Kua rongo katoa tātou i te korenga o te rino, arā, te mate toto, tika? He maha ngā wā ka rongo tātou i ngā tohutohu kia kai i te pīnihi, kia kai i te pīnihi, kia tango pire rino hoki. Engari kua whakaarohia e koe te mea ka puta mēnā he nui rawa te rino i roto i te tinana? Ae, he raruraru nui anō hoki tēnā. Koinei te mea e kiia nei e tātou i roto i te rongoā ko te Hemochromatosis, ko te Iron Overload rānei. I tēnei rā, ka kōrerohia tēnei mea me te taipitopito, he tino māmā noa iho.
He aha te Hemochromatosis?
Whakaarohia tō tinana he whare putunga. Ka mimiti tātou i ngā matūkai e hiahiatia ana e tātou mai i ngā kai e kainga ana e tātou, e inu ana hoki. Ko te rino tētahi o ngā matūkai nui. He mea nui te rino mō te hanga toto whero i roto i ō tātou toto, me te whakarato pūngao ki te tinana. Engari, pērā i ngā mea katoa, ka raru pea te nui rawa o te rino mēnā ka nui rawa te tango.
Ko te hemochromatosis te raruraru. I roto i tēnei āhuatanga, he nui ake te rino e mimitihia ana e tō tinana i te mea e hiahiatia ana mai i te kai. Ko te raruraru, kāore he huarahi a tō tātou tinana ki te whakakore i tēnei rino nui. Nā, he aha te mahi a te tinana? Ka tīmata te kohikohi i tēnei rino nui ki roto i ngā whekau nui pēnei i te ate, te ngākau, me te repeure. He rite ki te penapena i ngā mea kāore e whakamahia ana e tātou ki roto i te kāpata. I roto i te wā, ka tīmata te kino o ēnei rino kua kohikohia ki aua whekau, ā, ka whakararu i tā rātou mahi. Ki te kore e rongoatia, ka mate pea. Engari ko te rongo pai, ki te kitea wawe, he mate ka taea te whakahaere katoa.
He aha ngā tohu? Āhea ēnei ka puta mai?
Ko tētahi o ngā āhuatanga ahurei o tēnei mate ko te roa o te wā ka puta mai ngā tohu. Ahakoa he whānau tonu tēnei mate, ka puta noa ngā tohu ina kohia te rino i roto i te tinana, ā, ka tīmata te kino o ngā whekau. Ka roa pea tēnei mahi. Ko te nuinga o te tangata kāore e puta ngā tohu tae noa ki te 40-50 tau te pakeke. Ko ētahi tāngata he tino ngawari te ahua o te mate, ā, kāore pea e whakaatu i ngā tohu mō ō rātou oranga katoa.
Kia tirohia tātou he aha ngā tohu matua.
| Tohu | He whakamārama māmā |
|---|---|
| Ngenge tonu | E ngenge tonu ana koe, kāore he take. Ahakoa kua moe pai koe, e ngenge tonu ana. |
| Mamae hononga | Mamae, inā koa i ngā hononga o ngā maihao, te maihao tohu, me te maihao waenga. Ka kiia hoki tēnei ko te "ringa rino". |
| Te pouri o te kiri | Ka huri te kiri i te hina, i te parahi rānei. |
| E wiri ana te ngākau | Te āhua nei kei te tere te pao o tō ngākau, me te mea kei te rere te hau i roto i tō uma (arrhythmias). |
| Te hekenga o te hiahia moepuku | Ka taea e ngā wāhine me ngā tāne te heke o te hiahia moepuku. Ka taea hoki e ngā tāne te pāngia e te ngoikore o te ure. |
| Mamae o te puku o runga | Tērā pea ka mamae te taha matau o raro i ngā rara, te wāhi kei reira te ate. |
| Te ngaronga taumaha mō te kore take | Mena kei te whakaitihia tō taumaha, engari kāore koe e kai ana i tētahi kai tōtika, e whakakori tinana rānei, me āwangawanga koe. |
He aha tēnei e tupu nei? He aha ngā take?
E rua ngā momo take matua mō tēnei.
1. Te take matua: Te Hemochromatosis tuku iho
Ko te nuinga o te tangata ka pāngia e tēnei mate nā te hapa ira, arā, he panoni iti noa iho i roto i ngā ira i riro mai i ngā mātua e rua.
