Kāore pea koe i te mōhio he mate manawa tōu mai i tō tamarikitanga. Engari i a koe e pakeke haere ana, i a koe e pakeke haere ana rānei, kua tīmata koe ki te ngenge, ki te poto o te manawa, ki te pāorooro rānei i roto i tō uma? He tokomaha te hunga e whakaaro ana ko te mate manawa he mea e puta mai ana i te kaumātuatanga. Engari ko te pono, ko ētahi mate manawa he mea tuku iho. I tēnei rā, e kōrero ana tātou mō ngā mate manawa whānau, ka kitea, ka rongoātia rānei i te pakeketanga.
He aha te Mate Ngākau Whānau o te Pakeke (ACHD)?
Ki te kī māmā noa, he hapa tēnei o te āhua, o te hanganga rānei o tō ngākau e kitea ana i te wā e whānau ana koe. Ko te tikanga o te kupu "whanautanga" ko "mai i te whānautanga." Ka puta ēnei hapa i te wā e noho tonu ana te pēpi i roto i te kōpū. Ka pā pea ēnei hapa ki te rere o te toto i roto i te ngākau . Ka kiia hoki ēnei he "hapa ngākau whānautanga."
He tino ngawari ētahi o ēnei mate ngākau. Ko ētahi he tino kino. I runga i te momo me te kaha o te hapa, karekau pea ētahi tāngata e pāngia e ngā tohu tae noa ki te pakeketanga. Ko ētahi atu karekau he tohu i roto i ō rātou oranga katoa. Ko ētahi ka rongoatia pea mō tēnei mate i te tamarikitanga engari ka pāngia e ngā pānga roa i te pakeketanga.
Engari kāore he take e manukanuka ai. Nā te whanaketanga o te rongoā hou, kua tino pai ake ngā tikanga mō te tautuhi me te rongoā i ēnei mate. Inaa, neke atu i te 90% o te hunga i rongoatia mō ēnei mate ngākau i a rātou e tamariki ana ka ora tonu i te ora hauora. Ahakoa kua tautuhia koe ki tēnei mate i a koe e tamariki ana, e pakeke ana rānei, me whai tohutohu hauora me te whakamātautau koe mō te roanga o tō oranga hei aroturuki i tō āhua.
He aha ngā wāhanga o te ngākau ka pāngia e tēnei?
Ka pāngia e ēnei mate ngākau whānau tetahi wāhanga o te ngākau. Ko ngā wāhanga matua ka pāngia ko:
- Ngā uaua toto : Ka haria te toto e ngā uaua toto i roto i te ngākau puta noa i te tinana, hoki atu ana ki te ngākau. Ka haria e ngā uaua toto he toto whai hāora mai i te ngākau ki te tinana. Ka haria e ngā uaua toto kore hāora ki te ngākau.
- Ngā rūma o te ngākau: Te pā o te ngākau me te rere o te totoE whakahaerehia ana e ēnei rūma. E rua ngā rūma o runga (te atria matau me te maui) me ngā rūma o raro e rua (ngā ventricle matau me te maui). E wehea ana ēnei rūma e tētahi pakitara (septum).
- Ngā takirere o te ngākau : Ka āwhina ēnei takirere e whā i te rere o te toto i roto i te ngākau i te taha kotahi anake. He rite ēnei ki ngā tatau e aukati ana i te rere o te toto i te taha hē.
He aha ngā momo matua o te mate ngakau whānau?
He maha ngā momo mate manawa whānau e kitea whānuitia ana i waenga i ngā pakeke. Me titiro tātou ki ēnei momo.
| Te āhua o te hapa | Ngā tauira me te whakamārama māmā |
|---|---|
| Ngā hapa o ngā oko toto | Ina whaiti ngā oko toto i ētahi wāhi, me kaha ake te mahi a te ngākau ki te pupuhi toto. I ētahi wā ka hē te tūnga o ngā oko toto, ka taea ai te rere o te toto rawakore-hāora ki te tinana, me te toto whai-hāora ki ngā pukahukahu. Tauira: Te pūngao o te aorta, te patent ductus arteriosus (PDA), te stenosis o te uaua pūkahukahu . |
| Ngā hapa o te takirere o te ngākau | Ka taea e ngā takirere o te ngākau te whaiti, te kore e kati tika, te kati rawa, te hanga hē rānei, ka uaua ai te pupuhi toto i roto i te tinana. Tauira: Te mate takirere aorta bicuspid, te anomaly a Ebstein, te Mitral valve prolapse (MVP) . |
| Ngā hapa o te septal (ngā hapa i roto i ngā pakitara i waenganui i ngā rūma o te ngākau) | Koinei ngā "kōhao i te ngākau" kua rongo katoa tātou. He kōhao tēnei i te pakitara i waenganui i ngā rūma o runga e rua (atria) me ngā rūma o raro e rua (atrium). Mā tēnei ka taea te whakaranu i te toto whai hāora me te toto rawakore. Mā tēnei ka whakaitihia te nui o te hāora i roto i te toto e haere ana mai i te ngākau ki te tinana. Ngā Tauira: Te Koha o te Septum Atrial (ASD), Te Patent Foramen Ovale (PFO), Te Koha o te Septum Ventricular (VSD) . |
Ko wai te mea ka nui ake te tūponotanga ka pāngia e ēnei āhuatanga?
