi. Ko te nuinga o te wā ka pupuhi i:
- Retina : Koinei te kiriuhi e aro ana ki te māramatanga kei muri o tō tātou kanohi. He rite ki te kiriata i roto i te kāmera. Ka tuhia ngā whakaahua e kitea ana e tātou ki konei.
- Kōroide : Kei raro i te retina tēnei. Koinei te kiriuhi e hono ana i te retina ki te wāhanga mā o te kanohi, e tuku toto ana ki te retina, arā, e whāngai ana i a ia.
Ko te āhuatanga tino kitea o tēnei mate ko te putanga mai o ngā ira iti, porowhita, tae kirīmi i te wāhanga hohonu o te retina me te paparanga o runga o te choroid. Ko ngā tohu tōmua ko ngā mea mangu e rere ana i mua i ngā kanohi (ngā mea e rere ana) , te tirohanga pōuri , ngā mea e rua rānei. I te nuinga o te wā ka pā tēnei āhuatanga ki ngā kanohi e rua .
I roto i te wā, ka taea e tēnei kino te arahi ki ngā āhuatanga pēnei i te cystoid macular edema , te glaucoma rānei. Ahakoa kāore he rongoā, he mate ka taea te rongoā i te Birdshot Chorioretinopathy. He mea nui te kitenga wawe mō te maimoatanga angitu.
Ko wai ka pāngia e te Birdshot Chorioretinopathy?
Ina hoki, ka taea e te tangata te pāngia e tēnei mate. Engari ko te nuinga o te wā ka pāngia e ngā pakeke mā, he pakeke waenga-pakeke, i waenga i te 40 me te 60 tau te pakeke. He tino onge te pāngia o ngā tamariki e tēnei mate.
He mate anō kei reira e rite ana ki tēnei (Birdshot Chorioretinopathy)?
Ae, he maha atu anō ngā mate, tae atu ki ētahi atu mate o te rōpū Uveitis, ka rite pea ngā tohu ki te Birdshot Chorioretinopathy. Nō reira, he mea nui kia tika te tautuhi mate kia taea ai e koe te whiwhi maimoatanga tika. Ko ētahi o ngā mate ka rite ki te BSCR ko:
- Lymphoma (he momo mate pukupuku)
- Sarcoidosis (he mate e puta ai ngā pupuhi iti i ngā wāhanga rerekē o te tinana)
- `(Ophthalmia Sympathetic)` (He momo uveitis onge i puta mai i te whara o te kanohi)
- Te Syphilis (he mate tuku iho i te taatai)
- `(Te mate histoplasmosis kanohi e kiia ana (POHS))` (He mate e pā ana ki ngā kanohi nā te mate harore)
- `(Te mate kohi)` (Te mate kohi)
- `(Te mate Vogt-Koyanagi-Harada)` (he mate e pā ana ki te pūnaha io, e pā kino ana ki te tirohanga me te whakarongo)
Tērā anō tētahi rōpū mate mumura e kiia nei ko ngā "white dot syndromes", ka taea hoki e ēnei te whakaatu i ngā tohu o te BSCR. Ka puta he "whara" ki te retina me te choroid. Ko ētahi tauira ko:
- `(Te mate epitheliopati pigment placoid maha-focal o muri (APMPPE))`
- `(Te koroiti maha-kanohi me te panuveitis (MCP))`
- `(Te mate ira ma maha e memeha haere ana (MEWDS))`
- `(Te koroipōtia o roto o te puku (PIC))`
He aha i huaina ai tēnei ko te Birdshot Chorioretinopathy?
He mate hou tēnei, i whakaahuatia tuatahitia i te tau 1949. Nō te tau 1980 ka tapaina e ngā tākuta kanohi e rua ko "(Birdshot Chorioretinopathy)". Ko te take o tēnei , he marara noa ngā ira puta noa i te retina, he kirīmi, he karaka te tae . I ahu mai te ingoa i te mea he rite te tauira o ēnei ira ki te tauira o ngā matā iti (birdshot) e whakamahia ana hei pupuhi manu. Whakaarohia, he ira kei roto i te kanohi, pērā i ngā matā e marara ana ina pupuhihia he pū.
