Ka puta mai ētahi puku pēnei i tō tinana i ētahi wā? E ngenge ana rānei koe, kāore he take, e ahua ana rānei kei te heke tō taumaha? I te nuinga o te wā, he mea noa ēnei, engari i ētahi wā he tohu pea nō tētahi mate e hiahia ana kia arohia. I tēnei rā ka kōrero tātou mō tētahi momo lymphoma onge e kiia nei ko te `(Marginal Zone Lymphoma - MZL)` me mōhio tātou katoa. Kaua e manukanuka, ka kōrerohia tēnei e tātou i roto i tētahi huarahi māmā noa iho, ā, i roto i tētahi huarahi e mārama ai koe.
He aha te `(Marginal Zone Lymphoma - MZL)`? He māmā noa iho...
Ko te Lymphoma Rohe Tawhiti he ingoa noa mō ētahi momo lymphoma onge e puhoi ana te tipu, arā, kāore e tere te horapa, ā, nō roto i tētahi rōpū mate pukupuku e kiia nei ko te Lymphoma Non-Hodgkin. Ko te tikanga ka puta ēnei i roto i te kiko lymphoid, he wāhanga o te pūnaha ārai mate o tō tātou tinana. Kei roto i ēnei kiko tētahi momo toto mā e kiia nei ko ngā pūtau B. I mōhio koe he rite ngā pūtau B ki ngā kaitiaki o te tinana, he momo pūtau e āwhina ana ki te tiaki i a tātou mai i te mate? Ko te nuinga o te wā ka kitea i roto i ō tātou kōpū lymph (e kiia ana ko ngā kōpū lymph) me te whēkau.
Inaianei tirohia, kei roto i ō tātou pona lymph he wāhi iti e kiia nei ko `(lymphoid follicles)`. E rua ngā rohe o ēnei `(lymphoid follicles)` - ko tētahi e kiia ana ko `(mantle zone)`, ko tētahi ko `(marginal zone)`. Pērā i te tāpiri i tētahi atu paparanga ki tētahi keke, kei te taha o te `(mantle zone)` tēnei `(marginal zone)`. Ka puta te `(Marginal Zone Lymphoma)` ina whakarerekētia ngā `(B cells)` o taua `(marginal zone)`, arā, ka rerekē haere, ka noho hei pūtau rerekē, ā, ka tīmata te whakanui me te kore e taea te whakahaere.
Ko tēnei āhuatanga, ko te "Marginal Zone Lymphoma", ka kitea nuitia i roto i te hunga neke atu i te 60 tau te pakeke. He paku noa ake hoki te kitea i roto i ngā tāne i ngā wāhine.
He aha ngā momo matua o te `(Marginal Zone Lymphoma)`?
E toru ngā momo matua o te `(MZL)`. Kia tirohia tātou he aha ēnei:
1. Lymphoma kiko lymphoid āwhina-mucosa (MALT): Koinei te momo MALT tino noa. I ētahi wā ka kiia e ngā tākuta ko te lymphoma pūtau taha extranodal. Ko te tikanga o te "Extranodal" ka tīmata i waho o ngā kōpū lymph. Ka taea e tēnei momo lymphoma te tīmata i roto i te arai o te puku (gastric MALT), i roto rānei i ngā pukahukahu, te kiri, te tairoi, ngā repe huware, ngā whekau, ngā wāhi rānei e karapoti ana i ngā kanohi (non-gastric MALT).
2. Nodal marginal zone lymphoma: Ka pāngia ō kōpuku lymph e tēnei momo. Arā, ō kōpuku lymph. Engari i ētahi wā ka kitea anō hoki i roto i tō hinu wheua.
3. Splenic marginal zone lymphoma: He momo onge tēnei. Ka pā ki tō whēkau, toto, me te hinu wheua.
He aha ngā tohu o te `(Marginal Zone Lymphoma)`?