Ka pāngia te tangata e ēnei āhuatanga, ahakoa te ira tangata, te tau, te iwi rānei. Heoi, he nui ake te kitea o ētahi āhuatanga i roto i ngā wāhine i ngā tāne. Hei tauira, he nui ake te kitea o ngā āhuatanga pēnei i te 'Atrial septal defect (ASD)' me te 'Mitral valve prolapse (MVP)' i roto i ngā wāhine. He nui ake te kitea o ngā āhuatanga pēnei i te 'Aortic coarctation' i roto i ngā tāne. Waihoki, ko te hunga whai āhuatanga ira pēnei i te 'Down syndrome' me te 'Turner syndrome' rānei, he nui ake te mōrearea ki te whakawhanake i te mate manawa whānau.
He aha tēnei e tupu ai? He aha ngā āhuatanga mōrearea?
He maha ngā wā, kāore e taea e ngā tākuta te kī tika he aha i puta ai tēnei momo mate ngākau whānau. Ko ētahi o ēnei ka taea te tuku iho. Arā, mā roto i ngā ira.
Waihoki, ko ētahi āhuatanga e pā ana ki te whaea i te wā e hapu ana ka whakanui ake i tēnei mōrearea mō te pēpi.
- Mena ka pangia te whaea e te mate huaketo pēnei i te rubela , te rewharewha rānei i ngā marama tuatahi e toru o te hapūtanga.
- Mena he mate huka te whaea (Momo 1, Momo 2 rānei) .
- Ka taea te whakamahi i ētahi rongoā e whakamahia ana mō ngā mate pēnei i te hakihaki me te mate haurangi i te wā e hapū ana.
- Ki te tango koe i ngā rongoā whakamamae pēnei i te ibuprofen i muri i te 30 wiki o te hapūtanga.
Kei a koe anō ēnei tohu?
He rerekē ngā tohu o te ACHD i ia tangata, i ia tangata. Kei runga i tō tau, te maha o ngā mate ngākau kei a koe, te kaha o te mate, me te momo mate. Tērā pea kāore he tohu o ētahi tāngata. Mēnā ka puta ngā tohu, ko ēnei pea:
- Te tae kikorangi o ngā maikuku, ngutu, me te kiri (Cyanosis): Ka puta tēnei ina kore e nui te hāora i roto i te toto e rere ana ki te tinana.
- Pōuriuri.
- Te ngenge wawe: Te āhua nei ka hinga koe ahakoa te mahi iti, te hikoi rānei.
- Haruru ngākau: Kāore e taea e koe te rongo i tēnei. Ka rangona tēnei tangi rerekē ina whakanohoia e te tākuta he stethoscope ki tō uma.
- Te tere o te pā o te ngākau: He kare ā-roto e pā ana te ngākau ki te kaha me te tere o te pā.
- Ngā rerekētanga o te pā o te ngakau (Arrhythmia).
- Te uaua ki te manawa (Dyspnea).
- Te pupuhi (edema) o ngā pona, ngā waewae, ngā ringaringa rānei.
Ko te mea nui, ehara i te mea he mate manawa whānau tō te katoa e pāngia ana e ēnei tohu. Engari, ki te pāngia koe e ēnei tohu, he mea nui kia kite i te tākuta me te kōrero mō tēnei mea.
Me pēhea e kitea ai tēnei e koe, e Tākuta?
, , . , .
Hei whakaū i te mate, ka tonoa pea koe kia mahi i tētahi, i ētahi atu rānei o ngā whakamātautau e whai ake nei:
- X-ray o te uma: He whakamātautau x-ray o te uma.
- Echocardiogram (echo): He rite tēnei ki te matawai i te ngākau. Ka kitea mārama te āhua o te ngākau, ngā rūma, me te mahi a ngā takirere.
