Kei te ngoikore koe? Kei te wiriwiri ō waewae? Me ako tātou mō te CIDP (Chronic Inflammatory Demyelinating Polyneuropathy)!

I ētahi wā ka tino ngenge koe, ka ngoikore ō ringaringa me ō waewae, ka pāngia rānei koe e te mākūkū? I ētahi wā, kāore pea koe e aro nui ki ēnei mea. Heoi, i ētahi wā onge, ka taea e ēnei tohu te tohu i tētahi mea kino ake. Ko tētahi mate onge engari he mea nui kia mōhio koe ko te CIDP (Chronic Inflammatory Demyelinating Polyneuropathy) . Ahakoa te ahua roa o te ingoa, kia māmā noa iho.

He aha te CIDP (Chronic Inflammatory Demyelinating Polyneuropathy)?

Ahakoa te ahua uaua o tēnei ingoa, ki te āta tirohia tōna tikanga, ka taea e tātou te mārama ake ki tēnei mate.

• Pūmau: Ko te tikanga o tēnei he "wā roa." Ko te tikanga kāore te CIDP e puta ohorere mai, ā, ka tere te pai ake. Ka āta whanake, mō te wā e waru wiki pea te roa. I ētahi wā ka memeha haere ngā tohu, kātahi ka puta anō i muri i ngā marama, i ngā tau rānei. He rite ki tētahi raruraru e hokihoki mai ana.

• Mumura: Ko te tikanga o tēnei he "mumura" . Ina whara tātou i tētahi wāhi o tō tātou tinana, ka pupuhi, ka whero, tika? Koinā te tikanga. Engari i roto i te CIDP, ka puta tēnei mumura nā tētahi raruraru i roto i te pūnaha ārai mate o tō tātou ake tinana. I te kī poto, ka tīmata ngā hōia e tiakina ana tō tātou tinana ki te whakaeke i ō tātou ake io mā te hē. Ka kiia tēnei he "Whakaekenga Ā-tinana" . Ko te mumura nui i puta mai i tēnei ka kino i ō tātou io ā-taha . Ko ēnei io ā-taha ko ngā io e toro atu ana i te roro me te taurakira.

• Te Whakaiti i te Myelination: He kupu hōhonu tēnei. He uhi tiaki kei roto i ō tātou neurons. He rite ki te uhi kirihou e karapoti ana i te waea hiko. Ko te ingoa o tēnei uhi ko te `(Myelin Sheath)` . Ko tēnei uhi myelin te mea e taea ai e ngā karere io te tere me te tika te haere. Ko te tikanga o te `(Demyelinating)` ko te whakangaromanga, te pakaru rānei o te uhi myelin. Kātahi, pērā i te wā e tangohia ai te kirihou i runga i te waea, ka turuturu te iahiko, ā, kāore e tika te haere o ngā karere io.

• Polyneuropathy: Ko te tikanga o te kupu "Poly" he "maha." Ko te tikanga o te kupu "Neuropathy" he kino ki ngā io. Ko te tikanga o te polyneuropathy he kino ki ngā io ā-taha maha o te tinana i te wā kotahi. Ka pā mai pea ēnei raruraru maha pērā i te ngoikore o te uaua, te ngoikore o te ngākau, me te koretake o te tinana.

Nō reira, ki te whakarapopototia, he mate roa te CIDP e pakaru ai te pūeru myelin e karapoti ana i ngā io ā-taha nā te korenga o te mahi a tō tātou ake pūnaha ārai mate, ka hua ake te kore mahi a te maha o ngā io. Kei te mārama koe?

He aha te rerekētanga i waenga i te Guillain-Barré Syndrome (GBS) me te CIDP?

Tērā pea koeKua rongo pea koe i te `(Guillain-Barré Syndrome)` me te `(GBS) rānei.` He tino rite te mate CIDP ki te GBS. E whakaaro ana ngā tākuta he momo GBS roa te CIDP. He mate onge hoki te GBS e whakaekehia ai e tō tātou pūnaha ārai mate ngā io ā-taha.

Engari ko te rerekētanga matua ko te wā. Ko te wā tino kino o te GBS ka puta i te rua ki te toru wiki i muri i te tīmatanga o ngā tohu. Engari ko te nuinga o te tangata ka pai haere i muri i tērā. Engari ka roa ake te CIDP. Ka kino haere ngā tohu i roto i te waru wiki pea .

He pēhea te noa o te CIDP?