Whakaarohia pēnei. He ira motuhake kei reira e whakahaere ana i te mimiti o te rino i roto i tō tātou tinana. Ka kiia e mātou ko te `(ira HFE)`. Ka whiwhi ia tamaiti i tētahi tārua o tēnei ira mai i tōna whaea, me tētahi tārua mai i tōna pāpā. Hei whakawhanake i te hemochromatosis, me whai hapa te tārua o te ira mai i tōna whaea me te tārua o te ira mai i tōna pāpā.
Whakaarohia kei te whiwhi koe i tētahi pukapuka mai i tō whaea, tētahi mai i tō pāpā. Kia puta ai tēnei mate, me whai hapa iti ngā pukapuka e rua i te whārangi e whakahaere ana i te rino. Mena kotahi anake te pukapuka kei a ia te hapa, he kaikawe noa koe i te mate. E kore koe e pāngia e te mate.
Nō reira, ahakoa he kawe tēnei ira hapa ngā mātua e rua, kāore pea he tohu e pā ki a rāua. Heoi, ki te whiwhi te tamaiti i whānau mai i a rāua i ngā tārua e rua o tēnei ira hapa, tera pea ka pāngia te tamaiti e te mate. Ko ngā momo hapa matua e rua e kitea ana i roto i te `(ira HFE)` ko `(C282Y)` me `(H63D)`.
Hei tāpiritanga, he momo onge kei te kīia ko te "Juvenile Hemochromatosis" e puta mai ana i te wā taitamariki, arā, i waenga i te 15-30 tau. Ka puta mai i ngā whakarerekētanga ira i roto i ētahi atu ira "(HJV, HAMP)".
2. Nā ētahi atu mate hauora (Hemochromatosis Tuarua)
I ētahi wā, ka puta te nui rawa o te rino i tētahi atu mate hauora, i tētahi atu maimoatanga rānei. Ehara tēnei i te mea tuku iho.
- Te whakawhiti toto auau: Ko te hunga whai mate toto (pērā i te anemia pērā i te thalassemia) me whakawhiti toto i te nuinga o te wā. Ina tukuna te toto pēnei mō te wā roa, ka taea e te rino i roto i taua toto te hanga i roto i te tinana, ka puta ai tēnei āhuatanga.
- Mate ate kino: Ko te ate te okana matua e whakahaere ana i te pākia o te rino i roto i te tinana. Mena kua tino pakaru te ate (hei tauira, te cirrhosis), tera pea kāore e taea e ia te whakahaere tika i te rino, ā, tera pea ka kohia i roto i te tinana.
- Te inu nui rawa i te waipiro: Ehara i te mea ka kino noa te ate i te waipiro, engari ka whakanui ake hoki i te mimiti o te rino e te tinana.
He aha ngā kino ka pā mai i te nui rawa o te rino ki te tinana?
E ai ki tā mātou i kōrero ai i mua ake nei, he rite te nui rawa o te rino ki te paitini ki te tinana. Ka āta hanga ake te rino i roto i ngā whekau, ā, ka tīmata te kino ki a rātou. Ka arahi pea tēnei ki ngā raruraru nui.
| Ngā whekau matua e pāngia ana | Ngā raruraru kino pea |
|---|---|
| Ate | Te ate nui, te ate momona, te cirrhosis (te whakaitiiti o te ate), me te nui ake o te mōrearea ki te mate pukupuku ate. |
| Ngākau | Te ngoikore o te ngakau, te arrhythmias. |
| Pancreas | Ka taea e te kino o te repe taiaki te arahi ki te ngoikore o te hanga insulin me te mate huka. Ka kiia hoki tēnei ko te "Momo Mate Huka Momo 3c". |
| Ngā hononga | Ngā mate rumatiki, te mamae me te pupuhi o ngā hononga. |
| Ētahi atu repe | Ka pāngia pea ngā repe whakaputa homoni, pērā i te repe pituitary me te repe thyroid, ka puta ai ngā koretake o te taurite o ngā homoni. |
Me pēhea e kitea ai tēnei e koe, e Tākuta?
Mena kei a koe tētahi o ngā tohu kua whakahuatia ake nei, kei tētahi rānei o tō whānau e pāngia ana e tēnei mate, me toro atu koe ki te tākuta. Ka pātai tuatahi te tākuta i ētahi pātai ki a koe, ā, ka tirotirohia koe.