He mate puhoi te tipu o te Marginal Zone Lymphoma. Nō reira, tera pea ka roa te wā e pāngia ana koe e te mate, kāore he tohu. Ka rerekē ngā tohu i runga i te momo lymphoma. I te nuinga o te wā, ka puta pea ngā tohu pēnei i te Marginal Zone Lymphoma:
- Te kirika (te kirika e puta mai ana me te kore he take)
- Te werawera nui i te pō (nā te nui o te werawera ka mākū ngā whāriki moenga)
- Te whakaheke taumaha mō te kore take (mēnā ka whakaheke taumaha koe me te kore e ngana)
I ētahi wā ka kiia ēnei he "āhuatanga B".
Ngā tohu o te Lymphoma `(MALT)`
He rerekē ngā tohu o te `(Extranodal marginal zone lymphoma)` me te `(MALT)` lymphoma i runga i te wāhi kei reira te lymphoma. Hei tauira, ki te mea he `(MALT)` lymphoma kei roto i tō puku, ka pāngia pea koe e ēnei tohu:
- Whakapairuaki me te ruaki
- Te mamae o te puku , te koretake rānei
- Kei te kī tonu ahakoa he iti noa te kai i muri i te kai
Mena kei tētahi atu wāhi o te puku te lymphoma (non-gastric MALT), hei tauira i te kanohi, ka kitea pea ngā panoni i roto i te conjunctiva, i ngā repe waikura rānei.
Ngā tohu o te `(Nodal marginal zone lymphoma)`
I tēnei momo, ko te tohu matua ko te pupuhi o ngā ure. Hei tāpiri, ka puta pea ngā tohu noa kua whakahuatia i mua ake nei:
- Kirika
- Te werawera o te pō
- Te ngaronga taumaha mō te kore take
Ngā tohu o te `(Splenic marginal zone lymphoma)`
Ka taea e tēnei momo mate pukupuku whēkau te whakaputa i ngā tohu pēnei i:
- Te ngenge me te ngenge
- Te whēkau nui (tērā pea ka taumaha, ka kī rānei i te taha maui o runga o te puku)
- Te werawera o te pō
- Te ngaronga taumaha mō te kore take
He aha ngā take o te `(Marginal Zone Lymphoma)`?
Ko te tikanga, he hītori whānau tō te hunga whai Marginal Zone Lymphoma mō te lymphoma, he maha rānei ngā mate pāwera, he mate pūnaha ārai mate rānei. Heoi, he take motuhake mō ia momo.
- lymphoma MALT: Ko te nuinga o te wā ka puta mai tēnei i ngā mate kitakita, inā koa ko H. pylori. Kua rongo pea koe ko te gastritis ka puta mai anō hoki i ēnei kitakita. Hei tāpiri, ko ngā mate pūnaha ārai mate pēnei i te mate a Hashimoto (he mate e pā ana ki te repe tairoi) te mate a Sjögren rānei (he mate e whakamaroke ana i ngā repe huware me ngā repe roimata), me te hītori whānau o te lymphoma ka waiho hei take mōrearea.
- Lymphoma rohe taha splenic: E pā ana tēnei ki te mate huaketo hepatitis C me ngā mate pūnaha ārai mate.
- lymphoma nodal marginal zone: Kua kitea hoki he hononga tēnei ki te mate Hepatitis C.
He mea nui:Ehara i te mea ka pāngia te katoa e te `(MZL)` nā ēnei take. Waihoki, ka taea e ētahi tāngata te pāngia me te kore tetahi o ēnei take. He āhuatanga mōrearea noa iho ēnei.
He aha ngā āhuatanga mōrearea mō te `(Marginal Zone Lymphoma)`?
E ai ki te kōrero i mua ake nei, ko ngā āhuatanga mōrearea matua ko te hītori whānau o te lymphoma, ētahi mate (pērā i te H. pylori, te Hepatitis C), me ngā mate pūnaha ārai mate (te mate a Hashimoto, te mate a Sjögren).
Me pēhea te tātaritanga o te Lymphoma Rohe Tawhiti?
Ka pātai tuatahi tō tākuta ki a koe i ētahi pātai hei tātaritanga i tēnei mate. Kei roto i tēnei ko ngā tohumate kei a koe, tō hītori hauora, me te mea kua pāngia tētahi o tō whānau e ngā mate ōrite.