He tino onge te mate CIDP. E ai ki ngā kairangahau, ko te maha o ngā kēhi hou o te CIDP i te United States kei waenga i te 0.8 me te 8.9 mō ia 100,000 tāngata ia tau. He nui rawa tēnei awhe, nā te mea ka pā te CIDP ki ngā tāngata rerekē i ngā huarahi rerekē, ā, nā te mea he uaua ki te tautuhi i te mate.

Ka taea e te CIDP te whanake i nga tau katoa.

He aha ngā tohu o te CIDP?

Ka rerekē pea ngā tohu o te CIDP i runga i te momo. Heoi, ko te tohu tino kitea ko te ngoikore haere o te uaua e mau ana mō te waru wiki neke atu rānei. I te nuinga o te wā ka pā tēnei ki ngā taha e rua o te tinana. Ina koa:

• Ngā uaua o te rohe hope me te huha
• Ngā uaua o te pakihiwi me te ringa o runga
• Nikau me ngā maihao
• Waewae me ngā matimati

Whakaarohia, ka kitea ohoreretia e koe he uaua ki te whakatika ake i te tūru, me te mea kāore e taea e koe te piki i te arawhata, me te mea rānei he uaua ki te heru i ō makawe, ki te pupuri rānei i te kapu. Ka taea ēnei āhuatanga te tupu.

Ko ētahi atu tohu ka kitea pea ko:

• Te ngoikore o ngā uaua e pāngia ana
• Te ngenge, te ngau, te ngaro rānei o te kare ā- roto o ngā maihao me ngā matimati (Paresthesia)
• He uaua ki te pupuri i te taurite o te tinana me te kore e pai te taunga (pēnei i te tūtukitanga)
• Te uaua ki te hikoi , te ngaro katoa rānei o te hikoi
• Te ngaronga, te ngoikore rānei o ngā urupare uaua hōhonu (koinei te mea ka whakamatautauria e te tākuta mā te patuki i te turi ki te hama iti)
• Mamae Neuropathique. He mamae tēnei e rite ana ki te wera, ki te ru hiko rānei.

He tino onge, ka kitea pea ēnei tohu:

• Te uaua ki te horomi (Dysphagia) me te ngoikore o te kaki o runga
• Tirohanga Takirua

Ka rerekē pea ēnei tohu i roto i te wā. Tērā pea ka tīmata āta, ka tere rānei te horapa. I ētahi wā ka haere mai, ka ngaro, ka memeha haere i muri i ētahi rā, kātahi ka hoki mai anō. Mēnā kei a koe ēnei tohu, he mea nui kia kite wawe koe i te tākuta.He mea nui te tautuhi me te maimoatanga wawe ki te oranga tonutanga.

He rerekē ngā momo CIDP?

Ae, he rerekē ngā momo o te CIDP, ā, he rerekē paku ngā tohu.

Ko te momo tino noa ko te CIDP noa , e puta ai te ngoikore o te uaua me ngā tohumate pārongo (pēnei i te māuiui) i ngā taha e rua o te tinana.

Ko ētahi o ngā momo rerekē ko:

• `(Multifocal Motor Neuropathy)`: Ka pāngia anake e te ngoikore o te uaua. He ngoikore kore-taurite hoki tēnei, arā, ka pā ki tētahi wāhi anake i te taha kotahi o te tinana, ki ētahi wāhi rānei i ngā huarahi rerekē.
• ` (Te Mate Lewis-Sumner): Kei roto i tēnei ko te ngoikore o te uaua kore taurite me ngā tohu pānga o te rongo.
• `(Pure Sensory CIDP)`: Ka pā mai pea te ngoikore o te tinana, te mamae, ngā raruraru taurite, me te āhua rerekē o te haere. Engari kāore he ngoikore o te uaua.
• `(Pure Motor CIDP):`: I roto i tēnei, ka kitea te ngoikore o te uaua me te ngaronga o ngā urupare e pā ana ki ngā taha e rua o te tinana, engari kāore he tohu pānga.

Kei te rangahau tonu ngā kairangahau i ētahi atu momo o te CIDP.

He aha te take o te CIDP?

E ai ki tā tātou i kōrero ai i mua, e whakapono ana ngā kairangahau ko te CIDP te take o tētahi hapa i roto i tō tātou pūnaha ārai mate . Ahakoa kāore anō kia mōhiotia te tino take, e kite ana tō tātou pūnaha ārai mate i te pukupuku myelin hei hoariri, kātahi ka tīmata ki te whakaeke i taua mea (he tauhohenga ārai mate).