He ingoa kē atu anō mō tēnei?
Āe, he maha atu anō ngā ingoa e whakamahia ana mō te mate (Birdshot Chorioretinopathy):
- `(Te kororetinitis o te manu)`
- `(Birdshot retinochoroiditis)`
- `(Birdshot retinochoroidopathy)`
- `(Te uveitis o te manu)`
- `(BSCR)` (ingoa poto)
- `(Uveitis muri)` (uveitis e puta ana i muri i te kanohi)
- `(Te mate koroiti kiriuhi)`
He pēhea te noa o te Chorioretinopathy Birdshot?
He mate tino onge tēnei. E whakapono ana ngā kairangahau he iti iho i te kotahi i roto i te kotahi rau mano tāngata e pāngia ana. Ko te tikanga, ahakoa i Sri Lanka, tera pea he tāngata e pāngia ana e tēnei mate, engari he tino iti te tokomaha.
He aha te take o te Birdshot Chorioretinopathy?
Kāore anō kia mōhiotia e ngā kairangahau te tino pūtake o te mate, engari e whakapae ana rātou he mate pūnaha ārai mate . I roto i ngā kupu māmā noa iho, ka whakaekea hētia e te pūnaha ārai mate o tō tātou tinana ō tātou ake kiko hauora.
Neke atu i te 90% o te hunga kua tāpaetia ki te mate (BSCR) he ira paturopi (he ngota e whakaoho ana i te pūnaha ārai mate) e kiia nei ko te `(HLA-A29)` kei roto i ō rātou tinana. He mea tuku iho tēnei mai i ngā mātua. Heoi, kāore e hiahiatia te `(HLA-A29)` hei whakawhanake i te (Birdshot Chorioretinopathy). Waihoki, tera pea kei a rātou tēnei ira paturopi engari kāore e whanake te mate.
He aha ngā tohu o te Birdshot Chorioretinopathy?
Ka rerekē ngā tohu o tēnei mate i ia tangata, i ia tangata.Ko te mate e haere whakamua ana he mate e kino haere ana i roto i te wā o ngā marama ki ngā tau.
Ko ngā tohu tuatahi o te Birdshot Chorioretinopathy ko:
- Te kite i ngā mea mangu e mānu ana i mua i ngā kanohi (ngā mea e mānu ana)
- Te tirohanga pōuri
Kāore tēnei āhuatanga e pāngia e te mamae o ngā kanohi, e te whero rānei . Heoi, ka pāngia pea koe e ēnei e whai ake nei:
- Ka rerekē te tirohanga, ka heke rānei te tirohanga.
- Te hekenga o te tirohanga taha, te uaua rānei ki te aromatawai i te tawhiti.
- Te pēhanga teitei i roto i te kanohi (te toto toto tiketike).
- Matapo pō (nyctalopia) (he tirohanga pōuri i te pō).
- Ngā raruraru tirohanga tae (`(matapo tae)`), te uaua ki te wehewehe i ētahi tae (`(dychromatopsia)`.
- Te aro nui ki te mārama kanapa, ki te kanapa rānei (photophobia).
Tērā pea ka pāngia ētahi tāngata e ngā panoni tirohanga rerekē, e ngā raruraru hinengaro rānei. Hei tauira:
- Te pānga o te pā hau tuanui : Ina katia ō kanohi, ka rite ki te mea kei te hurihuri te pā hau tuanui, te mira hau rānei.
- Te kitenga i ngā uira mārama, i te kanapa rānei (photopsia) te kitenga rānei i ngā āhua piro (metamorphopsia) .
- He tirohanga pōuri, he tirohanga kanapa, me te mea kei te titiro mā roto i te wai, i te karāhe paru rānei .
I ngā wā tino kino, ka puta pea ngā āhuatanga pēnei i te katarata, te glaucoma rānei. Ka taea e ēnei te whakararu nui i te tirohanga ahakoa kua rongoatia te pupuhi. Ka taea hoki e te Birdshot Chorioretinopathy te arahi ki ngā raruraru i te wāhanga pokapū o te retina, pēnei i te cystoid macular edema me ngā kiriuhi epiretinal.