- Pātai atu mēnā he nui rawa te rino i roto i ō mātua, i tētahi atu rānei o tō whānau, he mate ate rānei.
- Ka pātai atu rātou mēnā kei te tango koe i ngā pire rino, i ngā tāpiringa huaora C rānei (ka whakanui ake te huaora C i te mimiti o te rino).
- Ka pātai rātou mō te nui o te waipiro e inumia ana e koe.
I muri i tēnā, ka whakahaerehia he maha o ngā whakamātautau hei whakaū i te mate.
- Ngā whakamātautau toto: Koinei te whakamātautau tino taketake. Ka whakamātauria tō toto mō ngā taumata rino (Serum Iron), he pūmua e penapena ana i te rino (Serum Ferritin), me te nui o te pūmua kawe rino (Transferrin Saturation). Mena ka teitei ake ēnei taumata, tera pea ka whakapaehia he hemochromatosis.
- Whakamātautau ira: Ka taea te tango toto hei tirotiro i ngā hapa o te ira HFE. Ka āwhina tēnei ki te whakatau mēnā kei a koe te āhua tuku iho.
- Matawai MRI: Ka taea e tēnei te ine i te nui o te rino e whakatakotoria ana ki te ate me te ngākau, me te kore mamae.
- Kohikohi ate: I ētahi wā, hei whakatau i te whānuitanga tika o te kino o te ate, ka tangohia he wahi kiko iti mai i te ate mā te whakamahi i tētahi ngira iti, ā, ka tirohia i raro i te karu hiko.
He aha te rongoā? Ka taea te whakaora i tēnei?
Ae, kei reira ngā maimoatanga whai hua mō tēnei. Ko te whāinga matua o te maimoatanga he whakaiti i te nui o te rino i roto i te tinana, kia mau tonu ki te taumata noa, me te ārai i ngā kino atu ki ngā whekau.
Ko te mea nui , ko te tere o te tautuhi i tēnei mate, ka nui ake te angitu o te maimoatanga. Mēnā ka tīmata wawe te maimoatanga, ka taea te whakakore i ētahi o ngā kino ki ngā whekau.
He maha ngā tikanga maimoatanga matua.
| Tikanga maimoatanga | Ka ahatia? |
|---|---|
| Te Whakaora i te Phlebotomy | Koinei te maimoatanga matua, ā, ko te mea tino whai hua. He rite ki te tuku toto. Ka tangohia he toto iti (450-500 ml te nuinga) mai i tō tinana mā te whakamahi i te ngira. Ko te nuinga o te rino i roto i tō tātou tinana kei roto i ō tātou toto whero. Nō reira, ina tangohia te toto, ka tangohia hoki te rino me taua ngira. I te tuatahi, me mahi pea i te kotahi i te wiki. Kia mau tonu ō taumata rino, me mahi pea i ia torutoru marama. |
| Te Whakaora Chelation Rino | Kāore e taea e ētahi tāngata (hei tauira, te hunga he mate manawa, he mate toto iti rānei) te whakawhiti toto. Ka tukuna tēnei maimoatanga ki ēnei tāngata. Ko te tikanga o tēnei ko te hoatu i tētahi rongoā e herea ana ki te rino, ā, ka tangohia te rino mai i te tinana i roto i te mimi me te paru. Ka taea te tango i tēnei rongoā hei pire, hei werohanga rānei. |
| Te whakarerekē i ngā tikanga kai | Haunga te maimoatanga, me aroturuki anō hoki koe i tō kai.
|
Karere Tangohia ki te Kāinga
- Ko te hemochromatosis he mate e nui rawa ai te rino e kohia ana i roto i te tinana. He maha ngā wā ka tukuna iho tēnei mate.
- Kaua e warewarehia ngā tohu pēnei i te ngenge tonu, te mamae o ngā hononga, me te rerekētanga o te kiri, ina koa kua neke atu koe i te 40 tau.
- Ka taea e tēnei mate te whakararu nui i ngā whekau nui pērā i te ate, te ngākau, me te pancreas.
- Engari ki te kitea wawetia, ā, ka rongoatia tika, ka taea te whakahaere pai, ā, ka taea e koe te noho hauora, noa iho.
- Mena he ruarua āu mō tēnei, ki te pāngia rānei tētahi o tō whānau e tēnei mate, kia mōhio koe ki te kōrero ki tō tākuta.
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