I muri i tēnā, me whakahaere he maha ngā whakamātautau hei whakaū i te mate.
He aha ngā whakamātautau tātaritanga?
Tērā pea ka rerekē ngā whakamātautau e mahia ana i runga i te momo lymphoma, engari i te nuinga o te wā, ka taea te mahi i ēnei whakamātautau e whai ake nei:
- Tatau Toto Katoa (CBC): Ka tirohia te maha o ngā momo pūtau rerekē (ngā pūtau whero, ngā pūtau ma, ngā pereti toto) i roto i te toto.
- Whakamātautau `(LDH - Lactate Dehydrogenase)`: He whākōkī tēnei e piki ake ana i roto i te toto ina pakaru ngā pūtau.
- `(Beta-2 microglobulin)`: Ka whakamahia tēnei hei tohu mō ngā matepukupuku toto.
- Ngā whakamātautau mahi ate .
- Ngā whakamātautau mahi a te whatukuhu (whatukuhu) .
- Te whakapūmautanga ārai mate pūmua toto (IFX): He whakamātautau hei rapu i ngā huringa o ngā pūmua i roto i te toto.
- Ngā whakamātautau mō ētahi mate kitakita me te mate huaketo (hei tauira, `(H. pylori)`, `(Hepatitis C)`).
- `(Matawai CT)`: Tangohia ngā whakaahua taipitopito o roto o te tinana. Tirohia ngā mea pēnei i te pupuhi o ngā kōpū lymph me te whēkau kua nui haere.
- Kohikohi ngira: Ka tangohia he tauira iti o te kiko mai i te kōpū lymph pupuhi, i tētahi atu wāhi rānei ki te ngira, ā, ka tirohia i raro i te karuārai. Koinei anake te huarahi hei mōhio mēnā kei reira ngā pūtau lymphoma.
- Te koiora wheua: Ka mahia tēnei whakamātautau i ētahi wā hei tirotiro mēnā kua horapa te lymphoma ki te wheua.
- Ētahi atu whakamātautau '(Biopsy)': Te tango tauira o ngā pūtau, o ngā kiko rānei mai i tētahi wāhi o te tinana e whakaarohia ana kua pāngia, ka whakamātautau i taua tauira.
He aha ngā wāhanga o te mate pukupuku i roto i te `(MZL)`?
Ko te whakatau i te horapa o te mate pukupuku he huarahi hei whakatau i te horapa o te mate pukupuku i roto i te tinana. He mea nui tēnei mō te whakamahere maimoatanga me te whai whakaaro mō te ahunga whakamua o te mate. Ko ngā wāhanga o te MZL e whai ake nei:
- Wāhanga I: Kei te rohe kotahi anake o te kōpū lymph te mate pukupuku.
- Wāhanga II:Kei roto i ngā rohe o ngā kōpuku lymph e rua, neke atu rānei, te mate pukupuku i te taha kotahi, i runga ake rānei, i raro rānei i te diaphragm (te uaua e wehe ana i te uma me te puku).
- Wāhanga III: Kua horapa te mate pukupuku ki ngā rohe o ngā kōpū lymph i runga ake me raro iho i te diaphragm, arā, he kōpū lymph kei ngā taha e rua.
- Wāhanga IV: Kua horapa te mate pukupuku ki waho o te pūnaha lymphatic ki tētahi, ki ētahi atu rānei okana, pērā i te ate, ngā pukahukahu, te hinu wheua rānei.
He aha ngā maimoatanga mō te `(Marginal Zone Lymphoma)`?
Nā te mea he mate puhoi te tipu o te Marginal Zone Lymphoma, kāore pea ētahi tāngata e hiahia ki te tīmata tonu i te maimoatanga. I ētahi wā ka tūtohu ngā tākuta i tētahi huarahi maimoatanga e kiia nei ko te "watchful waiting" me te "active surveillance" rānei. Ko te tikanga o tēnei me aroturukitia tonutia koe kia puta rā anō ngā tohu, kia kino rawa atu rānei te mate.