- Irahiko-karukaru (EKG): Mā tēnei ka whakamātautau i te ngohe hiko o te ngākau, arā, te manawataki o te pao o te ngakau.
- Whakamātautau ahotea whakakori tinana: Ka mahia he EKG i a koe e hikoi ana, e oma ana rānei i runga i te mīhini oma, hei tirotiro i te urupare a tō ngākau ki te whakakori tinana.
- MRI o te ngākau me te matawai CT o te ngākau: He matawai e whakaputa ana i ngā whakaahua mārama ake, toru-ahu o te ngākau.
- Cardiac catheterization: . (catheter) .
He aha ngā maimoatanga mō tēnei?
. , (checkups) .
Ko ētahi e hiahia ana kia rongoatia. Ko te momo maimoatanga e whakawhirinaki ana ki te momo me te kaha o tō mate.
Ngā rongoā
. , , (diuretics) .
Ngā Pūrere Manawa Tāuranga
- Pūrere tere o te manawa: Ka whakauruhia tēnei taputapu ki raro i te kiri hei whakahaere i te tere o te manawa, ina koa mēnā he puhoi te tere o te manawa.
- ICD (Implantable Cardioverter Defibrillator): He taputapu e kite ai i ngā pāorooro ngakau koretake e morearea ana ki te ora, ā, ka tukuna he ru hiko hei whakatika.
Tikanga Whakatārewatanga Ngākau
. , , (ASD ) . , .
Pokanga
. , (open-heart surgery) (minimally invasive surgery) .
Te Whakatō Manawa
. , .
Me pēhea koe e tiaki ai i a koe anō?
I a koe e noho tahi ana me te ACHD, me tiaki hoki koe i tō hauora.
- Whakamahi i tētahi momo noho hauora: Kai i tētahi kai taurite, kōrero ki tō tākuta me te mahi i ngā mahi whakakori tinana e tika ana māu, ā, karohia rawatia te momi hikareti me te waipiro.
- Kōrero atu ki ō tākuta katoa: Ahakoa kei te haere koe ki te tākuta niho, ki tētahi atu tākuta rānei, kia tino mōhio koe kei a koe te ACHD.
- Tirohia te tākuta ngakau i ia wā: Ahakoa kāore he tohu, me haere tonu ki te tirotiro i a koe anō kia rite ki te whakahau a tō tākuta.
- Tiakina ō niho: Kia ma ō niho. Mēnā ka pangia ō kapia, ka taea e ngā iroriki te haere mā roto i ō toto ka pā ki tō ngākau (endocarditis).
- Rapua he tohutohu hauora i mua i te haputanga: Mena he wahine koe e hapu ana, he mea nui kia kōrero koe ki tō tākuta ngakau, me te rapu tohutohu hoki i mua i te ngana ki te hapu.
Āhea koe ka hiahia ohorere ai ki te toro atu ki te tākuta?
Ki te pāngia koe e tētahi o ngā tohu e whai ake nei, arā, he tohu pea nō te ngoikore o te ngākau, haere tonu ki te Tari Ohotata (ETU) o te hōhipera tata .
- Te uaua nui ki te manawa.
- Te pupuhi i te puku, i ngā waewae rānei o raro.
- Te ngenge nui rawa, te ngenge rerekē, kāore he take e kitea ana.
Waihoki, ki te puta he tohu hou ki a koe, ki te kite rānei koe kei te kino haere ō tohu o nāianei, me toro atu ki tō tākuta tonu.
Karere Tangohia ki te Kāinga
- Ko te mate ngakau whānau (ACHD) he hapa hanganga o te ngakau e kitea ana i te whānautanga mai.
- Kāore pea ētahi tāngata e pāngia e ngā tohu tae noa ki te pakeketanga.
- Ko te uaua ki te manawa, te ngenge whānui, te kikī o te uma, me te kiri kikorangi ētahi o ngā tohu noa.
- Nā ngā maimoatanga hou o ēnei rā (te rongoā, te pokanga, ngā tikanga whakauru catheter), ka taea e te tini o te tangata te noho ora noa, te ora kaha.
- Mena kei a koe tēnei āhuatanga, ahakoa kāore he tohu, he mea nui kia noho tonu koe i raro i te tirotiro a te tākuta ngakau mō te roanga atu o tō oranga.
Mate ngakau whānau, mate ngakau, ACHD, Mate ngakau whānau Pakeke sinhala, kōhao i te ngakau, uaua ki te manawa, mamae o te uma, pokanga ngakau, tohumate mate ngakau











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