Ko te pūkahu myelin te paparanga tiaki e karapoti ana i ō tātou pūtau io. Ka takai i te wāhanga roa o te muka io (axon). Ko te myelin te mea e āhei ai ngā hikohiko te haere tika i te taha o te io. Ina pakaru te myelin, ka tino puhoi te haere o ēnei hikohiko, ka ngaro katoa rānei. Kātahi ka kore ngā "karere" e tae ki te wāhi e tika ana kia haere. Koinei te take o ngā tohu o te CIDP.

Whakaarohia he waea hiko kua āraia pai. He tino pai te kawe i te iahiko. Engari, he aha te mea ka puta mēnā ka motu te uhi kirihou o taua waea i ētahi wāhi? Ka turuturu te iahiko, kāore rānei e rere tika, tika? Koinei te mea ka tupu ina pakaru te uhi myelin.

Me pēhea te tātaritanga o te CIDP?

He uaua te tautuhi i te CIDP nā te mea he rerekē ngā tohu o ia momo. Hei tautuhi i te CIDP, mā tō tākuta ēnei mahi:

• Ka whakarongo pai rātou ki ō tohumate , ā, ka pātai atu mō tō hītori hauora .
• Ka whakahaerehia he whakamātautau tinana me te whakamātautau pūnaha io .
• Ka taea te tono i ētahi whakamātautau motuhake hei whakaū i te mate, hei whakakore rānei i ētahi atu āhuatanga.

He aha ngā whakamātautau e whakamahia ana hei tautuhi i te CIDP?

Koinei ngā whakamātautau hei āwhina i te whakaū i te CIDP me te whakakore i ētahi atu take:

• Te Whakamātautau Hikohiko (EMG) me te Whakahaere i ngā Io: Ka tirohia e ēnei whakamātautau te hauora me te mahi a ō uaua me ngā io e whakahaere ana i a rātou. He tino whai hua ēnei whakamātautau mō te rapu i ngā huringa demyelinating (te tuku puhoi o ngā tohu io, te aukati, me ētahi atu) pērā i te CIDP. Ka taea e tēnei te āwhina ki te wehewehe i te CIDP mai i ētahi atu momo polyneuropathies noa.

• Te Tātari Tuaiwi / Te Werohanga o te Lumbar: I tēnei whakamātautau, ka werohia e te tākuta he ngira iti ki roto i tō tuara o raro, ka tangohia he tauira o tō wai cerebrospinal (CSF) . Ka tukuna tēnei tauira ki tētahi taiwhanga hei whakamātautau. I roto i te 85% ki te 90% o te hunga whai CIDP, he noa te maha o ngā toto toto mā, engari he teitei ake te taumata pūmua. Ko ētahi atu āhuatanga rerekē i roto i te CSF he tohu pea i tētahi atu mate.

• Matawai Whakaahua Āhua Aukume (MRI) o te tuara o raro: Mena ka mimitihia e ngā pakiaka io o tō tuara o raro he tae rerekē i te wā o te matawai MRI, ka taea e ia te āwhina ki te tautuhi i te CIDP.

• Ngā Whakamātautau Toto: Ka tono pea tō tākuta i ngā whakamātautau toto hei whakakore i ētahi atu āhuatanga ka puta ai te neuropathy, pērā i te mate huka, te korenga o ngā huaora, te mate tairoi, te mate Lyme, te HIV/AIDS, me te lymphoma. Ka tirohia pea e rātou ētahi paturopi kua kitea he hononga ki te CIDP.

• Kohikohi io: He tino onge te wā ka tūtohu te tākuta i te kohikohi io, e tangohia ai tētahi wahi io, ka tirotirohia ai mēnā kua pakaru te pūeru myelin.

He aha ngā maimoatanga mō te CIDP?

E toru ngā maimoatanga matua (rārangi tuatahi) mō te CIDP:

• Corticosteroids: Ka āwhina ngā rongoā steroids, pērā i te prednisolone, ki te whakaiti i te mumura. Mō te tini o te tangata, ka taea e ēnei steroids anake te āwhina ki te whakaiti i ngā tohu. Heoi, ka pāngia pea e ngā steroids ngā pānga taha kino, nō reira he iti noa te whakamahinga mō te wā roa o ēnei rongoā. Ka tohua pea e tō tākuta ētahi atu rongoā (ngā immunosuppressants) me ngā steroids.