Mena e hiahiatia ana he maimoatanga, ka rerekē te maimoatanga e hoatu ana i runga i te momo lymphoma. Ko ngā maimoatanga noa ko:
- Ngā rongoā paturopi: Ina koa mēnā ko te huakita H. pylori te pūtake o te lymphoma, ka hoatu ngā rongoā paturopi hei patu i ngā huakita. I roto i te nuinga o ngā wā, ka taea e tēnei te whakaora i te lymphoma.
- Te rongoā matepukupuku: Ngā rongoā e hoatu ana hei patu i ngā pūtau matepukupuku.
- Whakaora irahiko: Te whakamahinga o ngā hihi kaha-nui hei whakangaro i ngā pūtau matepukupuku. Ka whakamahia tēnei i te nuinga o te wā ina kitea te lymphoma i te rohe.
- Whakaora arotahi: He momo rongoā hou ēnei e mahi ana mā te arotahi ki ngā ngota motuhake i roto i ngā pūtau matepukupuku.
- Ārai Mate: Ka whakaoho i te pūnaha ārai mate o te tinana kia whawhai ki ngā pūtau matepukupuku.
Ka taea te whakaora katoa i te `(Marginal Zone Lymphoma)`?
Ko tēnei e whakawhirinaki ana ki te momo lymphoma, te wāhanga, me tō hauora whānui. Hei tauira, ko te lymphoma puku (MALT) i puta mai i te mate H. pylori he nui te tūponotanga ka ora katoa mā te rongoā paturopi.
I ētahi atu momo, ka taea e te maimoatanga te whakamutu i te mate. Ko te tikanga o te "whakamutu" kua ngaro ngā tohu, ā, kāore he tohu o te mate i roto i ngā whakamātautau. Heoi, ka taea e te "Marginal Zone Lymphoma" te hoki mai anō i ētahi wā ('hoki mai anō') i muri i te maimoatanga. Nō reira, ka haere tonu te aro turuki a ngā tākuta i a koe.
He aha te ōrau oranga mō te `(Marginal Zone Lymphoma)`?
He tatauranga noa iho ngā reiti ora. E whakaatu ana i te ōrau o te hunga e ora ana i ngā tau e rima i muri i te tātaritanga. Engari ka rerekē pea i ia tangata, i ia tangata. Tērā pea ka rerekē ō wheako.
E ai ki tētahi rangahau:
- Tata ki te 88% o te hunga e pāngia ana e te lymphoma rohe taha tawhiti o waho o te nonodal (MALT) e ora tonu ana i muri i te rima tau o te tautuhi mate.
- Tata ki te 79% o te hunga e pāngia ana e te lymphoma rohe taha o te splenic e ora tonu ana i roto i ngā tau e rima i muri i te tautuhi.
- Tata ki te 76.5% o te hunga e pāngia ana e te nodal marginal zone lymphoma e ora tonu ana i muri i te rima tau i te tautuhia.
Kia maumahara: He toharite noa iho ēnei. Nā te mea ka puta te Marginal Zone Lymphoma i roto i ngā kaumātua, he tokomaha o ēnei tāngata ka mate i ngā take ehara i te lymphoma. Ko tō tākuta anake ka taea te hoatu ki a koe ngā mōhiohio pai rawa atu mō tō āhuatanga. Nō reira, kaua e mataku ki ēnei tatauranga anake.
Ka taea te ārai i te mate Lymphoma Rohe Tawhiti?
Kāore e taea e tātou te whakahaere i ētahi o ngā āhuatanga e whai wāhi ana ki te whanaketanga o tēnei mate, pērā i ngā mate pūnaha ārai mate, ngā awe ira rānei. Heoi, ki te mea he mate pāwera ki te `(H. pylori)`, ka taea te whakaiti i tōna pānga mā te tango i te maimoatanga tika me te mahi i ngā mahi hei tiaki i a koe mai i ngā mate pāwera pērā i te `(Hepatitis C)`.