Me pēhea te tātaritanga o te Birdshot Chorioretinopathy?
He uaua pea te tautuhi i tēnei mate i ētahi wā nā te mea he mate onge, ā, kāore pea e kitea ngā ira motuhake i ngā wāhanga tōmua o te mate.
He maha ngā wā ka tātarihia e ngā tākuta kanohi te BSCR mā te whakamātautau kanohi. Ka whakahaerehia hoki e rātou he whakamātautau toto hei tirotiro mēnā kei a koe te paturopi HLA-A29.
Tērā pea ka whakamahia e ngā tākuta he maha ngā whakamātautau hei aroturuki i a koe i roto i te wā. He mea nui kia noho whakapā atu koe ki tō tākuta kia whiwhi ai koe i te tiaki e hiahiatia ana e koe.
He rongoā katoa kei te wātea mō te Birdshot Chorioretinopathy?
Engari, kāore he rongoā katoa mō tēnei mate. Heoi, ki te kitea wawetia te mate, ā, ka rongoatia , ka taea te whakaiti i ngā tohu, ā, ka taea te ārai i te kino haere o te mate.
Kia maumahara: ko te mea nui ko te tautuhi wawe i te mate me te tīmata maimoatanga!
Ko wai ka taea te whakauru atu ki taku tīma maimoatanga?
Ka tūtohu tō tīma tiaki i ngā maimoatanga, ka aroturuki i a koe, ka whakarerekē hoki i ō rongoā i runga i tō āhua me ngā pānga taha. Tērā pea kei roto i tō tīma:
- Tākuta kanohi : Ko te tākuta matua e mahi ana ki ngā kanohi.
- Tākuta Niho : Nā te mea ka pāngia ngā whatukuhu e ētahi maimoatanga.
- Tohunga ārai mate kanohi: He tākuta whai whakangungu motuhake ki ngā raruraru o te pūnaha ārai mate o te kanohi.
- Rūmātīni: He tākuta e tohunga ana ki ngā mate e pā ana ki te mumura o te tinana, nā te mea he mate mumura anō hoki tēnei.
- Tākuta wheua : Nā te mea ka pāngia ngā wheua e ētahi maimoatanga.
Me pēhea te rongoā i te Birdshot Chorioretinopathy?
Ko te maimoatanga mō tēnei mate e whakawhirinaki ana ki te kaha o tō āhua me te āhua o tōna panonitanga i roto i te wā. Ko te whāinga matua o te maimoatanga he whakaiti i te pupuhi o ō kanohi, me te ārai, te whakaora rānei i ētahi o ngā tirohanga kua ngaro .
Ko te tikanga ka tohua tuatahitia e ngā tākuta he nui ngā horopeta o te corticosteroids (he momo rongoā steroid) hei whakahaere i te pupuhi o ngā kanohi. Kātahi ka whakaitihia mārire te horopeta hei whakaiti i te tūponotanga o ngā pānga taha. Ka taea e koe te tiki steroids i ēnei huarahi:
- Ngā pata kanohi
- Ngā rongoā ā-waha
- He taputapu iti ka whakatōkia ki roto i te kanohi mā te pokanga (whakatō intravitreal)
- Werohanga
- I hoatu ki roto i te uaua (IV - mā te uaua)
He maha hoki ngā tāngata me tango i ngā rongoā ārai mate mō te wā roa . Mā ēnei rongoā ka aukati i tō pūnaha ārai mate kei whakaeke i ō kanohi. Ka taea te whakamahi i tētahi, i ētahi rānei o ēnei e whai ake nei:
- `(Ngā kaiārai matū)`
- `(Ngā rongoā Antimetabolite)`
- `(Ngā kaihoko koiora)` (ngā rongoā koiora)
- `(Ngā aukati whakawhiti pūtau-T/calcineurin)`
Ka pā mai pea ngā pānga taha i ngā maimoatanga Birdshot Chorioretinopathy (Birdshot Chorioretinopathy)?