• Whakawhitinga Plasma / Plasmapheresis: I roto i tēnei maimoatanga, ka wehea e te mīhini te plasma mai i tō toto, ka rongoatia, kātahi ka whakahokia te plasma me te toto ki tō tinana. He māmā noa iho, ka tātarihia e ia ngā paturopi kino i roto i te plasma e whakaeke ana i ō io. He torutoru wiki noa iho te roa o te mahi a te whakawhiti plasma. Me whakamahi tonu pea koe i tēnei maimoatanga mō ngā marama, mō ngā tau rānei.

• Te Whakaora Immunoglobulin Ā-roto (IVIG): I roto i tēnei maimoatanga, ka tukuna mā te uaua (IV) ngā pūmua e kiia nei ko ngā immunoglobulin (ngā pūmua e hangaia ana e tō tātou pūnaha ārai mate hei whakaeke i ngā kaipahua). Ka riro mai tēnei immunoglobulin i te toto o ngā mano tini o ngā tāngata hauora. Ka taea e te IVIG te whakaiti i te kino o tō pūnaha ārai mate ki ō io. Tērā pea ka hoatu te IVIG i ngā horopeta tino teitei i te tīmatanga, ā, me whiwhi pea koe i tēnei maimoatanga i ia wā mō ngā marama, tae atu ki ngā tau.

Kei te rangahauhia e ngā kairangahau ētahi atu maimoatanga mō te CIDP. Tērā pea ka whai wāhi koe ki tētahi whakamātautau haumanu mō te CIDP. Kōrero ki tō tākuta mō tēnei.

He aha te āhua o te oranga me te CIDP? (Te Matapae)

Ko te roanga o te mate e whakawhirinaki ana ki ētahi āhuatanga:

• Tō tau i te tīmatanga o te CIDP.
• Te whanaketanga o te mate me te momo mate .
• Te tere o te tautuhi i te mate me te tīmatanga o te maimoatanga .
• Te tauhohenga tuatahi a tō tinana ki te maimoatanga.

Tata ki te 90% o te hunga whai CIDP ka taea te whakaora mā te rongoā. Engari tata ki te 50% o te hunga ka hoki anō ki te mate. I te nuinga o te wā, he pai te matapae mō te hunga kua kitea he CIDP i te wā taitamariki. Ki te kore koe e whiwhi rongoā mō te CIDP, ka pāngia pea koe e te kino tūturu o te io, ka arahi pea ki ētahi hauātanga.

Ka taea e tō tākuta te hoatu ki a koe he whakaaro pai mō ngā mea ka tumanakohia mō te heke mai i runga i tō āhua motuhake.

Ka whakapotohia e te CIDP te roanga o te oranga?

Ehara te CIDP i te mate whakamate. Ko te roanga o te oranga o te hunga whai mate nei he rite tonu ki te hunga kāore i te mate. Nō reira, kāore he mea hei manukanuka.

Ka taea te ārai i te CIDP?

Nā te mea kāore anō kia kitea e ngā kairangahau tētahi tino take mō te CIDP, kāore anō kia kitea he huarahi hei ārai i te whanaketanga o te mate.

Āhea ahau me haere ki te tākuta? / Āhea ahau me haere ki te rūma ohorere?

Mena kua tāpaetia koe kei te pāngia e te CIDP, me toro atu koe ki tō tākuta i ia wā, i ia wā, hei aroturuki i ō tohumate, hei whiwhi maimoatanga hoki. Ka taea e ngā tohumate CIDP te haere mai, te haere, te haere mō ngā marama, mō ngā tau rānei, nō reira me haere tonu te maimoatanga.

He tino onge te pānga o te CIDP ki ngā uaua e hiahiatia ana hei manawa . Mena kei te raru koe ki te manawa , waea atu ki te 911 (ki tō nama urupare ā-rohe rānei), haere rānei ki te rūma urupare tata. He urupare tēnei.

Hei whakamutunga, ngā mea hei maumahara

He mea whakamataku pea te whakaaro kāore e taea e koe te whakahaere i tō tinana. Engari ko te rongo pai ko ngā tohu o te CIDP (Chronic Inflammatory Demyelinating Polyneuropathy) ka taea te rongoā, inā koa mēnā ka tīmata wawe koe i te rongoā. Kia maumahara kei a koe tō tīma hauora i ia taahiraa o te ara hei whakatau i tēnei mate. Nō reira kia maia, kia whai i ngā tohutohu a tō tākuta.

CIDP , Neuropathy, Ngāwari Uaua, Ngoikore, Pūnaha Ārai Mate, Myelin, Pūnaha Io, Maimoatanga CIDP, Polyneuropathy Demyelinating Mumura Mau tonu