Āhea ahau me toro atu ki taku tākuta?
Mena kua tāpaetia koe kei te mate koe i te "Marginal Zone Lymphoma", me toro atu koe ki tō tākuta mēnā:
- Ki te kite koe i ngā panonitanga o tō tinana e whakaaro ana koe he tohu pea nō te Marginal Zone Lymphoma (hei tauira, ka puta he puku hou, ka nui haere tetahi puku o mua, ka kirika, ka werawera i te pō, ka heke te taumaha).
- Mena ka kino haere ō tohumate i a koe e whiwhi ana i te maimoatanga .
- Mena kei te heke tō hauora, ā, ka tīmata te kite i ngā tohu e hoki mai ana te mate, tera pea kua hoki mai anō .
Me pēhea taku tiaki i tōku hauora?
I te wā e noho tahi ana koe me te mate pēnei i te MZL, he mea tino nui te tiaki i a koe anō. Anei ētahi mea ka taea e koe te mahi:
- Whakahaerehia te ahotea: Ko ētahi tāngata whai MZL kāore pea he tohu, ā, kāore pea e hiahiatia he maimoatanga. Ahakoa he mea pai tēnā, tera pea kei te āwangawanga tonu koe mō "āhea ka kino haere?" Mā te whakakori tinana, te whakarongo waiata, te mahi yoga, te whai wāhi atu rānei ki tētahi mahi whakangahau e pai ana ki a koe ka āwhina i a koe ki te whakangā.
- Inumia he wai nui: Ka taea e ngā maimoatanga mate pukupuku me ōna pānga taha te whakamaroke i te tinana, no reira ngana ki te inu i te iti rawa i te 8 karāhe wai i te rā.
- Kai i tētahi kai taurite: Whakaurua ngā kai whai kiko pēnei i ngā hua rākau, ngā huawhenua, ngā nati, me ngā hua miraka ki roto i tō kai. Kai i ngā kai iti, kaua i ngā kai nui.
He aha ngā pātai me pātai atu e au ki taku tākuta?
Ka taea e koe te pātai atu ki te tākuta i ngā pātai penei:
- He aha te momo "Marginal Zone Lymphoma" kei a au?
- He aha te wāhanga o tōku mate?
- Me whiwhi maimoatanga tonu ahau?
- Mena e hiahiatia ana he maimoatanga, he aha te maimoatanga ka tūtohu koe, ā, he aha ai?
- He aha ngā pānga taha o ēnei maimoatanga?
- He whakamātautau haumanu kei reira ka taea e au te whakauru atu?
- He aha tāu e taea te kōrero mai mō te āhua o taku mate?
Hei whakamutunga, ngā mea hei maumahara (Karere hei tango ki te kāinga)
Ko te Marginal Zone Lymphoma (MZL) he momo lymphoma onge, he puhoi te tipu, e taka ana ki te kāwai o te Non-Hodgkin Lymphoma. He maha ngā momo lymphoma, ā, he rerekē ngā tohu, te maimoatanga, me te matapae i runga i te momo. Ko te mea nui, nā te mea he puhoi te whanaketanga o te mate, kāore pea ētahi tāngata e hiahia ki te maimoatanga mō ngā tau. Mō ētahi atu, ka taea e te maimoatanga te whakaora i te mate.
Ki te pāngia koe e tēnei mate, he pai ake kia kaua e mataku, engari me kōrero ki tō tākuta, kia whiwhi ai i ngā kōrero e tika ana mō tō āhuatanga. Mā tō tākuta koe e whakamārama ki te pānga o tēnei mate ki tō tinana me ngā kōwhiringa maimoatanga e wātea ana. Kia maumahara, ehara i te mea ko koe anake, ā, kei reira ngā tākuta me ō whanaunga hei āwhina i a koe.
` Lymphoma Rohe Tawhiti, MZL, Lymphoma Non-Hodgkin, Lymphoma, Matepukupuku, Lymphoma MALT, pūtau B, H. pylori, Chemotherapy, Ngā Pona Lymph











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