Ae, mā te whakamahinga roa o ngā steroids me ngā immunosuppressants ka pāngia e ngā pānga kino kino . Hei tauira, ka pāngia pea koe e ngā raruraru puku (ngā mate puku, ngā mate puku) me ngā raruraru wheua (osteoporosis). Ka taea hoki e ēnei rongoā te whakanui ake i te mōrearea o te whakawhanake i te katarata, te glaucoma rānei.
Ka tirotirohia koe e tō tākuta mō ngā pānga taha , ā, ka tohua hoki ētahi atu rongoā mēnā e tika ana. Mena kei te tango koe i ngā steroids ā-waha, ka tirohia koe e tō tākuta mō te ngaronga o te wheua (osteoporosis) me tō tūponotanga ki te whati wheua.
Tō tākutaTērā pea ka tūtohutia kia whakamahia he matawai kiato wheua. Tērā pea ka tohua hoki he rongoā (bisphosphonates) hei ārai i te ngaronga o te wheua.
He aha te momo aroturukitanga roa e hiahiatia ana e au mō (BSCR)?
Kia tūpato ki ngā huringa, ki ngā raruraru rānei o tō āhua. Ka whakahaerehia e tō tākuta he whakamātautau toto me te mimi hei tirotiro i te pai o te mahi a ō whatukuhu, ate, me te hinu wheua. Tērā pea me tirotiro tonu ō kanohi, ngā whakamātautau tirohanga, me ngā matawai tomography coherence tomography (OCT).
Ka taea e au te whakaiti i te tūponotanga o te pāngia e te Birdshot Chorioretinopathy?
Kāore anō kia mōhiotia he huarahi hei ārai i tēnei mate i tēnei wā. I te nuinga o te wā, e whakaponohia ana nā tētahi ira paturopi motuhake (antigen) i tuku iho mai i ngā mema o te whānau.
Mā te tirotiro kanohi auau ka āwhina i a koe ki te kite i ngā tohu wawe o te mate, kia taea ai e koe te whiwhi maimoatanga i te wā tika mēnā e tika ana. Kōrero atu ki tō tākuta mēnā he raruraru kanohi tō tētahi o tō whānau.
He aha te tirohanga mō te Birdshot Chorioretinopathy?
He rerekē te tirohanga mō tēnei mate i ia tangata, i ia tangata . Kei te kaha o te āhua me te angitu o te maimoatanga. I ngā take ngawari, ka taea e te maimoatanga te āwhina ki te pupuri, ki te whakapai ake rānei i te tirohanga.
Āhea ahau me rapu tohutohu hauora mō te (Birdshot Chorioretinopathy)?
He mea nui kia tere te rapu tātaritanga me te maimoatanga mai i te tākuta kanohi mō te Birdshot Chorioretinopathy. Ahakoa te āhua pai o tō tirohanga, ka taea e te tirotiro kanohi te kite i te pupuhi iti.
Kōrerotia ki tō tākuta ngā pānga taha, ngā huringa o ngā tohu, ngā tirohanga rānei mai i tō rongoā. Tērā pea ka hoatu he rongoā anō ki a koe mēnā e tika ana. Mā tō tākuta koe e kōrero mō ngā kōwhiringa e pai ana mōu.
Karere Whakamutunga mō te Tango ki te Kāinga
He mate onge engari ka taea te rongoā te (Birdshot Chorioretinopathy). Nō reira kaua e mataku. Ko te mea nui ko te tirotiro i ō kanohi i ia wā, me te whai i ngā tohutohu a tō tākuta . I roto i te wā, ka tohutohu tō tākuta ki a koe me pēhea te tiaki i tō tirohanga me te ārai i ngā raruraru. Kātahi ka taea e koe te kite mārama i te ao mō te wā roa. Tiakina ō kanohi, he tino utu nui hoki!
` Te Chorioretinopathy o te Birdshot, Ngā Mate Kanohi, Te Whakararuraru o te Tirohanga, Te Uveitis, Te Retina, Ngā Mate Pūnaha Ārai Mate, Te Maimoatanga o te Kanohi











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